ORTHOLOGY: K12567
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Entry
K12567 KO
Symbol
TTN
Name
titin [EC:
2.7.11.1
]
Pathway
map04820
Cytoskeleton in muscle cells
map05410
Hypertrophic cardiomyopathy
map05414
Dilated cardiomyopathy
Disease
H00292
Hypertrophic cardiomyopathy
H00294
Dilated cardiomyopathy
H00593
Limb-girdle muscular dystrophy
H00594
Distal myopathy
H00595
Myofibrillar myopathies
H01810
Congenital myopathy
H01976
Tibial muscular dystrophy
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09140 Cellular Processes
09142 Cell motility
04820 Cytoskeleton in muscle cells
K12567 TTN; titin
09160 Human Diseases
09166 Cardiovascular disease
05410 Hypertrophic cardiomyopathy
K12567 TTN; titin
05414 Dilated cardiomyopathy
K12567 TTN; titin
09180 Brite Hierarchies
09181 Protein families: metabolism
01001 Protein kinases
K12567 TTN; titin
09182 Protein families: genetic information processing
04131 Membrane trafficking
K12567 TTN; titin
09183 Protein families: signaling and cellular processes
04812 Cytoskeleton proteins
K12567 TTN; titin
04147 Exosome
K12567 TTN; titin
Enzymes [BR:
ko01000
]
2. Transferases
2.7 Transferring phosphorus-containing groups
2.7.11 Protein-serine/threonine kinases
2.7.11.1 non-specific serine/threonine protein kinase
K12567 TTN; titin
Protein kinases [BR:
ko01001
]
Serine/threonine kinases: CAMK group
MLCK family
K12567 TTN; titin
Membrane trafficking [BR:
ko04131
]
Others
Actin-binding proteins
Others
K12567 TTN; titin
Cytoskeleton proteins [BR:
ko04812
]
Eukaryotic cytoskeleton proteins
Actin filaments / Microfilaments
Actin-binding proteins
Others
K12567 TTN; titin
Exosome [BR:
ko04147
]
Exosomal proteins
Exosomal proteins of other body fluids (saliva and urine)
K12567 TTN; titin
BRITE hierarchy
Genes
HSA:
7273
(TTN)
PTR:
459784
(TTN)
PPS:
100994495
(TTN)
GGO:
101126591
(TTN)
PON:
100435464
(TTN)
NLE:
100602111
(TTN)
HMH:
116810598
(TTN)
MCC:
703527
(TTN)
MCF:
102118847
(TTN)
MTHB:
126932057
MNI:
105468968
(TTN)
CSAB:
103217425
(TTN)
CATY:
105579880
(TTN)
PANU:
100999619
(TTN)
TGE:
112636739
(TTN)
MLEU:
105548088
RRO:
104677536
104677716
RBB:
108527098
(TTN)
TFN:
117094789
117094790
PTEH:
111542778
(TTN)
CANG:
105513194
(TTN)
CJC:
100396664
(TTN)
SBQ:
101030681
104650071
CIMI:
108307339
(TTN)
CSYR:
103257647
(TTN)
MMUR:
105883014
(TTN)
PCOQ:
105815574
(TTN)
OGA:
100958078
(TTN)
MMU:
22138
(Ttn)
MCAL:
110310290
(Ttn)
MPAH:
110317826
(Ttn)
RNO:
84015
(Ttn)
MCOC:
116090352
(Ttn)
ANU:
117703765
(Ttn)
MUN:
110555976
(Ttn)
CGE:
100767264
(Ttn)
MAUA:
101830827
(Ttn)
PROB:
127222376
(Ttn)
PLEU:
114700805
(Ttn)
MORG:
121439150
MFOT:
126487912
AAMP:
119818668
(Ttn)
NGI:
103751793
(Ttn)
HGL:
101717863
(Ttn)
CPOC:
100722767
(Ttn)
CCAN:
109695426
(Ttn)
DORD:
105994103
(Ttn)
DSP:
122114971
(Ttn)
PLOP:
125350508
(Ttn)
NCAR:
124979875
MMMA:
107138514
(Ttn)
OCU:
100008570
(TTN)
OPI:
101518430
(TTN)
TUP:
102500174
(TTN)
GVR:
103585939
(TTN)
CFA:
478820
(TTN)
CLUD:
112668185
(TTN)
VVP:
112916359
(TTN)
VLG:
121501618
NPO:
129498493
(TTN)
AML:
100476638
(TTN)
UMR:
103659915
(TTN)
UAH:
113250712
(TTN)
ELK:
111151669
LLV:
125095799
MPUF:
101687481
(TTN)
MNP:
132014486
(TTN)
MLK:
131827034
(TTN)
NVS:
122902638
(TTN)
ORO:
101365205
(TTN)
EJU:
114223040
(TTN)
ZCA:
113920341
(TTN)
MLX:
118012274
(TTN)
NSU:
110592043
(TTN)
LWW:
102726884
(TTN)
FCA:
101080315
(TTN)
PYU:
121030759
(TTN)
PCOO:
112870607
(TTN)
PBG:
122481515
(TTN)
PVIV:
125172626
(TTN)
LRUF:
124514918
PTG:
102958083
(TTN)
PPAD:
109273778
(TTN)
PUC:
125911525
AJU:
106988330
HHV:
120224177
(TTN)
BTA:
540561
(TTN)
BOM:
102270908
(TTN)
BIU:
109566003
(TTN)
BBUB:
102401194
(TTN)
BBIS:
105002912
(TTN)
CHX:
102173234
(TTN)
OAS:
101122837
(TTN)
BTAX:
128043950
(TTN)
ODA:
120853971
(TTN)
MBEZ:
129537928
129538512
(TTN)
SSC:
100519519
(TTN)
CFR:
102520668
(TTN)
CBAI:
105072886
(TTN)
CDK:
105098680
116153051
VPC:
102543991
(TTN)
BACU:
103014047
103014327
BMUS:
118897883
(TTN)
LVE:
103074022
OOR:
101287117
(TTN)
DLE:
111172919
(TTN)
PCAD:
102978588
(TTN)
PSIU:
116756536
(TTN)
NASI:
112391471
(TTN)
ECB:
100053844
(TTN)
EPZ:
103547965
103547978
EAI:
106826586
(TTN)
MYB:
102252525
(TTN)
MYD:
102766243
(TTN)
MMYO:
118661115
(TTN)
MLF:
102440553
(TTN)
EFUS:
103283475
(TTN)
MNA:
107535206
(TTN)
DRO:
112305716
(TTN)
SHON:
118985648
(TTN)
AJM:
119037769
(TTN)
PDIC:
114495427
(TTN)
MMF:
118624956
(TTN)
HAI:
109388924
(TTN)
PALE:
102893689
(TTN)
PGIG:
120596864
(TTN)
PVP:
105291923
(TTN)
RAY:
107514656
(TTN)
TOD:
119255160
(TTN)
SARA:
101548803
SETR:
126008623
(TTN)
LAV:
104845494
TMU:
101353907
ETF:
101664425
(TTN)
DNM:
101422279
(TTN)
GAS:
123242183
(TTN)
SHR:
100923152
(TTN)
AFZ:
127554520
PCW:
110211623
(TTN)
110211624
OAA:
103171044
(TTN)
114814274
PCOC:
116234048
(TTN)
MGP:
100546807
(TTN)
CJO:
107316616
(TTN)
TPAI:
128076947
(TTN)
LMUT:
125696866
(TTN)
NMEL:
110400102
APLA:
101789520
(TTN)
ACYG:
106029845
CATA:
118261702
(TTN)
AFUL:
116490632
TGU:
100230340
(TTN)
116808599
LSR:
110482874
(TTN)
SCAN:
103814707
(TTN)
PMOA:
120499312
(TTN)
OTC:
121335418
(TTN)
PRUF:
121356773
(TTN)
GFR:
102045044
(TTN)
FAB:
101819370
(TTN)
OMA:
130255630
(TTN)
PHI:
102110498
(TTN)
106628041
PMAJ:
107207342
(TTN)
CCAE:
111932042
(TTN)
CCW:
104694159
(TTN)
109145671
CBRC:
103616627
(TTN)
ETL:
114055692
114064038
(TTN)
ZAB:
102064735
(TTN)
ACHL:
103811397
(TTN)
SVG:
106861576
(TTN)
MMEA:
130572206
HRT:
120754918
(TTN)
FPG:
101921795
(TTN)
FCH:
102055507
