ORTHOLOGY: K08766
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Entry
K08766 KO
Symbol
CPT2
Name
carnitine O-palmitoyltransferase 2 [EC:
2.3.1.21
]
Pathway
map00071
Fatty acid degradation
map01212
Fatty acid metabolism
map03320
PPAR signaling pathway
map04714
Thermogenesis
map05415
Diabetic cardiomyopathy
Reaction
R01923
palmitoyl-CoA:L-carnitine O-palmitoyltransferase
Disease
H00525
Disorders of mitochondrial fatty-acid oxidation
H01400
Secondary hyperammonemia
H01982
Carnitine palmitoyltransferase II deficiency
H02536
Infection-induced acute encephalopathy
H02596
Disorders of carnitine transport and the carnitine cycle
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09103 Lipid metabolism
00071 Fatty acid degradation
K08766 CPT2; carnitine O-palmitoyltransferase 2
09150 Organismal Systems
09152 Endocrine system
03320 PPAR signaling pathway
K08766 CPT2; carnitine O-palmitoyltransferase 2
09159 Environmental adaptation
04714 Thermogenesis
K08766 CPT2; carnitine O-palmitoyltransferase 2
09160 Human Diseases
09166 Cardiovascular disease
05415 Diabetic cardiomyopathy
K08766 CPT2; carnitine O-palmitoyltransferase 2
Enzymes [BR:
ko01000
]
2. Transferases
2.3 Acyltransferases
2.3.1 Transferring groups other than aminoacyl groups
2.3.1.21 carnitine O-palmitoyltransferase
K08766 CPT2; carnitine O-palmitoyltransferase 2
BRITE hierarchy
Other DBs
GO:
0004095
Genes
HSA:
1376
(CPT2)
PTR:
737945
(CPT2)
PPS:
100983874
(CPT2)
GGO:
101147523
(CPT2)
PON:
100442465
(CPT2)
NLE:
100594710
(CPT2)
HMH:
116457918
(CPT2)
MCC:
714150
(CPT2)
MCF:
102137160
(CPT2)
MTHB:
126962177
MNI:
105495080
(CPT2)
CSAB:
103224794
(CPT2)
CATY:
105596024
(CPT2)
PANU:
101016112
(CPT2)
TGE:
112619291
(CPT2)
MLEU:
105534872
(CPT2)
RRO:
104669303
(CPT2)
RBB:
108531224
(CPT2)
TFN:
117092570
(CPT2)
PTEH:
111523578
(CPT2)
CANG:
105500687
(CPT2)
CJC:
100414414
(CPT2)
SBQ:
101033529
(CPT2)
CIMI:
108286518
(CPT2)
CSYR:
103255442
(CPT2)
MMUR:
105877579
(CPT2)
LCAT:
123635635
(CPT2)
PCOQ:
105806351
(CPT2)
OGA:
100956504
(CPT2)
MMU:
12896
(Cpt2)
MCAL:
110293183
(Cpt2)
MPAH:
110323321
(Cpt2)
RNO:
25413
(Cpt2)
MCOC:
116096366
(Cpt2)
ANU:
117709415
(Cpt2)
MUN:
110563903
(Cpt2)
CGE:
100766757
(Cpt2)
MAUA:
101836358
(Cpt2)
PROB:
127225124
(Cpt2)
PLEU:
114706193
(Cpt2)
MORG:
121448912
(Cpt2)
MFOT:
126497994
AAMP:
119817978
(Cpt2)
NGI:
103730274
(Cpt2)
HGL:
101709766
(Cpt2)
CPOC:
100728173
(Cpt2)
CCAN:
109682869
(Cpt2)
DORD:
105990026
(Cpt2)
DSP:
122104937
(Cpt2)
PLOP:
125355174
(Cpt2)
NCAR:
124963347
MMMA:
107141751
(Cpt2)
OCU:
100346210
OPI:
101522484
(CPT2)
TUP:
102485726
