KEGG   ORTHOLOGY: K07966
Entry
K07966                      KO                                     
Symbol
B4GALT1
Name
beta-1,4-galactosyltransferase 1 [EC:2.4.1.22 2.4.1.90 2.4.1.38 2.4.1.-]
Pathway
map00052  Galactose metabolism
map00510  N-Glycan biosynthesis
map00513  Various types of N-glycan biosynthesis
map00514  Other types of O-glycan biosynthesis
map00515  Mannose type O-glycan biosynthesis
map00533  Glycosaminoglycan biosynthesis - keratan sulfate
map00601  Glycosphingolipid biosynthesis - lacto and neolacto series
map01100  Metabolic pathways
Module
M00071  Glycosphingolipid biosynthesis, neolacto-series, LacCer => nLc4Cer
M00075  N-glycan biosynthesis, complex type
Reaction
R00503  UDP-alpha-D-galactose:D-glucose 4-beta-D-galactosyltransferase
R05977  
R05989  UDP-galactose:N-acetyl-beta-D-glucosaminylglycopeptide beta-1,4-galactosyltransferase
R06033  
R06067  UDP-galactose:D-glucose 4-beta-D-galactotransferase
R07617  
R09299  
Disease
H00119  Congenital disorders of glycosylation type II
Brite
KEGG Orthology (KO) [BR:ko00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00052 Galactose metabolism
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
  09107 Glycan biosynthesis and metabolism
   00510 N-Glycan biosynthesis
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
   00513 Various types of N-glycan biosynthesis
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
   00515 Mannose type O-glycan biosynthesis
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
   00514 Other types of O-glycan biosynthesis
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
   00533 Glycosaminoglycan biosynthesis - keratan sulfate
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
   00601 Glycosphingolipid biosynthesis - lacto and neolacto series
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
 09180 Brite Hierarchies
  09181 Protein families: metabolism
   01003 Glycosyltransferases
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
  09182 Protein families: genetic information processing
   04131 Membrane trafficking
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
  09183 Protein families: signaling and cellular processes
   04147 Exosome
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
Enzymes [BR:ko01000]
 2. Transferases
  2.4  Glycosyltransferases
   2.4.1  Hexosyltransferases
    2.4.1.22  lactose synthase
     K07966  B4GALT1; beta-1,4-galactosyltransferase 1
    2.4.1.38  beta-N-acetylglucosaminylglycopeptide beta-1,4-galactosyltransferase
     K07966  B4GALT1; beta-1,4-galactosyltransferase 1
    2.4.1.90  N-acetyllactosamine synthase
     K07966  B4GALT1; beta-1,4-galactosyltransferase 1
Glycosyltransferases [BR:ko01003]
 Glycan extension
  Type 2 chain/Poly-N-acetyllactosamine
   K07966  B4GALT1; beta-1,4-galactosyltransferase 1
Membrane trafficking [BR:ko04131]
 Exocytosis
  Calcium ion-dependent exocytosis
   Acrosomal exocytosis proteins
    K07966  B4GALT1; beta-1,4-galactosyltransferase 1
Exosome [BR:ko04147]
 Exosomal proteins
  Exosomal proteins of breast milk
   K07966  B4GALT1; beta-1,4-galactosyltransferase 1
Other DBs
GO: 0004461 0003945 0003831
