Human Diseases in ICD-10 Classification

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 1. Certain infectious and parasitic diseases (A00-B99)
 2. Neoplasms (C00-D48)
 3. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
 4. Endocrine, nutritional and metabolic diseases (E00-E90)
   E00-E07  Disorders of thyroid gland
   E10-E14  Diabetes mellitus
   E15-E16  Other disorders of glucose regulation and pancreatic internal secretion
   E20-E35  Disorders of other endocrine glands
   E40-E46  Malnutrition
   E50-E64  Other nutritional deficiencies
   E65-E68  Obesity and other hyperalimentation
   E70-E90  Metabolic disorders
     E70  Disorders of aromatic amino-acid metabolism
     E71  Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
       H00172  Maple syrup urine disease
       H02000  Dihydrolipoamide dehydrogenase deficiency
       H00173  Isovaleric acidemia (IVA)
       H00181  3-Methylcrotonylglycinuria
       H00175  Propionic acidemia
       H00174  Methylmalonic aciduria (MMA)
       H00179  3-Hydroxy-3-methylglutaryl-CoA lyase deficiency
       H00162  Sjogren-Larsson syndrome
       H00176  Adrenoleukodystrophy (ALD)
       H00178  Glutaric acidemia
       H00525  Disorders of mitochondrial fatty-acid oxidation
       H01980  SCAD deficiency
       H00488  MCAD deficiency
       H00489  LCHAD deficiency
       H00392  VLCAD deficiency
       H01981  Carnitine palmitoyltransferase I deficiency
       H01982  Carnitine palmitoyltransferase II deficiency
       H01983  Carnitine-acylcarnitine translocase deficiency
       H00375  SBCAD deficiency
       H00654  Barth syndrome (BTHS)
       H00754  3-Methylglutaconic aciduria (MGCA)
       H00925  2-Methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiency
       H01121  Succinyl CoA:3-oxoacid CoA transferase (SCOT) deficiency
       H01123  HMG-CoA synthase (HMGCS) deficiency
       H01279  Isobutyryl-CoA dehydrogenase (IBD) deficiency
       H00177  Adrenoleukodystrophy, neonatal (NALD)
       H01349  Methacrylic aciduria
       H01352  Mitochondrial trifunctional protein deficiency
       H01364  3-Hydroxyacyl-CoA dehydrogenase deficiency
       H00407  Peroxisomal beta-oxidation enzyme deficiency
       H02085  Acyl-CoA dehydrogenase 9 deficiency
       H02096  Peroxisomal acyl-CoA oxidase deficiency
       H02098  D-bifunctional protein deficiency
       H01589  Systemic primary carnitine deficiency
       H01929  2,4-Dienoyl-CoA reductase deficiency
       H02109  Combined malonic and methylmalonic aciduria
       H02136  Branched-chain ketoacid dehydrogenase kinase deficiency
     E72  Other disorders of amino-acid metabolism
     E73  Lactose intolerance
     E74  Other disorders of carbohydrate metabolism
     E75  Disorders of sphingolipid metabolism and other lipid storage disorders
     E76  Disorders of glycosaminoglycan metabolism
     E77  Disorders of glycoprotein metabolism
     E78  Disorders of lipoprotein metabolism and other lipidaemias
     E79  Disorders of purine and pyrimidine metabolism
     E80  Disorders of porphyrin and bilirubin metabolism
     E83  Disorders of mineral metabolism
     E84  Cystic fibrosis
     E85  Amyloidosis
     E88  Other metabolic disorders
 5. Mental and behavioural disorders (F00-F99)
 6. Diseases of the nervous system (G00-G99)
 7. Diseases of the eye and adnexa (H00-H59)
 8. Diseases of the ear and mastoid process (H60-H95)
 9. Diseases of the circulatory system (I00-I99)
 10. Diseases of the respiratory system (J00-J99)
 11. Diseases of the digestive system (K00-K93)
 12. Diseases of the skin and subcutaneous tissue (L00-L99)
 13. Diseases of the musculoskeletal system and connective tissue (M00-M99)
 14. Diseases of the genitourinary system (N00-N99)
 15. Pregnancy, childbirth and the puerperium (O00-O99)
 16. Certain conditions originating in the perinatal period (P00-P96)
 17. Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
 18. Symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)
 19. Injury, poisoning and certain other consequences of external causes (S00-T98)
 20. External causes of morbidity and mortality (V01-Y98)
 21. Factors influencing health status and contact with health services (Z00-Z99)
 22. Codes for special purposes (U00-U85)

Last updated: July 12, 2018
Classification taken from ICD-10 Version 2016

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