KEGG   Camelus dromedarius (Arabian camel): 105093370
Entry
105093370         CDS       T04642                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
cdk  Camelus dromedarius (Arabian camel)
Pathway
cdk00280  Valine, leucine and isoleucine degradation
cdk00640  Propanoate metabolism
cdk00785  Lipoic acid metabolism
cdk01100  Metabolic pathways
cdk01210  2-Oxocarboxylic acid metabolism
Module
cdk_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:cdk00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    105093370 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    105093370 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    105093370 (BCKDHA)
Enzymes [BR:cdk01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     105093370 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 105093370
NCBI-ProteinID: XP_010983542
LinkDB
Position
9:65198917..65216110
AA seq 446 aa
MALAAAAARVWEPSRGLGQVGLLVLRRLGARGLARSHPQRQQQQHFSSLDDKPQFPGASA
EFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNVSDLGKGRQMPVHYGCQERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTYEQYRGDGIAARGPGYGILSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYLQGRGWWDDEQEKAWRKQSRRKVMEAFEQAERKLKPNPNLLFSDVYQEMPPQ
LRKQQESLARHLQTYGEHYPLDHFEK
NT seq 1341 nt   +upstreamnt  +downstreamnt
atggcgctggcagctgctgcggcgagggtttgggagccaagtcgaggcttgggccaggtc
ggcctcctggtcctgcggaggcttggggctcgggggcttgctagatctcacccccagagg
cagcagcagcagcacttctcgtccctggatgacaagccccagttcccaggggcctcagcg
gagtttatagacaagctagagttcatccagcccaatgtcatctctgggatccccatctac
cgtgtcatggaccggcagggccagatcatcaaccccagcgaggatccccacctgccccag
gagaaggtgctcaagttctacaagagcatgacgctgctcaacaccatggaccgcatcctc
tatgagtcccagaggcagggccggatatctttctacatgaccaactatggcgaggagggg
acgcacgtggggagtgcagccgccctggacaacacggacctggtgttcggccaataccgg
gaggcaggcgtgctcatgtaccgggactacccgctggaactgttcatggcccagtgctac
ggcaatgtgagcgacctgggcaagggacgccagatgcccgtccactatggctgccaggag
cgccacttcgtcaccatctcctctccgctggccacgcagatccctcaggcggtgggggcg
gcctatgcagccaagcgggccaacgccaacagggttgtcatctgttacttcggagagggg
gcagccagtgagggggacgcccacgctggcttcaacttcgctgccacacttgagtgcccc
atcatcttcttctgccggaacaatggctacgccatctccacgcccacctacgagcagtac
cgtggggatggcatcgcggctcgaggccctggatatggcatcctgtccatccgcgtggac
ggcaacgatgtgtttgccgtgtacaatgccacaaaggaggcccggcggcgggccgtggca
gagaaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcaccagc
gatgacagctcagcgtaccgctcggtggatgaggttaactactgggataagcaggaccac
cccatctcccggctgaggcactacctgcagggccgcggctggtgggatgatgagcaggag
aaggcctggaggaagcagtcccgcaggaaggtgatggaggcctttgagcaggctgagcgg
aagctgaagcccaaccccaacctgctcttctcagacgtgtatcaggagatgcctccccag
ctccgcaagcagcaggaatctctggcccgtcacctccagacctacggtgaacactacccc
ctggaccactttgagaagtga

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