CAZy: GT7
Genes
HSA: 2683(B4GALT1)
PTR: 100613700(B4GALT1)
PPS: 100974756(B4GALT1)
GGO: 101138982(B4GALT1)
PON: 100438031(B4GALT1)
NLE: 100597531(B4GALT1)
HMH: 116458785(B4GALT1)
MCC: 703541(B4GALT1)
MCF: 102131044(B4GALT1)
MTHB: 126937402
MNI: 105485655(B4GALT1)
CSAB: 103219294(B4GALT1)
CATY: 105590081(B4GALT1)
PANU: 101022281(B4GALT1)
TGE: 112607911(B4GALT1)
MLEU: 105539643(B4GALT1)
RRO: 104674271(B4GALT1)
RBB: 108518246(B4GALT1)
TFN: 117069449(B4GALT1)
PTEH: 111529202(B4GALT1)
CANG: 105526267(B4GALT1)
CJC: 100385157(B4GALT1)
SBQ: 101054125(B4GALT1)
CIMI: 108317680(B4GALT1)
CSYR: 103277047(B4GALT1)
MMUR: 105874372(B4GALT1)
LCAT: 123646221(B4GALT1)
PCOQ: 105820532(B4GALT1)
OGA: 100962109(B4GALT1)
MMU: 14595(B4galt1)
MCAL: 110292819(B4galt1)
MPAH: 110338771(B4galt1)
RNO: 24390(B4galt1)
MCOC: 116095826(B4galt1)
ANU: 117708230(B4galt1)
MUN: 110561670(B4galt1)
CGE: 100689430(B4galt1)
MAUA: 101824894(B4galt1)
PROB: 127224511(B4galt1)
PLEU: 114703257(B4galt1)
MORG: 121458383(B4galt1)
MFOT: 126509804
AAMP: 119826215(B4galt1)
NGI: 103741594(B4galt1)
HGL: 101698779 101721414(B4galt1)
CPOC: 100719604(B4galt1)
CCAN: 109681413
DORD: 105993397(B4galt1)
DSP: 122121438(B4galt1)
PLOP: 125363275(B4galt1)
NCAR: 124964217
MMMA: 107147853(B4galt1)
OCU: 100345726
OPI: 101522535(B4GALT1)
TUP: 102470655(B4GALT1)
GVR: 103606522(B4GALT1)
CFA: 481579(B4GALT1)
CLUD: 112649799(B4GALT1)
VVP: 112927554(B4GALT1)
VLG: 121494980(B4GALT1)
NPO: 129494858(B4GALT1)
AML: 100477164(B4GALT1)
UMR: 103667105(B4GALT1)
UAH: 113260528(B4GALT1)
UAR: 123781319(B4GALT1)
ELK: 111146253
LLV: 125083661
MPUF: 101693610(B4GALT1)
MNP: 132024670(B4GALT1)
MLK: 131812060(B4GALT1)
NVS: 122917530(B4GALT1)
ORO: 101362571(B4GALT1)
EJU: 114218153(B4GALT1)
ZCA: 113934251(B4GALT1)
MLX: 118018025(B4GALT1)
NSU: 110581489(B4GALT1)
LWW: 102726585(B4GALT1) 102727946
FCA: 101100927(B4GALT1)
PYU: 121034567(B4GALT1)
PCOO: 112850430(B4GALT1)
PBG: 122475074(B4GALT1)
LRUF: 124501308
PTG: 102959538(B4GALT1)
PPAD: 109252046(B4GALT1)
PUC: 125918726
AJU: 106976144
HHV: 120241747(B4GALT1)
BTA: 281781(B4GALT1)
BOM: 102269762(B4GALT1)
BIU: 109563168(B4GALT1)
BBUB: 102389487(B4GALT1)
BBIS: 104988709(B4GALT1)
CHX: 100860927(B4GALT1)
OAS: 100620048(B4GALT1)
BTAX: 128052146(B4GALT1)
CCAD: 122431686(B4GALT1)
MBEZ: 129556931(B4GALT1)
SSC: 100511655(B4GALT1)
CFR: 102517623(B4GALT1)
CBAI: 105078745(B4GALT1)
CDK: 105085573(B4GALT1)
VPC: 102530069(B4GALT1)
BACU: 102999260(B4GALT1)
LVE: 103086401(B4GALT1)
OOR: 101285364(B4GALT1)
DLE: 111163203(B4GALT1)
PCAD: 102981888(B4GALT1)
PSIU: 116755411(B4GALT1)
NASI: 112405411(B4GALT1)
ECB: 100068209(B4GALT1)
EPZ: 103555031(B4GALT1)
EAI: 106841463(B4GALT1)
MYB: 102240062(B4GALT1)
MYD: 102751484(B4GALT1)
MMYO: 118667396(B4GALT1)
MLF: 102435984(B4GALT1)
MNA: 107544980(B4GALT1)
PKL: 118716413(B4GALT1)
EFUS: 103286482(B4GALT1)
HAI: 109371790(B4GALT1)
DRO: 112304428(B4GALT1)
SHON: 118979827(B4GALT1)
AJM: 119060005(B4GALT1)
PDIC: 114507957(B4GALT1)
PHAS: 123819973(B4GALT1)
MMF: 118629472(B4GALT1)
RFQ: 117032000(B4GALT1)
PPAM: 129078214(B4GALT1)
PALE: 102878748(B4GALT1)
PGIG: 120612917(B4GALT1)
PVP: 105306412(B4GALT1)
RAY: 107502798(B4GALT1)
MJV: 108404111(B4GALT1)
