ORTHOLOGY: K09606
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Entry
K09606 KO
Symbol
C9ORF3
Name
aminopeptidase O [EC:3.4.11.-]
Disease
H00831
Primary dystonia
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09181 Protein families: metabolism
01002 Peptidases and inhibitors
K09606 C9ORF3; aminopeptidase O
Peptidases and inhibitors [BR:
ko01002
]
Metallo peptidases
Family M1
K09606 C9ORF3; aminopeptidase O
BRITE hierarchy
Genes
HSA:
84909
(AOPEP)
PTR:
741710
(AOPEP)
PPS:
100976077
(AOPEP)
GGO:
101132331
(AOPEP)
PON:
100456741
(AOPEP)
PPYG:
129044574
(AOPEP)
NLE:
100580480
(AOPEP)
HMH:
116475276
(AOPEP)
SSYN:
129479164
(AOPEP)
MCC:
709211
(AOPEP)
MCF:
101864850
(AOPEP)
MTHB:
126937346
MNI:
105498940
(CUNH9orf3)
CSAB:
103219831
(C12H9orf3)
CATY:
105579573
PANU:
101018421
(AOPEP)
TGE:
112608029
(C15H9orf3)
MLEU:
105536617
RRO:
104669114
(AOPEP)
RBB:
108529289
TFN:
117098262
(AOPEP)
PTEH:
111521698
(AOPEP)
CANG:
105501523
CJC:
100412895
(AOPEP)
SBQ:
101047939
CIMI:
108317053
(AOPEP)
ANAN:
105723766
(AOPEP)
CSYR:
103252261
(CUNH9orf3)
MMUR:
105862133
(C10H9orf3)
LCAT:
123646463
ERUF:
138388336
(AOPEP)
PCOQ:
105806846
OGA:
100962523
(CUNH9orf3)
MMU:
72061
(Aopep)
MCAL:
110307689
(Aopep)
MPAH:
110333820
(C16H9orf3)
RNO:
290963
(Aopep)
MCOC:
116081695
(Aopep)
ANU:
117713855
(Aopep)
ASYL:
127664683
(Aopep)
MUN:
110565319
(Aopep)
CGE:
100773268
(Aopep)
MAUA:
101822679
(Aopep)
PROB:
127229134
(Aopep)
PLEU:
114708433
PMAV:
102926312
(Aopep)
MORG:
121443390
121453545
MFOT:
126502448
AAMP:
119816103
CNL:
130885726
(Aopep)
NGI:
103740951
HGL:
101710782
CPOC:
111753287
CCAN:
109683423
DORD:
105999796
DSP:
122113612
DMER:
138834896
(Aopep)
PLOP:
125339685
NCAR:
124965290
MMMA:
107157644
(Aopep)
ITI:
101969802
(Aopep)
OCU:
100344283
(AOPEP)
OPI:
101536113
(AOPEP)
OCZ:
121162057
TUP:
102476059
102476651
GVR:
103594258
CFA:
484139
(C1H9orf3)
CLUD:
112644604
(AOPEP)
VVP:
112908712
(CUNH9orf3)
VLG:
121484097
NPO:
129499938
(AOPEP)
AML:
100476967
(AOPEP)
UMR:
103682233
(AOPEP)
UAH:
113269782
(AOPEP)
UAR:
123781471
ELK:
111139084
LLV:
125083334
MPUF:
101677582
MNP:
132024754
(AOPEP)
MLK:
131812071
(AOPEP)
NVS:
122917633
ORO:
101380707
EJU:
114223334
(AOPEP)
ZCA:
113934221
(AOPEP)
MLX:
118023336
(AOPEP)
NSU:
110569984
(AOPEP)
LWW:
102736916
(AOPEP)
FCA:
101088120
(AOPEP)
PYU:
121014186
PCOO:
112868584
(CUNH9orf3)
