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  Mitochondrial Biogenesis - Macaca nemestrina (pig-tailed macaque)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I C Mitochondrial respiratory chain complex III C Cytochrome c oxidase C F-type ATPase B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 105486567 POLRMT; DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 105466202 TFAM; transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial D 105478721 TFB1M; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 105474706 TFB2M; dimethyladenosine transferase 2, mitochondrial isoform X1 K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 105465051 MTIF2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2 D 105490212 MTIF3; translation initiation factor IF-3, mitochondrial isoform X2 K02520 infC; translation initiation factor IF-3 D 105474073 TSFM; elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts D 105482866 TUFM; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 105475140 GFM2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G D 105488550 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 105475485 MTERF1; transcription termination factor 1, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 105497677 MTERF2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 105473771 MTERF4; transcription termination factor 4, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 105476107 MTERF3; transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 105487693 GUF1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 105476088 POP1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 105487654 POP4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 105494696 POP5; ribonuclease P/MRP protein subunit POP5 isoform X1 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 105480476 RPP30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 105496902 POP7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 105485690 RPP25L; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 105490972 RPP25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 105468340 RPP38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 105487356 RPP40; ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 105477497 TRMT10C; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 105493784 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 105477971 KIAA0391; mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 105466021 MSS51; putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 105485198 TEFM; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 105497660 PTCD1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 105475173 PTCD2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 105465398 PTCD3; pentatricopeptide repeat domain-containing protein 3, mitochondrial isoform X1 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 105480389 DHX30; putative ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 105496263 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 105492039 AFG1L; AFG1-like ATPase isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 105474068 ATP23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 105466100 SUPV3L1; ATP-dependent RNA helicase SUPV3L1, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 105483599 LACTB2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 105486103 SLC25A31; ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 105478053 SLC25A6; ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 105466570 SLC25A4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 105468552 SLC25A5; LOW QUALITY PROTEIN: ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 105478414 SLC25A28; mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 105482057 SLC25A37; mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 105475691 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 105476405 ERAL1; GTPase Era, mitochondrial K03595 era; GTPase D 105484278 YARS2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 105494653 YARS; LOW QUALITY PROTEIN: tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 105467240 LARS; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 105480334 LARS2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 105484929 DARS2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 105475931 GARS; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 105496272 RARS2; LOW QUALITY PROTEIN: probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 105480950 RARS; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 105478773 QRSL1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 105463473 GATB; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 105494732 GATC; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 105479955 MTPAP; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 105482713 PDE12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 105471294 MTG1; mitochondrial ribosome-associated GTPase 1 isoform X2 K19828 MTG1; mitochondrial GTPase 1 D 105463563 NOA1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 105477421 NSUN3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial isoform X1 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 105494963 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 105477667 RPUSD3; mitochondrial mRNA pseudouridine synthase RPUSD3 isoform X1 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 105476244 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 105466398 RCC1L; LOW QUALITY PROTEIN: RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 105464091 LOW QUALITY PROTEIN: neugrin-like K23496 NGRN; neugrin D 105488308 NGRN; neugrin K23496 NGRN; neugrin D 105463979 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 isoform X1 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 105468019 FASTKD2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 105494173 CUNH12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor D 105489039 RMND1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1 D 105477390 GRSF1; LOW QUALITY PROTEIN: G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1 D 105471466 METTL15; probable methyltransferase-like protein 15 isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 105474280 CUNH12orf10; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 105478764 CUNH6orf203; uncharacterized protein C6orf203 homolog K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 105488334 POLG; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 105469003 POLG2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 D 105466578 PRIMPOL; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 105463997 ENDOG; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial D 105486849 MGME1; mitochondrial genome maintenance exonuclease 1 isoform X1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 