KEGG    Network variation - Urea cycle
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ENTRYnt06010
NameUrea cycle
CategoryPathway view; Amino acid metabolism
Pathwayhsa00220 Arginine biosynthesis
Modulehsa_M00029 Urea cycle
DiseaseH01398 Urea cycle disorders
Display drug-target relation   disease type
N00593   
    CPS1 deficiency
    OTC deficiency
    ASS deficiency
    ASL deficiency
    ARG1 deficiency
 
N00599   
N10011   
N00600    NAGS deficiency

Disease nameDisease category
CPS1 deficiencyH00164Carbamoyl phosphate synthetase I deficiencyInherited metabolic disorder
OTC deficiencyH00187Ornithine transcarbamylase deficiencyInherited metabolic disorder
ASS deficiencyH00185CitrullinemiaInherited metabolic disorder
ASL deficiencyH01028Argininosuccinic aciduriaInherited metabolic disorder
ARG1 deficiencyH00186HyperargininemiaInherited metabolic disorder
NAGS deficiencyH01032N-acetylglutamate synthase deficiencyInherited metabolic disorder