ORTHOLOGY: K16749
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Entry
K16749 KO
Symbol
BBS7
Name
Bardet-Biedl syndrome 7 protein
Disease
H00418
Bardet-Biedl syndrome
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09183 Protein families: signaling and cellular processes
03037 Cilium and associated proteins
K16749 BBS7; Bardet-Biedl syndrome 7 protein
Cilium and associated proteins [BR:
ko03037
]
Primary cilia and associated proteins
BBSome
K16749 BBS7; Bardet-Biedl syndrome 7 protein
BRITE hierarchy
Other DBs
GO:
0034464
Genes
HSA:
55212
(BBS7)
PTR:
461468
(BBS7)
PPS:
100986769
(BBS7)
GGO:
101130603
(BBS7)
PON:
100454525
(BBS7)
NLE:
100589409
(BBS7)
HMH:
116463521
(BBS7)
MCC:
707478
(BBS7)
MCF:
102121516
(BBS7)
MTHB:
126955740
MNI:
105486146
(BBS7)
CSAB:
103236203
(BBS7)
CATY:
105571515
(BBS7)
PANU:
100999564
(BBS7)
TGE:
112624450
(BBS7)
MLEU:
105536887
(BBS7)
RRO:
104661789
(BBS7)
RBB:
108515585
(BBS7)
TFN:
117085860
(BBS7)
PTEH:
111546229
(BBS7)
CANG:
105516410
(BBS7)
CJC:
100387927
(BBS7)
SBQ:
101053564
(BBS7)
CIMI:
108281888
(BBS7)
CSYR:
103270885
(BBS7)
MMUR:
105882108
(BBS7)
LCAT:
123638599
(BBS7)
PCOQ:
105815250
(BBS7)
OGA:
100966803
(BBS7)
MMU:
71492
(Bbs7)
MCAL:
110291117
(Bbs7)
MPAH:
110320175
(Bbs7)
RNO:
361930
(Bbs7)
MCOC:
116095105
(Bbs7)
ANU:
117706715
(Bbs7)
MUN:
110559631
(Bbs7)
CGE:
100758793
(Bbs7)
MAUA:
101842240
(Bbs7)
PROB:
127223311
(Bbs7)
PLEU:
114707178
(Bbs7)
MORG:
121452821
(Bbs7)
MFOT:
126499254
AAMP:
119826747
(Bbs7)
NGI:
103746956
(Bbs7)
HGL:
101718716
(Bbs7)
CPOC:
100717774
(Bbs7)
CCAN:
109681817
109681819
DORD:
105989847
(Bbs7)
DSP:
122119083
(Bbs7)
PLOP:
125341518
(Bbs7)
NCAR:
124994693
MMMA:
107136569
(Bbs7)
107159502
OCU:
100356131
OPI:
101519070
(BBS7)
TUP:
102474961
(BBS7)
GVR:
103608005
(BBS7)
CFA:
476092
(BBS7)
CLUD:
112642735
(BBS7)
VVP:
112933631
(BBS7)
VLG:
121493361
(BBS7)
NPO:
129504313
(BBS7)
AML:
100482017
(BBS7)
UMR:
103661847
(BBS7)
UAH:
113255630
(BBS7)
UAR:
123793311
(BBS7)
ELK:
111154812
LLV:
125093341
MPUF:
101676084
(BBS7)
MNP:
132002818
(BBS7)
MLK:
131828514
(BBS7)
NVS:
122889166
(BBS7)
ORO:
101362928
(BBS7)
EJU:
114208261
(BBS7)
ZCA:
113924238
(BBS7)
MLX:
118022567
(BBS7)
NSU:
110573039
(BBS7)
LWW:
102730770
(BBS7)
FCA:
101088159
(BBS7)
PYU:
121030268
(BBS7)
PCOO:
112858300
(BBS7)
PBG:
122476486