PBG:
122475127
PVIV:
125149850
(AOPEP)
LRUF:
124529219
LGF:
123593803
AJU:
106971451
(AOPEP)
PTG:
102952835
PPAD:
109251665
(CUNH9orf3)
PUC:
125925318
PLEZ:
122204446
HHV:
120240827
BTA:
531757
(C8H9orf3)
BOM:
102285366
(AOPEP)
BIU:
109562566
(C8H9orf3)
BBUB:
102400918
(AOPEP)
BBIS:
104985724
CHX:
102186309
(C8H9orf3)
OAS:
105607129
(AOPEP)
BTAX:
128052234
(AOPEP)
CSUM:
138080859
(AOPEP)
ODA:
120867013
CCAD:
122431703
MREE:
136176757
(AOPEP)
OVR:
110141903
(AOPEP)
MBEZ:
129556986
(AOPEP)
SSC:
100513615
(C10H9orf3)
CFR:
106729961
(AOPEP)
CBAI:
105078862
CDK:
105084714
(AOPEP)
VPC:
102535348
(AOPEP)
BACU:
102997680
BMUS:
118897357
LVE:
103086134
OOR:
101285044
(AOPEP)
LALB:
132523772
(AOPEP)
GMF:
115840244
(AOPEP)
DDP:
132427480
(AOPEP)
DLE:
111166832
(AOPEP)
PCAD:
102991114
(AOPEP)
PSIU:
116756152
(AOPEP)
PPHC:
136124207
(AOPEP)
NASI:
112405427
(CUNH9orf3)
ECB:
100061428
(C23H9orf3)
EPZ:
103551336
(AOPEP)
EAI:
106841118
(AOPEP)
MYB:
102260525
MYD:
102772336
MMYO:
118667637
MLF:
102427896
(CUNH9orf3)
MDT:
132211819
(AOPEP)
MYUM:
138998861
(AOPEP)
PKL:
118732247
EFUS:
129151576
MNA:
107532311
DRO:
112302891
(CUNH9orf3)
SHON:
118993714
AJM:
119040356
(AOPEP)
PDIC:
114512547
PHAS:
123819436
MMF:
118629797
PPAM:
129082369
(AOPEP)
HAI:
109396725
(CUNH9orf3)
RFQ:
117031800
(AOPEP)
PALE:
102881917
(CUNH9orf3)
PGIG:
120616901
PVP:
105306917
(CUNH9orf3)
RAY:
107518079
(AOPEP)
MJV:
108402189
TOD:
119232200
(AOPEP)
SFUM:
130035696
(AOPEP)
SETR:
126006797
(AOPEP)
LAV:
100654578
(CUNH9orf3)
TMU:
101346069
ETF:
101662827
(AOPEP)
DNM:
101421623
(CUNH9orf3)
MDO:
100013409
(C6H9orf3)
GAS:
123235266
SHR:
116419189
(AOPEP)
AFZ:
127561713
PCW:
110197622
(CUNH9orf3)
TVP:
118834457
PBRV:
138161152
(AOPEP)
MLAO:
141498209
(AOPEP)
OAA:
103167493
TACU:
119946712
GGA:
427467
(CZH9ORF3)
PCOC:
116232288
(AOPEP)
MGP:
100547145
CJO:
107306260
(AOPEP)
TPAI:
128089583
(AOPEP)
LMUT:
125687230
NMEL:
110389444
(CZH9orf3)
APLA:
101804080
(AOPEP)
AACU:
137847765
(AOPEP)
ACYG:
106047346
(AOPEP)
CATA:
118257360
(AOPEP)
AFUL:
116501199
(AOPEP)
TGU:
100231427
(AOPEP)
LSR:
110471012
(AOPEP)
SCAN:
103822943
(AOPEP)
PMOA:
120511946
OTC:
121333283
PRUF:
121360698
ATRC:
139588960
(AOPEP)
GFR:
102031964
FAB:
101818082
(CZH9orf3)
OMA:
130265279
(AOPEP)
PHI:
102114480
PMAJ:
107216300
(AOPEP)
CCAE:
111941800
(CZH9orf3)
CCW:
104692013
(AOPEP)
CBRC:
103619840