TOD: 119232854(B4GALT1)
SARA: 101543700(B4GALT1)
LAV: 100659897(B4GALT1)
TMU: 101341812
ETF: 101642283(B4GALT1)
DNM: 101415414(B4GALT1)
MDO: 100010600(B4GALT1)
GAS: 123250673(B4GALT1) 123253937
SHR: 100929465(B4GALT1)
AFZ: 127561996
PCW: 110194785(B4GALT1)
OAA: 100075703(B4GALT1)
GGA: 396121(B4GALT1)
PCOC: 116239467(B4GALT1)
MGP: 100543545(B4GALT1)
CJO: 107306674(B4GALT1)
TPAI: 128089755(B4GALT1)
LMUT: 125686500(B4GALT1)
NMEL: 110389893(B4GALT1)
APLA: 101792817(B4GALT1)
ACYG: 106040136(B4GALT1)
CATA: 118256243(B4GALT1)
AFUL: 116500363(B4GALT1)
TGU: 100223650(B4GALT1)
LSR: 110474049(B4GALT1)
SCAN: 103821842(B4GALT1)
PMOA: 120513595(B4GALT1)
OTC: 121332678(B4GALT1)
PRUF: 121363773(B4GALT1)
GFR: 102041517(B4GALT1)
FAB: 101807052(B4GALT1)
OMA: 130265161(B4GALT1)
PHI: 102109081(B4GALT1)
PMAJ: 107198186(B4GALT1)
CCAE: 111941228(B4GALT1)
CCW: 104689823(B4GALT1)
ETL: 114057877(B4GALT1)
ZAB: 102064480(B4GALT1)
ACHL: 103801382(B4GALT1)
SVG: 106860347(B4GALT1)
MMEA: 130577574(B4GALT1)
HRT: 120765371(B4GALT1)
FPG: 101918852(B4GALT1)
FCH: 102046112(B4GALT1)
CLV: 102088289(B4GALT1)
NNI: 104022647(B4GALT1)
PCRI: 104025828(B4GALT1)
PLET: 104625205(B4GALT1)
PCAO: 104052520(B4GALT1)
ACUN: 113490200(B4GALT1)
TALA: 116963851(B4GALT1)
PADL: 103921076(B4GALT1)
AFOR: 103903797(B4GALT1)
ACHC: 115337075(B4GALT1)
HALD: 104314820
HLE: 104838429(B4GALT1)
AGEN: 126036022
GCL: 127027500
CCRI: 104155887(B4GALT1)
CSTI: 104558467(B4GALT1)
CMAC: 104477194(B4GALT1)
MUI: 104538516
BREG: 104635241(B4GALT1)
FGA: 104075898(B4GALT1)
GSTE: 104255114(B4GALT1)
LDI: 104343891(B4GALT1)
OHA: 104338458(B4GALT1)
NNT: 104406822(B4GALT1)
SHAB: 115600665(B4GALT1)
DPUB: 104300430(B4GALT1)
PGUU: 104462621(B4GALT1)
CPEA: 104391690(B4GALT1)
AVIT: 104277655
CVF: 104282639(B4GALT1)
RTD: 128902483(B4GALT1)
CUCA: 104059508(B4GALT1)
TEO: 104383756(B4GALT1)
BRHI: 104498469(B4GALT1)
AAM: 106486901(B4GALT1)
AROW: 112975301(B4GALT1)
NPD: 112948927(B4GALT1)
TGT: 104578635(B4GALT1)
DNE: 112989803(B4GALT1)
SCAM: 104144374(B4GALT1)
ASN: 102372956(B4GALT1)
AMJ: 102559129(B4GALT1)
CPOO: 109323453(B4GALT1)
GGN: 109298077(B4GALT1)
PSS: 102459690(B4GALT1)
CMY: 102942662(B4GALT1)
CCAY: 125636525(B4GALT1)
DCC: 119855468(B4GALT1)
CPIC: 101932379(B4GALT1)
TST: 117878876(B4GALT1)
CABI: 116829702(B4GALT1)
ACS: 100561064(b4galt1)
ASAO: 132768145(B4GALT1)
PVT: 110087350(B4GALT1)
SUND: 121921206(B4GALT1)
PBI: 103065477(B4GALT1)
PMUR: 107285615(B4GALT1)
CTIG: 120303843(B4GALT1)
TSR: 106557055(B4GALT1)
PGUT: 117661724(B4GALT1)
APRI: 131189543
PTEX: 113444148(B4GALT1)
NSS: 113415476(B4GALT1)
VKO: 123017487(B4GALT1)
PMUA: 114587454(B4GALT1)
PRAF: 128404702(B4GALT1)
ZVI: 118097645(B4GALT1)
HCG: 128345618(B4GALT1)
GJA: 107110573(B4GALT1)
STOW: 125436666(B4GALT1)
EMC: 129334204(B4GALT1)
XLA: 108704693(b4galt1l.S) 108706812(b4galt1.1.S) 108706813(b4galt1.2.S) 108712215(b4galt1.1.L) 108712216(b4galt1.2.L) 108712940 108712957(b4galt1l.L)
XTR: 100145518(b4galt1.1) 100485024(b4galt1l) 549418(b4galt1.2)
RTEM: 120915210(B4GALT1) 120932030
BBUF: 120989596 120989622(B4GALT1)
BGAR: 122927900(B4GALT1) 122928504
MUO: 115463633(B4GALT1)
GSH: 117347383(B4GALT1)
DRE: 550425(b4galt1) 768123(b4galt1l)