(BBS7)
PVIV:
125163537
(BBS7)
LRUF:
124521028
PTG:
102958839
(BBS7)
PPAD:
109248819
(BBS7)
PUC:
125918222
125918224
AJU:
106977099
HHV:
120238028
(BBS7)
BTA:
100138953
(BBS7)
BOM:
102273308
(BBS7)
BIU:
109560205
(BBS7)
BBUB:
102393575
(BBS7)
BBIS:
105001882
(BBS7)
CHX:
102188122
(BBS7)
OAS:
101107867
(BBS7)
BTAX:
128049808
(BBS7)
ODA:
120861662
(BBS7)
CCAD:
122422111
(BBS7)
MBEZ:
129561792
(BBS7)
CFR:
102513415
(BBS7)
CBAI:
105067119
(BBS7)
CDK:
105093660
(BBS7)
VPC:
102534471
(BBS7)
BACU:
103020086
(BBS7)
BMUS:
118895370
(BBS7)
LVE:
103073155
(BBS7)
OOR:
101273341
(BBS7)
DLE:
111186110
(BBS7)
PCAD:
102986883
(BBS7)
PSIU:
116754139
(BBS7)
NASI:
112399816
(BBS7)
ECB:
100063923
(BBS7)
EPZ:
103559558
(BBS7)
EAI:
106834072
(BBS7)
MYB:
102251685
(BBS7)
MYD:
102755671
(BBS7)
MMYO:
118659023
(BBS7)
MLF:
102442216
(BBS7)
PKL:
118725963
(BBS7)
EFUS:
103301645
(BBS7)
MNA:
107528450
(BBS7)
DRO:
112312343
(BBS7)
SHON:
118995491
(BBS7)
AJM:
119037628
(BBS7)
PDIC:
114502926
(BBS7)
PHAS:
123813710
(BBS7)
MMF:
118616092
(BBS7)
PPAM:
129062533
(BBS7)
HAI:
109396564
(BBS7)
RFQ:
117037815
(BBS7)
PALE:
102894334
(BBS7)
PGIG:
120616220
(BBS7)
PVP:
105302211
(BBS7)
RAY:
107521203
(BBS7)
MJV:
108400100
(BBS7)
TOD:
119234609
(BBS7)
SARA:
101554828
(BBS7)
LAV:
100670426
(BBS7)
TMU:
101359229
ETF:
101644861
(BBS7)
DNM:
101416119
(BBS7)
MDO:
100011060
(BBS7)
GAS:
123251141
(BBS7)
SHR:
100913620
(BBS7)
AFZ:
127541194
PCW:
110222991
(BBS7)
OAA:
100081581
(BBS7)
GGA:
771481
(BBS7)
PCOC:
116231226
(BBS7)
MGP:
100551304
(BBS7)
CJO:
107313560
(BBS7)
TPAI:
128080262
(BBS7)
LMUT:
125692049
(BBS7)
NMEL:
110397624
(BBS7)
APLA:
101797526
(BBS7)
ACYG:
106042456
(BBS7)
CATA:
118251148
(BBS7)
AFUL:
116489189
(BBS7)
TGU:
100232493
(BBS7)
LSR:
110484344
(BBS7)
SCAN:
103821412
(BBS7)
PMOA:
120508909
(BBS7)
OTC:
121339891
(BBS7)
PRUF:
121361546
(BBS7)
GFR:
102035191
(BBS7)
FAB:
101807759
(BBS7)
OMA:
130252448
(BBS7)
PHI:
102105763
(BBS7)
PMAJ:
107203022
(BBS7)
CCAE:
111929081
(BBS7)
CCW:
104693710
(BBS7)
CBRC:
103617446
(BBS7)
ETL:
114067395
(BBS7)
ZAB:
102073805
(BBS7)
ACHL:
103802107
(BBS7)
SVG:
106859430
(BBS7)
MMEA:
130582078
(BBS7)
HRT:
120753340
(BBS7)
FPG:
101923262
(BBS7)
FCH:
102058128
(BBS7)
CLV:
102094191
(BBS7)
EGZ:
104129321
(BBS7)
NNI:
104019144
(BBS7)
PCRI:
104037453
(BBS7)
PLET:
104624180