(CUNH9orf3)
ACOE:
138103915
(AOPEP)
ETL:
114055231
(AOPEP)
ZAB:
102073759
(CUNH9orf3)
ZLE:
135459552
(AOPEP)
SVG:
106848907
MMEA:
130575823
(AOPEP)
HRT:
120765132
(AOPEP)
SATI:
136373811
(AOPEP)
CCIC:
134056375
(AOPEP)
FPG:
101914999
FCH:
102056672
(AOPEP)
NNT:
104400962
SHAB:
115619450
(AOPEP)
ACUN:
113489955
(CZH9orf3)
TALA:
104363366
(AOPEP)
ACHC:
115336437
HLE:
104832467
AGEN:
126036459
HHAR:
128136850
(AOPEP)
BBUT:
142027525
(AOPEP)
GCL:
127027482
CSTI:
104563204
LDI:
104351302
DPUB:
104298785
PPUS:
135193260
(AOPEP)
AVIT:
104277521
EGZ:
104125918
(AOPEP)
NNI:
104011765
PCAO:
104046147
PARX:
142050734
(AOPEP)
PADL:
103920405
AFOR:
103893815
(CUNH9orf3)
FGA:
104069158
CBOR:
142075881
(AOPEP)
CBOY:
140650890
(AOPEP)
MAME:
142421779
(AOPEP)
CLV:
102091636
102098351
(CUNH9orf3)
CNIC:
136001344
(AOPEP)
PLET:
104623627
CUCA:
104059934
(AOPEP)
OHA:
104331171
CPEA:
104397254
CVF:
104287168
RTD:
128902179
(AOPEP)
CRID:
134508480
(AOPEP)
LMIC:
141736127
(AOPEP)
AAM:
106493873
106495023
AROW:
112976805
(CUNH9orf3)
NPD:
112946423
(CUNH9orf3)
TGT:
104574598
DNE:
112978756
(CUNH9orf3)
SCAM:
104143023
ASN:
102383102
(CUNH9orf3)
AMJ:
102570488
(CUNH9orf3)
CPOO:
109323364
(CUNH9orf3)
GGN:
109297539
(CUNH9orf3)
PSS:
102445779
(CUNH9orf3)
CIZ:
142013563
(AOPEP)
CMY:
102933933
(AOPEP)
CCAY:
125637107
LKP:
140911604
(AOPEP)
NDS:
141987633
(AOPEP)
DCC:
119856417
CPIC:
101942763
(AOPEP)
TST:
117878985
(AOPEP)
CABI:
116821159
(AOPEP)
MRV:
120407914
ACS:
100556100
(c2h9orf3)
ASAO:
132767300
(AOPEP)
132780467
PVT:
110085554
(CUNH9orf3)
SUND:
121922612
PBI:
103053853
(CUNH9orf3)
PMUR:
107291724
(AOPEP)
CTIG:
120308186
TSR:
106548213
PGUT:
117661371
(AOPEP)
PCAE:
139313216
(AOPEP)
APRI:
131192104
(AOPEP)
PTEX:
113438493
(CUNH9orf3)
NSS:
113416549
(CUNH9orf3)
VKO:
123031414
PMUA:
114606346
(AOPEP)
PRAF:
128423507
(AOPEP)
ZVI:
118076719
(AOPEP)
HCG:
128345336
(AOPEP)
GJA:
107107651
107111663
STOW:
125436451
EMC:
129334527
(AOPEP)
XLA:
398991
(aopep.L)
XTR:
100145347
(aopep)
NPR:
108788140
(CUNH9orf3)
RTEM:
120941932
ACAT:
141146711
(AOPEP)
PADS:
140333352
(AOPEP)
BBUF:
120989100
BGAR:
122922787
DTC:
141049483
(AOPEP)
PWL:
138287524
(AOPEP)
MUO:
115463279
GSH:
117352030
(AOPEP)
DRE:
560737
(aopep)
SRX:
107724903
SANH:
107674500
SGH:
107602843
CCAR:
109048454
(aopep)
CAUA:
113107500
(c8h9orf3)
CGIB:
127963549
PTET:
122350784
