Congenital tracheal stenosis (CTS) is a rare but potentially life-threatening disorder that often leads to severe respiratory insufficiency, particularly in neonates and infants. CTS is characterized by complete cartilaginous rings of the trachea without the membranous portion, resulting in various clinical manifestations. More than half of patients with CTS have other congenital anomalies, particularly cardiovascular disease. Moreover, CTS is often associated with pulmonary agenesis or hypoplasia.
Category
Congenital malformation
Brite
Human diseases in ICD-11 classification [BR:br08403]
20 Developmental anomalies
Structural developmental anomalies primarily affecting one body system
Structural developmental anomalies of the respiratory system
LA73 Structural developmental anomalies of trachea
H02600 Congenital tracheal stenosis
