KEGG   ORTHOLOGY: K09492
Entry
K09492                      KO                                     
Symbol
MKKS
Name
McKusick-Kaufman syndrome protein
Disease
H00418  Bardet-Biedl syndrome
H02180  McKusick-Kaufman syndrome
Brite
KEGG Orthology (KO) [BR:ko00001]
 09180 Brite Hierarchies
  09182 Protein families: genetic information processing
   03110 Chaperones and folding catalysts
    K09492  MKKS; McKusick-Kaufman syndrome protein
  09183 Protein families: signaling and cellular processes
   03037 Cilium and associated proteins
    K09492  MKKS; McKusick-Kaufman syndrome protein
Chaperones and folding catalysts [BR:ko03110]
 Heat shock proteins
  HSP60 / Chaperonin
   K09492  MKKS; McKusick-Kaufman syndrome protein
Cilium and associated proteins [BR:ko03037]
 Primary cilia and associated proteins
  BBS-CCT complex
   K09492  MKKS; McKusick-Kaufman syndrome protein
Genes
HSA: 8195(MKKS)
PTR: 458098(MKKS)
PPS: 100983370(MKKS)
GGO: 101128121(MKKS)
PON: 100172008(MKKS)
NLE: 100579179(MKKS)
HMH: 116460882(MKKS)
MCC: 718547(MKKS)
MCF: 102133509
MTHB: 126929040
MNI: 105481521(MKKS)
CSAB: 103246466(MKKS)
CATY: 105582082(MKKS)
PANU: 101003771(MKKS)
TGE: 112633074(MKKS)
MLEU: 105552905(MKKS)
RRO: 104655768(MKKS)
RBB: 108527558(MKKS)
TFN: 117068460(MKKS)
PTEH: 111546444(MKKS)
CANG: 105516597(MKKS)
CJC: 100393149(MKKS)
SBQ: 101043883(MKKS)
CIMI: 108300951(MKKS)
CSYR: 103261978(MKKS)
MMUR: 105880049(MKKS)
LCAT: 123622209
PCOQ: 105820661(MKKS)
OGA: 100950710(MKKS)
MMU: 59030(Mkks)
MCAL: 110286491(Mkks)
MPAH: 110317667(Mkks)
RNO: 311456(Mkks)
MCOC: 116091008(Mkks)
ANU: 117704243(Mkks)
MUN: 110560825(Mkks)
CGE: 100769625(Mkks)
MAUA: 101836693(Mkks)
PLEU: 114702978(Mkks)
MORG: 121460232(Mkks)
MFOT: 126494525
AAMP: 119814030
NGI: 103729190(Mkks)
HGL: 101699409(Mkks)
CPOC: 100724231(Mkks)
CCAN: 109699990(Mkks)
DORD: 105981782(Mkks)
DSP: 122120448
PLOP: 125353257
NCAR: 124976062
MMMA: 107139989
OPI: 101526262(MKKS)
TUP: 102473545(MKKS)
GVR: 103608703(MKKS)
CFA: 485771(MKKS)
CLUD: 112673590
VVP: 112930045(MKKS)
VLG: 121477733(MKKS)
NPO: 129494654(MKKS)
AML: 100473266(MKKS)
UMR: 103674437(MKKS)
UAH: 113258338(MKKS)
UAR: 123799785(MKKS)
ELK: 111141574
LLV: 125109282
MPUF: 101684116(MKKS)
MNP: 132021727(MKKS)
MLK: 131808093(MKKS)
NVS: 122916263
ORO: 101380699(MKKS)
EJU: 114216424(MKKS)
ZCA: 113937356(MKKS)
MLX: 118011236(MKKS)
NSU: 110579524(MKKS)
FCA: 101092927(MKKS)
PYU: 121012490(MKKS)
PCOO: 112869221(MKKS)
PBG: 122496574(MKKS)