(BBS7)
EHS:
104502683
(BBS7)
PCAO:
104051779
(BBS7)
ACUN:
113479519
(BBS7)
TALA:
104355519
(BBS7)
PADL:
103926136
(BBS7)
AFOR:
103907359
(BBS7)
ACHC:
115344348
(BBS7)
HALD:
104317916
(BBS7)
HLE:
104836818
(BBS7)
AGEN:
126044840
GCL:
127015691
CCRI:
104164205
(BBS7)
CSTI:
104549384
(BBS7)
CMAC:
104483293
(BBS7)
BREG:
104629261
(BBS7)
FGA:
104069471
(BBS7)
GSTE:
104250865
(BBS7)
LDI:
104342968
(BBS7)
MNB:
103775010
(BBS7)
OHA:
104331424
(BBS7)
NNT:
104403919
(BBS7)
SHAB:
115605222
(BBS7)
DPUB:
104296213
(BBS7)
PGUU:
104457763
(BBS7)
ACAR:
104517589
(BBS7)
CPEA:
104389562
(BBS7)
AVIT:
104267195
(BBS7)
CVF:
104289005
(BBS7)
RTD:
128910046
(BBS7)
CUCA:
104065746
(BBS7)
TEO:
104383537
(BBS7)
BRHI:
104498656
(BBS7)
AAM:
106492041
(BBS7)
AROW:
112973508
(BBS7)
NPD:
112950245
(BBS7)
TGT:
104578070
(BBS7)
DNE:
112980902
(BBS7)
SCAM:
104144046
(BBS7)
ASN:
102388483
(BBS7)
AMJ:
102568308
(BBS7)
CPOO:
109309326
(BBS7)
GGN:
109301139
(BBS7)
PSS:
102459163
(BBS7)
CMY:
102946988
(BBS7)
CCAY:
125635469
(BBS7)
DCC:
119854610
(BBS7)
CPIC:
101941651
(BBS7)
TST:
117878008
(BBS7)
CABI:
116822279
(BBS7)
MRV:
120406662
(BBS7)
ACS:
100565577
(bbs7)
ASAO:
132777262
(BBS7)
PVT:
110072823
(BBS7)
SUND:
121932054
(BBS7)
PBI:
103066709
PMUR:
107296601
(BBS7)
CTIG:
120297483
(BBS7)
TSR:
106549541
(BBS7)
PGUT:
117680174
(BBS7)
APRI:
131202944
(BBS7)
PTEX:
113434688
(BBS7)
NSS:
113411806
(BBS7)
VKO:
123023008
(BBS7)
PMUA:
114603942
(BBS7)
PRAF:
128421145
(BBS7)
ZVI:
118084072
(BBS7)
HCG:
128327328
(BBS7)
GJA:
107115400
(BBS7)
STOW:
125440244
(BBS7)
EMC:
129337058
(BBS7)
XLA:
100380993
(bbs7.L)
XTR:
100125216
(bbs7)
NPR:
108793715
(BBS7)
RTEM:
120918661
(BBS7)
BBUF:
120989942
(BBS7)
BGAR:
122943926
(BBS7)
MUO:
115461739
(BBS7)
GSH:
117357538
(BBS7)
DRE:
557491
(bbs7)
SRX:
107741577
107756470
SANH:
107680674
107694969
SGH:
107550842
107575872
107601472
(bbs7)
CCAR:
109058789
109101563
CAUA:
113114048
(bbs7)
CGIB:
127971151
PTET:
122357308
(bbs7)
LROH:
127176530
(bbs7)
OMC:
131553391
(bbs7)
PPRM:
120461125
(bbs7)
RKG:
130089744
(bbs7)
MAMB:
125259038
(bbs7)
CIDE:
127494734
MASI:
127413037
127417894
TROS:
130563778
(bbs7)
TDW:
130438367
(bbs7)
MANU:
129422122
(bbs7)
IPU:
108269152
IFU:
128611904
(bbs7)
PHYP:
113542683
(bbs7)
SMEO:
124386408
(bbs7)
TFD:
113647672
(bbs7)
TVC:
132855794
(bbs7)
AMEX:
