ORTHOLOGY: K18426
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Entry
K18426 KO
Symbol
ECHDC1
Name
ethylmalonyl-CoA/methylmalonyl-CoA decarboxylase [EC:
4.1.1.94
4.1.1.-]
Pathway
map00640
Propanoate metabolism
map01100
Metabolic pathways
Reaction
R00923
(S)-methylmalonyl-CoA carboxy-lyase (propanoyl-CoA-forming)
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
K18426 ECHDC1; ethylmalonyl-CoA/methylmalonyl-CoA decarboxylase
Enzymes [BR:
ko01000
]
4. Lyases
4.1 Carbon-carbon lyases
4.1.1 Carboxy-lyases
4.1.1.94 ethylmalonyl-CoA decarboxylase
K18426 ECHDC1; ethylmalonyl-CoA/methylmalonyl-CoA decarboxylase
BRITE hierarchy
Other DBs
GO:
0004492
Genes
HSA:
55862
(ECHDC1)
PTR:
745395
(ECHDC1)
PPS:
100992035
(ECHDC1)
GGO:
101134705
(ECHDC1)
PON:
100173900
(ECHDC1)
NLE:
100592701
(ECHDC1)
HMH:
116471834
(ECHDC1)
MCC:
712072
(ECHDC1)
MCF:
102132641
(ECHDC1)
MTHB:
126953270
MNI:
105465575
(ECHDC1)
CSAB:
103240408
(ECHDC1)
CATY:
105589458
105600484
(ECHDC1)
PANU:
101016170
(ECHDC1)
TGE:
112622317
(ECHDC1)
MLEU:
105548860
(ECHDC1)
RRO:
104665004
(ECHDC1)
RBB:
108534272
(ECHDC1)
TFN:
117097037
(ECHDC1)
PTEH:
111554989
(ECHDC1)
CANG:
105525884
(ECHDC1)
CJC:
100400374
(ECHDC1)
SBQ:
101054287
(ECHDC1)
CIMI:
108307833
(ECHDC1)
CSYR:
103268054
(ECHDC1)
MMUR:
105878187
(ECHDC1)
LCAT:
123633243
(ECHDC1)
PCOQ:
105823603
(ECHDC1)
OGA:
100949061
(ECHDC1)
MMU:
52665
(Echdc1)
MCAL:
110303168
(Echdc1)
MPAH:
110338255
(Echdc1)
RNO:
361465
(Echdc1)
MCOC:
116097870
(Echdc1)
ANU:
117701177
(Echdc1)
MUN:
110557228
(Echdc1)
CGE:
100764713
(Echdc1)
MAUA:
101843111
(Echdc1)
PROB:
127215093
(Echdc1)
PLEU:
114692524
(Echdc1)
MORG:
121449189
(Echdc1)
MFOT:
126499119
AAMP:
119820353
(Echdc1)
NGI:
103734575
(Echdc1)
HGL:
101721458
(Echdc1)
CPOC:
100723257
100728941
(Echdc1)
CCAN:
109686373
(Echdc1)
DORD:
105993597
(Echdc1)
DSP:
122127034
(Echdc1)
PLOP:
125357266
(Echdc1)
NCAR:
124988747
MMMA:
107155200
(Echdc1)
OCU:
100339488
OPI:
101520583
(ECHDC1)
TUP:
102478961
102498422
(ECHDC1)
GVR:
103583714
(ECHDC1)
CFA:
609850
(ECHDC1)
CLUD:
112644543
(ECHDC1)
VVP:
112930904
(ECHDC1)
VLG:
121477145
121485820
(ECHDC1)
NPO:
129500438
(ECHDC1)
AML:
100469062
(ECHDC1)
UMR:
103663427
(ECHDC1)
UAH:
113259426
(ECHDC1)
UAR:
123797609
(ECHDC1)
ELK:
111147650
LLV:
125103212
MPUF:
101680513
(ECHDC1)
101693790
MNP:
132018145
(ECHDC1)
MLK:
131833819
(ECHDC1)
NVS:
122906857
(ECHDC1)
ORO:
101378337
(ECHDC1)
EJU:
114219464
