KEGG   Capricornis sumatraensis (Sumatran serow): 138096379
Entry
138096379         CDS       T10522                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
csum  Capricornis sumatraensis (Sumatran serow)
Pathway
csum00280  Valine, leucine and isoleucine degradation
csum00640  Propanoate metabolism
csum00785  Lipoic acid metabolism
csum01100  Metabolic pathways
csum01210  2-Oxocarboxylic acid metabolism
Module
csum_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:csum00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    138096379 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    138096379 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    138096379 (BCKDHA)
Enzymes [BR:csum01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     138096379 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 138096379
NCBI-ProteinID: XP_068848647
LinkDB
Position
20:55910583..55929179
AA seq 447 aa
MAVAAAAARVWRPSRGLGRAGLPLLRLLGARGLARSHPHRWQQQRHFSSLDDKPQFPGAS
AEFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDRI
LYESQRQGRISFYMTNYGEEGTHVGSAAALDDTDLVFGQYREAGVLMYRDYPLELFMAQC
YGNVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGE
GAASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRV
DGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQD
HPISRLRHHLQSRGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPNPNLIFSDVYQEMPA
QLRKQQESLARHLQTYGEHYPLDHFEK
NT seq 1344 nt   +upstreamnt  +downstreamnt
atggcggtggcggctgcggcggcgagggtttggagaccaagtcgaggcttgggacgggcg
ggcctcccgctcctgcggctgcttggggctcgtgggctggctagatctcacccccacagg
tggcagcaacagcggcacttctcgtccctggatgacaagccgcagttcccaggggcctca
gcggagttcatagacaagctcgagttcatccagcccaatgtcatctctgggatccccatc
taccgggtcatggaccggcagggccagatcatcaaccccagcgaggatccccatctgccc
caggagaaggtgctcaaattctacaagagcatgaccttgctcaataccatggaccgcatc
ctctatgagtcccagaggcagggccgcatatccttctacatgaccaactatggcgaagag
gggacgcacgtgggcagcgcggcagccctggacgacacagacctagtgtttggccagtat
cgggaggcaggtgtgctcatgtaccgggactaccccctggagctgttcatggcccagtgc
tacggcaacgtgagcgacctgggcaaggggcgccagatgcccgtccactacggctgcagg
gagcgccacttcgtcaccatctcctctccgctggccacgcagatcccccaggcggtcggg
gcagcctacgcagccaagcgggccaacgccaacagggtggtcatctgttacttcggagag
ggggcagccagtgagggggacgcccacgccggcttcaacttcgccgccaccctcgagtgc
cccatcatcttcttctgtcggaacaatggctacgccatctccacgcccacctcagagcaa
taccgcggggacggcatcgcggctcgaggccccgggtacggcatcctgtccatccgcgtg
gatggcaatgatgtgtttgctgtgtacaacgccaccaaggaggcccggcggcgggccgtg
gcggagaaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcacc
agtgatgacagctcggcgtaccgctcagtggacgaggtcaactactgggacaagcaggac
caccccatctcccggctgcggcatcacctgcagagccgcggctggtgggatgacgagcag
gagaaggcctggaggaagcagtcccgcaagaaggtaatggaggcctttgagcaggctgag
cggaagctgaagcccaaccccaacttgatcttctcggacgtgtatcaggagatgcctgcc
cagctccgcaagcagcaggagtctctggcacgtcacctccagacctacggcgaacactac
ccactggaccacttcgagaagtga

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