ORTHOLOGY: K09492
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Entry
K09492 KO
Symbol
MKKS
Name
McKusick-Kaufman syndrome protein
Disease
H00418
Bardet-Biedl syndrome
H02180
McKusick-Kaufman syndrome
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03110 Chaperones and folding catalysts
K09492 MKKS; McKusick-Kaufman syndrome protein
09183 Protein families: signaling and cellular processes
03037 Cilium and associated proteins
K09492 MKKS; McKusick-Kaufman syndrome protein
Chaperones and folding catalysts [BR:
ko03110
]
Heat shock proteins
HSP60 / Chaperonin
K09492 MKKS; McKusick-Kaufman syndrome protein
Cilium and associated proteins [BR:
ko03037
]
Primary cilia and associated proteins
BBS-CCT complex
K09492 MKKS; McKusick-Kaufman syndrome protein
BRITE hierarchy
Genes
HSA:
8195
(MKKS)
PTR:
458098
(MKKS)
PPS:
100983370
(MKKS)
GGO:
101128121
(MKKS)
PON:
100172008
(MKKS)
NLE:
100579179
(MKKS)
HMH:
116460882
(MKKS)
MCC:
718547
(MKKS)
MCF:
102133509
MTHB:
126929040
MNI:
105481521
(MKKS)
CSAB:
103246466
(MKKS)
CATY:
105582082
(MKKS)
PANU:
101003771
(MKKS)
TGE:
112633074
(MKKS)
MLEU:
105552905
(MKKS)
RRO:
104655768
(MKKS)
RBB:
108527558
(MKKS)
TFN:
117068460
(MKKS)
PTEH:
111546444
(MKKS)
CANG:
105516597
(MKKS)
CJC:
100393149
(MKKS)
SBQ:
101043883
(MKKS)
CIMI:
108300951
(MKKS)
CSYR:
103261978
(MKKS)
MMUR:
105880049
(MKKS)
LCAT:
123622209
PCOQ:
105820661
(MKKS)
OGA:
100950710
(MKKS)
MMU:
59030
(Mkks)
MCAL:
110286491
(Mkks)
MPAH:
110317667
(Mkks)
RNO:
311456
(Mkks)
MCOC:
116091008
(Mkks)
ANU:
117704243
(Mkks)
MUN:
110560825
(Mkks)
CGE:
100769625
(Mkks)
MAUA:
101836693
(Mkks)
PROB:
127221382
(Mkks)
127234429
127234482
127234483
PLEU:
114702978
(Mkks)
MORG:
121460232
(Mkks)
MFOT:
126494525
AAMP:
119814030
NGI:
103729190
(Mkks)
HGL:
101699409
(Mkks)
CPOC:
100724231
(Mkks)
CCAN:
109699990
(Mkks)
DORD:
105981782
(Mkks)
DSP:
122120448
PLOP:
125353257
NCAR:
124976062
MMMA:
107139989
OCU:
100339806
127482570
OPI:
101526262
(MKKS)
TUP:
102473545
(MKKS)
GVR:
103608703
(MKKS)
CFA:
485771
(MKKS)
CLUD:
112673590
VVP:
112930045
(MKKS)
VLG:
121477733
(MKKS)
NPO:
129494654
(MKKS)
AML:
100473266
(MKKS)
UMR:
103674437
(MKKS)
UAH:
113258338
(MKKS)
UAR:
123799785
(MKKS)
ELK:
111141574
LLV:
125109282
MPUF:
101684116
(MKKS)
MNP:
132021727
(MKKS)
MLK:
131808093
(MKKS)
NVS:
122916263
ORO:
101380699
(MKKS)
EJU:
114216424
(MKKS)
ZCA:
113937356
(MKKS)
MLX:
118011236
(MKKS)
NSU:
110579524
(MKKS)
FCA:
101092927
(MKKS)
PYU:
121012490
(MKKS)
PCOO:
112869221
(MKKS)
PBG:
122496574
(MKKS)
LRUF:
124503645
PTG:
102958378
(MKKS)
PPAD:
109274707
(MKKS)
PUC:
125936816
AJU:
106983340
HHV:
120226306