(ECHDC1)
ZCA:
113926576
(ECHDC1)
MLX:
118000720
(ECHDC1)
NSU:
110583662
(ECHDC1)
LWW:
102726756
(ECHDC1)
FCA:
101086310
(ECHDC1)
PYU:
121030024
(ECHDC1)
PCOO:
112862292
(ECHDC1)
PBG:
122489964
(ECHDC1)
PVIV:
125165318
(ECHDC1)
LRUF:
124528307
PTG:
102958239
(ECHDC1)
PPAD:
109248516
(ECHDC1)
PUC:
125938903
AJU:
106976806
HHV:
120247810
(ECHDC1)
BTA:
536284
(ECHDC1)
BOM:
102265974
(ECHDC1)
BIU:
109563748
(ECHDC1)
BBUB:
102392783
(ECHDC1)
BBIS:
105004216
(ECHDC1)
CHX:
102178542
(ECHDC1)
OAS:
101116321
(ECHDC1)
BTAX:
128053325
(ECHDC1)
ODA:
120862848
(ECHDC1)
CCAD:
122422513
(ECHDC1)
MBEZ:
129561337
(ECHDC1)
SSC:
100512509
(ECHDC1)
CFR:
102518806
(ECHDC1)
CBAI:
105077204
(ECHDC1)
CDK:
105096326
(ECHDC1)
VPC:
102531989
(ECHDC1)
BACU:
103017976
(ECHDC1)
BMUS:
118905426
(ECHDC1)
LVE:
103078139
(ECHDC1)
OOR:
101270675
(ECHDC1)
DLE:
111165431
(ECHDC1)
PCAD:
102992135
(ECHDC1)
PSIU:
116763214
(ECHDC1)
NASI:
112409075
(ECHDC1)
ECB:
100073045
(ECHDC1)
EPZ:
103567873
(ECHDC1)
EAI:
106838298
(ECHDC1)
MYB:
102258272
(ECHDC1)
MYD:
102751783
(ECHDC1)
MMYO:
118660408
(ECHDC1)
MLF:
102425047
(ECHDC1)
PKL:
118705199
(ECHDC1)
EFUS:
103283291
(ECHDC1)
MNA:
107525980
107544237
107544476
(ECHDC1)
DRO:
112297054
(ECHDC1)
SHON:
118986719
(ECHDC1)
AJM:
119044989
(ECHDC1)
PDIC:
114495482
(ECHDC1)
PHAS:
123821320
(ECHDC1)
MMF:
118621864
(ECHDC1)
PPAM:
129067762
(ECHDC1)
HAI:
109392627
(ECHDC1)
RFQ:
117020475
(ECHDC1)
PALE:
102893310
(ECHDC1)
PGIG:
120617338
(ECHDC1)
PVP:
105291145
(ECHDC1)
RAY:
107516901
(ECHDC1)
TOD:
119252865
(ECHDC1)
SETR:
126005854
(ECHDC1)
LAV:
100657207
(ECHDC1)
TMU:
101346877
ETF:
101653448
(ECHDC1)
DNM:
101411251
(ECHDC1)
MDO:
100030825
(ECHDC1)
GAS:
123247882
(ECHDC1)
SHR:
100919338
(ECHDC1)
AFZ:
127562191
PCW:
110208850
(ECHDC1)
OAA:
114809139
(ECHDC1)
GGA:
769021
(ECHDC1)
PCOC:
116240792
(ECHDC1)
MGP:
100546546
104909791
CJO:
107311738
(ECHDC1)
TPAI:
128078053
(ECHDC1)
LMUT:
125689340
(ECHDC1)
NMEL:
110395873
(ECHDC1)
APLA:
101804132
(ECHDC1)
ACYG:
106032483
(ECHDC1)
CATA:
118243952
(ECHDC1)
AFUL:
116487248
(ECHDC1)
TGU:
100227322
(ECHDC1)
LSR:
110479680
(ECHDC1)
SCAN:
103818103
(ECHDC1)
PMOA:
120501173
(ECHDC1)
OTC:
121346147
(ECHDC1)
PRUF:
121354802
(ECHDC1)
GFR:
102044218
(ECHDC1)
FAB:
101806230
(ECHDC1)
OMA:
130251844
(ECHDC1)
PHI:
102113663
(ECHDC1)
PMAJ:
107201912
(ECHDC1)
CCAE:
111927236
(ECHDC1)
CCW:
104690802
(ECHDC1)
CBRC:
103619418
(ECHDC1)
ETL:
114055919
(ECHDC1)
