|
KO |
09100 Metabolism
|
|
|
09101 Carbohydrate metabolism
|
00010 Glycolysis / Gluconeogenesis [PATH:hsa00010]
|
00020 Citrate cycle (TCA cycle) [PATH:hsa00020]
|
00030 Pentose phosphate pathway [PATH:hsa00030]
|
00040 Pentose and glucuronate interconversions [PATH:hsa00040]
|
00051 Fructose and mannose metabolism [PATH:hsa00051]
|
00052 Galactose metabolism [PATH:hsa00052]
|
00053 Ascorbate and aldarate metabolism [PATH:hsa00053]
|
00500 Starch and sucrose metabolism [PATH:hsa00500]
|
00520 Amino sugar and nucleotide sugar metabolism [PATH:hsa00520]
|
00620 Pyruvate metabolism [PATH:hsa00620]
|
00630 Glyoxylate and dicarboxylate metabolism [PATH:hsa00630]
|
84532 ACSS1; acyl-CoA synthetase short chain family member 1
55902 ACSS2; acyl-CoA synthetase short chain family member 2
4190 MDH1; malate dehydrogenase 1
4191 MDH2; malate dehydrogenase 2
1431 CS; citrate synthase
50 ACO2; aconitase 2
48 ACO1; aconitase 1
39 ACAT2; acetyl-CoA acetyltransferase 2
38 ACAT1; acetyl-CoA acetyltransferase 1
84693 MCEE; methylmalonyl-CoA epimerase
5095 PCCA; propionyl-CoA carboxylase subunit alpha
5096 PCCB; propionyl-CoA carboxylase subunit beta
4594 MMUT; methylmalonyl-CoA mutase
51179 HAO2; hydroxyacid oxidase 2
54363 HAO1; hydroxyacid oxidase 1
847 CAT; catalase
9380 GRHPR; glyoxylate and hydroxypyruvate reductase
283871 PGP; phosphoglycolate phosphatase
189 AGXT; alanine--glyoxylate and serine--pyruvate aminotransferase
2752 GLUL; glutamate-ammonia ligase
6472 SHMT2; serine hydroxymethyltransferase 2
6470 SHMT1; serine hydroxymethyltransferase 1
2731 GLDC; glycine decarboxylase
275 AMT; aminomethyltransferase
1738 DLD; dihydrolipoamide dehydrogenase
2653 GCSH; glycine cleavage system protein H
81888 HYI; hydroxypyruvate isomerase (putative)
132158 GLYCTK; glycerate kinase
112817 HOGA1; 4-hydroxy-2-oxoglutarate aldolase 1
125061 AFMID; arylformamidase
|
K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K00025 MDH1; malate dehydrogenase [EC:1.1.1.37]
K00026 MDH2; malate dehydrogenase [EC:1.1.1.37]
K01647 CS; citrate synthase [EC:2.3.3.1]
K01681 ACO; aconitate hydratase [EC:4.2.1.3]
K01681 ACO; aconitate hydratase [EC:4.2.1.3]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K05606 MCEE; methylmalonyl-CoA/ethylmalonyl-CoA epimerase [EC:5.1.99.1]
K01965 PCCA; propionyl-CoA carboxylase alpha chain [EC:6.4.1.3]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K11517 HAO; (S)-2-hydroxy-acid oxidase [EC:1.1.3.15]
K11517 HAO; (S)-2-hydroxy-acid oxidase [EC:1.1.3.15]
K03781 katE; catalase [EC:1.11.1.6]
K00049 GRHPR; glyoxylate/hydroxypyruvate reductase [EC:1.1.1.79 1.1.1.81]
K19269 PGP; phosphoglycolate phosphatase [EC:3.1.3.18 3.1.3.48]
K00830 AGXT; alanine-glyoxylate transaminase / serine-glyoxylate transaminase / serine-pyruvate transaminase [EC:2.6.1.44 2.6.1.45 2.6.1.51]
K01915 glnA; glutamine synthetase [EC:6.3.1.2]
K00600 glyA; glycine hydroxymethyltransferase [EC:2.1.2.1]
K00600 glyA; glycine hydroxymethyltransferase [EC:2.1.2.1]
K00281 GLDC; glycine dehydrogenase [EC:1.4.4.2]
K00605 gcvT; aminomethyltransferase [EC:2.1.2.10]
K00382 DLD; dihydrolipoamide dehydrogenase [EC:1.8.1.4]
K02437 gcvH; glycine cleavage system H protein
K01816 hyi; hydroxypyruvate isomerase [EC:5.3.1.22]
K11529 gck; glycerate 2-kinase [EC:2.7.1.165]
K18123 HOGA1; 4-hydroxy-2-oxoglutarate aldolase [EC:4.1.3.16]
K01432 AFMID; arylformamidase [EC:3.5.1.9]
|
00640 Propanoate metabolism [PATH:hsa00640]
|
84532 ACSS1; acyl-CoA synthetase short chain family member 1