(MKKS)
BTA:
614288
(MKKS)
BOM:
102286225
(MKKS)
BIU:
109567855
(MKKS)
BBUB:
102390376
BBIS:
104984478
(MKKS)
CHX:
102182886
(MKKS)
OAS:
101109032
(MKKS)
BTAX:
128058411
(MKKS)
ODA:
120869180
(MKKS)
CCAD:
122441396
122448862
MBEZ:
129556503
(MKKS)
SSC:
100157552
(MKKS)
CFR:
102512059
(MKKS)
CBAI:
105064954
(MKKS)
CDK:
105101220
(MKKS)
VPC:
102532029
(MKKS)
BACU:
103000942
(MKKS)
LVE:
103090010
(MKKS)
OOR:
101273130
(MKKS)
DLE:
111165625
(MKKS)
PCAD:
102974739
(MKKS)
PSIU:
116740914
(MKKS)
NASI:
112393303
(MKKS)
ECB:
100064409
(MKKS)
EPZ:
103551775
(MKKS)
EAI:
106825826
MYB:
102239229
(MKKS)
MYD:
102755059
(MKKS)
MMYO:
118663644
(MKKS)
MLF:
102417903
(MKKS)
MNA:
107536361
(MKKS)
PKL:
118707680
(MKKS)
EFUS:
103285674
(MKKS)
HAI:
109378989
(MKKS)
DRO:
112303801
(MKKS)
SHON:
118990861
(MKKS)
AJM:
119042691
(MKKS)
PDIC:
114506366
(MKKS)
PHAS:
123814673
MMF:
118618969
(MKKS)
RFQ:
117015750
(MKKS)
PPAM:
129070864
(MKKS)
PALE:
102883595
(MKKS)
PGIG:
120611907
(MKKS)
PVP:
105299458
(MKKS)
RAY:
107507101
(MKKS)
MJV:
108408348
(MKKS)
TOD:
129144620
(MKKS)
SARA:
101544884
(MKKS)
LAV:
100658211
(MKKS)
TMU:
101353677
ETF:
101645997
DNM:
101447985
(MKKS)
MDO:
100031632
(MKKS)
GAS:
123234753
SHR:
100931631
(MKKS)
AFZ:
127548491
PCW:
110208113
(MKKS)
OAA:
100078571
(MKKS)
GGA:
416737
(MKKS)
PCOC:
116231989
(MKKS)
MGP:
100545671
(MKKS)
CJO:
107310946
(MKKS)
TPAI:
128087191
(MKKS)
LMUT:
125690177
(MKKS)
NMEL:
110395548
(MKKS)
APLA:
101801138
(MKKS)
ACYG:
106036612
CATA:
118251075
AFUL:
116487578
(MKKS)
TGU:
100230586
(MKKS)
LSR:
110475839
(MKKS)
SCAN:
103819228
(MKKS)
PMOA:
120505975
(MKKS)
OTC:
121342596
(MKKS)
PRUF:
121357062
(MKKS)
GFR:
102044968
(MKKS)
FAB:
101807131
(MKKS)
OMA:
130250571
(MKKS)
130250574
PHI:
102099580
(MKKS)
PMAJ:
107201867
(MKKS)
CCAE:
111926471
(MKKS)
CCW:
104691527
(MKKS)
CBRC:
103622979
(MKKS)
ETL:
114057369
(MKKS)
ZAB:
102071118
(MKKS)
ACHL:
103802937
(MKKS)
SVG:
106865165
(MKKS)
MMEA:
130583535
(MKKS)
130583542
HRT:
120749873
(MKKS)
131378509
FPG:
101917754
(MKKS)
FCH:
102053778
(MKKS)
CLV:
102098132
(MKKS)
EGZ:
104132999
(MKKS)
NNI:
104022437
(MKKS)
PCRI:
104030832
(MKKS)
PLET:
104620967
(MKKS)
EHS:
104502440
(MKKS)
PCAO:
104050868
(MKKS)
ACUN:
113478115
(MKKS)
TALA:
104359536
PADL:
103913120
(MKKS)
AFOR:
103901616
(MKKS)
ACHC:
115344467
(MKKS)
HALD:
104323441
(MKKS)
HLE:
104836303
(MKKS)
AGEN:
126038866
GCL:
127015003
CCRI:
104154431
(MKKS)
CSTI:
104549162
(MKKS)
CMAC:
104484699
(MKKS)
MUI:
104544971
(MKKS)
BREG:
104642534
(MKKS)
FGA:
104080099
(MKKS)
GSTE:
104257141
(MKKS)
LDI:
104350579
(MKKS)
MNB:
103781631
(MKKS)
OHA:
104330715
(MKKS)
NNT:
104413386
