PATHWAY: ko00650
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Entry
ko00650 Pathway
Name
Butanoate metabolism
Class
Metabolism; Carbohydrate metabolism
BRITE hierarchy
Pathway map
ko00650
Butanoate metabolism
Ortholog table
Module
M00027
GABA (gamma-Aminobutyrate) shunt [PATH:
ko00650
]
Disease
H00179
3-Hydroxy-3-methylglutaryl-CoA lyase deficiency
H00835
Succinic semialdehyde dehydrogenase deficiency
H01121
Succinyl CoA:3-oxoacid CoA transferase (SCOT) deficiency
H01123
HMG-CoA synthase deficiency
H01280
L-2-hydroxyglutaric aciduria
H01364
3-Hydroxyacyl-CoA dehydrogenase deficiency
Orthology
K00626
acetyl-CoA C-acetyltransferase [EC:
2.3.1.9
]
K00074
3-hydroxybutyryl-CoA dehydrogenase [EC:
1.1.1.157
]
K00022
3-hydroxyacyl-CoA dehydrogenase [EC:
1.1.1.35
]
K07516
3-hydroxyacyl-CoA dehydrogenase [EC:
1.1.1.35
]
K01825
3-hydroxyacyl-CoA dehydrogenase / enoyl-CoA hydratase / 3-hydroxybutyryl-CoA epimerase / enoyl-CoA isomerase [EC:
1.1.1.35
4.2.1.17
5.1.2.3
5.3.3.8
]
K01782
3-hydroxyacyl-CoA dehydrogenase / enoyl-CoA hydratase / 3-hydroxybutyryl-CoA epimerase [EC:
1.1.1.35
4.2.1.17
5.1.2.3
]
K01692
enoyl-CoA hydratase [EC:
4.2.1.17
]
K01715
enoyl-CoA hydratase [EC:
4.2.1.17
]
K07515
enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:
4.2.1.17
1.1.1.211
]
K07514
enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:
4.2.1.17
1.1.1.35
5.3.3.8
]
K07511
enoyl-CoA hydratase [EC:
4.2.1.17
]
K00248
butyryl-CoA dehydrogenase [EC:
1.3.8.1
]
K00209
enoyl-[acyl-carrier protein] reductase / trans-2-enoyl-CoA reductase (NAD+) [EC:
1.3.1.9
1.3.1.44
]
K17829
crotonyl-CoA reductase [EC:
1.3.1.86
]
K01034
acetate CoA/acetoacetate CoA-transferase alpha subunit [EC:
2.8.3.8
2.8.3.9
]
K01035
acetate CoA/acetoacetate CoA-transferase beta subunit [EC:
2.8.3.8
2.8.3.9
]
K19709
acetate CoA-transferase [EC:
2.8.3.8
]
K23756
medium-chain acyl-CoA ligase / lipoate-activating enzyme [EC:
6.2.1.2
]
K01896
medium-chain acyl-CoA synthetase [EC:
6.2.1.2
]
K01913
acetate/butyrate---CoA ligase [EC:
6.2.1.1
6.2.1.2
]
K00929
butyrate kinase [EC:
2.7.2.7
]
K00634
phosphate butyryltransferase [EC:
2.3.1.19
]
K00132
acetaldehyde dehydrogenase (acetylating) [EC:
1.2.1.10
]
K04072
acetaldehyde dehydrogenase / alcohol dehydrogenase [EC:
1.2.1.10
1.1.1.1
]
K04073
acetaldehyde dehydrogenase [EC:
1.2.1.10
]
K18366
acetaldehyde/propanal dehydrogenase [EC:
1.2.1.10
1.2.1.87
]
K00100
butanol dehydrogenase [EC:1.1.1.-]
K21317
butane monooxygenase alpha subunit [EC:
1.14.13.230
]
K21318
butane monooxygenase beta subunit [EC:
1.14.13.230
]
K21319
butane monooxygenase gamma subunit [EC:
1.14.13.230
]
K21320
butane monooxygenase reductase
K21321
butane monooxygenase regulatory protein
K21322
butane monooxygenase hypothetical assembly protein
K17865
3-hydroxybutyryl-CoA dehydratase [EC:
4.2.1.55
]
K03821
polyhydroxyalkanoate synthase subunit PhaC [EC:2.3.1.-]
K22881
polyhydroxyalkanoate synthase subunit PhaE