(TTN)
CLV:
102097216
EGZ:
104132701
(TTN)
NNI:
104010285
(TTN)
PCRI:
104036909
(TTN)
PLET:
104618131
(TTN)
PCAO:
104048240
(TTN)
ACUN:
113482096
(TTN)
TALA:
104364258
(TTN)
PADL:
103924608
(TTN)
AFOR:
103898363
(TTN)
ACHC:
115343298
(TTN)
HALD:
104323679
HLE:
104832896
(TTN)
AGEN:
126039321
GCL:
127018733
CCRI:
104158934
(TTN)
104161377
CSTI:
104558054
(TTN)
CMAC:
104483584
BREG:
104642875
(TTN)
FGA:
104072333
(TTN)
GSTE:
104257643
(TTN)
LDI:
104351086
(TTN)
MNB:
103777436
(TTN)
OHA:
104329015
(TTN)
NNT:
104410297
SHAB:
115607849
(TTN)
DPUB:
104298970
(TTN)
PGUU:
104462808
ACAR:
104520459
(TTN)
CPEA:
104387550
(TTN)
AVIT:
104269868
CVF:
104286974
(TTN)
RTD:
128913202
(TTN)
CUCA:
104054646
(TTN)
TEO:
104379330
(TTN)
BRHI:
104495360
(TTN)
AAM:
106499120
(TTN)
AROW:
112970591
(TTN)
NPD:
112958242
(TTN)
TGT:
104572228
(TTN)
DNE:
112997475
(TTN)
SCAM:
104145028
(TTN)
ASN:
102384137
(TTN)
AMJ:
102568392
(TTN)
CPOO:
109322476
(TTN)
GGN:
109301625
(TTN)
PSS:
102451731
102452728
(TTN)
CMY:
102929944
(TTN)
CCAY:
125645059
(TTN)
DCC:
119863516
(TTN)
CPIC:
101932983
101933242
(TTN)
TST:
117884986
(TTN)
CABI:
116817943
MRV:
120374675
(TTN)
ACS:
100560476
(ttn)
ASAO:
132767889
PVT:
110084610
(TTN)
SUND:
121918854
(TTN)
PBI:
103063864
(TTN)
PMUR:
107290010
(TTN)
CTIG:
120306336
(TTN)
TSR:
106544574
(TTN)
PGUT:
117672110
(TTN)
APRI:
131201584
(TTN)
PTEX:
113434038
(TTN)
NSS:
113412441
(TTN)
VKO:
123021802
(TTN)
PMUA:
114606328
(TTN)
PRAF:
128424255
(TTN)
ZVI:
118094033
(TTN)
118094235
HCG:
128333300
(TTN)
GJA:
107112583
(TTN)
STOW:
125426212
(TTN)
EMC:
129324198
(TTN)
XLA:
108701391
108701392
108702272
XTR:
105948415
733882
(ttn)
NPR:
108791207
(TTN)
RTEM:
120944437
(TTN)
BBUF:
121008927
(TTN)
BGAR:
122944640
(TTN)
MUO:
115475109
(TTN)
GSH:
117361557
(TTN)
DRE:
100001684
(ttn.1)
317731
(ttn.2)
SRX:
107714355
107714356
107714399
107716993
SANH:
107657493
107657509
107657510
107698997
SGH:
107601611
107601612
CCAR:
109090096
109100768
109100830
CAUA:
113053689
113108328
(ttn)
CGIB:
127964821
128020136
PTET:
122351533
122351535
122351560
LROH:
127170397
OMC:
131546791
(ttn.2)
131546794
(ttn.1)
PPRM:
120459835
(ttn.1)
120487099
(ttn.2)
RKG:
130100290
130100293
(ttn.2)
MAMB:
125270622
(ttn.2)
125270626
CIDE:
127519253
127519254
MASI:
127447316
127447317
TROS:
130555496
(ttn.2)
130556061
(ttn.1)
TDW:
130427110
130427112
MANU:
129451647
(ttn.2)
129451648
(ttn.1)
IPU:
108266288
(ttn.2)
108266290
(ttn.1)
IFU:
128608502
(ttn.2)
128608503
(ttn.1)
PHYP:
113525688
113525696
SMEO:
124383274
(ttn.2)
124383275
(ttn.1)
TFD:
113653143
(ttn.1)
113653147
(ttn.2)
TVC:
132850442
(ttn.2)
132850638
(ttn.1)
AMEX:
103024627
103024947
111194931
CMAO:
118809477
(ttn.2)
118809483
(ttn.1)