(MKKS)
SHAB:
115609262
(MKKS)
DPUB:
104305968
(MKKS)
PGUU:
104457441
(MKKS)
ACAR:
104522284
(MKKS)
CPEA:
104390965
(MKKS)
AVIT:
104270086
(MKKS)
CVF:
104287342
(MKKS)
RTD:
128907640
CUCA:
104055379
(MKKS)
TEO:
104369624
(MKKS)
BRHI:
104493420
(MKKS)
AAM:
106490423
(MKKS)
AROW:
112965321
(MKKS)
NPD:
112958927
(MKKS)
TGT:
104578408
(MKKS)
DNE:
112980028
(MKKS)
SCAM:
104143474
(MKKS)
ASN:
102379292
(MKKS)
AMJ:
102575835
(MKKS)
CPOO:
109319498
(MKKS)
GGN:
109296720
(MKKS)
PSS:
102458411
(MKKS)
CMY:
102944088
CCAY:
125633386
DCC:
119852894
CPIC:
101951199
TST:
117874227
(MKKS)
CABI:
116836502
(MKKS)
MRV:
120401087
(MKKS)
ACS:
100560025
(mkks)
ASAO:
132781554
(MKKS)
PVT:
110086122
(MKKS)
SUND:
121934756
PBI:
103068070
(MKKS)
PMUR:
107297768
107301513
CTIG:
120315295
(MKKS)
TSR:
106543004
(MKKS)
PGUT:
117674380
(MKKS)
APRI:
131197448
(MKKS)
PTEX:
113442675
(MKKS)
NSS:
113412728
(MKKS)
VKO:
123035740
PMUA:
114593665
(MKKS)
PRAF:
128410011
ZVI:
118082490
(MKKS)
HCG:
128340043
(MKKS)
GJA:
107106799
(MKKS)
STOW:
125435107
125438949
EMC:
129341205
(MKKS)
XLA:
108716568
(mkks.L)
XTR:
100125210
(mkks)
NPR:
108795386
(MKKS)
RTEM:
120937807
(MKKS)
BBUF:
120997374
120999015
(MKKS)
BGAR:
122934450
(MKKS)
122936115
MUO:
115465673
(MKKS)
GSH:
117356865
(MKKS)
DRE:
393134
(mkks)
SRX:
107739894
(mkks)
SANH:
107654981
107683876
SGH:
107585538
(mkks)
CCAR:
109099381
(mkks)
CAUA:
113112513
CGIB:
127970660
128026056
PTET:
122356391
(mkks)
LROH:
127174772
(mkks)
OMC:
131551864
(mkks)
PPRM:
120463916
(mkks)
RKG:
130088292
(mkks)
MAMB:
125277157
(mkks)
CIDE:
127525556
MASI:
127414162
TROS:
130559284
(mkks)
TDW:
130431807
(mkks)
MANU:
129416278
(mkks)
IPU:
108277806
IFU:
128621661
(mkks)
PHYP:
113539393
(mkks)
SMEO:
124394400
(mkks)
TFD:
113642036
(mkks)
TVC:
132858324
(mkks)
AMEX:
111191658
(mkks)
CMAO:
118816476
(mkks)
EEE:
113579965
(mkks)
CHAR:
105911570
(mkks)
TRU:
101068226
(mkks)
TFS:
130533363
(mkks)
TNG:
GSTEN00030852G001
LCO:
104918214
(mkks)
NCC:
104952545
(mkks)
TBEN:
117499975
(mkks)
CGOB:
115020091
(mkks)
PGEO:
117459849
(mkks)
GACU:
117553227
(mkks)
ELY:
117248147
(mkks)
EFO:
125903493
(mkks)
PLEP:
121955012
(mkks)
SLUC:
116051317
(mkks)
ECRA:
117960839
(mkks)
ESP:
116705048
(mkks)
PFLV:
114572660
(mkks)
GAT:
120820517
(mkks)
PPUG:
119214123
(mkks)
AFB:
129092704
(mkks)
CLUM:
117744148
(mkks)
SCHU:
122883984
(mkks)
CUD:
121510838
(mkks)
ALAT:
119033349
(mkks)
MZE:
101484611
(mkks)
ONL:
100690262
(mkks)
OAU:
116318584
(mkks)
OLA:
101167146
(mkks)
OML:
112161523
(mkks)
XMA:
102231474
(mkks)
XCO:
114138401
(mkks)
XHE:
116712839
(mkks)
PRET:
103477239
(mkks)
PFOR:
103137680
(mkks)
