Entry |
|
Symbol |
UCHL1, HEL-117, HEL-S-53, NDGOA, PARK5, PGP_9.5, PGP9.5, PGP95, SPG79, SPG79A, UCHL-1, Uch-L1
|
Name |
(RefSeq) ubiquitin C-terminal hydrolase L1
|
KO |
|
Organism |
|
Pathway |
hsa05022 | Pathways of neurodegeneration - multiple diseases |
|
Network |
|
Element |
N01027 | UCHL1-mediated hydrolysis |
N01028 | Mutation-inactivated UCHL1 to UCHL1-mediated hydrolysis |
|
Disease |
H00266 | Hereditary spastic paraplegia |
|
Brite |
KEGG Orthology (KO) [BR:hsa00001]
09160 Human Diseases
09164 Neurodegenerative disease
05012 Parkinson disease
7345 (UCHL1)
05022 Pathways of neurodegeneration - multiple diseases
7345 (UCHL1)
09180 Brite Hierarchies
09181 Protein families: metabolism
01002 Peptidases and inhibitors [BR:hsa01002]
7345 (UCHL1)
09182 Protein families: genetic information processing
04121 Ubiquitin system [BR:hsa04121]
7345 (UCHL1)
Enzymes [BR:hsa01000]
3. Hydrolases
3.4 Acting on peptide bonds (peptidases)
3.4.19 Omega peptidases
3.4.19.12 ubiquitinyl hydrolase 1
7345 (UCHL1)
Peptidases and inhibitors [BR:hsa01002]
Cysteine peptidases
Family C12: ubiquitin C-terminal hydrolase family
7345 (UCHL1)
Ubiquitin system [BR:hsa04121]
Deubiquitinating enzyme (DUB)
Ubiquitin-specific proteases (UBPs)
UCH
7345 (UCHL1)
|
SSDB |
|
Motif |
|
Other DBs |
|
Structure |
|
LinkDB |
|
Position |
4:41256928..41268455
|
AA seq |
223 aa
MQLKPMEINPEMLNKVLSRLGVAGQWRFVDVLGLEEESLGSVPAPACALLLLFPLTAQHE
NFRKKQIEELKGQEVSPKVYFMKQTIGNSCGTIGLIHAVANNQDKLGFEDGSVLKQFLSE
TEKMSPEDRAKCFEKNEAIQAAHDAVAQEGQCRVDDKVNFHFILFNNVDGHLYELDGRMP
FPVNHGASSEDTLLKDAAKVCREFTEREQGEVRFSAVALCKAA |
NT seq |
672 nt +upstreamnt +downstreamnt
atgcagctcaagccgatggagatcaaccccgagatgctgaacaaagtgctgtcccggctg
ggggtcgccggccagtggcgcttcgtggacgtgctggggctggaagaggagtctctgggc
tcggtgccagcgcctgcctgcgcgctgctgctgctgtttcccctcacggcccagcatgag
aacttcaggaaaaagcagattgaagagctgaagggacaagaagttagtcctaaagtgtac
ttcatgaagcagaccattgggaattcctgtggcacaatcggacttattcacgcagtggcc
aataatcaagacaaactgggatttgaggatggatcagttctgaaacagtttctttctgaa
acagagaaaatgtcccctgaagacagagcaaaatgctttgaaaagaatgaggccatacag
gcagcccatgatgccgtggcacaggaaggccaatgtcgggtagatgacaaggtgaatttc
cattttattctgtttaacaacgtggatggccacctctatgaacttgatggacgaatgcct
tttccggtgaaccatggcgccagttcagaggacaccctgctgaaggacgctgccaaggtc
tgcagagaattcaccgagcgtgagcaaggagaagtccgcttctctgccgtggctctctgc
aaggcagcctaa |