Congenital mitral stenosis (MS) is a spectrum of defects that result in functional and anatomic obstruction of inflow into the left ventricle. Congenital MS classically has been divided into 4 anatomic types: typical, hypoplastic, supramitral ring, and parachute mitral valve. Clinically, the patients present mitral regurgitation, secondary pulmonary hypertension, lung disease and/or cardiac lesions.
Category
Congenital malformation
Brite
Human diseases in ICD-11 classification [BR:br08403]
20 Developmental anomalies
Structural developmental anomalies primarily affecting one body system
Structural developmental anomalies of the circulatory system
Structural developmental anomaly of heart or great vessels
LA87 Congenital anomaly of an atrioventricular valve or atrioventricular septum
H02603 Congenital mitral valve stenosis