LROH:
127169663
(aopep)
GRF:
141286630
(aopep)
OMC:
131545282
(aopep)
PPRM:
120464495
120484633
RKG:
130072457
(aopep)
MAMB:
125279700
CIDE:
127516930
CERY:
137027087
(aopep)
MASI:
127414918
TROS:
130568057
(aopep)
TDW:
130440000
(aopep)
MANU:
129414095
(aopep)
PDAB:
135729505
(aopep)
IPU:
108265658
(aopep)
IFU:
128607841
(aopep)
PHYP:
113527242
(cunh9orf3)
SMEO:
124399639
TFD:
113656335
(aopep)
TVC:
132854042
(aopep)
CGAR:
128529942
(aopep)
NGRA:
132893117
(aopep)
TRN:
134318144
(aopep)
AMEX:
103032991
(aopep)
CMAO:
118813169
EEE:
113591306
(cunh9orf3)
CHAR:
105894170
(aopep)
SPIL:
134059679
(aopep)
ASAD:
121690028
TRU:
101065317
(aopep)
TFS:
130526460
(aopep)
TNG:
GSTEN00032663G001
LCO:
104920665
(ciiih9orf3)
NCC:
104942475
TBEN:
117473181
(aopep)
CGOB:
115013238
(aopep)
PGEO:
117451961
(aopep)
GACU:
117558587
(aopep)
EMAC:
134874016
(aopep)
ELY:
117252785
(aopep)
EFO:
125890308
PLEP:
121944473
SLUC:
116054052
ECRA:
117944628
(aopep)
ESP:
116688887
(aopep)
PFLV:
114555952
(aopep)
GAT:
120830898
PPUG:
119224759
(aopep)
AFB:
129101068
(aopep)
CLUM:
117736903
(aopep)
PSWI:
130197050
(aopep)
CANA:
137779158
(aopep)
CVE:
137867621
(aopep)
MSAM:
119891224
SCHU:
122876054
EARM:
139283915
(aopep)
CUD:
121510533
SPUL:
138610574
(aopep)
LMIX:
132974608
(aopep)
HTC:
141790537
(aopep)
ALAT:
119019843
ASTR:
137591464
(aopep)
PKLU:
139203892
(aopep)
MZE:
101470200
(lg12h9orf3)
ONL:
100699926
(lg12h9orf3)
OAU:
116311161
OLA:
101166558
(c9h9orf3)
OML:
112148201
(aopep)
CSAI:
133450599
(aopep)
XMA:
106700482
(c12h9orf3)
XCO:
114154619
(aopep)
XHE:
116729841
(aopep)
PRET:
103470157
(clg9h9orf3)
PFOR:
103135445
PLAI:
106940369
PMEI:
106917878
GAF:
122828765
PPRL:
129365870
(aopep)
CVG:
107098244
CTUL:
119781105
GMU:
124877253
NFU:
107394088
(csgr18h9orf3)
KMR:
108244806
(aopep)
ALIM:
106513721
NWH:
119413046
AOCE:
111588637
(aopep)
EJA:
138215807
(aopep)
BFRE:
138621450
(aopep)
MCEP:
125012036
CSEM:
103398566
POV:
109639340
(cunh9orf3)
SSEN:
122769410
SSOE:
131463917
(aopep)
HHIP:
117767530
(aopep)
HSP:
118115446
PPLT:
128438625
(aopep)
SMAU:
118313966
LCF:
108878486
(aopep)
SDU:
111236164
(cunh9orf3)
SLAL:
111644619
(cunh9orf3)
HCQ:
109520669
(cunh9orf3)
SSCV:
125965835
(aopep)
SBIA:
133499852
(aopep)
PEE:
133399904
(aopep)
PTAO:
133475249
(aopep)
BPEC:
110167037
(cunh9orf3)
ENY:
140346898
(aopep)
MALB:
109956539
