KEGG   DRUG: Cebsulfase alfa
Entry
D12462                      Drug                                   
Name
Cebsulfase alfa (USAN/INN)
Formula
C2322H3564N628O679S24
Exact mass
51877.6956
Mol weight
51910.55
Sequence
RPPNIVLIFA DDLGYGDLGC YGHPSSTTPN LDQLAAGGLR FTDFYVPVSL GTPSRAALLT
GRLPVRMGMY PGVLVPSSRG GLPLEEVTVA EVLAARGYLT GMAGKWHLGV GPEGAFLPPH
QGFHRFLGIP YSHDQGPCQN LTCFPPATPC DGGCDQGLVP IPLLANLSVE AQPPWLPGLE
ARYMAFAHDL MADAQRQDRP FFLYYASHHT HYPQFSGQSF AERSGRGPFG DSLMELDAAV
GTLMTAIGDL GLLEETLVIF TADNGPETMR MSRGGCSGLL RCGKGTTYEG GVREPALAFW
PGHIAPGVTH ELASSLDLLP TLAALAGAPL PNVTLDGFDL SPLLLGTGKS PRQSLFFYPS
YPDEVRGVFA VRTGKYKAHF FTQGSAHSDT TADPACHASS SLTAHEPPLL YDLSKDPGEN
YNLLGGVAGA TPEVLQALKQ LQLLKAQLDA AVTFGPSQVA RGEDPALQIC CHPGCTPRPA
CCHCPDPHA
(Disulfide bridge: 138-154, 143-150, 282-396, 470-482, 471-484, 475-481)
  Type
Peptide
Efficacy
Enzyme replacement
  Type
Enzyme replacement therapy product
Comment
Treatment of metachromic leukodystrophy
Target
ARSA [HSA:410] [KO:K01134]
  Pathway
hsa00600  Sphingolipid metabolism
hsa04142  Lysosome
Brite
Target-based classification of drugs [BR:br08310]
 Enzymes
  Hydrolases (EC3)
   Sulfatases
    ARSA
     D12462  Cebsulfase alfa (USAN/INN)
Other DBs
CAS: 2640112-07-6
PubChem: 497620875
LinkDB

» Japanese version   » Back

DBGET integrated database retrieval system