103037676
(bbs7)
CMAO:
118807024
(bbs7)
EEE:
113570761
(bbs7)
CHAR:
105904380
(bbs7)
TRU:
101069996
(bbs7)
TFS:
130531261
(bbs7)
TNG:
GSTEN00024451G001
LCO:
104919405
(bbs7)
NCC:
104957163
(bbs7)
TBEN:
117485219
(bbs7)
CGOB:
115014582
(bbs7)
PGEO:
117453884
(bbs7)
GACU:
117535099
(bbs7)
EMAC:
134859346
(bbs7)
ELY:
117260684
(bbs7)
EFO:
125894282
(bbs7)
PLEP:
121948157
(bbs7)
SLUC:
116062495
(bbs7)
ECRA:
117951868
(bbs7)
ESP:
116696390
(bbs7)
PFLV:
114562871
(bbs7)
GAT:
120817611
(bbs7)
PPUG:
119211284
(bbs7)
AFB:
129090193
(bbs7)
CLUM:
117737362
(bbs7)
PSWI:
130210187
(bbs7)
MSAM:
119888365
(bbs7)
SCHU:
122880588
(bbs7)
CUD:
121515963
(bbs7)
ALAT:
119007799
(bbs7)
MZE:
101477287
(bbs7)
ONL:
100693153
(bbs7)
OAU:
116322819
(bbs7)
OLA:
101166368
(bbs7)
OML:
112145460
(bbs7)
CSAI:
133447453
(bbs7)
XMA:
102231681
(bbs7)
XCO:
114139205
(bbs7)
XHE:
116714443
(bbs7)
PRET:
103471862
(bbs7)
PFOR:
103137312
(bbs7)
PLAI:
106937634
(bbs7)
PMEI:
106932371
(bbs7)
GAF:
122836717
(bbs7)
PPRL:
129360246
129360248
CVG:
107089171
(bbs7)
CTUL:
119798501
(bbs7)
GMU:
124859866
(bbs7)
NFU:
107380167
(bbs7)
KMR:
108236618
(bbs7)
ALIM:
106525881
(bbs7)
NWH:
119408760
(bbs7)
AOCE:
111578175
(bbs7)
MCEP:
125008158
(bbs7)
CSEM:
103390717
(bbs7)
POV:
109640436
(bbs7)
SSEN:
122778647
(bbs7)
HHIP:
117769625
(bbs7)
HSP:
118111837
(bbs7)
SMAU:
118319895
(bbs7)
LCF:
108901510
SDU:
111232636
(bbs7)
SLAL:
111644670
(bbs7)
111650293
XGL:
120784908
(bbs7)
HCQ:
109526267
(bbs7)
SSCV:
125990854
SBIA:
133508513
(bbs7)
PEE:
133407685
(bbs7)
PTAO:
133484635
(bbs7)
BPEC:
110153739
(bbs7)
MALB:
109958100
(bbs7)
BSPL:
114864880
(bbs7)
SJO:
128362486
128362487
(bbs7)
SASA:
100380351
(bbs7)
STRU:
115170264
(bbs7)
OTW:
112221068
(bbs7)
OMY:
110488949
(bbs7)
OGO:
123994123
(bbs7)
ONE:
115130832
(bbs7)
OKI:
109864861
(bbs7)
OKE:
118379854
(bbs7)
SALP:
111965848
(bbs7)
SNH:
120047414
(bbs7)
CCLU:
121535334
121540523
(bbs7)
ELS:
105026041
(bbs7)
SFM:
108930793
(bbs7)
PKI:
111833029
(bbs7)
AANG:
118231161
(bbs7)
LOC:
102692741
(bbs7)
PSPA:
121329021
(bbs7)
ARUT:
117409624
PSEX:
120527630
(bbs7)
LCM:
102363432
(BBS7)
CMK:
103188314
(bbs7)
CPLA:
122539325
(bbs7)
HOC:
132833240
(bbs7)
LERI:
129704187
(bbs7)
PMRN:
116942904
(BBS7)
LRJ:
133342932
(BBS7)
BFO:
118419720
BBEL:
109487694
CIN:
100177775
SCLV:
120340727
SPU:
586040
LPIC:
129260920
APLC:
110977234
AJC:
117108154
SKO:
102808648
ECOE:
129942800
AGA:
1280761
ACOZ:
120958252
AARA:
120903626
AMER:
121600430
ASTE:
118508064
AFUN:
125770151
AMOU:
128296882
AALI:
118462725
AAG:
5567459
AALB:
109410746
CPII:
120428793
CNS:
116340255
BCOO:
119074329
AME:
411651
ACER:
107996490
ALAB:
122717062
ADR:
102674982
AFLR:
100863061
BIM:
100744730
BBIF:
117214271
BVK:
117242434
BVAN:
117161107
BTER:
100643183
BAFF:
126925501
BPYO:
122576486
BPAS:
132914505
FVI:
122535719
CCAL:
108623584
OBB:
114876656
OLG:
117606669
MGEN:
117224025
NMEA:
116426002
CGIG:
122400093
SOC:
105193046
MPHA:
105834627
AEC:
105153974
ACEP:
105618043
PBAR:
105433011
VEM:
105563405
HST:
105189730
DQU:
106741821
CFO:
105258259
FEX:
115242330
LHU:
105673346
PGC:
109858818
OBO:
105282486
PCF:
106788277
PFUC:
122515496
VPS:
122635712
VCRB:
124428442
VVE:
124956209
NVI:
100119413
CSOL:
105362660
TPRE:
106651140
LHT:
122508629
LBD:
127281116
MDL:
103573603
CGLO:
123270968
FAS:
105264361
DAM:
107038702
AGIF:
122859575
CINS:
118071372
VCAN:
122407061
CCIN:
107268072
DSM:
124412704
NPT:
124221017
NFB:
124184239
NLO:
107221102
NVG:
124306829
AROA:
105693122
TCA:
664027
DPA:
109543098
SOY:
115875831
AGRG:
126744637
ATD:
109595854
CSET:
123309901
AGB:
108909012
LDC:
111507065
NVL:
108562218
PPYR:
116168026
OTU:
111415792
BMOR:
101735609
BMAN:
114245278
MSEX:
115452324
DPL:
KGM_207476
BANY:
112053640
MJU:
123866163
NIQ:
126781801
VCD:
124544418
MCIX:
123669870
PMAC:
106708593
PPOT:
106100703
PXU:
106123319
PRAP:
110996540
ZCE:
119833470
LSIN:
126970557
HAW:
110372376
HZE:
124632645
TNL:
113508378
SLIU:
111358575
OFU:
114354743
PGW:
126366383
CFEL:
113385640
113385642
CCRN:
123293266
API:
103309366
DNX:
107171562
AGS:
114132426
114132703
RMD:
113552095
ACOO:
126843316
DVT:
126897059
BTAB:
109044405
DCI:
103512178
CLEC:
106668881
HHAL:
106679067
NLU:
111055874
HVI:
124357459
MQU:
128984543
128984555
PHU:
Phum_PHUM123960
FOC:
113209002
TPAL:
117647518
ZNE:
110834249
CSEC:
111865741
SGRE:
126281937
BROR:
134536659
IEL:
124162789
FCD:
110843279
DPX:
DAPPUDRAFT_197260
DMK:
123469580
DPZ:
124314019
PVM:
113829942
PJA:
122263479
PCHN:
125043768
PMOO:
119585838
HAME:
121869186
PCLA:
123753996
CQD:
128700598
PTRU:
123505176
ESN:
126981344
HAZT:
108666492
EAF:
111711634
LSM:
121119973
