KEGG   ENZYME: 5.4.99.63
Entry
EC 5.4.99.63                Enzyme                                 
Name
ethylmalonyl-CoA mutase;
Ecm
Class
Isomerases;
Intramolecular transferases;
Transferring other groups
Sysname
(2R)-ethylmalonyl-CoA CoA-carbonylmutase
Reaction(IUBMB)
(2R)-ethylmalonyl-CoA = (2S)-methylsuccinyl-CoA [RN:R09292]
Reaction(KEGG)
R09292
Substrate
(2R)-ethylmalonyl-CoA [CPD:C20238]
Product
(2S)-methylsuccinyl-CoA [CPD:C18324]
Comment
The enzyme, characterized from the bacterium Rhodobacter sphaeroides, is involved in the ethylmalonyl-CoA pathway for acetyl-CoA assimilation. Requires adenosylcobalamin for activity.
History
EC 5.4.99.63 created 2015
Pathway
ec00630  Glyoxylate and dicarboxylate metabolism
ec01100  Metabolic pathways
Orthology
K14447  ethylmalonyl-CoA mutase
Genes
KAKKalk_01785
ALKMNKI27_11395
ASEMNNL22_07750
OMEOLMES_2175
CBLYIPM89_03185
GPBHDN1F_15990(smbA)
APPCAP2UW1_2499
ACOGHWD57_21420
PLAPlav_1625
KMNHW532_10490
RBSRHODOSMS8_02644(scpA)
RHZRHPLAN_11770
BVVBHK69_28685
BOPAXW83_14150
BOSBSY19_4455
BOIBLM15_27815
BOFFQV39_17330
BOWNWE53_21895
BOSERMR04_05440
XAUXaut_1197
XDIEZH22_01050
AZCAZC_0992
AQIJ5J86_19840
PTAWDW352_14945
MEAMex_1p0180(ecm)
MDIMETDI0163(ecm)
MEXMext_0290
MCHMchl_0334
MPOMpop_0366
MZAB2G69_08710
METQMSPGM_02520
MRDMrad2831_1106
METM446_0036
MNOMnod_0038
MORMOC_1330
METAY590_00905
MAQUMaq22A_1p32005(meaA)
MPHYMCBMB27_00697
MEEDA075_05080
METDC0214_01275
METXA3862_25065
METSDK389_18850
METIDK427_18530
MMESMMSR116_22780
MTEADK419_07960
MINDmvi_52660
MOGMMB17_10640
MECLCLZ_01550
MFUJABC766_03580
MENIGU700_01550
MENSLOK46_05785
MBRCEBB05_08650
RHJHZY79_04305
CHELAL346_09690
CDQBOQ54_02765
HDNHden_0218
HDTHYPDE_23653
HMCHYPMC_0095(ecm)
HNIW911_17410
HYPHHNF_2948(ecm)
RVARvan_1142
RLACQMO75_08255
FILBN1229_v1_1371(meaA)
FIYBN1229_v1_1370(meaA)
MCGGL4_3338
METGHT051_02990
BVRBVIR_89
BLAGBLTE_34290
MSCBN69_1950
MBRYB1812_17295
MROSEHO51_15485
MHEYH2LOC_019260
MPARF7D14_06260
MIWASS37A_03150
MESZLNB28_09140
MECIRVU70_07885
MEMCOGR47_00525
MTWCQW49_20150
MECQMSC49_02790
MSPRMSP5_003062
MYSSMs3S1_39780
PLEOOHA_1_02830(meaA)
HDIHDIA_3962(scpA_2)
PSINCAK95_11855
NOHG5V57_10415
RBMTEF_03475
PSFPSE_0116(mutB)
PPHRAPZ00_07820
LAPACP90_02775
LABRCHH27_17720
LABPFJ695_06480
LABTFIU93_08400(scpA1)
LAGGB0E33_14255
RPOPK1718_03850
RAGGQUB73_03770
SIWGH266_11595