LRUF: 124503645
PTG: 102958378(MKKS)
PPAD: 109274707(MKKS)
PUC: 125936816
AJU: 106983340
HHV: 120226306(MKKS)
BTA: 614288(MKKS)
BOM: 102286225(MKKS)
BIU: 109567855(MKKS)
BBUB: 102390376
BBIS: 104984478(MKKS)
CHX: 102182886(MKKS)
OAS: 101109032(MKKS)
BTAX: 128058411(MKKS)
ODA: 120869180(MKKS)
MBEZ: 129556503(MKKS)
SSC: 100157552(MKKS)
CFR: 102512059(MKKS)
CBAI: 105064954(MKKS)
CDK: 105101220(MKKS)
VPC: 102532029(MKKS)
BACU: 103000942(MKKS)
LVE: 103090010(MKKS)
OOR: 101273130(MKKS)
DLE: 111165625(MKKS)
PCAD: 102974739(MKKS)
PSIU: 116740914(MKKS)
NASI: 112393303(MKKS)
ECB: 100064409(MKKS)
EPZ: 103551775(MKKS)
EAI: 106825826
MYB: 102239229(MKKS)
MYD: 102755059(MKKS)
MMYO: 118663644(MKKS)
MLF: 102417903(MKKS)
MNA: 107536361(MKKS)
PKL: 118707680(MKKS)
EFUS: 103285674(MKKS)
HAI: 109378989(MKKS)
DRO: 112303801(MKKS)
SHON: 118990861(MKKS)
AJM: 119042691(MKKS)
PDIC: 114506366(MKKS)
PHAS: 123814673
MMF: 118618969(MKKS)
RFQ: 117015750(MKKS)
PPAM: 129070864(MKKS)
PALE: 102883595(MKKS)
PGIG: 120611907(MKKS)
PVP: 105299458(MKKS)
RAY: 107507101(MKKS)
MJV: 108408348(MKKS)
TOD: 129144620(MKKS)
SARA: 101544884(MKKS)
LAV: 100658211(MKKS)
TMU: 101353677
ETF: 101645997
DNM: 101447985(MKKS)
MDO: 100031632(MKKS)
GAS: 123234753
SHR: 100931631(MKKS)
AFZ: 127548491
PCW: 110208113(MKKS)
OAA: 100078571(MKKS)
GGA: 416737(MKKS)
PCOC: 116231989(MKKS)
MGP: 100545671(MKKS)
CJO: 107310946(MKKS)
TPAI: 128087191(MKKS)
LMUT: 125690177(MKKS)
NMEL: 110395548(MKKS)
APLA: 101801138(MKKS)
ACYG: 106036612
CATA: 118251075
AFUL: 116487578(MKKS)
TGU: 100230586(MKKS)
LSR: 110475839(MKKS)
SCAN: 103819228(MKKS)
PMOA: 120505975(MKKS)
OTC: 121342596(MKKS)
PRUF: 121357062(MKKS)
GFR: 102044968(MKKS)
FAB: 101807131(MKKS)
OMA: 130250571(MKKS) 130250574
PHI: 102099580(MKKS)
PMAJ: 107201867(MKKS)
CCAE: 111926471(MKKS)
CCW: 104691527(MKKS)
CBRC: 103622979(MKKS)
ETL: 114057369(MKKS)
ZAB: 102071118(MKKS)
ACHL: 103802937(MKKS)
SVG: 106865165(MKKS)
MMEA: 130583535(MKKS) 130583542
HRT: 120749873(MKKS) 131378509
FPG: 101917754(MKKS)
FCH: 102053778(MKKS)
CLV: 102098132(MKKS)
EGZ: 104132999(MKKS)
NNI: 104022437(MKKS)
PCRI: 104030832(MKKS)
PLET: 104620967(MKKS)
EHS: 104502440(MKKS)
PCAO: 104050868(MKKS)
ACUN: 113478115(MKKS)
TALA: 104359536
PADL: 103913120(MKKS)
AFOR: 103901616(MKKS)
ACHC: 115344467(MKKS)
HALD: 104323441(MKKS)
HLE: 104836303(MKKS)
AGEN: 126038866
GCL: 127015003
CCRI: 104154431(MKKS)
CSTI: 104549162(MKKS)
CMAC: 104484699(MKKS)
MUI: 104544971(MKKS)