105480209 EXOG; nuclease EXOG, mitochondrial K15050 EXOG; nuclease EXOG, mitochondrial D 105478383 TWNK; twinkle protein, mitochondrial isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3] D 105488557 PIF1; LOW QUALITY PROTEIN: ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 105471265 SSBP1; single-stranded DNA-binding protein, mitochondrial isoform X2 K03111 ssb; single-strand DNA-binding protein D 105498324 ATPase family AAA domain-containing protein 3 isoform X1 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 105498344 LOW QUALITY PROTEIN: ATPase family AAA domain-containing protein 3A-like K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 105474471 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 105492217 DNAJA2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 105496421 TOMM34; mitochondrial import receptor subunit TOM34 isoform X1 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 105485218 RHOT1; mitochondrial Rho GTPase 1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 105476325 HSPA8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 105497606 HSPA1L; heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 105497607 heat shock 70 kDa protein 1 isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 105498221 HSPA6; LOW QUALITY PROTEIN: heat shock 70 kDa protein 6 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 105498547 LOW QUALITY PROTEIN: heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 105469685 AIP; AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein D 105472754 AIPL1; aryl-hydrocarbon-interacting protein-like 1 isoform X1 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 105498211 TOMM40L; mitochondrial import receptor subunit TOM40B isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 105478520 TOMM40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 105477480 TOMM70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 105464442 TOMM22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 105473620 TOMM20L; TOMM20-like protein 1 isoform X1 K17770 TOM20; mitochondrial import receptor subunit TOM20 D 105474598 TOMM20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 105475682 TOMM7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 105475217 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 105477166 TOMM5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 D 105468723 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 105464310 SAMM50; sorting and assembly machinery component 50 homolog K07277 SAM50; outer membrane protein insertion porin family C Porin D 105467147 VDAC1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 105465993 VDAC2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 105476522 VDAC3; voltage-dependent anion-selective channel protein 3 isoform X1 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 105475081 MTX3; metaxin-3 isoform X1 K17776 MTX; metaxin D 105498259 metaxin-1 K17776 MTX; metaxin D 105498005 metaxin-1-like K17776 MTX; metaxin D 105483182 MTX2; metaxin-2 isoform X1 K17776 MTX; metaxin D 105476872 MYO19; LOW QUALITY PROTEIN: unconventional myosin-XIX K25838 MYO19; myosin XIX D 105499325 ARMCX2; armadillo repeat-containing X-linked protein 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2 D 105499323 ARMCX3; armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3 D 105499322 protein ARMCX6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6 D 105493479 MARC1; mitochondrial amidoxime-reducing component 1 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] D 105493481 MARC2; mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 105473619 TIMM9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 105477153 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 105496062 TIMM10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 105488689 TIMM10B; mitochondrial import inner membrane translocase subunit Tim10 B isoform X1 K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 105478243 mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 105499312 TIMM8A; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 105493612 TIMM8B; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 105485802 TIMM13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 105477749 CHCHD4; mitochondrial intermembrane space import and assembly protein 40 isoform X1 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 105485825 GFER; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 105483109 MINOS1; MICOS complex subunit MIC10 isoform X1 K17784 MICOS10; MICOS complex subunit MIC10 D 105465399 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 105484920 CUNH19orf70; MICOS complex subunit MIC13 isoform X1 K24624 MICOS13; MICOS complex subunit MIC13 D 105471361 CHCHD3; MICOS complex subunit MIC19 isoform X1 K17563 CHCHD3; MICOS complex subunit MIC19 D 105470224 CHCHD6; MICOS complex subunit MIC25 isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 105478233 APOO; MICOS complex subunit MIC26 K24625 APOO; MICOS complex subunit MIC26 D 105483650 APOOL; MICOS complex subunit MIC27 isoform X1 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 105483109 MINOS1; MICOS complex subunit MIC10 isoform X1 K17784 MICOS10; MICOS complex subunit MIC10 D 105465399 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 105471548 TIMM22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 105486619 mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 105493912 TIMM17B; mitochondrial import inner membrane translocase subunit Tim17-B isoform X1 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 105484725 TIMM17A; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 105489336 TIMM21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 105495366 TIMM50; mitochondrial import inner membrane translocase subunit TIM50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 105466039 MCU; calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial D 105466042 MICU1; calcium uptake protein 1, mitochondrial isoform X1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 105490270 MICU2; LOW QUALITY PROTEIN: calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial D 105486265 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial isoform X1 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 105464353 SMDT1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 105482453 MCUR1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 105483840 LETM1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 105471493 IMMP1L; mitochondrial inner membrane protease subunit 1 isoform X1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 105475279 IMMP2L; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 105468852 TMEM126A; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 105487553 MPC1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 