ORTHOLOGY: K02261
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Entry
K02261 KO
Symbol
COX2
Name
cytochrome c oxidase subunit 2
Pathway
map00190
Oxidative phosphorylation
map01100
Metabolic pathways
map04260
Cardiac muscle contraction
map04714
Thermogenesis
map04932
Non-alcoholic fatty liver disease
map05010
Alzheimer disease
map05012
Parkinson disease
map05014
Amyotrophic lateral sclerosis
map05016
Huntington disease
map05020
Prion disease
map05022
Pathways of neurodegeneration - multiple diseases
map05208
Chemical carcinogenesis - reactive oxygen species
map05415
Diabetic cardiomyopathy
Module
M00154
Cytochrome c oxidase
Disease
H01368
Cytochrome c oxidase (COX) deficiency
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09102 Energy metabolism
00190 Oxidative phosphorylation
K02261 COX2; cytochrome c oxidase subunit 2
09150 Organismal Systems
09153 Circulatory system
04260 Cardiac muscle contraction
K02261 COX2; cytochrome c oxidase subunit 2
09159 Environmental adaptation
04714 Thermogenesis
K02261 COX2; cytochrome c oxidase subunit 2
09160 Human Diseases
09161 Cancer: overview
05208 Chemical carcinogenesis - reactive oxygen species
K02261 COX2; cytochrome c oxidase subunit 2
09164 Neurodegenerative disease
05010 Alzheimer disease
K02261 COX2; cytochrome c oxidase subunit 2
05012 Parkinson disease
K02261 COX2; cytochrome c oxidase subunit 2
05014 Amyotrophic lateral sclerosis
K02261 COX2; cytochrome c oxidase subunit 2
05016 Huntington disease
K02261 COX2; cytochrome c oxidase subunit 2
05020 Prion disease
K02261 COX2; cytochrome c oxidase subunit 2
05022 Pathways of neurodegeneration - multiple diseases
K02261 COX2; cytochrome c oxidase subunit 2
09166 Cardiovascular disease
05415 Diabetic cardiomyopathy
K02261 COX2; cytochrome c oxidase subunit 2
09167 Endocrine and metabolic disease
04932 Non-alcoholic fatty liver disease
K02261 COX2; cytochrome c oxidase subunit 2
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis
K02261 COX2; cytochrome c oxidase subunit 2
Mitochondrial biogenesis [BR:
ko03029
]
Mitochondrial DNA transcription, translation, and replication factors
Mitochondrial DNA-encoded proteins
Cytochrome c oxidase
K02261 COX2; cytochrome c oxidase subunit 2
BRITE hierarchy
Other DBs
COG:
COG1622
TC:
3.D.4.11
3.D.4.7
3.D.4.8
Genes
HSA:
4513
(COX2)
PTR:
807864
(COX2)
PPS:
807874
(COX2)
GGO:
6742682
(COX2)
PON:
808475
(COX2)
NLE:
16545238
(COX2)
MCC:
2846628
(COX2)
MCF:
7857740
(COX2)
CSAB:
4097491
(COX2)
CATY:
26408635
(COX2)
PANU:
14444632
(COX2)
TGE:
14216784
(COX2)
RRO:
4171537
(COX2)
RBB:
10549370
(COX2)
TFN:
18985075
(COX2)
CJC:
22203903
(COX2)
SBQ:
13228914
(COX2)
CSYR:
7944469
(COX2)
MMUR:
26823976
(COX2)
LCAT:
68929184
(COX2)
PCOQ:
6458115
(COX2)
MMU:
17709
(COX2)
MCAL:
20832245
(COX2)
MPAH:
36165343
(COX2)
RNO:
26198
(COX2)
MCOC:
34683002
(COX2)
MUN:
18129807
(COX2)
CGE:
3979186
(COX2)
MAUA:
8457926
(COX2)
PROB:
30213873
(BOP69_gp10)
PLEU:
36275554
(COX2)
NGI:
15088426
(COX2)
HGL:
10201212
(COX2)
CPOC:
808635
(COX2)
CCAN:
31082906
(COX2)
DSP:
122102258
PLOP:
125345647
OCU:
808233
(COX2)
OPI:
2717276
(COX2)
GVR:
804969
(COX2)
CFA:
804479
(COX2)
VVP:
4355754
(COX2)
VLG:
23629749
(COX2)
NPO:
8690243
(COX2)
AML:
5179728
(COX2)
UMR:
804870
(COX2)
UAR:
804844
(COX2)
LLV:
71922415
(COX2)
MNP:
20466141
(COX2)
NVS:
14841842
(COX2)
EJU:
805022
(COX2)
ZCA:
4355791
(COX2)
MLX:
4355867
(COX2)
LWW:
4355829
(COX2)
FCA:
807936
(COX2)
PYU:
26129874
(COX2)
PCOO:
11473381
(COX2)
PBG:
26129494
(COX2)
PVIV:
26129646
(COX2)
PPAD:
6262377
(COX2)
PUC:
6262410
(COX2)
AJU:
2654015
(COX2)
HHV:
14842158
(COX2)
BTA:
3283880
(COX2)
BOM:
22161769
(COX2)
BIU:
2885980
(COX2)
BBUB:
56055856
(COX2)
CHX:
1485859
(COX2)
OAS:
808252
(COX2)
BTAX:
8250963
(COX2)
ODA:
11452041
(COX2)
CCAD:
59433139
(COX2)
MBEZ:
7872545
(COX2)
SSC:
808504
(COX2)
CFR:
5326224
(COX2)
CBAI:
5309940
(COX2)
CDK:
5618959
(COX2)
VPC:
809428
(COX2)
BMUS:
807732
(COX2)
LVE:
3802095
(COX2)
OOR:
72909420
(COX2)
DLE:
31412987
(COX2)
PCAD:
809416
(COX2)
ECB:
807845
(COX2)
EPZ:
19019450
(COX2)
EAI:
808064
(COX2)
MYB:
20964695
(COX2)
MYD:
22203917
(COX2)
MMYO:
26889527
(COX2)
MLF:
27214819
(COX2)
DRO:
17046633
(COX2)
AJM:
808333
(COX2)
HAI:
13539868
(COX2)
PALE:
17963494
(COX2)
RAY:
3666154
(COX2)
MJV:
24019672
(COX2)
TOD:
38289020
(D9W85_mgp10)
LAV:
808790
(COX2)
ETF:
802328
(COX2)
DNM:
808136
(COX2)
MDO:
3074663
(COX2)
GAS:
63652837
(COX2)
SHR:
13826435
(COX2)
AFZ:
65342081
(COX2)
PCW:
4108297
(COX2)
OAA:
808709
(COX2)
GGA:
39116936
(COX2)
PCOC:
10609898
(COX2)
MGP:
5848004
(COX2)
CJO:
804666
(COX2)
LMUT:
31079467
(COX2)
NMEL:
32282791
(COX2)
APLA:
5405812
(COX2)
CATA:
7996700
(COX2)
AFUL:
19909398
(COX2)
TGU:
3950793
(COX2)
SCAN:
37275782
(COX2)
PMOA:
20355699
(COX2)
OTC:
22548461
(COX2)
PRUF:
17674378
(COX2)
FAB:
16027875
(COX2)
PHI:
9480995
(COX2)
PMAJ:
39089585
(COX2)
CCW:
71712383
(COX2)
MMEA:
20357135
(COX2)
FPG:
808592
(COX2)
FCH:
23808612
(COX2)
CLV:
8889998
(COX2)
EGZ:
18985250
(COX2)
NNI:
4108695