(CPT2)
GVR:
103602728
(CPT2)
CFA:
489585
(CPT2)
CLUD:
112647046
(CPT2)
125755872
VVP:
112926120
(CPT2)
VLG:
121499528
(CPT2)
NPO:
129497587
(CPT2)
AML:
100465139
(CPT2)
UMR:
103670701
(CPT2)
UAH:
113254653
(CPT2)
UAR:
123793680
(CPT2)
ELK:
111142846
LLV:
125096962
MPUF:
101681793
(CPT2)
MNP:
132000891
(CPT2)
MLK:
131808846
(CPT2)
NVS:
122899986
(CPT2)
ORO:
101367746
(CPT2)
EJU:
114212164
(CPT2)
ZCA:
113911907
(CPT2)
MLX:
118019395
(CPT2)
NSU:
110575297
(CPT2)
LWW:
102742053
(CPT2)
FCA:
101093287
(CPT2)
PYU:
121027147
(CPT2)
PCOO:
112863689
(CPT2)
PBG:
122480515
(CPT2)
LRUF:
124515655
PTG:
102948684
(CPT2)
PPAD:
109266859
(CPT2)
PUC:
125912600
AJU:
106975005
HHV:
120236239
(CPT2)
BTA:
504502
(CPT2)
BOM:
102281690
(CPT2)
BIU:
109556280
(CPT2)
BBUB:
102411862
(CPT2)
BBIS:
104993770
(CPT2)
CHX:
102180988
(CPT2)
OAS:
101118317
(CPT2)
BTAX:
128044653
(CPT2)
ODA:
120856131
(CPT2)
CCAD:
122436958
(CPT2)
MBEZ:
129540285
(CPT2)
SSC:
100519491
(CPT2)
CFR:
102519937
(CPT2)
CBAI:
105066439
(CPT2)
CDK:
105090776
(CPT2)
VPC:
102532414
(CPT2)
BACU:
103007290
(CPT2)
LVE:
103082924
(CPT2)
OOR:
101278411
(CPT2)
DLE:
111175829
(CPT2)
PCAD:
102989455
(CPT2)
PSIU:
116758829
(CPT2)
NASI:
112395846
(CPT2)
ECB:
100061061
(CPT2)
EPZ:
103558611
(CPT2)
EAI:
106833186
(CPT2)
MYB:
102243793
(CPT2)
MYD:
102766661
(CPT2)
MMYO:
118676036
(CPT2)
MLF:
102432707
(CPT2)
MNA:
107535396
(CPT2)
PKL:
118722909
(CPT2)
EFUS:
103284008
(CPT2)
HAI:
109395421
(CPT2)
DRO:
112314640
(CPT2)
SHON:
118984981
(CPT2)
AJM:
119061379
(CPT2)
PDIC:
114497429
(CPT2)
PHAS:
123830877
(CPT2)
MMF:
118626083
(CPT2)
RFQ:
117026851
(CPT2)
PPAM:
129070312
(CPT2)
PALE:
102886099
(CPT2)
PGIG:
120621294
(CPT2)
PVP:
105298970
(CPT2)
RAY:
107497952
(CPT2)
MJV:
108409318
(CPT2)
TOD:
119236194
(CPT2)
SARA:
101539844
(CPT2)
LAV:
100665512
(CPT2)
TMU:
101355326
ETF:
101656559
(CPT2)
DNM:
101428085
(CPT2)
MDO:
100010920
100017404
(CPT2)
100017446
GAS:
123231390
123244458
(CPT2)
123245804
SHR:
100921521
(CPT2)
100921785
100927393
AFZ:
127559866
127563303
127563306
PCW:
110209363
110209364
(CPT2)
110223414
OAA:
100077549
100083175
(CPT2)
100083621
100093378
GGA:
424649
(CPT2)
PCOC:
116234831
(CPT2)
MGP:
100540756
(CPT2)
CJO:
107317653
(CPT2)
TPAI:
128072222
(CPT2)
LMUT:
125693112
(CPT2)
NMEL:
110402524
(CPT2)
APLA:
101804289
(CPT2)
ACYG:
106033001
(CPT2)
CATA:
118243379
(CPT2)
AFUL:
116491766
(CPT2)
TGU:
100222209
(CPT2)
LSR:
110470169
(CPT2)
SCAN:
103815033
(CPT2)
PMOA:
120503334
(CPT2)
OTC:
121344939
(CPT2)
PRUF:
121361908
(CPT2)
FAB:
101821336
(CPT2)
OMA:
130255946
(CPT2)
PHI:
102106295
(CPT2)
PMAJ:
107208252
(CPT2)
CCAE:
111944660
(CPT2)
CCW:
104695521
(CPT2)
CBRC:
103615087
(CPT2)
ETL:
114062806
(CPT2)
ZAB:
102061542
(CPT2)
ACHL:
103799595
(CPT2)
SVG:
106849769
(CPT2)
MMEA:
130574052
(CPT2)
HRT:
120756429
(CPT2)
FPG:
101916680
(CPT2)
FCH:
102046436
(CPT2)
CLV:
102085732
(CPT2)
EGZ:
104131502
(CPT2)
NNI:
104009358
(CPT2)
PCRI:
104029640
(CPT2)
PLET:
104616841
(CPT2)
EHS:
104517137
(CPT2)
PCAO:
104048209
(CPT2)
ACUN:
113483174
(CPT2)
TALA:
104363442
(CPT2)
PADL:
103913665
(CPT2)
AFOR:
103905737
(CPT2)
ACHC:
115348945
(CPT2)
HALD:
104318538
(CPT2)
HLE:
104841187
(CPT2)
AGEN:
126042295
GCL:
127018860
CCRI:
104156221
(CPT2)
CSTI:
104554662
(CPT2)
CMAC:
104487519
(CPT2)
MUI:
104534213
(CPT2)
BREG:
104631114
(CPT2)
FGA:
104071591
(CPT2)
GSTE:
104252501
(CPT2)
LDI:
104345928
(CPT2)
MNB:
103781510
(CPT2)
OHA:
104334161
(CPT2)
NNT:
104412977
(CPT2)
SHAB:
115611247
(CPT2)
DPUB:
104307049
(CPT2)
PGUU:
104459700
(CPT2)
ACAR:
104524187
(CPT2)
CPEA:
104385170
(CPT2)
AVIT:
104277659
(CPT2)
CVF:
104286244
(CPT2)
RTD:
128913546
(CPT2)
CUCA:
104060183
(CPT2)
TEO:
104379404
(CPT2)
BRHI:
104493784
(CPT2)
AAM:
106491073
(CPT2)
AROW:
112975973
(CPT2)
NPD:
112943264
(CPT2)
112951400
TGT:
104567075
104568252
(CPT2)
DNE:
112980280
112986182
(CPT2)
SCAM:
104149587
(CPT2)
104150563
ASN:
102378221
(CPT2)
102381122
(SPATA9)
AMJ:
102569677
(CPT2)
109282261
CPOO:
109307486
(CPT2)
109308122
GGN:
109286641
(CPT2)
109297225
PSS:
102453263
(CPT2)
102460096
CMY:
102932067
(CPT2)
102948102
CCAY:
125636850
125641836
(CPT2)
DCC:
119855425
119859622
(CPT2)
CPIC:
101939045
101939314
(CPT2)
TST:
117879005
117881379
(CPT2)
CABI:
116817927
(CPT2)
116835666
MRV:
120370925
(CPT2)
120407600
ACS:
100559925
(cpt2)
100564964
ASAO:
132767159
132773942
(CPT2)
PVT:
110078753
110082263
(CPT2)
SUND:
121922741
121927573
(CPT2)
PBI:
103050777
(CPT2)
103059017
PMUR:
107283066
(CPT2)
107302781
CTIG:
120297397
(CPT2)
120306723
TSR:
106546060
(CPT2)
106554574
PGUT:
117664244
(CPT2)
117679075
APRI:
131191097
131194307
(CPT2)
PTEX:
113440611
(CPT2)
113448564
NSS:
113411030
(CPT2)
113415267
VKO:
123023330
(CPT2)
123031313
PMUA:
114598982
(CPT2)
114606227
PRAF:
128415753
(CPT2)
128423630
ZVI:
118076851
118088432
(CPT2)
HCG:
128323651
(CPT2)
128343506
(SPATA9)
GJA:
107120570
(CPT2)
107124700
STOW:
125432796
(CPT2)
125436981
EMC:
129330092
(CPT2)
129335109
XLA:
108714327
(cpt2.L)
379893
(cpt2.S)
XTR:
394801
(cpt2)
NPR:
108783819
(CPT2)
RTEM:
120945904
(CPT2)
BBUF:
120979411
(CPT2)
BGAR:
122943265
(CPT2)
MUO:
115459495
115471981
(CPT2)
GSH:
117346959
(CPT2)
DRE:
100005717
(cpt2)
SRX:
107731280