TCF:
131878561
PPOI:
119091976
DSV:
119449347
RSAN:
119381037
RMP:
119162682
VDE:
111253335
VJA:
111266666
TUT:
107367089
107367848
DPTE:
113793787
DFR:
124490255
CSCU:
111620296
PTEP:
107449211
ABRU:
129968667
UDV:
129218341
SDM:
118182145
LPOL:
106476094
CEL:
CELE_Y75B8A.12
(osm-12)
CBR:
CBG_23043
(Cbr-osm-12)
CRQ:
GCK72_008348
NAI:
NECAME_17284
BMY:
BM_BM7137
(Bma-osm-12)
LOA:
LOAG_07257
TSP:
Tsp_06914
HRO:
HELRODRAFT_80019
LGI:
LOTGIDRAFT_223884
PVUL:
126830005
PCAN:
112560110
BGT:
106065200
GAE:
121375264
HRF:
124110473
HRJ:
124289479
CRG:
105336556
CVN:
111125668
CANU:
128156151
OED:
125679190
MYI:
110447191
PMAX:
117329201
MCAF:
127728289
MMER:
123556345
RPHI:
132731911
132738223
132754411
DPOL:
127858134
127858939
OBI:
106877720
OSN:
115218520
LAK:
106175948
SMM:
Smp_138120
SHX:
MS3_00004889
(BBS7)
OVI:
T265_00173
NVE:
5513507
EPA:
110242536
ATEN:
116305782
ADF:
107352122
AMIL:
114977677
PDAM:
113676810
SPIS:
111327219
DGT:
114524462
XEN:
124446358
HMG:
100214695
HSY:
130648677
TAD:
TRIADDRAFT_25051
AQU:
100639559
CRE:
CHLRE_01g043750v5
MNG:
MNEG_3162
MIS:
MICPUN_100192
MPP:
MICPUCDRAFT_16331
(JGI:MicpuC2_16331)
SRE:
PTSG_09820
TET:
TTHERM_00655860
PTM:
GSPATT00026091001
SMIN:
v1.2.012081.t1
(symbB.v1.2.012081.t1)
v1.2.012082.t1
(symbB.v1.2.012082.t1)
AAF:
AURANDRAFT_22539
PIF:
PITG_01067
PSOJ:
PHYSODRAFT_538781
SPAR:
SPRG_00356
GTT:
GUITHDRAFT_103854
TBR:
Tb927.3.3640
TBG:
TbgDal_III3940
TCR:
503811.70
506989.130
LMA:
LMJF_29_0710
LIF:
LINJ_29_0740
LDO:
LDBPK_290740
LMI:
LMXM_08_29_0710
LBZ:
LBRM_29_0720
LPAN:
LPMP_290700
NGR:
NAEGRDRAFT_68114
TVA:
TVAG_2v0966990
» show all
Taxonomy
UniProt
Reference
PMID:
18000879
Authors
Oeffner F, Moch C, Neundorf A, Hofmann J, Koch M, Grzeschik KH
Title
Novel interaction partners of Bardet-Biedl syndrome proteins.
Journal
Cell Motil Cytoskeleton 65:143-55 (2008)
DOI:
10.1002/cm.20250
Sequence
[hsa:
55212
]
Reference
PMID:
17574030
Authors
Nachury MV, Loktev AV, Zhang Q, Westlake CJ, Peranen J, Merdes A, Slusarski DC, Scheller RH, Bazan JF, Sheffield VC, Jackson PK
Title
A core complex of BBS proteins cooperates with the GTPase Rab8 to promote ciliary membrane biogenesis.
Journal
Cell 129:1201-13 (2007)
DOI:
10.1016/j.cell.2007.03.053
Sequence
[hsa:
55212
]
LinkDB
All DBs
DBGET
integrated database retrieval system