Camelus dromedarius (Arabian camel): 105093370
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Entry
105093370 CDS
T04642
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
cdk
Camelus dromedarius (Arabian camel)
Pathway
cdk00280
Valine, leucine and isoleucine degradation
cdk00640
Propanoate metabolism
cdk00785
Lipoic acid metabolism
cdk01100
Metabolic pathways
cdk01210
2-Oxocarboxylic acid metabolism
Module
cdk_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
cdk00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
105093370 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
105093370 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
105093370 (BCKDHA)
Enzymes [BR:
cdk01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
105093370 (BCKDHA)
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
105093370
NCBI-ProteinID:
XP_010983542
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Position
9:65198917..65216110
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AA seq
446 aa
AA seq
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MALAAAAARVWEPSRGLGQVGLLVLRRLGARGLARSHPQRQQQQHFSSLDDKPQFPGASA
EFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNVSDLGKGRQMPVHYGCQERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTYEQYRGDGIAARGPGYGILSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYLQGRGWWDDEQEKAWRKQSRRKVMEAFEQAERKLKPNPNLLFSDVYQEMPPQ
LRKQQESLARHLQTYGEHYPLDHFEK
NT seq
1341 nt
NT seq
+upstream
nt +downstream
nt
atggcgctggcagctgctgcggcgagggtttgggagccaagtcgaggcttgggccaggtc
ggcctcctggtcctgcggaggcttggggctcgggggcttgctagatctcacccccagagg
cagcagcagcagcacttctcgtccctggatgacaagccccagttcccaggggcctcagcg
gagtttatagacaagctagagttcatccagcccaatgtcatctctgggatccccatctac
cgtgtcatggaccggcagggccagatcatcaaccccagcgaggatccccacctgccccag
gagaaggtgctcaagttctacaagagcatgacgctgctcaacaccatggaccgcatcctc
tatgagtcccagaggcagggccggatatctttctacatgaccaactatggcgaggagggg
acgcacgtggggagtgcagccgccctggacaacacggacctggtgttcggccaataccgg
gaggcaggcgtgctcatgtaccgggactacccgctggaactgttcatggcccagtgctac
ggcaatgtgagcgacctgggcaagggacgccagatgcccgtccactatggctgccaggag
cgccacttcgtcaccatctcctctccgctggccacgcagatccctcaggcggtgggggcg
gcctatgcagccaagcgggccaacgccaacagggttgtcatctgttacttcggagagggg
gcagccagtgagggggacgcccacgctggcttcaacttcgctgccacacttgagtgcccc
atcatcttcttctgccggaacaatggctacgccatctccacgcccacctacgagcagtac
cgtggggatggcatcgcggctcgaggccctggatatggcatcctgtccatccgcgtggac
ggcaacgatgtgtttgccgtgtacaatgccacaaaggaggcccggcggcgggccgtggca
gagaaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcaccagc
gatgacagctcagcgtaccgctcggtggatgaggttaactactgggataagcaggaccac
cccatctcccggctgaggcactacctgcagggccgcggctggtgggatgatgagcaggag
aaggcctggaggaagcagtcccgcaggaaggtgatggaggcctttgagcaggctgagcgg
aagctgaagcccaaccccaacctgctcttctcagacgtgtatcaggagatgcctccccag
ctccgcaagcagcaggaatctctggcccgtcacctccagacctacggtgaacactacccc
ctggaccactttgagaagtga
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