107745829
SANH:
107668114
107695271
SGH:
107549124
107585892
CCAR:
109095159
109105328
CAUA:
113069936
113107223
CGIB:
127963924
128018740
PTET:
122350759
(cpt2)
LROH:
127170280
(cpt2)
OMC:
131545706
(cpt2)
PPRM:
120483056
(cpt2)
RKG:
130086195
(cpt2)
MAMB:
125279356
(cpt2)
CIDE:
127517561
MASI:
127415077
127424650
TROS:
130567955
(cpt2)
TDW:
130407212
(cpt2)
MANU:
129414201
(cpt2)
IPU:
108265663
IFU:
128607953
(cpt2)
PHYP:
113532675
(cpt2)
SMEO:
124399770
(cpt2)
TFD:
113656266
(cpt2)
TVC:
132853520
132853586
CMAO:
118813738
(cpt2)
EEE:
113581083
113581106
CHAR:
105900892
(cpt2)
TRU:
101070259
101076236
(cpt2)
101076461
115247131
115247134
115247234
TFS:
130520289
130528254
130528263
130528828
(cpt2)
130529003
TNG:
GSTEN00010632G001
GSTEN00013741G001
GSTEN00013742G001
GSTEN00020421G001
GSTEN00020422G001
LCO:
104921749
(cpt2)
NCC:
104944020
(cpt2)
TBEN:
117490933
(cpt2)
CGOB:
115006982
(cpt2)
PGEO:
117445631
(cpt2)
GACU:
117558987
(cpt2)
ELY:
117254507
(cpt2)
EFO:
125896030
(cpt2)
PLEP:
121941017
(cpt2)
SLUC:
116063212
(cpt2)
ECRA:
117949864
(cpt2)
ESP:
116695793
(cpt2)
PFLV:
114561349
(cpt2)
GAT:
120823513
(cpt2)
PPUG:
119216292
(cpt2)
AFB:
129094142
129094143
129094607
CLUM:
117729619
117730042
117731266
MSAM:
119901228
(cpt2)
SCHU:
122877265
(cpt2)
CUD:
121512408
(cpt2)
ALAT:
119028852
(cpt2)
MZE:
101474307
(cpt2)
ONL:
100706914
(cpt2)
OAU:
116334431
(cpt2)
OLA:
101167863
(cpt2)
OML:
112150667
(cpt2)
XMA:
102234740
(cpt2)
XCO:
114151224
(cpt2)
XHE:
116726163
(cpt2)
PRET:
103464005
(cpt2)
PFOR:
103139826
(cpt2)
PLAI:
106936235
(cpt2)
PMEI:
106928209
(cpt2)
GAF:
122839079
(cpt2)
PPRL:
129379692
(cpt2)
CVG:
107091690
(cpt2)
CTUL:
119787701
(cpt2)
GMU:
124874230
(cpt2)
NFU:
107387358
(cpt2)
KMR:
108246660
(cpt2)
ALIM:
106529298
(cpt2)
NWH:
119407901
(cpt2)
AOCE:
111576145
(cpt2)
MCEP:
125009004
(cpt2)
CSEM:
103399070
(cpt2)
POV:
109625365
109625820
(cpt2)
SSEN:
122780329
(cpt2)
HHIP:
117759687
117759692
HSP:
118120624
118120711
(cpt2)
LCF:
108878922
(cpt2)
108901685
SDU:
111231966
(cpt2)
SLAL:
111671960
(cpt2)
XGL:
120790499
(cpt2)
HCQ:
109516966
(cpt2)
SSCV:
125975144
SBIA:
133503908
(cpt2)
PEE:
133406462
(cpt2)
PTAO:
133480291
(cpt2)
BPEC:
110154766
(cpt2)
110155185
110155196
MALB:
109965690
(cpt2)
BSPL:
114853066
(cpt2)
SJO:
128361459
(cpt2)
SASA:
106560431
(cpt2)
STRU:
115158680
(cpt2)
OTW:
112251345
(cpt2)
OMY:
110524692
(cpt2)
OGO:
123996687
(cpt2)
ONE:
115108624
(cpt2)
OKI:
109902809
(cpt2)
OKE:
118393511
(cpt2)
SALP:
111975354
(cpt2)
SNH:
120054980
(cpt2)
CCLU:
121533851
(cpt2)
121540473
ELS:
105005902
(cpt2)
SFM:
108935158