PHRC6569_14510
PSTGE8M01_09075
PAQTE8L99_11580
MFLGABS361_20930
CCRCC_3081
CCSCCNA_03177
CAKCaul_0836
CSECseg_3643
CHQAQ619_02915
CMBCSW64_02215
CFHC1707_03485
CAUFCSW63_19575
CAUBAMEJIAPC_03968(ecm)
CAUEACN2C6_13715
TSVDSM104635_01212(scpA_1)
SILSPO0368
SITTM1040_3106
RUAD1823_12095
RUTFIU92_01400(scpA1)
RCONK3740_01530
RUYNOR97_01090
JANJann_0797
JOVP8627_07330
RDERD1_1635(mutB)
RLIRLO149_c030730(mutB2)
RPONG3256_15270
RFUROLI_006680(ecm)
RALGAB4K19_002220
DSHDshi_2855(mutB)
PGAPGA1_c03840(mutB)
PGLPGA2_c03390(mutB)
PGDGal_03117
PHPPhaeoP97_02971(mutB)
PPICPhaeoP14_00302(mutB)
PHQD1820_14780
PHAEN1037_04455
PBRZACEQPH_16560
OATOAN307_c41380(mutB2)
OAROA238_c04410(mutB1)
OTMOSB_04900(mutB)
OCTFTO60_13710
LMDMETH_03400
LEJETW24_04235
LAQUR2C4_13550
LEVETW23_15965
LCAEK3721_03520
LEIMK3557_14155
CIDP73_3853
CMARIMCC12053_3008
CEHCEW89_10030
CBAKDA792_14045
MALGMALG_02725
CONTQ29_02505
YPACCEW88_11100
YANAYJ57_04480
TPROGa0080559_TMP1108
PABYGa0080574_TMP3168
SBRUPVT71_02965
SUAMBOO69_13595
SULZC1J03_18105
SULIC1J05_18030
SULDB5M07_05045
SPOTG6548_04215
SMEDJNX03_18130
SINLDSM14862_02474(mutB)
SFAVPL335_11785
SUALKDD17_02235
SDUBR1T39_14865
SULBIV89_002870
SULYABM428_04025
SULPAADW22_04330
SUSQK3756_13390
SRHDAB4X18_10260
SULQT8A63_13735
SLCZR1T45_18025
SULMDSM110093_02407(mutB)
SPSESULPSESMR1_00407(scpA)
PSDMDSM107133_00773(scpA_1)
TOMBWR18_01110
TATEACMHLQ_07730
TATYACERHN_04545
RMMROSMUCSMR3_01834(scpA)
ROKRAK1035_1351
RIDRIdsm_00119(scpA_1)
ROMEI983_03065
ROHFIU89_18790(scpA3)
RPELN7U68_09855
RPHCRZ517_17445
AHTANTHELSMS3_02143
SAGUCDO87_04305
SSTLABFK29_17190
SAGZQNI11_04660
THAACFI11_20745
OCDFHY55_05945
ROTFIV09_01475(scpA1)
RMHLVO79_01135
MALUKU6B_41670(MeaA)
TGLHFZ77_08330
TMDKUV46_08240
HATRC74_09415
PALXGQA70_04875
LSALKBK07_01480
LALGLentiSH36_00622(mutB)
TRYQF118_18595
MARUFIU81_04175(mutB)
RMAIMACH21_04620(MeaA)
REDroselon_01711
ACLDACIRQ6_03255
SEOHACMUJL_15010
SSAKABWH93_07915
MATGACMVPR_20625
BOOE2K80_01925
RPOHABWH90_12995
PRHDN4R57_14340
AALCU5922_002550
RSPRSP_0961(MeaA)
RSHRsph17029_2621
RSQRsph17025_3008
RSKRSKD131_2353
CAZTLV780_12825
RBLB6K69_07525
FYTQF092_18065
PDEPden_3875
PAMIJCM7686_1037
PYEA6J80_12665
PCONB0A89_06935
PZHCX676_11120
PAROCUV01_03090
PAMNJCM7685_2154
PMUTDPM13_11120
PARREOJ32_14930
PAAKFIU66_03195
PKDF8A10_08035
PPANESD82_06405
PLIAE4191_03285
PSANHGN31_12035