ZAB:
102061724
(ECHDC1)
ACHL:
103810147
(ECHDC1)
SVG:
106851908
(ECHDC1)
MMEA:
130572133
(ECHDC1)
HRT:
120749923
(ECHDC1)
FPG:
101918396
(ECHDC1)
FCH:
102055851
(ECHDC1)
CLV:
102084911
(ECHDC1)
EGZ:
104131447
104131979
(ECHDC1)
NNI:
104008849
(ECHDC1)
PCRI:
104029363
(ECHDC1)
PLET:
104620274
EHS:
104508873
(ECHDC1)
PCAO:
104041737
(ECHDC1)
ACUN:
113478487
(ECHDC1)
TALA:
104360780
(ECHDC1)
PADL:
103918333
(ECHDC1)
AFOR:
103900770
(ECHDC1)
ACHC:
115349339
(ECHDC1)
HALD:
104315673
HLE:
104828656
(ECHDC1)
AGEN:
126046184
GCL:
127014757
CCRI:
104157724
(ECHDC1)
CSTI:
104561419
(ECHDC1)
CMAC:
104473158
(ECHDC1)
MUI:
104538103
(ECHDC1)
BREG:
104634838
104635680
(ECHDC1)
FGA:
104081190
(ECHDC1)
GSTE:
104256882
(ECHDC1)
LDI:
104344787
(ECHDC1)
MNB:
103776557
(ECHDC1)
OHA:
104327043
(ECHDC1)
NNT:
104403891
(ECHDC1)
SHAB:
115609391
(ECHDC1)
DPUB:
104308362
(ECHDC1)
PGUU:
104463179
(ECHDC1)
ACAR:
104523725
(ECHDC1)
CPEA:
104390034
(ECHDC1)
CVF:
104282079
(ECHDC1)
RTD:
128907311
(ECHDC1)
CUCA:
104061023
(ECHDC1)
BRHI:
104495221
(ECHDC1)
AAM:
106497960
(ECHDC1)
AROW:
112968200
(ECHDC1)
NPD:
112951379
(ECHDC1)
TGT:
104566652
DNE:
112985989
(ECHDC1)
SCAM:
104149296
(ECHDC1)
ASN:
102383062
(ECHDC1)
AMJ:
102560692
(ECHDC1)
CPOO:
109312000
(ECHDC1)
GGN:
109299794
(ECHDC1)
PSS:
102451093
(ECHDC1)
CMY:
102945116
(ECHDC1)
CCAY:
125634193
(ECHDC1)
DCC:
119853125
(ECHDC1)
CPIC:
101939758
(ECHDC1)
TST:
117874955
(ECHDC1)
CABI:
116833326
(ECHDC1)
MRV:
120400941
(ECHDC1)
ACS:
100552293
(echdc1)
ASAO:
132760953
(ECHDC1)
PVT:
110077561
(ECHDC1)
SUND:
121923063
(ECHDC1)
PBI:
103055176
(ECHDC1)
PMUR:
107287702
(ECHDC1)
CTIG:
120299825
(ECHDC1)
TSR:
106537842
(ECHDC1)
PGUT:
117666251
(ECHDC1)
APRI:
131192745
(ECHDC1)
PTEX:
113439577
(ECHDC1)
NSS:
113411165
(ECHDC1)
VKO:
123020796
(ECHDC1)
PMUA:
114594127
(ECHDC1)
PRAF:
128410519
(ECHDC1)
ZVI:
118081999
(ECHDC1)
HCG:
128340517
(ECHDC1)
GJA:
107121808
(ECHDC1)
STOW:
125429768
(ECHDC1)
EMC:
129331443
(ECHDC1)
XLA:
496330
(echdc1.L)
XTR:
496886
(echdc1)
NPR:
108795294
(ECHDC1)
RTEM:
120937299
(ECHDC1)
BBUF:
120997063
(ECHDC1)
BGAR:
122934623
(ECHDC1)
MUO:
115465960
(ECHDC1)
115465961
GSH:
117357122
(ECHDC1)
DRE:
553585
(echdc1)
SRX:
107726240
SANH:
107688988
(echdc1)
SGH:
107569445
107580483
CCAR:
109098239
(echdc1)
CAUA:
113060063
(echdc1)
CGIB:
128031206
PTET:
122360180
(echdc1)
LROH:
127179189
(echdc1)
OMC:
131521416
(echdc1)
PPRM:
120462653
(echdc1)
