Prepubertal periodontitis (PPP) is a rare and rapidly progressive disease of young children that results in destruction of the periodontal support of the primary dentition. Both autosomal dominant and recessive forms have been reported for PPP. Mutations in cathepsin C gene cause this disease.
Category
Digestive system disease
Brite
Human diseases in ICD-11 classification [BR:br08403]
13 Diseases of the digestive system
Diseases or disorders of orofacial complex
DA0C Periodontal disease
H02050 Prepubertal periodontitis