PMAUCP157_00623(mutB)
PMEHJWJ88_03145
PSEWJHW44_03810
PSAPJHX88_04430
PFISJHX87_08935
PAEXJHW48_12340
PSTLJHW45_04620
PALPJHW40_09130
PVERE3U25_03755
PFEOE3U26_19280
PHOIACLISE_01810
PQOPXD02_12960
PTPRCA23_c09170(mcmA1)
RSUNHU_00738
RHMB5V46_04545
RHCRGUI_0611
RHOVACK8CO_05065
RMBK529_020835
TSCOR1T40_12655
DAAAKL17_0910
DONBSK21_00875
MALCQQG91_11090
RBZB9057_00660
THWBMG03_18270
TECAKL02_018630
TLBRPE78_02940
LVSLOKVESSMR4R_02788(mutB)
YAGAABB28_11330
YRHAABB31_20690
GEHHYN69_12825
GFUKM031_13360
TAWEI545_06890
SALOEF888_18455
SEDIEBB79_02315
PPSOQPJ95_04630
PSEBEOK75_09455
PPRUFDP22_03525
PAEDG5B38_14090
PAMOBAR1_15105
POZI0K15_10705
MONG8E03_01705
PALWPSAL_018860(ecm)
PSHQF3W81_20345
PGVSL003B_0357
CACTHZ995_03600
THASC6Y53_10575
HDHG5B40_19125
CMAGCBW24_14090
GCEKYE46_04140
GYJAADW23_01375
NSMJO391_13160
ACROK3J57_10555
AALKLGT41_0001995
AMYLQBD29_12735
AMAQGO499_14280
RHOCQTA57_01965
PBAEP8S53_09415
RBGBG454_09815
BOSGGKR98_08645
MANHLA6_001002(scpA_1)
MASXACK3BB_20175
FAQG5B39_05190
SINRO5O51_13230
RCPRCAP_rcc03241(mutB)
RHPLPB142_14600
RBXI3V23_06925
HNEHNE_3115
HBAHbal_0291
CBOTATE48_04280
HBCAEM38_09250
SKTIGS68_10665
SMUCJL100_016565
SROEJL101_014990
RRURru_A3062
RRFF11_15685
MGYMGMSRv2__2673(yliK)
MGRYMSR1_36930(scpA_3)
MAGXXM1_1238
MAGNWV31_14305
FERFNB15_00560
DEXHWD60_01565
DVNHQ394_14995
AALUABWI00_18550
MAGamb0310
HTQFRZ44_46210
HADHFRZ61_44140
TXITH3_17590
THACCSC3H3_16680
TIIDY252_04215
THAIIT893_16595
TLUR1T41_05145
TTBMACH01_32640
THGOM9H61_16760
THADIT971_18710
MAGQMGMAQ_3101
VSUP3M64_11865
TMOTMO_0118(meaA)
ECOGFIV45_15320
SNEANBZ79_17905
MINWACMVY4_21690
MZLGKS04_05860
LILLB_074(sbm)
LIELIF_B059(sbm)
LICLIC_20058(mcm2)
LISLIL_20066(mcm1)
LBJLBJ_4062(meaA)
LBLLBL_4062(meaA)
LBILEPBI_II0044(mcm2)
LBFLBF_4043(meaA)
LSTLSS_18738
LAJA0128_19665
LMAYDPV73_18965
LKMEFP84_19380
LWLFHG68_19780
LKBLPTSP3_g37080(mcm2_1)
LNOMAL08_18090
LKRFH602_00460
LMILAB3N58_16340
LIOWAB3N60_17915
LGORAB3N59_19870
LMGOAB3N62_17695
LCINAB3N61_17335
TPXTurpa_0280
EUZDVS28_a3923
RANTRHODO2019_03895
SCOSCO6472(SC9C7.08c)
SALBXNR_0457
SMASAVERM_1912(meaA1)
SGRSGR_1171
SGBWQO_29555
SFISFUL_6326
SANLKZO11_31640
SGRFSGFS_030180
SCYER2B67_04495
SCBSCAB_17631
SSXSACTE_5659
SVLStrvi_2500
SHYSHJG_7433
SHOSHJGH_7193
SRCM271_13260
SMALSMALA_6100
SAUOBV401_34295
SSOII1A49_34350
SANTQR300_11060
SFASfla_0906