RKG:
130090632
(echdc1)
MAMB:
125243099
(echdc1)
CIDE:
127497726
MASI:
127454419
TROS:
130549722
(echdc1)
TDW:
130432351
(echdc1)
MANU:
129449239
(echdc1)
IPU:
108270580
IFU:
128614380
(echdc1)
PHYP:
113526745
(echdc1)
SMEO:
124384524
(echdc1)
TFD:
113644222
(echdc1)
TVC:
132845673
(echdc1)
AMEX:
103032922
(echdc1)
CMAO:
118820087
(echdc1)
EEE:
113572187
(echdc1)
CHAR:
105908914
(echdc1)
TRU:
101067683
(echdc1)
TFS:
130532328
(echdc1)
TNG:
GSTEN00035369G001
LCO:
104926210
(echdc1)
NCC:
104955220
(echdc1)
TBEN:
117480106
(echdc1)
CGOB:
115021294
(echdc1)
PGEO:
117460978
(echdc1)
GACU:
117537438
(echdc1)
EMAC:
134861964
(echdc1)
ELY:
117265535
(echdc1)
EFO:
125893204
(echdc1)
PLEP:
121946058
(echdc1)
SLUC:
116035226
(echdc1)
ECRA:
117946797
(echdc1)
ESP:
116690751
(echdc1)
PFLV:
114556750
(echdc1)
GAT:
120810187
(echdc1)
PPUG:
119197660
(echdc1)
AFB:
129109829
(echdc1)
CLUM:
117745088
(echdc1)
PSWI:
130191626
(echdc1)
MSAM:
119897928
(echdc1)
SCHU:
122881052
(echdc1)
CUD:
121513091
(echdc1)
ALAT:
119006856
(echdc1)
MZE:
101482663
(echdc1)
ONL:
100712005
(echdc1)
OAU:
116322596
(echdc1)
OLA:
101165254
(echdc1)
OML:
112143315
(echdc1)
CSAI:
133440919
(echdc1)
XMA:
102231312
(echdc1)
XCO:
114141955
(echdc1)
XHE:
116717448
(echdc1)
PRET:
103478333
(echdc1)
PFOR:
103135856
(echdc1)
PLAI:
106939841
(echdc1)
PMEI:
106908798
(echdc1)
GAF:
122831591
(echdc1)
PPRL:
129367405
(echdc1)
CVG:
107089614
(echdc1)
CTUL:
119777051
(echdc1)
GMU:
124863512
(echdc1)
NFU:
107378790
(echdc1)
KMR:
108232210
(echdc1)
ALIM:
106536791
(echdc1)
NWH:
119410190
(echdc1)
AOCE:
111562493
(echdc1)
MCEP:
125015767
(echdc1)
CSEM:
103388602
(echdc1)
POV:
109632074
(echdc1)
SSEN:
122758626
122774405
(echdc1)
HHIP:
117776391
(echdc1)
HSP:
118114255
(echdc1)
SMAU:
118314075
(echdc1)
LCF:
108888597
SDU:
111227797
(echdc1)
SLAL:
111658063
(echdc1)
XGL:
120783598
(echdc1)
HCQ:
109522145
109525601
109531047
SSCV:
125975482
SBIA:
133500385
(echdc1)
PEE:
133402011
(echdc1)
PTAO:
133479150
(echdc1)
BPEC:
110171745
(echdc1)
MALB:
109958274
(echdc1)
BSPL:
114843697
(echdc1)
SJO:
128366373
(echdc1)
SASA:
106572885
106599002
STRU:
115187901
115187916
OTW:
112239354
112239356
OMY:
110510292
(echdc1)
OGO:
124017640
124017641
ONE:
115127936
(echdc1)
OKI:
109885705
116359282
(echdc1)
OKE:
127923452
(echdc1)
SALP:
112077607
(echdc1)
SNH:
120040890
(echdc1)
CCLU:
121542579
121585430
ELS:
105023514
(echdc1)
SFM:
108937328
(echdc1)
