Entry |
|
Symbol |
BCKDHA
|
Name |
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
|
KO |
K00166 | 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4] |
|
Organism |
csum Capricornis sumatraensis (Sumatran serow)
|
Pathway |
csum00280 | Valine, leucine and isoleucine degradation |
|
Module |
csum_M00036 | Leucine degradation, leucine => acetoacetate + acetyl-CoA |
|
Brite |
KEGG Orthology (KO) [BR:csum00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
138096379 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
138096379 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
138096379 (BCKDHA)
Enzymes [BR:csum01000]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
138096379 (BCKDHA)
|
SSDB |
|
Motif |
|
Other DBs |
|
LinkDB |
|
Position |
20:55910583..55929179
|
AA seq |
447 aa
MAVAAAAARVWRPSRGLGRAGLPLLRLLGARGLARSHPHRWQQQRHFSSLDDKPQFPGAS
AEFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDRI
LYESQRQGRISFYMTNYGEEGTHVGSAAALDDTDLVFGQYREAGVLMYRDYPLELFMAQC
YGNVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGE
GAASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRV
DGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQD
HPISRLRHHLQSRGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPNPNLIFSDVYQEMPA
QLRKQQESLARHLQTYGEHYPLDHFEK |
NT seq |
1344 nt +upstreamnt +downstreamnt
atggcggtggcggctgcggcggcgagggtttggagaccaagtcgaggcttgggacgggcg
ggcctcccgctcctgcggctgcttggggctcgtgggctggctagatctcacccccacagg
tggcagcaacagcggcacttctcgtccctggatgacaagccgcagttcccaggggcctca
gcggagttcatagacaagctcgagttcatccagcccaatgtcatctctgggatccccatc
taccgggtcatggaccggcagggccagatcatcaaccccagcgaggatccccatctgccc
caggagaaggtgctcaaattctacaagagcatgaccttgctcaataccatggaccgcatc
ctctatgagtcccagaggcagggccgcatatccttctacatgaccaactatggcgaagag
gggacgcacgtgggcagcgcggcagccctggacgacacagacctagtgtttggccagtat
cgggaggcaggtgtgctcatgtaccgggactaccccctggagctgttcatggcccagtgc
tacggcaacgtgagcgacctgggcaaggggcgccagatgcccgtccactacggctgcagg
gagcgccacttcgtcaccatctcctctccgctggccacgcagatcccccaggcggtcggg
gcagcctacgcagccaagcgggccaacgccaacagggtggtcatctgttacttcggagag
ggggcagccagtgagggggacgcccacgccggcttcaacttcgccgccaccctcgagtgc
cccatcatcttcttctgtcggaacaatggctacgccatctccacgcccacctcagagcaa
taccgcggggacggcatcgcggctcgaggccccgggtacggcatcctgtccatccgcgtg
gatggcaatgatgtgtttgctgtgtacaacgccaccaaggaggcccggcggcgggccgtg
gcggagaaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcacc
agtgatgacagctcggcgtaccgctcagtggacgaggtcaactactgggacaagcaggac
caccccatctcccggctgcggcatcacctgcagagccgcggctggtgggatgacgagcag
gagaaggcctggaggaagcagtcccgcaagaaggtaatggaggcctttgagcaggctgag
cggaagctgaagcccaaccccaacttgatcttctcggacgtgtatcaggagatgcctgcc
cagctccgcaagcagcaggagtctctggcacgtcacctccagacctacggcgaacactac
ccactggaccacttcgagaagtga |