55902 ACSS2; acyl-CoA synthetase short chain family member 2
79611 ACSS3; acyl-CoA synthetase short chain family member 3
593 BCKDHA; branched chain keto acid dehydrogenase E1 subunit alpha
594 BCKDHB; branched chain keto acid dehydrogenase E1 subunit beta
1629 DBT; dihydrolipoamide branched chain transacylase E2
1738 DLD; dihydrolipoamide dehydrogenase
35 ACADS; acyl-CoA dehydrogenase short chain
8310 ACOX3; acyl-CoA oxidase 3, pristanoyl
51 ACOX1; acyl-CoA oxidase 1
3030 HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
1962 EHHADH; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
1892 ECHS1; enoyl-CoA hydratase, short chain 1
26275 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase
31 ACACA; acetyl-CoA carboxylase alpha
32 ACACB; acetyl-CoA carboxylase beta
23417 MLYCD; malonyl-CoA decarboxylase
18 ABAT; 4-aminobutyrate aminotransferase
5095 PCCA; propionyl-CoA carboxylase subunit alpha
5096 PCCB; propionyl-CoA carboxylase subunit beta
55862 ECHDC1; ethylmalonyl-CoA decarboxylase 1
84693 MCEE; methylmalonyl-CoA epimerase
4594 MMUT; methylmalonyl-CoA mutase
8802 SUCLG1; succinate-CoA ligase GDP/ADP-forming subunit alpha
8801 SUCLG2; succinate-CoA ligase GDP-forming subunit beta
8803 SUCLA2; succinate-CoA ligase ADP-forming subunit beta
4329 ALDH6A1; aldehyde dehydrogenase 6 family member A1
160287 LDHAL6A; lactate dehydrogenase A like 6A
92483 LDHAL6B; lactate dehydrogenase A like 6B
3939 LDHA; lactate dehydrogenase A
3945 LDHB; lactate dehydrogenase B
3948 LDHC; lactate dehydrogenase C
39 ACAT2; acetyl-CoA acetyltransferase 2
38 ACAT1; acetyl-CoA acetyltransferase 1
|
K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01895 ACSS1_2; acetyl-CoA synthetase [EC:6.2.1.1]
K01908 ACSS3; propionyl-CoA synthetase [EC:6.2.1.17]
K00166 BCKDHA; 2-oxoisovalerate dehydrogenase E1 component alpha subunit [EC:1.2.4.4]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component beta subunit [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoamide dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K00232 E1.3.3.6; acyl-CoA oxidase [EC:1.3.3.6]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K11262 ACACA; acetyl-CoA carboxylase / biotin carboxylase 1 [EC:6.4.1.2 6.3.4.14 2.1.3.15]
K01946 ACACB; acetyl-CoA carboxylase / biotin carboxylase 2 [EC:6.4.1.2 6.3.4.14 2.1.3.15]
K01578 MLYCD; malonyl-CoA decarboxylase [EC:4.1.1.9]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K01965 PCCA; propionyl-CoA carboxylase alpha chain [EC:6.4.1.3]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K18426 ECHDC1; ethylmalonyl-CoA/methylmalonyl-CoA decarboxylase [EC:4.1.1.94 4.1.1.-]
K05606 MCEE; methylmalonyl-CoA/ethylmalonyl-CoA epimerase [EC:5.1.99.1]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K01899 LSC1; succinyl-CoA synthetase alpha subunit [EC:6.2.1.4 6.2.1.5]
K01900 LSC2; succinyl-CoA synthetase beta subunit [EC:6.2.1.4 6.2.1.5]
K01900 LSC2; succinyl-CoA synthetase beta subunit [EC:6.2.1.4 6.2.1.5]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00016 LDH; L-lactate dehydrogenase [EC:1.1.1.27]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
|
00650 Butanoate metabolism [PATH:hsa00650]
|
00660 C5-Branched dibasic acid metabolism
|
00562 Inositol phosphate metabolism [PATH:hsa00562]
|
|
|
09102 Energy metabolism
|
|
|
09103 Lipid metabolism
|
|
|
09104 Nucleotide metabolism
|
|
|
09105 Amino acid metabolism
|
00250 Alanine, aspartate and glutamate metabolism [PATH:hsa00250]
