1. Certain infectious and parasitic diseases (A00-B99)
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2. Neoplasms (C00-D48)
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3. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
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4. Endocrine, nutritional and metabolic diseases (E00-E90)
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E00-E07 Disorders of thyroid gland
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E10-E14 Diabetes mellitus
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E15-E16 Other disorders of glucose regulation and pancreatic internal secretion
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E20-E35 Disorders of other endocrine glands
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E40-E46 Malnutrition
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E50-E64 Other nutritional deficiencies
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E65-E68 Obesity and other hyperalimentation
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E70-E90 Metabolic disorders
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E70 Disorders of aromatic amino-acid metabolism
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E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
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E72 Other disorders of amino-acid metabolism
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H00275 Cystinosis
H00843 Hartnup disorder
H00692 Lowe syndrome
H00182 Cystathioninuria
H00183 Homocystinuria
H00184 Hypermethioninemia
H00164 Carbamoyl phosphate synthetase I deficiency
H00185 Citrullinemia
H00186 Hyperargininemia
H00178 Glutaric acidemia
H00188 Hyperlysinemia
H00189 Ornithinaemia
H00187 Ornithine transcarbamylase deficiency
H00190 Hyperprolinemia
H00191 Nonketotic hyperglycinemia
H00200 Beta-ureidopropionase deficiency
H00834 Guanidinoacetate methyltransferase (GAMT) deficiency
H00835 Succinic semialdehyde dehydrogenase (SSADH) deficiency
H00849 Creatine deficiency syndrome
H00899 Lysinuric protein intolerance (LPI)
H00901 Cystinuria
H00905 Iminoglycinuria
H00923 Congenital systemic glutamine deficiency (CSGD)
H01003 Dimethylglycine dehydrogenase deficiency (DMGDHD)
H01028 Argininosuccinic aciduria (ARGINSA)
H01032 N-acetylglutamate synthase (NAGS) deficiency
H01079 3-Phosphoglycerate dehydrogenase (3-PGDH) deficiency
H01076 Alpha-methylacetoacetic aciduria
H01119 Prolidase deficiency (PD)
H01198 Fanconi renotubular syndrome (FTS)
H01237 Sulfite oxidase deficiency
H01242 Saccharopinuria
H01257 GABA-transaminase deficiency
H01268 Hyperornithinemia-hyperammonemia-homocitrullinuria syndrome
H01283 Malonyl-CoA decarboxylase deficiency
H01386 Asparagine synthetase deficiency
H01285 Methylcobalamin deficiency type G (cblG)
H01398 Primary hyperammonemic disorders (Urea cycle disorders)
H01400 Secondary hyperammonemia
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E73 Lactose intolerance
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E74 Other disorders of carbohydrate metabolism
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E75 Disorders of sphingolipid metabolism and other lipid storage disorders
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E76 Disorders of glycosaminoglycan metabolism
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E77 Disorders of glycoprotein metabolism
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E78 Disorders of lipoprotein metabolism and other lipidaemias
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E79 Disorders of purine and pyrimidine metabolism
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E80 Disorders of porphyrin and bilirubin metabolism
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E83 Disorders of mineral metabolism
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E84 Cystic fibrosis
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E85 Amyloidosis
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E88 Other metabolic disorders
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5. Mental and behavioural disorders (F00-F99)
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6. Diseases of the nervous system (G00-G99)
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7. Diseases of the eye and adnexa (H00-H59)
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8. Diseases of the ear and mastoid process (H60-H95)
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9. Diseases of the circulatory system (I00-I99)
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10. Diseases of the respiratory system (J00-J99)
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11. Diseases of the digestive system (K00-K93)
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12. Diseases of the skin and subcutaneous tissue (L00-L99)
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13. Diseases of the musculoskeletal system and connective tissue (M00-M99)
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14. Diseases of the genitourinary system (N00-N99)
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15. Pregnancy, childbirth and the puerperium (O00-O99)
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16. Certain conditions originating in the perinatal period (P00-P96)
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17. Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
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18. Symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)
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19. Injury, poisoning and certain other consequences of external causes (S00-T98)
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20. External causes of morbidity and mortality (V01-Y98)
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21. Factors influencing health status and contact with health services (Z00-Z99)
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22. Codes for special purposes (U00-U85)
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