(COX2)
PADL:
26737700
(COX2)
AGEN:
7256434
(COX2)
GSTE:
3416063
(COX2)
RTD:
84348656
(COX2)
AROW:
62676598
(COX2)
NPD:
62676487
(COX2)
DNE:
803265
(COX2)
ASN:
806139
(COX2)
AMJ:
808245
(COX2)
CPOO:
4108087
(COX2)
GGN:
4178385
(COX2)
PSS:
2943122
(COX2)
CMY:
808646
(COX2)
CCAY:
11747786
(COX2)
CPIC:
18982997
(COX2)
CABI:
60253689
(COX2)
ACS:
6385975
(COX2)
PVT:
3338350
(CO2)
PBI:
YP_008083602
PMUR:
107301994
15822633
(COX2)
APRI:
131187388
PMUA:
7056463
(COX2)
ZVI:
118075331
24146102
(YC27_gp10)
GJA:
26044429
(COX2)
STOW:
125434155
EMC:
30861819
(COX2)
XLA:
2642081
(COX2)
XTR:
3283495
(COX2)
NPR:
24020214
(COX2)
BGAR:
4356057
(COX2)
MUO:
18490096
(COX2)
GSH:
14469872
(COX2)
DRE:
140540
(COX2)
SRX:
24419178
(COX2)
SANH:
24419954
(COX2)
SGH:
8382165
(COX2)
CCAR:
807772
(COX2)
CGIB:
9222067
(COX2)
PTET:
5787378
(COX2)
LROH:
12079593
(COX2)
OMC:
18668120
(COX2)
PPRM:
26048344
(COX2)
RKG:
130077635
130077636
130077639
130077641
MAMB:
5912295
(COX2)
CIDE:
5857710
(COX2)
MASI:
3131136
(COX2)
TROS:
14048438
(COX2)
TDW:
36952192
(COX2)
MANU:
6879712
(COX2)
IPU:
804875
(COX2)
IFU:
26118487
(COX2)
PHYP:
16216570
(COX2)
SMEO:
10079900
(COX2)
TVC:
10079789
(COX2)
CHAR:
5228440
(COX2)
TRU:
805219
(COX2)
TFS:
19524534
(COX2)
TNG:
BAE79220
(COII)
LCO:
7095384
(COX2)
NCC:
10752025
(COX2)
PGEO:
67284259
(COX2)
EMAC:
30862040
(COX2)
ELY:
7095519
(COX2)
EFO:
14412330
(COX2)
PLEP:
4363285
(COX2)
SLUC:
23629805
(COX2)
ESP:
40141436
(COX2)
PFLV:
14048219
(COX2)
PPUG:
119199130
7042820
(COX2)
AFB:
13230431
(COX2)
PSWI:
72130141
(COX2)
MSAM:
4100028
(COX2)
SCHU:
10965113
(COX2)
CUD:
8774886
(COX2)
MZE:
26037644
(APK84_gp10)
ONL:
8677314
(COX2)
OAU:
8745942
(COX2)
OLA:
805431
(COX2)
OML:
13540110
(COX2)
CSAI:
804092
(COX2)
XMA:
6986206
(COX2)
XCO:
26048192
(COX2)
XHE:
8302509
(COX2)
PRET:
19590712
(COX2)
GAF:
805448
(COX2)
CVG:
26048382
(COX2)
CTUL:
26129152
(COX2)
NFU:
7256399
(COX2)
KMR:
804466
(COX2)
AOCE:
4850669
(COX2)
CSEM:
7996482
(COX2)
POV:
808848
(COX2)
SSEN:
4266842
(COX2)
HHIP:
5405727
(COX2)
HSP:
5405783
(COX2)
SMAU:
8382075
(COX2)
LCF:
3703590
(COX2)
SDU:
11669689
(COX2)
XGL:
7871597
(COX2)
HCQ:
14658013
(COX2)
SSCV:
125966266
125966267
SBIA:
35996588
(COX2)
PTAO:
74193753
(COX2)
BPEC:
YP_004935134.1
MALB:
803940
(COX2)
BSPL:
23631935
(COX2)
SJO:
8703816
(COX2)
SASA:
808315
(COX2)
STRU:
19099178
(COX2)
OTW:
KEF73_p10
(COX2)
OMY:
807980
(COX2)
OGO:
6383209
(COX2)
ONE:
4555710
(COX2)
OKI:
4955090
(COX2)
OKE:
12486862
(COX2)
SALP:
808546
(COX2)
SNH:
35115221