|
00260 Glycine, serine and threonine metabolism [PATH:hsa00260]
|
00270 Cysteine and methionine metabolism [PATH:hsa00270]
|
00280 Valine, leucine and isoleucine degradation [PATH:hsa00280]
|
587 BCAT2; branched chain amino acid transaminase 2
586 BCAT1; branched chain amino acid transaminase 1
259307 IL4I1; interleukin 4 induced 1
593 BCKDHA; branched chain keto acid dehydrogenase E1 subunit alpha
594 BCKDHB; branched chain keto acid dehydrogenase E1 subunit beta
1629 DBT; dihydrolipoamide branched chain transacylase E2
1738 DLD; dihydrolipoamide dehydrogenase
35 ACADS; acyl-CoA dehydrogenase short chain
34 ACADM; acyl-CoA dehydrogenase medium chain
3712 IVD; isovaleryl-CoA dehydrogenase
36 ACADSB; acyl-CoA dehydrogenase short/branched chain
27034 ACAD8; acyl-CoA dehydrogenase family member 8
3030 HADHA; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha
1962 EHHADH; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase
1892 ECHS1; enoyl-CoA hydratase, short chain 1
3033 HADH; hydroxyacyl-CoA dehydrogenase
3028 HSD17B10; hydroxysteroid 17-beta dehydrogenase 10
30 ACAA1; acetyl-CoA acyltransferase 1
10449 ACAA2; acetyl-CoA acyltransferase 2
3032 HADHB; hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta
5095 PCCA; propionyl-CoA carboxylase subunit alpha
5096 PCCB; propionyl-CoA carboxylase subunit beta
84693 MCEE; methylmalonyl-CoA epimerase
4594 MMUT; methylmalonyl-CoA mutase
26275 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase
11112 HIBADH; 3-hydroxyisobutyrate dehydrogenase
4329 ALDH6A1; aldehyde dehydrogenase 6 family member A1
217 ALDH2; aldehyde dehydrogenase 2 family member
224 ALDH3A2; aldehyde dehydrogenase 3 family member A2
219 ALDH1B1; aldehyde dehydrogenase 1 family member B1
501 ALDH7A1; aldehyde dehydrogenase 7 family member A1
223 ALDH9A1; aldehyde dehydrogenase 9 family member A1
316 AOX1; aldehyde oxidase 1
197322 ACSF3; acyl-CoA synthetase family member 3
18 ABAT; 4-aminobutyrate aminotransferase
64902 AGXT2; alanine--glyoxylate aminotransferase 2
56922 MCCC1; methylcrotonoyl-CoA carboxylase 1
64087 MCCC2; methylcrotonoyl-CoA carboxylase 2
549 AUH; AU RNA binding methylglutaconyl-CoA hydratase
3155 HMGCL; 3-hydroxy-3-methylglutaryl-CoA lyase
54511 HMGCLL1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase like 1
5019 OXCT1; 3-oxoacid CoA-transferase 1
64064 OXCT2; 3-oxoacid CoA-transferase 2
65985 AACS; acetoacetyl-CoA synthetase
39 ACAT2; acetyl-CoA acetyltransferase 2
38 ACAT1; acetyl-CoA acetyltransferase 1
3157 HMGCS1; 3-hydroxy-3-methylglutaryl-CoA synthase 1
3158 HMGCS2; 3-hydroxy-3-methylglutaryl-CoA synthase 2
|
K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K00826 E2.6.1.42; branched-chain amino acid aminotransferase [EC:2.6.1.42]
K03334 IL4I1; L-amino-acid oxidase [EC:1.4.3.2]
K00166 BCKDHA; 2-oxoisovalerate dehydrogenase E1 component alpha subunit [EC:1.2.4.4]
K00167 BCKDHB; 2-oxoisovalerate dehydrogenase E1 component beta subunit [EC:1.2.4.4]
K09699 DBT; 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase) [EC:2.3.1.168]
K00382 DLD; dihydrolipoamide dehydrogenase [EC:1.8.1.4]
K00248 ACADS; butyryl-CoA dehydrogenase [EC:1.3.8.1]
K00249 ACADM; acyl-CoA dehydrogenase [EC:1.3.8.7]
K00253 IVD; isovaleryl-CoA dehydrogenase [EC:1.3.8.4]
K09478 ACADSB; short-chain 2-methylacyl-CoA dehydrogenase [EC:1.3.8.5]
K11538 ACAD8; isobutyryl-CoA dehydrogenase [EC:1.3.99.-]
K07515 HADHA; enoyl-CoA hydratase / long-chain 3-hydroxyacyl-CoA dehydrogenase [EC:4.2.1.17 1.1.1.211]