K05973
poly(3-hydroxybutyrate) depolymerase [EC:
3.1.1.75
]
K00023
acetoacetyl-CoA reductase [EC:
1.1.1.36
]
K01615
glutaconyl-CoA decarboxylase subunit alpha [EC:
7.2.4.5
]
K20509
carboxybiotin decarboxylase [EC:
7.2.4.1
]
K23351
glutaconyl-CoA/methylmalonyl-CoA decarboxylase subunit gamma
K23352
glutaconyl-CoA/methylmalonyl-CoA decarboxylase subunit delta
K01039
glutaconate CoA-transferase, subunit A [EC:
2.8.3.12
]
K01040
glutaconate CoA-transferase, subunit B [EC:
2.8.3.12
]
K00109
2-hydroxyglutarate dehydrogenase [EC:
1.1.99.2
]
K07246
tartrate dehydrogenase/decarboxylase / D-malate dehydrogenase [EC:
1.1.1.93
4.1.1.73
1.1.1.83
]
K01799
maleate isomerase [EC:
5.2.1.1
]
K00239
succinate dehydrogenase / fumarate reductase, flavoprotein subunit [EC:
1.3.5.1
1.3.5.4
]
K00240
succinate dehydrogenase / fumarate reductase, iron-sulfur subunit [EC:
1.3.5.1
1.3.5.4
]
K00241
succinate dehydrogenase / fumarate reductase, cytochrome b subunit
K00242
succinate dehydrogenase / fumarate reductase, membrane anchor subunit
K18859
succinate dehydrogenase / fumarate reductase, subunit D
K18860
putative succinate dehydrogenase / fumarate reductase, subunit D
K00244
fumarate reductase flavoprotein subunit [EC:
1.3.5.4
]
K00245
fumarate reductase iron-sulfur subunit [EC:
1.3.5.4
]
K00246
fumarate reductase subunit C
K00247
fumarate reductase subunit D
K01580
glutamate decarboxylase [EC:
4.1.1.15
]
K00823
4-aminobutyrate aminotransferase [EC:
2.6.1.19
]
K14268
5-aminovalerate/4-aminobutyrate aminotransferase [EC:
2.6.1.48
2.6.1.19
]
K07250
4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase / 5-aminovalerate transaminase [EC:
2.6.1.19
2.6.1.22
2.6.1.48
]
K13524
4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:
2.6.1.19
2.6.1.22
]
K16871
4-aminobutyrate---pyruvate transaminase [EC:
2.6.1.96
]
K00135
succinate-semialdehyde dehydrogenase / glutarate-semialdehyde dehydrogenase [EC:
1.2.1.16
1.2.1.79
1.2.1.20
]
K00139
succinate-semialdehyde dehydrogenase [EC:
1.2.1.24
]
K17761
succinate-semialdehyde dehydrogenase, mitochondrial [EC:
1.2.1.24
]
K08324
succinate-semialdehyde dehydrogenase [EC:
1.2.1.16
1.2.1.24
]
K18118
succinyl-CoA:acetate CoA-transferase [EC:
2.8.3.18
]
K18119
succinate-semialdehyde dehydrogenase [EC:
1.2.1.76
]
K18120
4-hydroxybutyrate dehydrogenase [EC:
1.1.1.61
]
K00043
4-hydroxybutyrate dehydrogenase [EC:
1.1.1.61
]
K08318
4-hydroxybutyrate dehydrogenase / sulfolactaldehyde 3-reductase [EC:
1.1.1.61
1.1.1.373
]
K18121
glyoxylate/succinic semialdehyde reductase [EC:
1.1.1.79
1.1.1.-]
K18122
4-hydroxybutyrate CoA-transferase [EC:2.8.3.-]
K14534
4-hydroxybutyryl-CoA dehydratase / vinylacetyl-CoA-Delta-isomerase [EC:
4.2.1.120
5.3.3.3
]
K00656
formate C-acetyltransferase [EC:
2.3.1.54
]
K00169
pyruvate ferredoxin oxidoreductase alpha subunit [EC:
1.2.7.1
]
K00170
pyruvate ferredoxin oxidoreductase beta subunit [EC:
1.2.7.1
]
K00172
pyruvate ferredoxin oxidoreductase gamma subunit [EC:
1.2.7.1
]
K00189
2-oxoisovalerate/pyruvate ferredoxin oxidoreductase gamma subunit [EC:
1.2.7.7
1.2.7.1
]
K00171
pyruvate ferredoxin oxidoreductase delta subunit [EC:
1.2.7.1
]
K03737
pyruvate-ferredoxin/flavodoxin oxidoreductase [EC:
1.2.7.1
1.2.7.-]
K00174
2-oxoglutarate/2-oxoacid ferredoxin oxidoreductase subunit alpha [EC:
1.2.7.3
1.2.7.11
]
K00175
2-oxoglutarate/2-oxoacid ferredoxin oxidoreductase subunit beta [EC:
1.2.7.3
1.2.7.11
]
K01641
hydroxymethylglutaryl-CoA synthase [EC:
2.3.3.10
]
K01640
hydroxymethylglutaryl-CoA lyase [EC:
4.1.3.4
]
K01027
3-oxoacid CoA-transferase [EC:
2.8.3.5
]
K01028
3-oxoacid CoA-transferase subunit A [EC:
2.8.3.5
]
K01029
3-oxoacid CoA-transferase subunit B [EC:
2.8.3.5
]
K01907
acetoacetyl-CoA synthetase [EC:
6.2.1.16
]
K00019
3-hydroxybutyrate dehydrogenase [EC:
1.1.1.30
]
K07518
hydroxybutyrate-dimer hydrolase [EC:
3.1.1.22
]
K01652
acetolactate synthase I/II/III large subunit [EC:
2.2.1.6
]
K01653
acetolactate synthase I/III small subunit [EC:
2.2.1.6
]
K11258
acetolactate synthase II small subunit [EC:
2.2.1.6
]
K01575
acetolactate decarboxylase [EC:
4.1.1.5
]
K00004
(R,R)-butanediol dehydrogenase / meso-butanediol dehydrogenase / diacetyl reductase [EC:
1.1.1.4
1.1.1.-
1.1.1.303
]
K03366
meso-butanediol dehydrogenase / (S,S)-butanediol dehydrogenase / diacetyl reductase [EC:1.1.1.-
1.1.1.76
1.1.1.304
]
K18009
meso-butanediol dehydrogenase / (S,S)-butanediol dehydrogenase / diacetyl reductase [EC:1.1.1.-
1.1.1.76
1.1.1.304
]
Compound
C00022
Pyruvate
C00024
Acetyl-CoA
C00025
L-Glutamate
C00026
2-Oxoglutarate
C00042
Succinate
C00091
Succinyl-CoA
C00122
Fumarate
C00136
Butanoyl-CoA
C00164
Acetoacetate
C00232
Succinate semialdehyde
C00246
Butanoic acid
C00332
Acetoacetyl-CoA
C00334
4-Aminobutanoate
C00356
(S)-3-Hydroxy-3-methylglutaryl-CoA
C00497
(R)-Malate
C00741
Diacetyl
C00810
(R)-Acetoin
C00877
Crotonoyl-CoA
C00989
4-Hydroxybutanoic acid
C01089
(R)-3-Hydroxybutanoate
C01144
(S)-3-Hydroxybutanoyl-CoA
C01384
Maleic acid
C01412
Butanal
C01769
(S)-Acetoin
C02331
Vinylacetyl-CoA
C02411
Glutaconyl-1-CoA
C02527
Butanoylphosphate
C02630
2-Hydroxyglutarate
C03044
(R,R)-Butane-2,3-diol
C03046
(S,S)-Butane-2,3-diol
C03058
2-Hydroxyglutaryl-CoA
C03561
(R)-3-Hydroxybutanoyl-CoA
C04546
(R)-3-((R)-3-Hydroxybutanoyloxy)butanoate
C06010
(S)-2-Acetolactate
C06142
1-Butanol
C06143
Poly-beta-hydroxybutyrate
C06144
3-Butynoate
C06145
3-Butyn-1-al
C06146
3-Butyn-1-ol
C11062
4-Hydroxybutyryl-CoA
C20657
meso-2,3-Butanediol
C21390
Butane
Related
pathway
ko00010
Glycolysis / Gluconeogenesis
ko00020
Citrate cycle (TCA cycle)
ko00072
Synthesis and degradation of ketone bodies
ko00250
Alanine, aspartate and glutamate metabolism
ko00330
Arginine and proline metabolism
ko00620
Pyruvate metabolism
ko00750
Vitamin B6 metabolism
ko01056
Biosynthesis of type II polyketide backbone
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