(COX2)
CCLU:
14842634
(COX2)
ELS:
806650
(COX2)
SFM:
3416107
(COX2)
AANG:
3190268
(COX2)
LOC:
807196
(COX2)
PSPA:
805412
(COX2)
ARUT:
17097821
(COX2)
LCM:
808086
(COX2)
CMK:
9385347
(COX2)
RTP:
18267179
(COX2)
CPLA:
7768745
(COX2)
LERI:
11452181
(COX2)
PMRN:
807803
(COX2)
LRJ:
9385084
(COX2)
BFO:
808727
(COX2)
BBEL:
806244
(COX2)
SCLV:
36165621
(COX2)
SPU:
2652720
(COX2)
APLC:
3907676
(COX2)
SKO:
3703602
(COX2)
DME:
Dmel_CG34069
(COX2)
DSE:
116800960
2760949
(COX2)
DSI:
COX2
DYA:
COX2
DAN:
116655089
26514691
DMN:
117194305
117194311
DGR:
116806152
CCAT:
808517
(COX2)
BOD:
2717267
(COX2)
BDR:
4657574
(COX2)
AOQ:
79023077
(COX2)
TDA:
119664760
MDE:
20358596
(COX2)
LSQ:
5469264
(COX2)
ECOE:
35199149
(COX2)
HIS:
33350929
(COX2)
ACOZ:
26121321
(COX2)
AARA:
26121207
(COX2)
AMER:
26121511
(COX2)
AFUN:
76054171
(COX2)
AMOU:
73620845
(COX2)
AALI:
118463013
AAG:
33307558
(COX2)
AALB:
3260126
(COX2)
CQU:
COX2
BCOO:
119084558
ACER:
9385639
(COX2)
ALAB:
34829161
(COX2)
AFLR:
15822484
(COX2)
BAFF:
126926943
BPAS:
132915722
OBB:
114881506
114882498
OLG:
117611528
SOC:
9977790
(COX2)
VEM:
27912175
(COX2)
LHU:
42265443
(COX2)
TPRE:
111693314
LHT:
122510120
CGLO:
123274420
123274744
AGIF:
63649819
(COX2)
CCIN:
107274034
7872292
(COX2)
DSM:
124415517
NPT:
124224121
124224122
124224123
NFB:
124187554
124187555
124187563
NVG:
124306994
TCA:
803826
(COX2)
SOY:
28481402
(COX2)
ATD:
34926357
(COX2)
CSET:
123314001
AGB:
108912903
4171598
(COX2)
APLN:
28479672
(COX2)
OTU:
111422026
111425647
BMOR:
119631134
809267
(COX2)
BMAN:
804645
(COX2)
MSEX:
5848748
(COX2)
DPL:
AGL76300
(COX2)
BANY:
128199777
128199780
PMAC:
13080342
(COX2)
PPOT:
20159555
(COX2)
PXU:
26836885
(COX2)
PRAP:
11030479
(COX2)
PBX:
123718330
PNAP:
125062967
125062968
60241344
(COX2)
LSIN:
126973514
HAW:
9977713
(COX2)
HZE:
124645585
71203127
(COX2)
TNL:
44149127
(COX2)
SLIU:
17427395
(COX2)
PXY:
20834447
(COX2)
PGW:
73956679
(COX2)
API:
7055876
(COX2)
DNX:
17428410
(COX2)
AGS:
19909101
(COX2)
BTAB:
3077222
(COX2)
DCI:
108252528
27914404
(COX2)
CLEC:
27787574
(COX2)
HHAL:
8457883
(COX2)
NLU:
16216527
(COX2)
HVI:
3332284
(COX2)
MQU:
32891620
(COX2)
FOC:
YP_006576372
TPAL:
38092109
(COX2)
ZNE:
110840503
20004829
(COX2)
SGRE:
73491794
(COX2)
DPX:
AAD33232
(COII)
DMK:
24147206
(COX2)
PVM:
5333214
(COX2)
PJA:
3416043
(COX2)
PCHN:
5333403
(COX2)
PMOO:
808978
(COX2)
HAME:
10743673
(COX2)
PCLA:
11763611
(COX2)
CQD:
17728511
(COX2)
PTRU:
1482825
(COX2)
ESN:
3355548
(COX2)
HAZT:
38169114
(COX2)
EAF:
54124856