K07514 EHHADH; enoyl-CoA hydratase / 3-hydroxyacyl-CoA dehydrogenase / 3,2-trans-enoyl-CoA isomerase [EC:4.2.1.17 1.1.1.35 5.3.3.8]
K07511 ECHS1; enoyl-CoA hydratase [EC:4.2.1.17]
K00022 HADH; 3-hydroxyacyl-CoA dehydrogenase [EC:1.1.1.35]
K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
K07513 ACAA1; acetyl-CoA acyltransferase 1 [EC:2.3.1.16]
K07508 ACAA2; acetyl-CoA acyltransferase 2 [EC:2.3.1.16]
K07509 HADHB; acetyl-CoA acyltransferase [EC:2.3.1.16]
K01965 PCCA; propionyl-CoA carboxylase alpha chain [EC:6.4.1.3]
K01966 PCCB; propionyl-CoA carboxylase beta chain [EC:6.4.1.3 2.1.3.15]
K05606 MCEE; methylmalonyl-CoA/ethylmalonyl-CoA epimerase [EC:5.1.99.1]
K01847 MUT; methylmalonyl-CoA mutase [EC:5.4.99.2]
K05605 HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [EC:3.1.2.4]
K00020 HIBADH; 3-hydroxyisobutyrate dehydrogenase [EC:1.1.1.31]
K00140 mmsA; malonate-semialdehyde dehydrogenase (acetylating) / methylmalonate-semialdehyde dehydrogenase [EC:1.2.1.18 1.2.1.27]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K00128 ALDH; aldehyde dehydrogenase (NAD+) [EC:1.2.1.3]
K14085 ALDH7A1; aldehyde dehydrogenase family 7 member A1 [EC:1.2.1.31 1.2.1.8 1.2.1.3]
K00149 ALDH9A1; aldehyde dehydrogenase family 9 member A1 [EC:1.2.1.47 1.2.1.3]
K00157 AOX; aldehyde oxidase [EC:1.2.3.1]
K18660 ACSF3; malonyl-CoA/methylmalonyl-CoA synthetase [EC:6.2.1.-]
K13524 ABAT; 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase [EC:2.6.1.19 2.6.1.22]
K00827 AGXT2; alanine-glyoxylate transaminase / (R)-3-amino-2-methylpropionate-pyruvate transaminase [EC:2.6.1.44 2.6.1.40]
K01968 E6.4.1.4A; 3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
K01969 E6.4.1.4B; 3-methylcrotonyl-CoA carboxylase beta subunit [EC:6.4.1.4]
K05607 AUH; methylglutaconyl-CoA hydratase [EC:4.2.1.18]
K01640 E4.1.3.4; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01640 E4.1.3.4; hydroxymethylglutaryl-CoA lyase [EC:4.1.3.4]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01027 OXCT; 3-oxoacid CoA-transferase [EC:2.8.3.5]
K01907 AACS; acetoacetyl-CoA synthetase [EC:6.2.1.16]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K00626 ACAT; acetyl-CoA C-acetyltransferase [EC:2.3.1.9]
K01641 E2.3.3.10; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
K01641 E2.3.3.10; hydroxymethylglutaryl-CoA synthase [EC:2.3.3.10]
|
00290 Valine, leucine and isoleucine biosynthesis [PATH:hsa00290]
|
00300 Lysine biosynthesis
|
00310 Lysine degradation [PATH:hsa00310]
|
00220 Arginine biosynthesis [PATH:hsa00220]
|
00330 Arginine and proline metabolism [PATH:hsa00330]
|
00340 Histidine metabolism [PATH:hsa00340]
|
00350 Tyrosine metabolism [PATH:hsa00350]
|
00360 Phenylalanine metabolism [PATH:hsa00360]
|
00380 Tryptophan metabolism [PATH:hsa00380]
|
00400 Phenylalanine, tyrosine and tryptophan biosynthesis [PATH:hsa00400]
|
|
|
09106 Metabolism of other amino acids
|
|
|
09107 Glycan biosynthesis and metabolism
|
|
|
09108 Metabolism of cofactors and vitamins
|
|
|
09109 Metabolism of terpenoids and polyketides
|
|
|
09110 Biosynthesis of other secondary metabolites
|
|
|
09111 Xenobiotics biodegradation and metabolism
|
|
|
09112 Not included in regular maps
|
|
|
09120 Genetic Information Processing
|
|
|
09130 Environmental Information Processing
|
|
|
09140 Cellular Processes
|
|
|
09150 Organismal Systems
|
|
|
09160 Human Diseases
|
|
|
09180 Brite Hierarchies
|
|
|
09190 Not Included in Pathway or Brite
|