Chionomys nivalis (European snow vole): 130870340
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Entry
130870340 CDS
T11437
Symbol
Bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
cnl Chionomys nivalis (European snow vole)
Pathway
cnl00280
Valine, leucine and isoleucine degradation
cnl00640
Propanoate metabolism
cnl00785
Lipoic acid metabolism
cnl01100
Metabolic pathways
cnl01210
2-Oxocarboxylic acid metabolism
Module
cnl_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
cnl00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
130870340 (Bckdha)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
130870340 (Bckdha)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
130870340 (Bckdha)
Enzymes [BR:
cnl01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
130870340 (Bckdha)
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NCBI-GeneID:
130870340
NCBI-ProteinID:
XP_057619014
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Position
2:complement(80500435..80524638)
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AA seq
477 aa
AA seq
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MAVAMCMAKIWRPSGGLGQAALLLLRRPGVRGLARFTECLIAEGRFEPMILLPSPPRAGI
TGVSCLIQHPSRQQQQFPSLDDKPQFPGASAEFVDKLEFIQPNVISGIPIYRVMDRQGQI
INPSEDPHLPQEEVLKLYRSMTLLNTMDRILYESQRQGRISFYMTNYGEEGTHVGSAAAL
DHADLVFGQYREAGVLMYRDYPLELFMAQCYGNVSDPGKGRQMPVHYGCKERHFVTISSP
LATQIPQAVGAAYAAKRANANRIVICYFGEGAASEGDAHAGFNFAATLECPIIFFCRNNG
YAISTPTSEQYRGDGIAARGPGYGILSIRVDGNDVFAVYNATREARRRAVAENQPFLIEA
MTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPISRLRQYLLNQGWWDEEQEKTWRKQSRK
KVMEAFEQAERKLKPNPNLLFSDVYQEMPAQLRRQQESLARHLQTYGEHYPLDHFDK
NT seq
1434 nt
NT seq
+upstream
nt +downstream
nt
atggcggtagcgatgtgtatggccaagatctggaggccgagtggtggcctgggtcaggct
gctctcctgctgctgcggcggcctggggttcggggcttggctagattcacagaatgtctc
atagctgagggtcgctttgaacccatgattcttctaccttcacctccaagggctgggatt
acaggtgtgagttgcctcatccagcaccccagcagacaacagcagcagttcccatccctg
gacgacaagccccagttcccaggggcctcggcagagtttgtagacaagcttgagttcatc
caacccaatgtcatttctggcatccccatctaccgtgtcatggaccgccagggccagatc
atcaaccccagtgaagacccccatctgccccaggaggaggtactgaagttatacaggagc
atgacactgctcaacaccatggaccgaattctctatgaatcccaacggcagggccggatc
tccttctacatgaccaactatggtgaggaggggacacatgtggggagtgctgccgccctg
gaccatgcagacctggtgtttggccaataccgggaggcaggtgtgctcatgtaccgggac
taccctctggagctgttcatggcccagtgctatggcaacgtgagtgacccaggcaagggg
cgccagatgcccgttcactatggctgcaaggagcgccacttcgtcaccatctcctctcca
ctagccacacagatccctcaggcggtgggggcagcctatgctgccaagcgggccaatgcc
aaccggattgtgatctgttactttggcgagggggcagccagtgaaggggatgcccatgcc
ggcttcaactttgcagccaccttggaatgtcctatcatcttcttctgccggaacaatggc
tatgccatttccacaccaacctctgagcagtaccgtggggacggcatcgcggctcggggc
cctgggtatggcatcctgtcaatccgtgtggacggcaacgacgtgtttgcagtgtacaat
gccactagggaggcccggcggcgggctgtggctgagaaccagcccttcctcattgaggcc
atgacctacaggattggacatcacagtaccagtgacgacagctcagcataccgttcagtg
gacgaggtcaattactgggacaagcaggaccacccgatctcgaggctgaggcagtatctg
ctgaaccagggctggtgggatgaggagcaggagaagacctggcggaagcagtcacgaaag
aaggtgatggaggcctttgaacaggccgagcggaagctaaagcccaacccaaacctgctg
ttctctgacgtataccaggagatgcccgcccagctccgcagacaacaggagtcactggca
cgacatctgcagacctacggggagcattaccccctggatcactttgacaagtga
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