PLAI:
106945336
(mkks)
PMEI:
106914897
(mkks)
GAF:
122842953
(mkks)
PPRL:
129359821
(mkks)
CVG:
107096522
(mkks)
CTUL:
119782862
(mkks)
GMU:
124858678
(mkks)
NFU:
107375449
(mkks)
KMR:
108248136
(mkks)
ALIM:
106515895
(mkks)
NWH:
119417702
(mkks)
AOCE:
111573723
(mkks)
MCEP:
125018930
(mkkS)
CSEM:
103387630
(mkks)
POV:
109636566
(mkks)
SSEN:
122781486
(mkks)
HHIP:
117775258
(mkks)
HSP:
118118628
(mkks)
LCF:
108885814
SDU:
111220695
(mkks)
SLAL:
111658925
(mkks)
XGL:
120796304
(mkks)
HCQ:
109516278
(mkks)
SSCV:
125978985
SBIA:
133510235
(mkks)
PEE:
133410034
(mkks)
PTAO:
133485620
(mkks)
BPEC:
110156790
(mkks)
MALB:
109961148
(mkks)
BSPL:
114841972
(mkks)
SJO:
128372894
(mkks)
SASA:
106578777
(mkks)
STRU:
115155542
(mkks)
OTW:
112236517
(mkks)
OMY:
110491222
(mkks)
OGO:
124047515
(mkks)
ONE:
115121475
(mkks)
OKI:
109882733
(mkks)
OKE:
118381833
(mkks)
SALP:
112075000
(mkks)
SNH:
120038493
(mkks)
CCLU:
121558702
(mkks)
ELS:
105029458
(mkks)
SFM:
108926974
(mkks)
PKI:
111835701
(mkks)
AANG:
118217540
(mkks)
LOC:
102693112
(mkks)
PSPA:
121316095
(mkks)
ARUT:
117402363
(mkks)
PSEX:
120516505
(mkks)
LCM:
102354287
(MKKS)
RTP:
109915158
(mkks)
CPLA:
122553089
(mkks)
HOC:
132819887
(mkks)
LERI:
129699277
(mkks)
PMRN:
116941561
(MKKS)
LRJ:
133344263
(MKKS)
BFO:
118420363
BBEL:
109474910
CIN:
100181523
SPU:
115921243
581756
LPIC:
129264713
129264715
APLC:
110981378
SKO:
100378108
HHAL:
106680208
NLU:
111057366
MQU:
128984266
FOC:
113203499
TPAL:
117650523
ZNE:
110830743
CSEC:
111870279
PVM:
113804605
PJA:
122251916
PCHN:
125034559
PMOO:
119589520
HAME:
121863256
PCLA:
123759679
PTRU:
123519884
HAZT:
108670251
LSM:
121117341
CSCU:
111631425
PTEP:
107454230
UDV:
129220170
SDM:
118190697
LPOL:
106472374
LGI:
LOTGIDRAFT_145572
PVUL:
126822676
PCAN:
112570011
BGT:
106065040
GAE:
121371535
HRF:
124141963
HRJ:
124287371
CRG:
105336786
CVN:
111130072
CANU:
128177376
OED:
125649995
MYI:
110454908
PMAX:
117323804
RPHI:
132743492
OBI:
106869678
OSN:
115212342
NVE:
5507417
EPA:
110242734
ATEN:
116294420
ADF:
107330633
107335811
AMIL:
114950210
PDAM:
113672132
SPIS:
111335173
DGT:
114530268
HMG:
100205571
HSY:
130653593
TAD:
TRIADDRAFT_53298
AQU:
105312770
PIF:
PITG_06847
PSOJ:
PHYSODRAFT_311965
» show all
Taxonomy
UniProt
Reference
PMID:
20080638
Authors
Seo S, Baye LM, Schulz NP, Beck JS, Zhang Q, Slusarski DC, Sheffield VC
Title
BBS6, BBS10, and BBS12 form a complex with CCT/TRiC family chaperonins and mediate BBSome assembly.
Journal
Proc Natl Acad Sci U S A 107:1488-93 (2010)
DOI:
10.1073/pnas.0910268107
Sequence
[hsa:
8195
]
LinkDB
All DBs
DBGET
integrated database retrieval system