ORTHOLOGY: K09479
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Entry
K09479 KO
Name
ACADVL
Definition
very long chain acyl-CoA dehydrogenase [EC:
1.3.8.9
]
Pathway
ko00071
Fatty acid degradation
ko01100
Metabolic pathways
ko01212
Fatty acid metabolism
Module
M00087
beta-Oxidation
Disease
H00392
VLCAD deficiency
H00525
Disorders of mitochondrial fatty-acid oxidation
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09103 Lipid metabolism
00071 Fatty acid degradation
K09479 ACADVL; very long chain acyl-CoA dehydrogenase
Enzymes [BR:
ko01000
]
1. Oxidoreductases
1.3 Acting on the CH-CH group of donors
1.3.8 With a flavin as acceptor
1.3.8.9 very-long-chain acyl-CoA dehydrogenase
K09479 ACADVL; very long chain acyl-CoA dehydrogenase
BRITE hierarchy
Other DBs
RN:
R01279
R03990
GO:
0017099
Genes
HSA:
37
(ACADVL)
PTR:
455237
(ACADVL)
PPS:
100986379
(ACADVL)
GGO:
101143346
(ACADVL)
PON:
100454381
(ACADVL)
NLE:
100585921
(ACADVL)
MCC:
714326
(ACADVL)
CSAB:
103242278
(ACADVL)
RRO:
104673335
(ACADVL)
RBB:
108514298
(ACADVL)
CJC:
100399197
(ACADVL)
SBQ:
101028298
(ACADVL)
MMU:
11370
(Acadvl)
MCAL:
110304163
(Acadvl)
MPAH:
110332221
(Acadvl)
RNO:
25363
(Acadvl)
MUN:
110555097
(Acadvl)
CGE:
100767527
(Acadvl)
NGI:
103752159
(Acadvl)
HGL:
101707761
(Acadvl)
CCAN:
109674520
(Acadvl)
OCU:
100346654
(ACADVL)
TUP:
102486032
(ACADVL)
CFA:
489463
(ACADVL)
VVP:
112924990
(ACADVL)
AML:
100472785
(ACADVL)
UMR:
103660348
(ACADVL)
UAH:
113271108
(ACADVL)
ORO:
101376612
(ACADVL)
ELK:
111161073
FCA:
101094144
(ACADVL)
PTG:
102968012
(ACADVL)
PPAD:
109245981
(ACADVL)
AJU:
106972414
(ACADVL)
BTA:
282130
(ACADVL)
BOM:
102273950
BIU:
109573934
(ACADVL)
BBUB:
102405745
(ACADVL)
CHX:
102181987
(ACADVL)
OAS:
101117173
(ACADVL)
SSC:
100520636
(ACADVL)
CFR:
102516576
(ACADVL)
CDK:
105103048
(ACADVL)
BACU:
103000307
(ACADVL)
LVE:
103077095
(ACADVL)
OOR:
101275668
(ACADVL)
DLE:
111185665
(ACADVL)
PCAD:
102973774
(ACADVL)
ECB:
100061583
(ACADVL)
EPZ:
103557744
(ACADVL)
EAI:
106844174
(ACADVL)
MYB:
102257348
(ACADVL)
MYD:
102774563
(ACADVL)
MNA:
107544584
(ACADVL)
HAI:
109394616
(ACADVL)
DRO:
112308631
(ACADVL)
PALE:
102879612
(ACADVL)
RAY:
107509515
(ACADVL)
MJV:
108401220
(ACADVL)
LAV:
100657276
(ACADVL)
TMU:
101361348
MDO:
100016619
(ACADVL)
100032148
SHR:
100925698
100931501
(ACADVL)
PCW:
110193114
110194404
(ACADVL)
OAA:
100089853
(ACADVL)
LSR:
110482134
(ACADVL)
CCAE:
111922435
(ACADVL)
AAM:
106485823
(ACADVL)
ASN:
102371669
102384902
(ACADVL)
AMJ:
102568802
(ACADVL)
102576922
PSS:
102443861
(ACADVL)
102456803
CMY:
102938508
(ACADVL)
CPIC:
101946768
101948805
(ACADVL)
PVT:
110082312
(ACADVL)
PBI:
103051941
103059781
(ACADVL)
PMUR:
107291707
107295343
(ACADVL)
TSR:
106542417
(ACADVL)
106551584
PMUA:
114581599
(ACADVL)
114598214
GJA:
107118083
(ACADVL)
107125630
XLA:
108711808
(acadvl.L)
XTR:
100216267
(acadvl)
DRE:
573723
(acadvl)
SRX:
107731915
107738021
SANH:
107675499
107683542
(acadvl)
SGH:
107595296
107597078
CCAR:
109073618
109092601
IPU:
108267840
(acadvl)
PHYP:
113540141
(acadvl)
AMEX:
103045531
(acadvl)
EEE:
113567683
(acadvl)
TRU:
101069830
(acadvl)
TNG:
GSTEN00019248G001
LCO:
104937817
(acadvl)
NCC:
104942951
MZE:
101472773
(acadvl)
ONL:
100703037
(acadvl)
OLA:
101165349
(acadvl)
XMA:
102217028
(acadvl)
XCO:
114157390
(acadvl)
PRET:
103480485
(acadvl)
CVG:
107087781
(acadvl)
NFU:
107372430
(acadvl)
KMR:
108241814
(acadvl)
ALIM:
106529201
(acadvl)
AOCE:
111575585
(acadvl)
CSEM:
103386901
(acadvl)
POV:
109634887
(acadvl)
LCF:
108897054
(acadvl)
SDU:
111232992
(acadvl)
SLAL:
111665745
(acadvl)
HCQ:
109506947
(acadvl)
BPEC:
110157677
(acadvl)
MALB:
109966474
(acadvl)
SASA:
106602820
(acadvl)
OTW:
112216747
SALP:
111950426
(acadvl)
ELS:
105010800
(acadvl)
SFM:
108918781
(acadvl)
108923151
PKI:
111860921
(acadvl)
LCM:
102364546
(ACADVL)
RTP:
109912656
109918899
(acadvl)
BFO:
118427578
CIN:
100183990
SPU:
584710
APLC:
110981027
SKO:
100369524
DME:
Dmel_CG7461
(CG7461)
DER:
6547331
DSE:
6609917
DSI:
Dsimw501_GD11444
(Dsim_GD11444)
DYA:
Dyak_GE12038
DAN:
6506293
DSR:
110177854
DPE:
6602657
DMN:
117188910
DGR:
Dgri_GH15160
DMO:
Dmoj_GI12099
DAZ:
108614533
DNV:
108651701
DHE:
111592309
DVI:
6623490
MDE:
101891231
LCQ:
111683088
AGA:
AgaP_AGAP008769
AAG:
23687873
5565366
5565367
AALB:
109400327
109400349
109425168
109425169
CQU:
CpipJ_CPIJ016451
CpipJ_CPIJ016452
CpipJ_CPIJ016453
CpipJ_CPIJ016454
AME:
412025
BIM:
100747671
BTER:
100651720
CCAL:
108632159
OBB:
114874036
SOC:
105200554
MPHA:
105838446
AEC:
105149521
ACEP:
105622411
PBAR:
105429882
VEM:
105562928
HST:
105188087
DQU:
106746266
CFO:
105251587
LHU:
105667331
PGC:
109854598
OBO:
105276471
PCF:
106788263
NVI:
100116828
CSOL:
105368265
MDL:
103574466
TCA:
659957
DPA:
109541041
ATD:
109601372
NVL:
108562362
108569494
BMOR:
101744941
BMAN:
114241040
DPL:
KGM_210602
PMAC:
106710891
PRAP:
110996061
HAW:
110380632
TNL:
113500974
API:
100162051
DNX:
107164135
AGS:
114127836
114127838
RMD:
113560282
BTAB:
109036499
CLEC:
106668658
PHU:
Phum_PHUM617730
ZNE:
110832869
FCD:
110843829
DPX:
DAPPUDRAFT_327246
PVM:
113813193
113823665
TUT:
107362076
DPTE:
113799491
CSCU:
111630174
PTEP:
107450301
CEL:
CELE_E04F6.5
(acdh-12)
CBR:
CBG13088
BMY:
Bm1_24055
LOA:
LOAG_00695
NAI:
NECAME_17750
TSP:
Tsp_10283
HRO:
HELRODRAFT_186034
LGI:
LOTGIDRAFT_177715
PCAN:
112555772
CRG:
105344745
MYI:
110463202
OBI:
106875659
LAK:
106158444
OVI:
T265_06522
NVE:
5510970
EPA:
110251159
ADF:
107343075
AMIL:
114953943
PDAM:
113681975
SPIS:
111335626
DGT:
114521443
HMG:
100201063
TAD:
TRIADDRAFT_20833
TRIADDRAFT_23854
TRIADDRAFT_30874
TRIADDRAFT_31731
TRIADDRAFT_31757
TRIADDRAFT_31810
TRIADDRAFT_34622
AQU:
100638454
GAU:
GAU_0440
» show all
Taxonomy
UniProt
Reference
PMID:
1730632
Authors
Izai K, Uchida Y, Orii T, Yamamoto S, Hashimoto T
Title
Novel fatty acid beta-oxidation enzymes in rat liver mitochondria. I. Purification and properties of very-long-chain acyl-coenzyme A dehydrogenase.
Journal
J Biol Chem 267:1027-33 (1992)
Sequence
[rno:
25363
]
Reference
PMID:
7769092
Authors
Aoyama T, Souri M, Ushikubo S, Kamijo T, Yamaguchi S, Kelley RI, Rhead WJ, Uetake K, Tanaka K, Hashimoto T
Title
Purification of human very-long-chain acyl-coenzyme A dehydrogenase and characterization of its deficiency in seven patients.
Journal
J Clin Invest 95:2465-73 (1995)
DOI:
10.1172/JCI117947
Sequence
[hsa:
37
]
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