EEE:
113584748
(ttn)
113584822
CHAR:
105905889
(ttn.2)
105905908
(ttn.1)
TRU:
101062366
TFS:
130521363
(ttn.2)
130536639
TNG:
GSTEN00004256G001
GSTEN00035869G001
LCO:
104931749
104936443
(ttn)
TBEN:
117490100
117496739
CGOB:
115004854
115005522
PGEO:
117442195
117442744
GACU:
117539376
117554724
(ttn.1)
EMAC:
134867389
134867399
ELY:
117249820
(ttn.2)
117251464
EFO:
125899772
(ttn.2)
125899773
PLEP:
121948672
(ttn.1)
121949594
SLUC:
116054860
(ttn.2)
116060878
ECRA:
117953067
117953076
ESP:
116686626
116702454
PFLV:
114563906
114564194
GAT:
120834350
(ttn.1)
120834353
(ttn.2)
PPUG:
119228960
119228965
AFB:
129104229
(ttn.2)
129104232
(ttn.1)
CLUM:
117750472
(ttn.2)
117750475
(ttn.1)
PSWI:
130205281
130205291
MSAM:
119903609
119903754
(ttn.2)
SCHU:
122885285
122885286
(ttn.2)
CUD:
121522697
(ttn.2)
121523030
ALAT:
119025425
(ttn.1)
119026352
(ttn.2)
MZE:
101471748
101481826
ONL:
100695257
100702396
OAU:
116327362
(ttn.1)
116332027
(ttn.2)
OLA:
101159719
101168333
OML:
112143467
(ttn.1)
112155183
(ttn.2)
CSAI:
133445626
(ttn.1)
133445628
(ttn.2)
XMA:
102219802
102230320
XCO:
114148749
114148751
XHE:
116723447
(ttn)
116723448
PRET:
103461768
103461835
PFOR:
103152099
103153921
(ttn)
PLAI:
106954028
(ttn)
106959964
PMEI:
106916095
(ttn)
106928839
GAF:
122839728
(ttn.2)
122840381
(ttn.1)
PPRL:
129374532
(ttn.2)
129374559
CVG:
107095541
(ttn)
107103236
107103971
CTUL:
119777371
119795836
GMU:
124870888
(ttn.1)
124870892
(ttn.2)
NFU:
107382781
107382785
107382786
KMR:
108247752
(ttn.2)
108247757
(ttn.1)
ALIM:
106530228
106532448
106535870
NWH:
119419483
(ttn.2)
119419485
(ttn.1)
AOCE:
111567531
111582718
MCEP:
125018031
(ttn.2)
125018033
CSEM:
103391545
103392380
POV:
109640662
109641824
109642081
SSEN:
122786903
(ttn.2)
122786910
HHIP:
117754476
(ttn.2)
117754477
(ttn.1)
HSP:
118119896
(ttn.1)
118119900
(ttn.2)
SMAU:
118282962
(ttn.2)
118320434
(ttn.1)
LCF:
108874498
108874713
SDU:
111230426
111230432
(ttn)
SLAL:
111647649
111651030
111652994
111655510
111667876
XGL:
120801371
(ttn.1)
120801508
(ttn.2)
HCQ:
109530038
109530478
109531004
(ttn)
SSCV:
125973799
125973801
SBIA:
133501955
(ttn.1)
133511862
(ttn.2)
PEE:
133410949
(ttn.2)
133411013
(ttn.1)
PTAO:
133486530
(ttn.2)
133486851
(ttn.1)
BPEC:
110158775
MALB:
109970431
109971935
BSPL:
114847603
(ttn.2)
114847604
(ttn.1)
SJO:
128368282
128368287
(ttn.2)
SASA:
106582275
106586456
STRU:
115155650
115155651
115160992
OTW:
112224854
112225561
(ttn.1)
112239048
OMY:
110501770
(ttn.1)
110501775
110520307
OGO:
123990012
123990170
124044015
ONE:
115112306
115113123
115116424
OKI:
109868355
109870941
109870942
OKE:
118366639
118385847
118386318
(ttn.1)
SALP:
111971388
(ttn)
111977581
111977590
112068763
SNH:
120058048
(ttn.2)
120063921
(ttn.1)
CCLU:
121536983
121554846
(ttn.1)
ELS:
105005730
105030839
SFM:
108924238
108924242
108928134
114909274
PKI:
111838565
111838612
111838613
111852999
AANG:
118222800
118222801
LOC:
102698563
(ttn)
PSPA:
121321943
121323044
(ttn.1)
ARUT:
117406791
PSEX:
120519232
(ttn.1)
LCM:
102365068
(TTN)
CMK:
103176499
(ttn.1)
103176583
CPLA:
122551920
(ttn.1)
HOC:
132817615
LERI:
129698610
(ttn.1)
PMRN:
116943744
(TTN)
BFO:
118405513
118405877
BBEL:
109471808
109471813
CIN:
100178935
(con)
SCLV:
120330499
SPU:
587668
590007
APLC:
110985841
110985846
AJC:
117112524
SKO:
100367544
DME:
Dmel_CG14964
(MnM)
Dmel_CG1915
(sls)
DER:
6543746
DSE:
6610578
DSI:
Dsimw501_GD13415
(Dsim_GD13415)
Dsimw501_GD17604
(Dsim_GD17604)
DYA:
Dyak_GE20711
Dyak_GE20886
DAN:
6493090
6507567
DSR:
110182785
110188799
DPO:
4813673
DPE:
6596217
6601226
DMN:
108151049
108152955
DWI:
6645630
DGR:
6557276
DMO:
Dmoj_GI11965
DAZ:
108612958
108614578
DNV:
108650745
108650825
DHE:
111596139
111601697
111603056
DVI:
6622408
6624256
BDR:
105227000
RZE:
108367918
108368606
AOQ:
129240728
TDA:
119667806
119672374
MDE:
101894949
LCQ:
111679299
111679307
LSQ:
119610531
GFS:
119631495
119631985
ECOE:
129944534
CLON:
129610249
129610456
HIS:
119647649
AGA:
1269678
ACOZ:
120948117
120949671
AARA:
120895627
120898496
AMER:
121593820
ASTE:
118512126
AFUN:
125771130
125771218
AMOU:
128305009
AAG:
5566332
5566333
5566334
5566335
AALB:
109411811
109411815
109419627
109419679
115265357
115265359
CQU:
CpipJ_CPIJ006894
CpipJ_CPIJ006896
CpipJ_CPIJ011430
CPII:
120425344
120425349
120425815
BCOO:
119073729
AME:
551259
ACER:
107993146
ALAB:
122719055
ADR:
102675378
AFLR:
100869706
BIM:
100743641
105681464
105681467
BBIF:
117210299
BVK:
117242036
BVAN:
117159374
BTER:
100643650
105665949
105665950
BAFF:
126923947
BPYO:
122569054
BPAS:
132904734
FVI:
122532898
CCAL:
108631257
108632877
113464523
OBB:
114878067
MGEN:
117223916
NMEA:
116424146
CGIG:
122402643
122402644
SOC:
105193639
105193641
MPHA:
105835260
105839056
105840013
AEC:
105153794
105153797
105153798
105153864
ACEP:
105624873
105624883
105624884
PBAR:
105424302
105424303
105424304
VEM:
105558388
105558390
105558393
HST:
105184333
105184334
105184337
DQU:
106750112
106750116
106750117
CFO:
105251526
105255184
(Titin)
105255188
FEX:
115244162
115244163
115244235
LHU:
105670417
105670419
105670420
PGC:
109859760
OBO:
105284950
105286657
PCF:
106785785
106785786
106790044
PFUC:
122524056
VPS:
122634087
VCRB:
124430547
VVE:
124949326
124954283
NVI:
100118006
100118672
100679567
CSOL:
105360581
105360800
LHT:
122502295
LBD:
127281907
MDL:
103577378
CGLO:
123267680
FAS:
105274082
DAM:
107045262
CINS:
118074223
CCIN:
107273400
107273401
