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ENTRY | nt06036 |
Name | Lysine degradation |
Category | Pathway view; Amino acid metabolism |
Pathway | hsa00310 Lysine degradation hsa00760 Nicotinate and nicotinamide metabolism hsa00380 Tryptophan metabolism |
Module | hsa_M00032 Lysine degradation, lysine => saccharopine => acetoacetyl-CoA hsa_M00912 NAD biosynthesis, tryptophan => quinolinate => NAD |
Display | drug-target relation disease type |
Disease name | Disease category | ||
Hyperlysinemia/Saccharopinuria | H00188 | Hyperlysinemia | Inherited metabolic disorder |
H01242 | Saccharopinuria | Inherited metabolic disorder | |
PDE | H01247 | Pyridoxine-dependent epilepsy | Nervous system disease |
DECR | H01929 | 2,4-Dienoyl-CoA reductase deficiency | Inherited metabolic disorder, Mitochondrial disease |
AAKAD | H02644 | Alpha-aminoadipic and alpha-ketoadipic aciduria | Inherited metabolic disorder |
GA1 | H00178 | Glutaric acidemia | Inherited metabolic disorder |
Hydroxykynureninuria/VCRL2 | H01583 | Hydroxykynureninuria | Inherited metabolic disorder |
H02087 | Vertebral, cardiac, renal, and limb defects syndrome | Inherited metabolic disorder | |
VCRL1 | H02087 | Vertebral, cardiac, renal, and limb defects syndrome | Inherited metabolic disorder |
VCRL3 | H02087 | Vertebral, cardiac, renal, and limb defects syndrome | Inherited metabolic disorder |