BREG: 104642534(MKKS)
FGA: 104080099(MKKS)
GSTE: 104257141(MKKS)
LDI: 104350579(MKKS)
MNB: 103781631(MKKS)
OHA: 104330715(MKKS)
NNT: 104413386(MKKS)
SHAB: 115609262(MKKS)
DPUB: 104305968(MKKS)
PGUU: 104457441(MKKS)
ACAR: 104522284(MKKS)
CPEA: 104390965(MKKS)
AVIT: 104270086(MKKS)
CVF: 104287342(MKKS)
RTD: 128907640
CUCA: 104055379(MKKS)
TEO: 104369624(MKKS)
BRHI: 104493420(MKKS)
AAM: 106490423(MKKS)
AROW: 112965321(MKKS)
NPD: 112958927(MKKS)
TGT: 104578408(MKKS)
DNE: 112980028(MKKS)
SCAM: 104143474(MKKS)
ASN: 102379292(MKKS)
AMJ: 102575835(MKKS)
CPOO: 109319498(MKKS)
GGN: 109296720(MKKS)
PSS: 102458411(MKKS)
CMY: 102944088
CCAY: 125633386
DCC: 119852894
CPIC: 101951199
TST: 117874227(MKKS)
CABI: 116836502(MKKS)
MRV: 120401087(MKKS)
ACS: 100560025(mkks)
ASAO: 132781554(MKKS)
PVT: 110086122(MKKS)
SUND: 121934756
PBI: 103068070(MKKS)
CTIG: 120315295(MKKS)
TSR: 106543004(MKKS)
PGUT: 117674380(MKKS)
APRI: 131197448(MKKS)
PTEX: 113442675(MKKS)
NSS: 113412728(MKKS)
VKO: 123035740
PMUA: 114593665(MKKS)
PRAF: 128410011
ZVI: 118082490(MKKS)
HCG: 128340043(MKKS)
GJA: 107106799(MKKS)
EMC: 129341205(MKKS)
XLA: 108716568(mkks.L)
XTR: 100125210(mkks)
NPR: 108795386(MKKS)
RTEM: 120937807(MKKS)
BBUF: 120997374 120999015(MKKS)
BGAR: 122934450(MKKS) 122936115
MUO: 115465673(MKKS)
GSH: 117356865(MKKS)
DRE: 393134(mkks)
SRX: 107739894(mkks)
SGH: 107585538(mkks)
CCAR: 109099381(mkks)
CAUA: 113112513
PTET: 122356391(mkks)
LROH: 127174772(mkks)
OMC: 131551864(mkks)
PPRM: 120463916(mkks)
RKG: 130088292(mkks)
MAMB: 125277157(mkks)
CIDE: 127525556
MASI: 127414162
TROS: 130559284(mkks)
TDW: 130431807(mkks)
MANU: 129416278(mkks)
IPU: 108277806
IFU: 128621661(mkks)
PHYP: 113539393(mkks)
SMEO: 124394400(mkks)
TFD: 113642036(mkks)
TVC: 132858324(mkks)
AMEX: 111191658(mkks)
CMAO: 118816476(mkks)
EEE: 113579965(mkks)
CHAR: 105911570(mkks)
TRU: 101068226(mkks)
TFS: 130533363(mkks)
LCO: 104918214(mkks)
NCC: 104952545(mkks)
TBEN: 117499975(mkks)
CGOB: 115020091(mkks)
PGEO: 117459849(mkks)
GACU: 117553227(mkks)
ELY: 117248147(mkks)
EFO: 125903493(mkks)
PLEP: 121955012(mkks)
SLUC: 116051317(mkks)
ECRA: 117960839(mkks)
ESP: 116705048(mkks)
PFLV: 114572660(mkks)
GAT: 120820517(mkks)
PPUG: 119214123(mkks)
AFB: 129092704(mkks)
CLUM: 117744148(mkks)
SCHU: 122883984(mkks)
CUD: 121510838(mkks)
ALAT: 119033349(mkks)
MZE: 101484611(mkks)
ONL: 100690262(mkks)
OAU: 116318584(mkks)
OLA: 101167146(mkks)
OML: 112161523(mkks)
XMA: 102231474(mkks)