(cpt2)
108935368
PKI:
111834941
111847544
(cpt2)
AANG:
118226614
(cpt2)
LOC:
102690419
(cpt2)
PSPA:
121326950
(cpt2)
ARUT:
117400626
(cpt2)
PSEX:
120514422
(cpt2)
LCM:
102353513
(CPT2)
CMK:
103191252
(cpt2)
RTP:
109913668
(cpt2)
CPLA:
122554389
(cpt2)
HOC:
132819075
(cpt2)
LERI:
129700991
(cpt2)
PMRN:
116956304
(CPT2)
LRJ:
133357158
133357164
BFO:
118403142
BBEL:
109461607
CIN:
100184443
SCLV:
120334893
SPU:
577810
LPIC:
129255920
129255921
APLC:
110984890
110988522
AJC:
117107835
SKO:
100367583
DME:
Dmel_CG2107
(CPT2)
DER:
6546366
DSE:
6610536
DSI:
Dsimw501_GD13716
(Dsim_GD13716)
DYA:
Dyak_GE20347
DAN:
6506889
DSR:
110185290
DPO:
4812068
DPE:
6600470
DMN:
108152712
DWI:
6639623
DGR:
6556518
DMO:
Dmoj_GI11407
DAZ:
108614616
DNV:
108652408
DHE:
111597483
DVI:
6622348
CCAT:
101449563
BOD:
106620733
BDR:
105233719
RZE:
108362965
AOQ:
129250476
TDA:
119680353
119683838
MDE:
101900258
SCAC:
106092181
LCQ:
111689180
LSQ:
119614984
GFS:
119633178
ECOE:
129953394
CLON:
129614254
HIS:
119659200
AGA:
1279874
ACOZ:
120959991
AARA:
120904748
AMER:
121598034
ASTE:
118509846
AFUN:
125761755
AMOU:
128302115
AALI:
118458894
AAG:
5569339
AALB:
109407255
115258606
CQU:
CpipJ_CPIJ010031
CPII:
120428257
CNS:
116349138
BCOO:
119085089
AME:
411473
ACER:
108003556
ALAB:
122720816
ADR:
102672224
AFLR:
100866475
BIM:
100741751
BBIF:
117211561
BVK:
117237850
BVAN:
117155266
BTER:
100646454
BAFF:
126919228
BPYO:
122570296
BPAS:
132910878
FVI:
122529415
CCAL:
108622603
108626576
OBB:
114879105
OLG:
117601038
MGEN:
117229209
NMEA:
116433196
CGIG:
122400011
SOC:
105199794
MPHA:
105828125
AEC:
105148003
ACEP:
105623464
PBAR:
105427874
VEM:
105560587
HST:
105189856
DQU:
106752100
CFO:
105251495
FEX:
115244445
LHU:
105676135
PGC:
109852599
OBO:
105280789
PCF:
106784515
PFUC:
122516773
VPS:
122627946
VCRB:
124422913
VVE:
124947854
NVI:
100122869
TPRE:
106658626
LHT:
122512972
122512987
LBD:
127283464
127283465
MDL:
103568817
CGLO:
123259534
FAS:
105269769
105272722
DAM:
107038246
107040887
AGIF:
122853334
CINS:
118070317
VCAN:
122414142
CCIN:
107263251
DSM:
124411881
NPT:
124219907
NFB:
124183296
NLO:
107221687
NVG:
124304649
AROA:
105687318
TCA:
660089
DPA:
109537965
ATD:
109609448
CSET:
123321914
AGB:
108916993
LDC:
111516417
NVL:
108557163
PPYR:
116166771
OTU:
111425135
BMOR:
101742025
BMAN:
114245920
MSEX:
115452032
DPL:
KGM_214065
BANY:
112044646
MJU:
123869613
NIQ:
126771256
VCD:
124531655
MCIX:
123655646
PMAC:
106714807
PPOT:
106106604
PXU:
106123507
PRAP:
110992241
PBX:
123717359
PNAP:
125055377
ZCE:
119834472
CCRC:
123693923
LSIN:
126965406
HAW:
110370720
HZE:
124629958
TNL:
113497138
113506919
SLIU:
111363119
OFU:
114365507
PXY:
105385809
105390237
PGW:
126368396
CFEL:
113373517
113373519
CCRN:
123302622
API:
100159310
DNX:
107164895
107168837
AGS:
114122536
RMD:
113559678
ACOO:
126836507
DVT:
126898923
BTAB:
109035238
CLEC:
106670487
HHAL:
106678760
NLU:
111050267
HVI:
124368847
MQU:
128998173
PHU:
Phum_PHUM616920
FOC:
113207810
TPAL:
117641528
ZNE:
110833009
CSEC:
111869337
SGRE:
126298014
IEL:
124166463
124170755
FCD:
110857985
DPX:
DAPPUDRAFT_221441
DMK:
116930955
DPZ:
124348902
PVM:
113812201
PJA:
122267804
PCHN:
125043383
PMOO:
119585147
119585373
HAME:
121856922
PCLA:
123769551
CQD:
128690021
PTRU:
123516220
ESN:
127004004
HAZT:
108667374
TCF:
131887577
PPOI:
119107017
DSV:
119460657
119460658
RSAN:
119396911
RMP:
119174992
VDE:
111247666
VJA:
111264141
TUT:
107363085
107363099
CSCU:
111628234
PTEP:
107441816
UDV:
129222749
129232540
SDM:
118197617
PMEO:
129596083
CEL:
CELE_R07H5.2
(cpt-2)
CBR:
CBG_06027
(Cbr-cpt-2)
CRQ:
GCK72_014072
NAI:
NECAME_12680
BMY:
BM_BM5293
(Bma-cpt-2)
LOA:
LOAG_06314
TSP:
Tsp_06820
LGI:
LOTGIDRAFT_225472
PVUL:
126828333
PCAN:
112572479
BGT:
106064240
GAE:
121367783
HRF:
124146142
HRJ:
124276519
CRG:
105333323
CVN:
111107126
111109503
CANU:
128159551
128159705
OED:
125654978
125654985
MYI:
110452625
PMAX:
117330644
MCAF:
127707540
MMER:
123528948
RPHI:
132733551
132756866
DPOL:
127882463
OBI:
106867325
OSN:
115209701
LAK:
106160133
OVI:
T265_13896
EGL:
EGR_03181
NVE:
5512309
EPA:
110242501
ATEN:
116303285
ADF:
107341910
AMIL:
114953476
PDAM:
113684833
SPIS:
111341399
DGT:
114521913
XEN:
124434034
HMG:
100214547
HSY:
130626069
TAD:
TRIADDRAFT_50581
AQU:
100631658
100632782
100640107
MBR:
MONBRDRAFT_34499
SRE:
PTSG_10400
ACAN:
ACA1_375940
PIF:
PITG_05664
PITG_19234
PSOJ:
PHYSODRAFT_344464
PHYSODRAFT_543375
SPAR:
SPRG_11111
SPRG_11333
EHX:
EMIHUDRAFT_468049
GTT:
GUITHDRAFT_73931
GUITHDRAFT_75247
TBR:
Tb927.7.2250
TBG:
TbgDal_VII2510
TCR:
511807.284
LMA:
LMJF_22_0310
LIF:
LINJ_22_0190
LDO:
LDBPK_220190
LMI:
LMXM_22_0310
LBZ:
LBRM_22_0300
LPAN:
LPMP_220310
NWD:
H3L96_07890
RKR:
I6G21_03760
» show all
Taxonomy
UniProt
Reference
PMID:
1988962
Authors
Finocchiaro G, Taroni F, Rocchi M, Martin AL, Colombo I, Tarelli GT, DiDonato S
Title
cDNA cloning, sequence analysis, and chromosomal localization of the gene for human carnitine palmitoyltransferase.
Journal
Proc Natl Acad Sci U S A 88:661-5 (1991)
DOI:
10.1073/pnas.88.2.661
Sequence
[hsa:
1376
]
LinkDB
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DBGET
integrated database retrieval system