SVESVEN_6306
SDVBN159_1953(meaA)
SALSSLNWT_0465
STRPF750_5948
SCIB446_29765
SLVSLIV_06065(meaA)
SGUSGLAU_27250(meaA)
SVTSVTN_30765
STREGZL_02324
SCWTU94_27470
SLDT261_1718
SLCSL103_24365
STRMM444_27575
STRCAA958_28640
SAMBSAM23877_6066(meaA)
SPRISPRI_1331
SCZABE83_04725
SCXAS200_10825
SRWTUE45_07074(mutB_2)
STRFASR50_29035
SLEsle_13030(sle_13030)
SRNA4G23_04916(scpA_5)
SPAVSpa2297_26925
STRTA8713_26355
SCLFBB341_03680
SGSAVL59_13885
STSIA4E84_33265
SKYD0C37_03825
SALWCP975_29940
SGMGCM10017557_14290
SCADDN051_09615
SPHWNFX46_11070
SGRSV9K83_05695
SLSSLINC_6871
SNRSNOUR_10730(meaA)
SALUDC74_6486
SALLSAZ_33455
SPLULK06_027855
STRDNI25_06040
SNWBBN63_05340
SSIAA7J05_06525
SVUB1H20_30385
SPUNBFF78_09065
SGVB1H19_32465
SLAUSLA_6260
SALFSMD44_07017(ecm)
SALJSMD11_1339(ecm)
SLXSLAV_08025(mutB1)
STROSTRMOE7_31095
SFKKY5_6786c
SNZDC008_28370
SGEDWG14_01739(scpA_1)
SRJSRO_1426
SVQN6Q81_28285
SLKSLUN_32570
SGDELQ87_06720
SQZFQU76_28250
SCYAEJ357_38670
SASTCD934_04585
SNQCP978_27095
STIRDDW44_26345
SKACP970_06745
SGZC0216_10220
SVNCP980_06485
SNKCP967_03940
SHAWCEB94_34115
SRKFGW37_26430
SFICEIZ62_05460
SGALCP966_29710
SSPODDQ41_27615
SVRCP971_08935
SPADDVK44_29745
SFYGFH48_09630
SAQUEJC51_37840
SGFHEP81_01392
SCAVCVT27_29035
SSEOD0Z67_24050
SBYH7H31_05445
SRIMCP984_07150
SSUBCP968_06980
SPHVF9278_39480
SCINCP977_28230
SFUGCNQ36_27175
SPACB1H29_06760
STSUB7R87_28640
SCHACP983_08260
SGXH4W23_31950
SCOECP976_35270
SBATG4Z16_04715
SSPBCP982_33015
SNFJYK04_06749(mutB_2)
SPLACP981_31655
SBROGQF42_34500
STUIGCM10017668_58320
SATAC5746_34335
SCHFIPT68_30320
SHUNDWB77_01616(scpA_1)
SCYGS1361_32250(scpA6)
SFEUIM697_30280
SLIAHA039_05420
SDWK7C20_30095
SVDCP969_31020
SCALI6J39_30190
SAUHSU9_028720
SFBCP974_26295
SMOBJ7W19_26400
SPRACP972_29690
SPEUCGZ69_30575
SROIIAG44_07410
SXNIAG42_06405
SGJIAG43_27265
SHKJ2N69_31305
SANUK7396_06915
SDDD9753_06040
SACTDMT42_31225
SGOBtest1122_23250
SINEKI385_35825
SLFJEQ17_10575
SDECL3078_37525
SAOVG3H79_06005
SDURM4V62_09170
SYANNRK68_28080
SRUGF0345_25090
SAKBK1J60_07750
STAALDH80_08495
SNIGHEK616_47030
SVIOHWN34_03180
SCAEIHE65_07985
STUBMMF93_27330
SSPNLXH13_31695
SCIRSTRCI_006605
SXTKPP03845_105977(mutB_2)
SLONLGI35_34445
SDRZNEH16_04240
STUDSTRTU_001168
STEEF3L20_13730
SENGOJ254_28095
SGKPET44_26100
SYUNMOV08_10530
SARGHKX69_05555
SJNRI060_07360
SCYNN8I84_32175
SOVQZH56_05545