PKI:
111844541
(echdc1)
AANG:
118214601
(echdc1)
LOC:
102682286
(echdc1)
PSPA:
121316267
(echdc1)
ARUT:
117402543
(echdc1)
PSEX:
120525485
(echdc1)
LCM:
102352882
(ECHDC1)
CMK:
103182298
(echdc1)
RTP:
109917264
(echdc1)
CPLA:
122544525
(echdc1)
HOC:
132806127
(echdc1)
LERI:
129697272
(echdc1)
PMRN:
116946686
(ECHDC1)
LRJ:
133353012
(ECHDC1)
BFO:
118410251
BBEL:
109480902
SCLV:
120339755
120339995
SPU:
115919003
584418
LPIC:
129280803
APLC:
110980172
AJC:
117124092
TCA:
659052
SOY:
115880460
AGB:
108914754
NVL:
108560577
APLN:
108739264
112904572
PPYR:
116161769
116162538
API:
100573761
DNX:
107166647
AGS:
114128566
114128574
RMD:
113558438
113558439
ACOO:
126844587
DVT:
126899424
BTAB:
109038214
CLEC:
106664392
HHAL:
106688853
HVI:
124368957
MQU:
128983706
PHU:
Phum_PHUM171680
FOC:
113212778
TPAL:
117654386
ZNE:
110830973
CSEC:
111866308
SGRE:
126278196
BROR:
134539235
FCD:
110851854
DPX:
DAPPUDRAFT_335707
DPZ:
124311305
PVM:
113812256
PJA:
122246691
PCHN:
125037073
HAME:
121872606
PCLA:
123759394
CQD:
128704785
PTRU:
123505401
ESN:
126987114
MNZ:
135200316
HAZT:
108680841
EAF:
111707020
LSM:
121125969
PPOI:
119099484
DSV:
119430995
119431281
RSAN:
119371844
119371847
RMP:
119163844
119163845
TUT:
107363239
DPTE:
113799364
DFR:
124496270
CSCU:
111639305
LPOL:
106472084
PMEO:
129595958
CEL:
CELE_C32E8.9
(C32E8.9)
CBR:
CBG_12007
CRQ:
GCK72_002184
NAI:
NECAME_01713
HRO:
HELRODRAFT_159708
HELRODRAFT_159709
LGI:
LOTGIDRAFT_116748
PVUL:
126818663
PCAN:
112573749
BGT:
106062219
106064380
GAE:
121375161
HRF:
124112771
HRJ:
124265295
CRG:
105325046
CANU:
128164236
MYI:
110456022
PMAX:
117325253
MCAF:
127736928
MMER:
123525273
RPHI:
132748831
DPOL:
127853596
OBI:
106867393
OSN:
115214032
NVE:
5507440
EPA:
110242745
ATEN:
116294421
ADF:
107335744
AMIL:
114950263
PDAM:
113672137
SPIS:
111335182
DGT:
114530270
XEN:
124438799
HMG:
100209361
TAD:
TRIADDRAFT_53519
MBR:
MONBRDRAFT_10298
SRE:
PTSG_02237
PIF:
PITG_03865
PSOJ:
PHYSODRAFT_349249
PHYSODRAFT_466815
SPAR:
SPRG_12932
» show all
Taxonomy
UniProt
Reference
PMID:
22016388
Authors
Linster CL, Noel G, Stroobant V, Vertommen D, Vincent MF, Bommer GT, Veiga-da-Cunha M, Van Schaftingen E
Title
Ethylmalonyl-CoA decarboxylase, a new enzyme involved in metabolite proofreading.
Journal
J Biol Chem 286:42992-3003 (2011)
DOI:
10.1074/jbc.M111.281527
Sequence
[hsa:
55862
] [rno:
361465
]
LinkDB
All DBs
DBGET
integrated database retrieval system