(cunh9orf3)
BSPL:
114862630
(aopep)
SJO:
128365392
(aopep)
SSCO:
133979321
(aopep)
TTY:
137198709
(aopep)
GMH:
115545410
(aopep)
SASA:
106585155
(cssa24h9orf3)
STRU:
115164236
(aopep)
OTW:
112248770
(aopep)
OMY:
110525922
(aopep)
OGO:
124034121
ONE:
115111825
OKI:
109882666
OKE:
118394093
(aopep)
OMM:
135544302
(aopep)
OCLA:
139411120
SALP:
111974263
(lg15h9orf3)
SNH:
120044357
SFON:
129853787
(aopep)
CCLU:
121585075
ELS:
105014109
(aopep)
114840675
OEP:
134014921
(aopep)
SFM:
108938636
(aopep)
PKI:
111839210
(cunh9orf3)
AANG:
118237076
(aopep)
AROT:
135233408
(aopep)
CCOG:
133140447
(aopep)
LOC:
102685914
(clg2h9orf3)
PSPA:
121303072
ARUT:
117411702
117973033
PSEX:
120532647
LCM:
102359227
CMK:
103182827
(aopep)
CPLA:
122561552
CPUN:
140486885
(aopep)
HOC:
132824116
(aopep)
SCAU:
119970344
LERI:
129695719
(aopep)
HAKA:
140741269
(aopep)
BFO:
118403384
BBEL:
109483867
SPU:
591339
LPIC:
129271258
LVG:
121423616
AJJ:
139980076
APLC:
110985787
ARUN:
117297531
AFIL:
140141134
SKO:
100367141
PFLL:
139139085
DMK:
116931210
PVM:
113814462
PJA:
122263620
PCHN:
125043183
HAME:
121875129
PCLA:
123758352
CQD:
128686869
PTRU:
123501040
MNZ:
135204014
MRJ:
136846452
PORN:
139751916
HAZT:
108682540
OOT:
143018257
EAF:
111713826
CSCU:
111622418
CVS:
136969002
PTEP:
107437810
ABRU:
129975264
UDV:
129227369
SDM:
118192150
LPOL:
106464056
PMEO:
129584565
PCAN:
112573986
LSAX:
138966224
BARL:
143295379
BGT:
106064144
GAE:
121375886
HRF:
124115599
HRJ:
124270605
124272782
HASI:
137290745
HCRA:
139479887
CRG:
105329533
CANU:
128165193
CVN:
111118125
111122435
OED:
125668864
MYI:
110448787
PMAX:
117325221
AIRR:
138325613
YBA:
132552184
RPHI:
132716708
DPOL:
127862000
MAEA:
128212974
OBI:
106872508
OSN:
115216559
LJP:
135470070
LAK:
106164409
LLON:
135487142
EPA:
110249507
ADF:
107356223
AMIL:
114968873
SPIS:
111338453
DGT:
114521309
HSY:
130655378
RES:
135685920
TAD:
TRIADDRAFT_58028
CCLM:
134185534
» show all
Taxonomy
UniProt
Reference
PMID:
15687497
Authors
Diaz-Perales A, Quesada V, Sanchez LM, Ugalde AP, Suarez MF, Fueyo A, Lopez-Otin C
Title
Identification of human aminopeptidase O, a novel metalloprotease with structural similarity to aminopeptidase B and leukotriene A4 hydrolase.
Journal
J Biol Chem 280:14310-7 (2005)
DOI:
10.1074/jbc.M413222200
Sequence
[hsa:
84909
]
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