SFIYF0344_03865
SHAUK9S39_10770
SKGKJK29_05560
SCOAQU709_07145
SLAIP8A22_05565
SROCRGF97_04315
SFPQUY26_06975
SCHGNRO40_24745
STTNBSL84_27870
SINNABB07_06450
STRZOYE22_05255
SCAYPYS65_05385
KBUQ4V64_45335
SARMDVA86_00480
SLUOPS467_31665
STPBQR97_30515
SRPAHEP86_32935
SMIBSMIR_03620
SCAJO1G22_08160
STRWQHG49_06950
STRLHEP84_40875
STSDHEP87_42415
SRPZHEP85_31810
SCHEQRN89_28730
SGLYP8A20_04850
SCATP8A18_29500
STIIDRB96_25085
STICDRB89_24680
SABDN8I86_30330
STRVEZV63_30875
SPAZABXI76_04525
SPIHABXR15_03210
SMODPOD33_25570
SPOFP8A21_33895
STBRABDE16_06595
SGROUBV09_28350
STACABII15_31570
STVBOH133_04965
SSOCABZO31_27310
SSLIR2D22_06995
STYIC9F11_32140(scpA4)
SCITV2W30_32455
SSIRWAB15_32920
SEXPSLV14_001415
SFLUACKTSN_08545
SOKEACE1N8_30035
SSTOACE1OC_08390
SLUAAB8735_29745
STGOKBP30_08560
STCMSCMC78_08900
STIDG7Z12_06475
STCZJHY03_60130
STSGB6R96_07150
STHUM1P56_23305
STRQCGL27_35725
SSECABZO29_10635
SHUGABVG11_09030
STRKR2B38_34665
STJLACE1OA_06980
STHPMQE23_09190
STRXA6E92_04040
STFRSFR_0766
STFDB1K54_29680
STSMB9S66_27355
STFIWID27_05995
STPGC1703_32860(mutB2)
STPJR1Y80_31550
SKORLUW75_02570
SSELVM636_03875
SBONACNNMR_37370
STHCAY578_27320
SCTSCAT_4858(meaA)
SCYSCATT_48520
KSKKSE_56500(meaA)
KABB7C62_31665
KAUB6264_03995
KITCFP65_5573
KISHUT16_26330
KCHO1G21_11815
KCMABWK59_24660
KNBACF9IK_10115
KICKCMC57_up18180
KPURACFCLZ_27565
STRIC7M71_024010
PPODAB0761_11180
YIALO772_12030
STRHGXP74_30640
STPZGXW83_25350
ABRYNYE86_24200
AGLAOIE69_10750
AREVRVR_8199
ICAIntca_2425
ARSADJ73_15700
JTEASJ30_04295
JLIEXU32_10505
JMEEEW87_010525
JAYH7A72_04265
JCRO9K63_00740
JAIV1351_04340
JTRV3C34_07290
TEHGKE56_08435
PHWG7075_02710
TEDU5C87_19870
KNOV6K52_06520
AUSIPK37_01675
NCANoca_1772
NDKI601_3918(mutB_2)
NOYEXE57_05100
NOIFCL41_11305
NOOFE634_09195
NBEBack2_04490
NANOG5V58_14510
NMESH9L09_15850
NAROCFH99_09950
NAQUENKNEFLB_01864(mutB_2)
NROK8W59_11225
NOQLN652_20100
NCQK6T13_05870
NPCKUV85_07875
NPSKRR39_03630
NMARHPC71_14910
NFCKG111_11470
NRNSHK17_06820
NBISHK19_14535
NOCROSR43_14915
NOCWABFU82_03625
NOCAncot_13015
NOCLKM427_09145
NOCDQJ852_16955
NOCQQI633_16230
NLBP5P86_14850
NOCSACUP6Y_14420
PSIMKR76_10535
AERAERYTH_06740
AEZC3E78_12405
AEBC6I20_10395
AEFGEV26_12445
ASEZH9L21_10400
ADBNP095_10595
AWNNQV15_13080
MUZH4N58_05980
MQRAB3M34_07285
SGRGL0C25_02485
NBTKLP28_14750
KFLKfla_5026
KQIF1D05_07480
KSLOG809_41255
