| Entry |
|
| Name |
IDUA
|
| Definition |
|
| Pathway |
| Glycosaminoglycan degradation | | Lysosome |
|
| Module |
| Dermatan sulfate degradation | | Heparan sulfate degradation |
|
| Disease |
| Mucopolysaccharidosis type I (MPS1) |
|
| Brite |
KEGG Orthology (KO) [BR:ko00001]
Metabolism
Glycan biosynthesis and metabolism
00531 Glycosaminoglycan degradation
K01217 IDUA; L-iduronidase
Cellular Processes
Transport and catabolism
04142 Lysosome
K01217 IDUA; L-iduronidase
KEGG pathway modules [BR:ko00002]
Pathway module
Carbohydrate and lipid metabolism
Glycosaminoglycan metabolism
M00076 Dermatan sulfate degradation
K01217 IDUA; L-iduronidase
M00078 Heparan sulfate degradation
K01217 IDUA; L-iduronidase
Enzymes [BR:ko01000]
3. Hydrolases
3.2 Glycosylases
3.2.1 Glycosidases, i.e. enzymes that hydrolyse O- and S-glycosyl compounds
3.2.1.76 L-iduronidase
K01217 IDUA; L-iduronidase
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| Other DBs |
|
| Genes |
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