KEGG   Pongo pygmaeus (Bornean orangutan): 129032560
Entry
129032560         CDS       T10128                                 
Symbol
MCCC1
Name
(RefSeq) methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X1
  KO
K01968  3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
Organism
ppyg  Pongo pygmaeus (Bornean orangutan)
Pathway
ppyg00280  Valine, leucine and isoleucine degradation
ppyg01100  Metabolic pathways
Module
ppyg_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:ppyg00001]
 09100 Metabolism
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    129032560 (MCCC1)
Enzymes [BR:ppyg01000]
 6. Ligases
  6.4  Forming carbon-carbon bonds
   6.4.1  Ligases that form carbon-carbon bonds (only sub-subclass identified to date)
    6.4.1.4  methylcrotonoyl-CoA carboxylase
     129032560 (MCCC1)
SSDB
Motif
Pfam: CPSase_L_D2 Biotin_carb_N Biotin_carb_C Biotin_lipoyl Dala_Dala_lig_C ATP-grasp Biotin_lipoyl_2 RimK ATP-grasp_3 ATPgrasp_ST BT_MCC_alpha ATP-grasp_4 GARS_A RnfC_N NQRA_N MCCA_BT 2OG-FeII_Oxy_2
Other DBs
NCBI-GeneID: 129032560
NCBI-ProteinID: XP_054335943
LinkDB
Position
2:complement(192234165..192311755)
AA seq 725 aa
MAAASAVSVLLVAAERNRWHRLPSLLLPPRTWVWRQRTMKYPTTTGRNITKVLIANRGEI
ACRVMRTAKKLGVQTVAVYSEADRNSMHVDMADEAYSIGPAPSQQSYLSMEKIIQVAKTS
AAQAIHPGYGFLSENMEFAELCKQEGIIFIGPPPSAIRDMGIKSTSKSIMAAAGVPVVEG
YHGEDQSDQCLKEHAGRIGYPVMIKAVRGGGGKGMRIVRSEQEFQEQLESARREAKKSFN
DDAMLIEKFVDTPRHVEVQVFGDHHGNAVYLFERDCSVQRRHQKIIEEAPAPGIKPEVRK
KLGEAAVRAAKAVNYVGAGTVEFIMDSKHNFYFMEMNTRLQVEHPVTEMITGTDLVEWQL
RIAAGEKIPLSQEEITLQGHAFEARIYAEDPGNNFMPGAGPLVHLSTPRADPSTRIETGV
RQGDEVSVHYDPMIAKLVVWAADRQAALTKLRYSLLQYNIVGLHTNIDFLLNLSGHPEFE
AGNVHTDFIPQHHKQLLLSQKAATKESLCQAALGLILKEKAMTDAFTLQAHDQFSPFSSS
SGRRLNISYTRNMTLKDGKNNVAIAVTYNHDGSYSMQIEDKTFQVLGDLYSEGDCTYLKC
SVNGVASKVKLIILENTIYLFSKEGSTEIDIPVPKYLSSVSSQGTQGGPLAPMTGTIEKV
FVKAGDKVKAGDSLMVMIAMKMEHTIKAPKDGTIKKVFYREGAQADRHTPLVEFEEEESD
KRESE
NT seq 2178 nt   +upstreamnt  +downstreamnt
atggcagcggcctctgcggtgtcggtgctgctagtggcggcggagaggaaccggtggcat
cgtctcccgagcctgcttctgccgccgaggacatgggtgtggaggcaaagaaccatgaag
tacccaacaaccacaggaagaaacattaccaaggtcctcattgcaaacagaggagaaatt
gcctgcagggtgatgcgcacagccaaaaaactgggtgtacagactgtggcggtttatagt
gaggctgacagaaattccatgcatgtagatatggcagatgaagcatattccatcggcccc
gctccctcccagcagagctacctatctatggagaaaatcattcaagtggccaagacatct
gctgcacaggctatccatccaggatatggttttctttcagaaaacatggaatttgctgaa
ctttgtaagcaagaaggaattatttttataggccctcctccatctgcaattagagacatg
ggtataaagagcacatccaaatccataatggctgctgctggagtacctgttgtggagggt
tatcatggtgaggaccaatcagatcagtgcctgaaggaacacgccgggagaattggctat
cctgtcatgattaaagccgtccggggtggaggaggaaaaggaatgaggattgttagatca
gaacaagaatttcaagaacagttagagtcagcgcggagagaagctaagaagtctttcaat
gatgatgctatgctgatcgagaagtttgtagacacaccgaggcatgtagaagtccaggtg
tttggtgatcaccatggcaatgctgtgtacttgtttgaaagagactgtagtgtgcagagg
cgacatcagaagatcattgaggaggccccagcgcctggtattaaacctgaagtaagaaaa
aagctgggagaagctgcagtcagagctgctaaagctgtaaattatgttggagcagggact
gtggagtttattatggactcgaaacataatttctatttcatggagatgaatacaaggctg
caagtggaacatcctgttactgagatgatcacaggaactgacttggtggagtggcagctt
agaattgcagcaggagagaagattcctttgagccaggaagaaataactctgcagggccat
gccttcgaagctagaatatacgcagaagatcctggcaataacttcatgcctggggctggc
ccattagtgcacctctctactcctcgagcagacccttccaccaggattgaaactggagta
cggcaaggagacgaagtttccgtgcattatgaccccatgattgcgaagctggtcgtgtgg
gctgcagatcgccaggcggcattgacaaaactgaggtacagccttcttcagtacaatatt
gttggactgcacaccaacattgacttcttactcaacctgtctggccacccagagtttgaa
gctgggaacgtgcacactgatttcatccctcaacaccacaaacagttgttgctcagtcag
aaggctgcaaccaaagagtctttatgccaggcagccctgggtctcatcctcaaggagaaa
gccatgaccgacgctttcactcttcaggcacacgatcaattctctccattttcatctagc
agtggaagaagactgaatatctcttataccagaaacatgactcttaaagatggtaaaaac
aatgtagccatagctgtaacatataaccatgatgggtcttatagcatgcagattgaagat
aaaactttccaagtcctcggtgatctttacagcgagggagactgcacttacctgaaatgt
tctgttaatggagttgctagtaaagtgaagctgattatcctggaaaacactatttaccta
ttttccaaggaaggaagtactgagattgacattccagtccccaaatacttatcttctgtg
agctcacaaggaactcagggaggccccttagctcctatgactggaaccattgaaaaggtg
tttgtcaaagctggagacaaagtgaaagcgggagattccctcatggttatgatcgccatg
aagatggagcataccataaaggctccaaaggatggcacaataaagaaagtgttctacaga
gagggtgctcaggccgacagacacactcctttagtcgagtttgaggaggaagaatcagac
aaaagggaatcggaataa

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