Homo sapiens (human): 4285
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Entry
4285 CDS
T01001
Symbol
MIPEP, COXPD31, HMIP, MIP
Name
(RefSeq) mitochondrial intermediate peptidase
KO
K01410
mitochondrial intermediate peptidase [EC:
3.4.24.59
]
Organism
hsa
Homo sapiens (human)
Disease
H00891
Combined oxidative phosphorylation deficiency
Brite
KEGG Orthology (KO) [BR:
hsa00001
]
09180 Brite Hierarchies
09181 Protein families: metabolism
01002 Peptidases and inhibitors [BR:
hsa01002
]
4285 (MIPEP)
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis [BR:
hsa03029
]
4285 (MIPEP)
Enzymes [BR:
hsa01000
]
3. Hydrolases
3.4 Acting on peptide bonds (peptidases)
3.4.24 Metalloendopeptidases
3.4.24.59 mitochondrial intermediate peptidase
4285 (MIPEP)
Peptidases and inhibitors [BR:
hsa01002
]
Metallo peptidases
Family M3
4285 (MIPEP)
Mitochondrial biogenesis [BR:
hsa03029
]
Mitochondrial protein import machinery
Matrix
Other matrix factors
4285 (MIPEP)
BRITE hierarchy
SSDB
Ortholog
Paralog
Gene cluster
GFIT
Motif
Pfam:
Peptidase_M3
TOP_N
Peptidase_M91
Motif
Other DBs
NCBI-GeneID:
4285
NCBI-ProteinID:
NP_005923
OMIM:
602241
HGNC:
7104
Ensembl:
ENSG00000027001
UniProt:
Q99797
LinkDB
All DBs
Position
13:complement(23730189..23889400)
Genome browser
AA seq
713 aa
AA seq
DB search
MLCVGRLGGLGARAAALPPRRAGRGSLEAGIRARRVSTSWSPVGAAFNVKPQGSRLDLFG
ERRGLFGVPELSAPEGFHIAQEKALRKTELLVDRACSTPPGPQTVLIFDELSDSLCRVAD
LADFVKIAHPEPAFREAAEEACRSIGTMVEKLNTNVDLYQSLQKLLADKKLVDSLDPETR
RVAELFMFDFEISGIHLDKEKRKRAVDLNVKILDLSSTFLMGTNFPNKIEKHLLPEHIRR
NFTSAGDHIIIDGLHAESPDDLVREAAYKIFLYPNAGQLKCLEELLSSRDLLAKLVGYST
FSHRALQGTIAKNPETVMQFLEKLSDKLSERTLKDFEMIRGMKMKLNPQNSEVMPWDPPY
YSGVIRAERYNIEPSLYCPFFSLGACMEGLNILLNRLLGISLYAEQPAKGEVWSEDVRKL
AVVHESEGLLGYIYCDFFQRADKPHQDCHFTIRGGRLKEDGDYQLPVVVLMLNLPRSSRS
SPTLLTPSMMENLFHEMGHAMHSMLGRTRYQHVTGTRCPTDFAEVPSILMEYFANDYRVV
NQFARHYQTGQPLPKNMVSRLCESKKVCAAADMQLQVFYATLDQIYHGKHPLRNSTTDIL
KETQEKFYGLPYVPNTAWQLRFSHLVGYGARYYSYLMSRAVASMVWKECFLQDPFNRAAG
ERYRREMLAHGGGREPMLMVEGMLQKCPSVDDFVSALVSDLDLDFETFLMDSE
NT seq
2142 nt
NT seq
+upstream
nt +downstream
nt
atgctgtgcgtcggaaggctgggcggcttgggagccagagcagcagctctgccgccccgc
cgggcgggccggggaagcctcgaagccgggatccgggcccgaagggtcagcaccagctgg
tctcccgtgggcgccgccttcaatgtcaagccccagggcagccgcttggacctgttcggc
gagcgccggggtctttttggagttcctgagctgagtgccccagaaggatttcatattgca
caagaaaaagccttgagaaagacagaattgcttgtggaccgtgcatgttccaccccacct
gggccccagaccgtgctgatcttcgatgagctctcggattccttatgcagagtggccgac
ttggctgattttgtgaaaatcgctcaccctgagccagcattcagagaagctgcggaagaa
gcttgtagaagtattggcaccatggtagagaagttgaacacaaatgtggatttatatcaa
agtttgcaaaaattactagctgataaaaaacttgtggattcccttgatccagaaacaagg
cgagtggctgaactgtttatgtttgattttgaaattagtggaatccatctagacaaagaa
aagcgtaaaagagcagtggacctcaatgttaaaatcttggatttgagtagtacatttctt
atgggaaccaattttcccaacaagattgagaagcatctcttaccagaacacattcgtcgt
aactttacatctgctggggatcatatcataattgatggtctccacgcagaatcaccagat
gacttggtgcgagaagctgcttataaaatttttctttatcccaatgctggtcaattgaaa
tgtttagaagaattgctcagcagcagagatcttctggcaaagttggtggggtattccacg
ttttctcacagggctctccaaggaacgatagctaaaaatccagagactgtcatgcagttc
cttgaaaaactatctgacaaactttctgaaagaactctgaaagattttgagatgatacga
gggatgaaaatgaaactgaatcctcaaaattccgaagtaatgccctgggaccccccttac
tacagtggtgtgattcgtgcagaaaggtataatattgagcccagcctatattgcccgttt
ttctctcttggagcatgcatggaaggcctgaatattttgcttaacagactgttggggatt
tcattatatgcagagcagcctgcaaaaggagaggtgtggagcgaagatgtccgaaaactg
gctgttgttcatgaatctgaaggattgttggggtacatttactgtgatttttttcagcga
gcagacaaaccacatcaggattgccatttcactatccgtggaggcagactaaaggaagat
ggagactatcaactcccagttgtagttcttatgctgaatcttccccgttcctcaaggagt
tctccaactttgctaactcctagcatgatggaaaatcttttccatgaaatgggacatgcc
atgcattcaatgctaggacgtactcgttaccaacacgtcactgggaccaggtgccctact
gattttgctgaggttccttctattctgatggagtactttgcaaatgattatcgagtagtt
aaccaatttgccagacattatcagactggacagccactgccaaaaaatatggtgtctcgt
ctttgtgaatctaaaaaggtttgtgctgcagctgatatgcaacttcaggtcttttatgcc
actctggatcaaatctaccatgggaagcatcccctgaggaattcaaccacagacattctc
aaggaaacacaagagaaattctatggcctaccatatgttccaaatactgcctggcagctg
cgattcagccacctcgtggggtatggtgctagatattactcttacctcatgtccagagcg
gtcgcctccatggtttggaaggagtgttttctacaggatcctttcaacagggctgccggg
gagcgctatcgcagggagatgctggcccacggtggaggcagggagcccatgctcatggtt
gaaggtatgcttcagaagtgtccttctgttgatgacttcgtaagtgccctcgtttccgac
ttggatctggacttcgaaactttcctcatggattctgaataa
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