XCO: 114138401(mkks)
XHE: 116712839(mkks)
PRET: 103477239(mkks)
PFOR: 103137680(mkks)
PLAI: 106945336(mkks)
PMEI: 106914897(mkks)
GAF: 122842953(mkks)
PPRL: 129359821(mkks)
CVG: 107096522(mkks)
CTUL: 119782862(mkks)
GMU: 124858678(mkks)
NFU: 107375449(mkks)
KMR: 108248136(mkks)
ALIM: 106515895(mkks)
NWH: 119417702(mkks)
AOCE: 111573723(mkks)
MCEP: 125018930(mkkS)
CSEM: 103387630(mkks)
POV: 109636566(mkks)
SSEN: 122781486(mkks)
HHIP: 117775258(mkks)
HSP: 118118628(mkks)
LCF: 108885814
SDU: 111220695(mkks)
SLAL: 111658925(mkks)
XGL: 120796304(mkks)
HCQ: 109516278(mkks)
SSCV: 125978985
SBIA: 133510235(mkks)
PEE: 133410034(mkks)
PTAO: 133485620(mkks)
BPEC: 110156790(mkks)
MALB: 109961148(mkks)
BSPL: 114841972(mkks)
SJO: 128372894(mkks)
SASA: 106578777(mkks)
STRU: 115155542(mkks)
OTW: 112236517(mkks)
OMY: 110491222(mkks)
OGO: 124047515(mkks)
ONE: 115121475(mkks)
OKI: 109882733(mkks)
OKE: 118381833(mkks)
SALP: 112075000(mkks)
SNH: 120038493(mkks)
CCLU: 121558702(mkks)
ELS: 105029458(mkks)
SFM: 108926974(mkks)
PKI: 111835701(mkks)
AANG: 118217540(mkks)
LOC: 102693112(mkks)
PSPA: 121316095(mkks)
ARUT: 117402363(mkks)
PSEX: 120516505(mkks)
LCM: 102354287(MKKS)
RTP: 109915158(mkks)
CPLA: 122553089(mkks)
HOC: 132819887(mkks)
LERI: 129699277(mkks)
PMRN: 116941561(MKKS)
LRJ: 133344263(MKKS)
BFO: 118420363
BBEL: 109474910
CIN: 100181523
APLC: 110981378
SKO: 100378108
HHAL: 106680208
NLU: 111057366
MQU: 128984266
FOC: 113203499
TPAL: 117650523
ZNE: 110830743
CSEC: 111870279
PVM: 113804605
PJA: 122251916
PCHN: 125034559
PMOO: 119589520
HAME: 121863256
PCLA: 123759679
PTRU: 123519884
HAZT: 108670251
LSM: 121117341
CSCU: 111631425
PTEP: 107454230
UDV: 129220170
SDM: 118190697
LPOL: 106472374
PVUL: 126822676
PCAN: 112570011
BGT: 106065040
GAE: 121371535
HRF: 124141963
HRJ: 124287371
CRG: 105336786
CVN: 111130072
CANU: 128177376
OED: 125649995
MYI: 110454908
PMAX: 117323804
RPHI: 132743492
OBI: 106869678
OSN: 115212342
NVE: 5507417
EPA: 110242734
ATEN: 116294420
AMIL: 114950210
PDAM: 113672132
SPIS: 111335173
DGT: 114530268
HMG: 100205571
HSY: 130653593
AQU: 105312770
 » show all
Reference
  Authors
Seo S, Baye LM, Schulz NP, Beck JS, Zhang Q, Slusarski DC, Sheffield VC
  Title
BBS6, BBS10, and BBS12 form a complex with CCT/TRiC family chaperonins and mediate BBSome assembly.
  Journal
Proc Natl Acad Sci U S A 107:1488-93 (2010)
DOI:10.1073/pnas.0910268107
  Sequence
[hsa:8195]
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