PTET: 122346701(b4galt1) 122357674(b4galt1l)
LROH: 127176044(b4galt1l) 127181503(b4galt1)
OMC: 131548760(b4galt1) 131553294(b4galt1l)
PPRM: 120460852(b4galt1l) 120478308(b4galt1)
RKG: 130072527(b4galt1l) 130097647(b4galt1)
MAMB: 125258644(b4galt1l) 125272471(b4galt1)
TROS: 130553360(b4galt1) 130563630(b4galt1l)
TDW: 130407450(b4galt1) 130437806(b4galt1l)
MANU: 129422271(b4galt1l) 129444864(b4galt1)
IPU: 108260689 108277608(b4galt1l)
IFU: 128604347(b4galt1) 128623370(b4galt1l)
PHYP: 113540104(b4galt1)
SMEO: 124381523 124396963(b4galt1l)
TVC: 132842016(b4galt1) 132861211 132861212(b4galt1l)
CMAO: 118816979(b4galt1) 118821644(b4galt1l)
NCC: 104951664
TBEN: 117482566 117482567(b4galt1l) 117484079
CGOB: 115025593
PLEP: 121948152(b4galt1l) 121960985 121960986
SLUC: 116051105 116060258(b4galt1l)
ESP: 116672118
PFLV: 114549363 114562966(b4galt1)
GAT: 120811611 120817303(b4galt1l)
PPUG: 119199018 119199020 119211455(b4galt1l)
AFB: 129090102(b4galt1l) 129111123
CLUM: 117737607(b4galt1l) 117749567
SCHU: 122866691 122880508(b4galt1l)
ALAT: 119007174(b4galt1l) 119008242
MZE: 101472320(b4galt1) 101486761
OAU: 116328309 116332053(b4galt1l) 116332060
OLA: 101171148(b4galt1)
OML: 112153596(b4galt1l)
GAF: 122824275 122824447 122836758(b4galt1l)
CTUL: 119784548(b4galt1l) 119784620 119787615
ALIM: 106517566 106531648 106533299(b4galt1)
NWH: 119408817(b4galt1l) 119426702
MCEP: 124995861 125007953(b4galt1l)
CSEM: 103376904 103390794(b4galt1)
POV: 109629466
SSEN: 122774288 122778195(b4galt1l)
HSP: 118098933 118112533(b4galt1l)
LCF: 108879172 108885296(b4galt1l) 108900792
SDU: 111233512(b4galt1) 111237265
SLAL: 111662869 111665610(b4galt1)
XGL: 120785455(b4galt1l) 120790010
HCQ: 109508336
SSCV: 125977506
SBIA: 133493033 133508416(b4galt1l)
PEE: 133396625 133407460(b4galt1l)
PTAO: 133469982 133484617(b4galt1l)
BPEC: 110161009 110168019(b4galt1)
MALB: 109963721
SJO: 128363282(b4galt1l) 128382304
PKI: 111848718(b4galt1)
AANG: 118227568 118231327(b4galt1l)
LOC: 102691443 107077118(b4galt1)
ARUT: 117409235(b4galt1l) 117420622
PSEX: 120532261(b4galt1l) 120532267
LCM: 102357329
CMK: 103177647(b4galt1l)
RTP: 109917086
CPLA: 122558311
LERI: 129695578
PMRN: 116951833
API: 100302475(NV135)
DNX: 107166054
AGS: 114128088
RMD: 113554920
NLU: 111053488
PCHN: 125039083
PTRU: 123520613
EAF: 111706179
TCF: 131884164
RSAN: 119391351
DPTE: 113798918
UDV: 129217749
BGT: 106050436
HRF: 124140904
MCAF: 127702162
DPOL: 127864768
XEN: 124455180
HSY: 130613054
 » show all
Reference
PMID:3091013
  Authors
Appert HE, Rutherford TJ, Tarr GE, Thomford NR, McCorquodale DJ
  Title
Isolation of galactosyltransferase from human milk and the determination of its N-terminal amino acid sequence.
  Journal
Biochem Biophys Res Commun 138:224-9 (1986)
DOI:10.1016/0006-291X(86)90269-X
Reference
PMID:3144273
  Authors
Masri KA, Appert HE, Fukuda MN
  Title
Identification of the full-length coding sequence for human galactosyltransferase (beta-N-acetylglucosaminide: beta 1,4-galactosyltransferase).
  Journal
Biochem Biophys Res Commun 157:657-63 (1988)
DOI:10.1016/s0006-291x(88)80300-0
  Sequence
[hsa:2683]
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