(COX2)
TCF:
4788291
(COX2)
DSV:
23630418
(COX2)
RSAN:
808373
(COX2)
RMP:
18250936
(COX2)
VDE:
806166
(COX2)
TUT:
6164216
(COX2)
DPTE:
7564645
(COX2)
CSCU:
111621898
LPOL:
106457924
106462804
803786
(COX2)
CEL:
KEF34_p03
(COX2)
CBR:
COX2
NAI:
804828
(COX2)
BMY:
KEF88_p03
(COX2)
LOA:
COX2
TSP:
COX2
PCAN:
19909179
(COX2)
BGT:
106050650
2746317
(COX2)
HRF:
35985148
(COX2)
HRJ:
2846695
(COX2)
CRG:
808828
(COX2)
CANU:
7865909
(COX2)
MMER:
55289785
(COX2)
OBI:
27205958
(COX2)
OSN:
62676620
(COX2)
LAK:
C2G87_mgp13
(COX2)
SMM:
COX2
SHX:
4097442
(COX2)
EGL:
41697839
(cox2)
ATEN:
41854791
(COX2)
ADF:
17674594
(COX2)
PDAM:
5580397
(COX2)
SPIS:
6798782
(COX2)
DGT:
8656279
(COX2)
XEN:
124455310
124455318
HMG:
6904233
(COX2)
TAD:
TradoM_p11
(COX2)
AQU:
4794355
(COX2)
ATH:
DA397_mgp01
(cox2)
CRB:
40490686
(cox2)
EUS:
EUTSA_v10023011mg
BRP:
56141033
(cox2-1)
BNA:
4237883
(cox2-1)
4237884
(cox2-2)
RSZ:
13630169
(cox2)
CPAP:
110820367
7441425
(cox2)
CIT:
36487036
(cox2)
GRA:
27429599
(cox2)
GHI:
24679512
(cox2)
GAB:
33134367
(cox2)
HSYR:
120126119
120183016
EGR:
38466595
(cox2)
GMX:
100782702
(COX2)
15308623
(cox2)
GSJ:
114367624
38334506
(cox2)
PVU:
PHAVU_009G252600g
VRA:
106760164
VAR:
108322296
VUN:
114163077
VUM:
124836963
CCAJ:
109814968
TPRA:
55290705
(cox2)
CAM:
101496649
PSAT:
127107515
VVO:
131637796
LJA:
Lj0g3v0062549.1
(Lj0g3v0062549.1)
Lj0g3v0175899.1
(Lj0g3v0175899.1)
Ljmtg3v0000870.1
(Ljmitog3v0000870.1)
ADU:
107472421
107492039
127746502
AIP:
107619623
AHF:
112742270
112770905
114926177
114926187
114927242
114927342
PCIN:
129294843
129294848
129294890
129295608
MDM:
13630207
(cox2)
MSYL:
126634178
73938921
(cox2)
PXB:
103935049
ZJU:
27215258
(cox2)
MNT:
39338986
(cox2)
CSAV:
27215472
(cox2)
CSV:
11123901
(cox2)
CMO:
107990889
127147454
127148059
127150340
BHJ:
120079271
MCHA:
111018435
CPEP:
111810906
RCU:
10221420
(cox2)
JCU:
119369480
HBR:
110639978
MESC:
42317494
(cox2)
PEU:
105138839
PALZ:
39331206
(cox2)
VVI:
132254509
7498556
(cox2)
SLY:
101264997
SPEN:
107030119
34926004
(cox2)
SOT:
107063149
SSTN:
125873763
CANN:
107855101
124898705
19989172
(cox2)
NTA:
3205306
(cox2)
NSY:
104227400
27214855
(cox2)
NTO:
104091428
NAU:
109208361
109241468
35198919
(cox2)
INI:
29082029
(cox2)
ITR:
116007904
SIND:
105179430
EGT:
105971535
SSPL:
121789916
SMIL:
18126272
(cox2)
HAN:
110942618
LSV:
40498720
(cox2)
DCR:
108214800
12598549
(cox2)
CSIN:
114304736
40867536
(cox2)
BVG:
809487
(cox2)
809574
(orf317)
SOE:
130460645
33876581
(cox2)
CQI:
39331948
