KEGG   DRUG: Cinaxadamtase alfa
Entry
D12570                      Drug                                   
Name
Cinaxadamtase alfa (INN);
Cinaxadamtase alfa (genetical recombination) (JAN)
Formula
C6287H9806N1862O1917S100
Exact mass
145259.9145
Mol weight
145353.21
Sequence
AAGGILHLEL LVAVGPDVFQ AHREDTERYV LTNLNIGAEL LRDPSLGAQF RVHLVKMVIL
TEPEGAPNIT ANLTSSLLSV CGWSQTINPE DDTDPGHADL VLYITRFDLE LPDGNRQVRG
VTQLGGACSP TWSCLITEDT GFDLGVTIAH EIGHSFGLEH DGAPGSGCGP SGHVMASDGA
APRAGLAWSP CSRRQLLSLL SAGRARCVWD PPRPQPGSAG HPPDAQPGLY YSANEQCRVA
FGPKAVACTF AREHLDMCQA LSCHTDPLDQ SSCSRLLVPL LDGTECGVEK WCSKGRCRSL
VELTPIAAVH GRWSSWGPRS PCSRSCGGGV VTRRRQCNNP RPAFGGRACV GADLQAEMCN
TQACEKTQLE FMSQQCARTD GQPLRSSPGG ASFYHWGAAV PHSQGDALCR HMCRAIGESF
IMKRGDSFLD GTRCMPSGPR EDGTLSLCVS GSCRTFGCDG RMDSQQVWDR CQVCGGDNST
CSPRKGSFTA GRAREYVTFL TVTPNLTSVY IANHRPLFTH LAVRIGGRYV VAGKMSISPN
TTYPSLLEDG RVEYRVALTE DRLPRLEEIR IWGPLQEDAD IQVYRRYGEE YGNLTRPDIT
FTYFQPKPRQ AWVWAAVRGP CSVSCGAGLR WVNYSCLDQA RKELVETVQC QGSQQPPAWP
EACVLEPCPP YWAVGDFGPC SASCGGGLRE RPVRCVEAQG SLLKTLPPAR CRAGAQQPAV
ALETCNPQPC PARWEVSEPS SCTSAGGAGL ALENETCVPG ADGLEAPVTE GPGSVDEKLP
APEPCVGMSC PPGWGHLDAT SAGEKAPSPW GSIRTGAQAA HVWTPAAGSC SVSCGRGLME
LRFLCMDSAL RVPVQEELCG LASKPGSRRE VCQAVPCPAR WQYKLAACSV SCGRGVVRRI
LYCARAHGED DGEEILLDTQ CQGLPRPEPQ EACSLEPCPP RWKVMSLGPC SASCGLGTAR
RSVACVQLDQ GQDVEVDEAA CAALVRPEAS VPCLIADCTY RWHVGTWMEC SVSCGDGIQR
RRDTCLGPQA QAPVPADFCQ HLPKPVTVRG CWAGPCVGQG TPSLVPHEEA AAPGRTTATP
AGASLEWSQA RGLLFSPAPQ PRRLLPGPQE NSVQSSACGR QHLEPTGTID MRGPGQADCA
VAIGRPLGEV VTLRVLESSL NCSAGDMLLL WGRLTWRKMC RKLLDMTFSS KTNTLVVRQR
CGRPGGGVLL RYGSQLAPET FYRECDMQLF GPWGEIVSPS LSPATSNAGG CRLFINVAPH
ARIAIHALAT NMGAGTEGAN ASYILIRDTH SLRTTAFHGQ QVLYWESESS QAEMEFSEGF
LKAQASLRGQ YWTLQSWVPE MQDPQSWKGK EGT
(Disulfide bridge: 81-134, 128-207, 168-191, 237-263, 248-273, 258-292, 286-297, 322-359, 326-364, 337-349, 376-413, 409-448, 434-453, 458-474, 471-481, 621-625, 636-650, 663-668, 695-711, 742-757, 785-790, 845-859, 903-921, 965-981, 1025-1039, 1118-1139, 1162-1180, 1225-1251)
  Type
Peptide
Remark
Product (mixture): D12835<JP/US>
Efficacy
Enzyme replacement (metalloproteinase)
Comment
Recombinant human von Willebrand factor-cleaving protease (ADAMTS13) analog (Q23R)
Target
ADAMTS13 [HSA:11093] [KO:K08627]
  Pathway
hsa04611  Platelet activation
Brite
Target-based classification of drugs [BR:br08310]
 Peptidases and inhibitors
  Metallo peptidases
   Family M12
    ADAMTS13
     D12570  Cinaxadamtase alfa (INN)
Other DBs
CAS: 2406308-29-8
PubChem: 497620983
LinkDB

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