KRIOX958_11650
FRAFrancci3_2169
FALFRAAL5921(meaA)
FREFranean1_1034
FSYFsymDg_3836
FRIFraEuI1c_0946
GOBGobs_4128
BSDBLASA_3911(mutB)
BLAPMVA48_21090
BMONABDB74_16165
AMDAMED_7761
AMNRAM_39870
AMMAMES_7643
AMZB737_7643
AOIAORI_6548(ecm)
AJAAJAP_06220(meaA)
AMQAMETH_1366(mutB)
AMYCCU254_31230
AMYBBKN51_26185
AABA4R43_22310
AMYYYIM_06440(scpA1)
AORISD37_07695
AACDLWP59_06670
APRTMUY14_45410
AROONQK81_33095
ATHML1857_09475
AMOGQRX60_20670
ACYNORV05_26385
ACORLCL61_35225
AMYZHUW46_05992(scpA_2)
ANWQP939_23820
ABARAMYBAR_001320
AMYEMJQ72_16915
AMYSCVV72_36670
ARHIAB5I40_36160
AMYOAB5J62_34515
PDXPsed_1691
PSEAWY02_10790
PSEEFRP1_03360
PSEHXF36_19370
PSEQAD006_10970
PECQAD017_18800
PHHAFB00_04680
PAUTPdca_54640
PBROHOP40_14510
PPELH6H00_13985
PSDSK1T35_40750
PALQPaSha_16620
SESPBN6_73420(meaA)
SSYIEKG83_40960
SACXIOD16_30600
KALKALB_7597
KUTJJ691_90040
KBRQ4V65_31945
KPHYAOZ06_46245
LEDBBK82_20750
LXRACRSBM_02900
ALOCRK59015
PMADBAY61_25430
ACTUActkin_05108(scpA_3)
AAURV5P93_006162
CROSN8J89_35150
ACTYOG774_11765
UMERM788_18105
STPStrop_3621
SAQSare_4003
MAUMicau_5116
MILML5_3195
MICBMicB006_4135
MTUACSH63_32095
MTEMGCE86_20210
MCABHXZ27_25790
MSAGGCM10017556_13680
MCHLPVK74_15850
MFEUH1D33_01100
MPRNQ3V37_12330
MHAWRMN56_17265
PSUUPsuf_019490
CATICS0771_21810
DVCDvina_07405
DMATDmats_06930
DFUDfulv_06855
DROSDrose_07215
DAURDaura_06785
DACTKZZ52_06655
CAICaci_1226
EKEEK0264_16435
JTLM6D93_07695
JCYM6B22_19755
JATSAMN05892883_2615
ABAIIMCC26256_11178
BSOLFSW04_11595
BALADSM104299_01919(ecm)
PBAJLRS13_14255
CWOCwoe_4193
PARNNBH00_07265
PARQDSM112329_01773(ecm)
SBAEDSM104329_01837(ecm)
TALUJDY09_03285
AFOAfer_0223
AYMYM304_38140(meaA)
ATQGH723_16475
AQZKSP35_16915
ADAEACE2AJ_12795
IAMHC251_22650
IMAPO878_20385
DHILH044_12360
AHAIAB8619_01810
TBHTbon_06985
TFLAO0235_07630
 » show all
Reference
1  [PMID:18819910]
  Authors
Erb TJ, Retey J, Fuchs G, Alber BE
  Title
Ethylmalonyl-CoA mutase from Rhodobacter sphaeroides defines a new subclade of coenzyme B12-dependent acyl-CoA mutases.
  Journal
J Biol Chem 283:32283-93 (2008)
DOI:10.1074/jbc.M805527200
  Sequence
[rsp:RSP_0961]
Other DBs
ExplorEnz - The Enzyme Database: 5.4.99.63
IUBMB Enzyme Nomenclature: 5.4.99.63
ExPASy - ENZYME nomenclature database: 5.4.99.63
BRENDA, the Enzyme Database: 5.4.99.63
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