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ENTRY	nt06021
Name	beta-Oxidation in peroxisome
Category	Pathway view; Lipid/glycolipid metabolism
Pathway	hsa01040 Biosynthesis of unsaturated fatty acids hsa00120 Primary bile acid biosynthesis
Module	hsa_M00861 beta-Oxidation, peroxisome, VLCFA hsa_M00862 beta-Oxidation, peroxisome, tri/dihydroxycholestanoyl-CoA => choloyl/chenodeoxycholoyl-CoA
Disease	H00407 Peroxisomal beta-oxidation enzyme deficiency
Display	drug-target relation   disease type

N00776    Very-long-chain-ac.. − ACOX1/3 ⇉ HSD17B4 ⇉ (ACAA1,SCP2) → Very-long-chain-ac..     ACOX1 deficiency     ACOX1*     DBP deficiency         HSD17B4* N00779    Trihydroxycholesta.. − AMACR ⇉ ACOX2 ⇉ HSD17B4 ⇉ SCP2 → Choloyl-CoA     AMACR deficiency     AMACR*     DBP deficiency             HSD17B4*     SCP2 deficiency                 SCP2*

		Disease name	Disease category
ACOX1 deficiency	H02096	Peroxisomal acyl-CoA oxidase deficiency	Inherited metabolic disorder
DBP deficiency	H02098	D-bifunctional protein deficiency	Inherited metabolic disorder
AMACR deficiency	H02099	Alpha-methylacyl-CoA racemase deficiency	Inherited metabolic disorder
SCP2 deficiency	H00874	Leukoencephalopathy with dystonia and motor neuropathy	Inherited metabolic disorder, Peroxisomal disease