DSM:
124416756
124416758
NPT:
124211112
124211113
NFB:
124175415
124175417
NLO:
107222576
107222577
NVG:
124297497
AROA:
105687951
TCA:
660101
DPA:
109536987
109536992
109536993
SOY:
115879935
AGRG:
126740640
126740641
ATD:
109600777
109600780
CSET:
123322980
AGB:
108913037
108914137
LDC:
111506365
NVL:
108561546
108561547
108566099
APLN:
108740273
PPYR:
116174774
OTU:
111425955
BMOR:
100141454
(Projectin)
692378
(Kettin)
BMAN:
114240293
114240394
MSEX:
115448899
DPL:
KGM_206797
KGM_207167
MJU:
123880526
NIQ:
126780253
VCD:
124543309
MCIX:
123669038
PMAC:
106717044
106717246
PPOT:
106104454
PXU:
106126120
PRAP:
110993988
110998159
PBX:
123718958
PNAP:
125062442
ZCE:
119835433
119835738
CCRC:
123704943
LSIN:
126978835
AAGE:
121738353
HAW:
110374530
135116679
(sls)
HZE:
124644798
TNL:
113503568
113504415
113504540
SLIU:
111362640
PXY:
105384109
CFEL:
113365982
113366531
CCRN:
123294999
123296560
API:
100160310
100169177
100572206
DNX:
107168390
107168391
107168453
AGS:
114128165
114128166
114128409
RMD:
113550869
113555241
113555242
BTAB:
109030446
109030469
CLEC:
106673577
106673897
HHAL:
106678791
NLU:
111045387
111050512
111051102
HVI:
124365929
MQU:
128994752
PHU:
Phum_PHUM541090
Phum_PHUM541140
FOC:
113211101
TPAL:
117653215
ZNE:
110827690
CSEC:
111862210
111864305
SGRE:
126267900
126365782
IEL:
124167723
FCD:
110842678
DPX:
DAPPUDRAFT_305290
PVM:
113807386
113819544
113819561
PJA:
122262949
122263725
PCHN:
125033189
PMOO:
119577527
HAME:
121859754
PCLA:
123767326
PTRU:
123506322
ESN:
126988202
126988203
EAF:
111699009
111709081
111709519
TCF:
131885534
DSV:
119436594
RSAN:
119379038
RMP:
119176676
VDE:
111254245
VJA:
111265087
TUT:
107361033
112539571
DPTE:
113789093
CSCU:
111628011
PTEP:
107439667
UDV:
129216163
SDM:
118183992
LPOL:
106460780
106462582
106471424
PMEO:
129588069
CEL:
CELE_F54E2.3
(ketn-1)
NAI:
NECAME_01255
LOA:
LOAG_17458
LOAG_17459
TSP:
Tsp_05689
HRO:
HELRODRAFT_191066
PCAN:
112570126
BGT:
106078342
GAE:
121387235
HRF:
124140501
HRJ:
124264120
124264125
CRG:
105342773
MYI:
110458512
PMAX:
117317403
117317872
MCAF:
127718789
MMER:
123537955
DPOL:
127847357
127849279
OBI:
106877301
OSN:
115225262
118762202
LAK:
106161274
NVE:
5521826
EPA:
110232235
ATEN:
116288075
ADF:
107339449
AMIL:
114976759
PDAM:
113679141
SPIS:
111338391
DGT:
114531572
XEN:
124452498
HMG:
100212532
» show all
Taxonomy
UniProt
Reference
PMID:
9804419
Authors
Mayans O, van der Ven PF, Wilm M, Mues A, Young P, Furst DO, Wilmanns M, Gautel M
Title
Structural basis for activation of the titin kinase domain during myofibrillogenesis.
Journal
Nature 395:863-9 (1998)
DOI:
10.1038/27603
Sequence
[hsa:
7273
]
LinkDB
All DBs
DBGET
integrated database retrieval system