(cox2)
ATRI:
130827079
NNU:
28482653
(cox2)
MING:
122081641
TSS:
122647080
122647081
OSA:
6450161
(cox2)
DOSA:
Os04t0343050-00
(Os04g0343050)
OGL:
127757119
127762850
127762851
TDC:
119281849
119283495
119299775
119302095
119315160
119320154
119325920
119328180
119332451
119361882
119363924
TAES:
123052508
123055615
123060679
123071716
123074751
123102879
123121942
123130606
123137017
123137270
34688777
(cox2)
TUA:
125528888
125535802
125537455
125546035
125552321
LPER:
127321049
LRD:
124687851
SBI:
4306043
(cox2)
SITA:
111256055
SVS:
117863734
117865664
PVIR:
120693817
120693836
PDA:
11542569
(cox2)
MUS:
103974065
MSIN:
131258351
NCOL:
36487337
(cox2)
ATR:
110006799
PPP:
3989052
(cox2)
CRE:
CHLRE_01g049500v5
VCN:
VOLCADRAFT_80299
(cox2B)
CSL:
CospCoM_p09
(cox2)
CVR:
OJ20_p06
(cox2)
APRO:
ChprMp035
(cox2)
OTA:
OstapMp32
(Cox2)
BPG:
BathyMg00040
(cox2)
MIS:
MicpuN_mit21
(cox2)
GSL:
JL72_p04
(cox2)
CCP:
ChcroMp04
(cox2)
SCE:
Q0250
(COX2)
SPAO:
A560_p01
(cox2)
AGO:
AGOS_AMI001W
KLA:
KllafMp06
(COX2)
KMX:
CRD48_mgp11
(COX2)
VPO:
VapofMp05
(cox2)
CGR:
CaglfMp11
(cox2)
DHA:
cox2
CAL:
CaalfMp01
(COX2)
YLI:
YalifMp18
(cox2)
CLUS:
16792604
(cox2)
NCR:
NCU16028
SMP:
SMAC_12689
(cox2)
PAN:
PoanfMp43
(cox2)
CTHR:
CTHT_m000310
SSCK:
SPSK_11049
FGR:
GizefMp06
(cox2)
PTKZ:
MRV25_mgp12
(cox2)
VAL:
VDBG_17011
CLUP:
AYB75_mgp09
(cox2)
SSL:
SS1G_20045
ANI:
ANID_20019
ANG:
Asnifp13
(cox2)
ALUC:
EJ508_mgp05
(cox2)
TML:
GSTUM_00001112001
SPO:
ScpofMp10
(cox2)
SOM:
PWB26_mgp08
(cox2)
MRT:
D9L16_mgp11
(cox2)
PSTR:
EFH26_mgp05
(cox2)
PFA:
PF3D7_1430900
PFD:
PFDG_00559
PFH:
PFHG_00500
PREI:
PRSY57_1430200
PGAB:
PGSY75_1430900
PYO:
PY17X_1015300
PCB:
PCHAS_1014600
PBE:
PBANKA_1013800
PVV:
PVVCY_1001860
PKN:
PKNH_1327800
PVX:
PVX_084995
PCY:
PCYB_132780
PMAL:
PMUG01_13029200
PREL:
PRELSG_1320200
TAN:
TA02790
TPV:
TP01_0683
TOT:
TOT_010000664
BEQ:
BEWA_037790
BBO:
BBOV_IV010440
BMIC:
BMR1_03g03415
BBIG:
BBBOND_0108140
TGO:
TGME49_310470
SMIN:
v1.2.011481.t1
(symbB.v1.2.011481.t1)
PSOJ:
PhsooMp05
(cox2)
» show all
Taxonomy
UniProt
Reference
PMID:
10486321
Authors
Rahman S, Taanman JW, Cooper JM, Nelson I, Hargreaves I, Meunier B, Hanna MG, Garcia JJ, Capaldi RA, Lake BD, Leonard JV, Schapira AH
Title
A missense mutation of cytochrome oxidase subunit II causes defective assembly and myopathy.
Journal
Am J Hum Genet 65:1030-9 (1999)
DOI:
10.1086/302590
Sequence
[hsa:
4513
]
LinkDB
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DBGET
integrated database retrieval system