Homo sapiens (human): 1371
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Entry
1371 CDS
T01001
Gene name
CPOX, COX, CPO, CPX, HARPO, HCP
Definition
(RefSeq) coproporphyrinogen oxidase
KO
K00228
coproporphyrinogen III oxidase [EC:
1.3.3.3
]
Organism
hsa
Homo sapiens (human)
Pathway
hsa00860
Porphyrin and chlorophyll metabolism
hsa01100
Metabolic pathways
hsa01240
Biosynthesis of cofactors
Module
hsa_M00868
Heme biosynthesis, animals and fungi, glycine => heme
Network
nt06011
Heme biosynthesis
Element
N00601
Heme biosynthesis
N00602
FECH deficiency in heme biosynthesis
N00603
PPOX deficiency in heme biosynthesis
N00604
CPOX deficiency in heme biosynthesis
Disease
H00202
Hepatic porphyria
H01763
Porphyria
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09100 Metabolism
09108 Metabolism of cofactors and vitamins
00860 Porphyrin and chlorophyll metabolism
1371 (CPOX)
Enzymes [BR:
hsa01000
]
1. Oxidoreductases
1.3 Acting on the CH-CH group of donors
1.3.3 With oxygen as acceptor
1.3.3.3 coproporphyrinogen oxidase
1371 (CPOX)
BRITE hierarchy
SSDB
Ortholog
Paralog
GFIT
Motif
Pfam:
Coprogen_oxidas
Motif
Other DBs
NCBI-GeneID:
1371
NCBI-ProteinID:
NP_000088
OMIM:
612732
HGNC:
2321
Ensembl:
ENSG00000080819
Vega:
OTTHUMG00000160016
Pharos:
P36551
(Tbio)
UniProt:
P36551
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Structure
PDB:
2AEX
Thumbnails
Position
3q11.2
AA seq
454 aa
AA seq
DB search
MALQLGRLSSGPCWLVARGGCGGPRAWSQCGGGGLRAWSQRSAAGRVCRPPGPAGTEQSR
GLGHGSTSRGGPWVGTGLAAALAGLVGLATAAFGHVQRAEMLPKTSGTRATSLGRPEEEE
DELAHRCSSFMAPPVTDLGELRRRPGDMKTKMELLILETQAQVCQALAQVDGGANFSVDR
WERKEGGGGISCVLQDGCVFEKAGVSISVVHGNLSEEAAKQMRSRGKVLKTKDGKLPFCA
MGVSSVIHPKNPHAPTIHFNYRYFEVEEADGNKQWWFGGGCDLTPTYLNQEDAVHFHRTL
KEACDQHGPDLYPKFKKWCDDYFFIAHRGERRGIGGIFFDDLDSPSKEEVFRFVQSCARA
VVPSYIPLVKKHCDDSFTPQEKLWQQLRRGRYVEFNLLYDRGTKFGLFTPGSRIESILMS
LPLTARWEYMHSPSENSKEAEILEVLRHPRDWVR
NT seq
1365 nt
NT seq
+upstream
nt +downstream
nt
atggccttgcagctgggcaggctgagctcgggcccctgctggctcgtggcgcggggcggc
tgcggagggccccgcgcctggtcccagtgcggcggcggagggctccgagcctggtcccag
cgcagcgcagccggacgcgtctgccggccccctggcccggctggcacggagcagagccgc
gggctggggcacggctcgacgtcgagaggcggcccctgggtggggacagggctggccgcg
gcgctggcggggttggtggggctggccaccgccgccttcgggcatgtgcagcgggcggag
atgttgcctaagacctcggggacgcgggccacttcgctggggaggccggaggaggaggag
gatgagctggcccaccgctgcagcagcttcatggccccgcctgtgaccgacctgggcgag
ctgcgaaggaggccgggcgacatgaagaccaagatggagctgctgattctggagacccag
gcccaggtgtgccaggctctggcacaggtagacgggggcgccaacttttctgtggaccgg
tgggagaggaaggaaggaggtggcggcatcagctgtgtacttcaagatgggtgtgttttc
gaaaaggctggggtgagcatttctgttgttcatggaaatctttcagaggaagctgcaaaa
caaatgagaagcagaggaaaagttctgaagactaaagatggtaaattgccattttgtgct
atgggcgtgagctctgttatccaccccaagaatcctcatgctcctactatccatttcaac
tacagatactttgaagtagaagaagctgatggcaacaagcagtggtggtttggtggtgga
tgtgacctcactccaacatacttgaatcaagaagacgctgtccattttcacagaactctg
aaggaggcttgtgaccagcatggtccagatctctaccccaaatttaaaaaatggtgtgat
gattacttctttatagcccatcgtggagaacggcggggcattggtggtatcttttttgat
gatcttgactctccgtccaaggaggaggtgtttcgctttgtacagagctgtgccagggct
gtagttccttcttacattccccttgtgaaaaagcactgtgatgactcattcaccccccag
gagaagctgtggcagcagctcagaagaggacggtatgtagaatttaatctgctgtatgat
cggggcacaaagtttggcctcttcactccaggatccagaattgaaagtatcttgatgtct
ttacctctaactgcccgatgggagtacatgcattcaccctcagagaattccaaagaagct
gaaattctggaagttctacgccatccaagggactgggtgcgttga
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