105499943 MPC1L; LOW QUALITY PROTEIN: mitochondrial pyruvate carrier 1-like protein K22138 MPC1; mitochondrial pyruvate carrier 1 D 105492997 MPC2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 105497393 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 105483991 TIMM44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 105467075 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 105466894 GRPEL2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 105483898 GRPEL1; grpE protein homolog 1, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE D 105480089 DNAJC19; mitochondrial import inner membrane translocase subunit TIM14 isoform X2 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 105467846 PAM16; mitochondrial import inner membrane translocase subunit TIM16 isoform X1 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 105471930 PMPCA; mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 105475348 PMPCB; mitochondrial-processing peptidase subunit beta isoform X1 K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 105490254 MIPEP; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 105486316 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 105483144 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 105484136 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 105467841 DNAJA3; dnaJ homolog subfamily A member 3, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 105477710 TAMM41; phosphatidate cytidylyltransferase, mitochondrial isoform X1 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 105471927 DNLZ; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 105463857 ETHE1; persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 105476178 POLDIP2; polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 105468005 CREB1; cyclic AMP-responsive element-binding protein 1 isoform X1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 105475140 GFM2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G D 105488550 GFM1; elongation factor G, mitochondrial K02355 fusA; elongation factor G D 105474275 SP1; transcription factor Sp1 isoform X1 K04684 SP1; transcription factor Sp1 D 105478215 YY2; transcription factor YY2 K09201 YY; transcription factor YY D 105497832 GABPB2; GA-binding protein subunit beta-2 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 105490483 GABPB1; GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 105466202 TFAM; transcription factor A, mitochondrial isoform X1 K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 105471403 NRF1; nuclear respiratory factor 1 isoform X1 K11831 NRF1; nuclear respiratory factor 1 D 105483176 NFE2L2; nuclear factor erythroid 2-related factor 2 isoform X1 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 105494045 metallothionein-2-like K14739 MT1_2; metallothionein 1/2 D 105494046 metallothionein-2-like K14739 MT1_2; metallothionein 1/2 D 105494048 metallothionein-1 isoform X2 K14739 MT1_2; metallothionein 1/2 D 105494050 metallothionein-2-like K14739 MT1_2; metallothionein 1/2 D 105494051 metallothionein-1E K14739 MT1_2; metallothionein 1/2 D 105494052 metallothionein-2 K14739 MT1_2; metallothionein 1/2 D 105494053 metallothionein-1A-like K14739 MT1_2; metallothionein 1/2 D 105494054 metallothionein-1B-like K14739 MT1_2; metallothionein 1/2 D 105494056 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2 D 105494057 metallothionein-1F K14739 MT1_2; metallothionein 1/2 D 105494058 metallothionein-2-like K14739 MT1_2; metallothionein 1/2 D 105494059 metallothionein-1L K14739 MT1_2; metallothionein 1/2 D 105494060 metallothionein-1E-like isoform X1 K14739 MT1_2; metallothionein 1/2 D 105494061 metallothionein-2 K14739 MT1_2; metallothionein 1/2 D 105494065 MT3; metallothionein-3 K14740 MT3; metallothionein 3 D 112428925 MT4; metallothionein-4 K14741 MT4; metallothionein 4 C Coactivators D 105487840 PPARGC1A; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X1 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 105466880 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 105478357 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X2 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 105485505 CRTC1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 105464388 EP300; histone acetyltransferase p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 105467854 CREBBP; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 105496279 NFS1; cysteine desulfurase, mitochondrial isoform X1 K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 105468312 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 105487361 LYRM4; LYR motif-containing protein 4 isoform X2 K22069 LYRM4; LYR motif-containing protein 4 D 105491777 FXN; frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1] D 105483761 frataxin, mitochondrial-like K19054 FXN; frataxin [EC:1.16.3.1] D 105493641 FDX1; adrenodoxin, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 105476387 FDX2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 105469138 FDXR; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X1 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 105467075 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 105487286 HSCB; LOW QUALITY PROTEIN: iron-sulfur cluster co-chaperone protein HscB, mitochondrial K04082 hscB; molecular chaperone HscB D 105472972 iron-sulfur cluster co-chaperone protein HscB, mitochondrial-like K04082 hscB; molecular chaperone HscB D 105467071 SIL1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1 D 105467470 GLRX5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 105498765 ISCA1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 105495794 ISCA2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 105499669 IBA57; putative transferase CAF17, mitochondrial isoform X1 K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 105465440 NFU1; LOW QUALITY PROTEIN: NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 105497789 BOLA1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 105465281 BOLA3; bolA-like protein 3 isoform X1 K22075 BOLA3; BolA-like protein 3 D 105478379 SFXN3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3 D 105480919 SFXN1; sideroflexin-1 isoform X1 K23500 SFXN1_3; sideroflexin-1/3 D 105478340 SFXN2; sideroflexin-2 isoform X2 K23501 SFXN2; sideroflexin-2 D 105467742 SFXN4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4 D 105465258 SFXN5; sideroflexin-5 isoform X1 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 105469713 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 105489740 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform isoform X1 K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21] D 105497188 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform isoform X1 K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21] D 105490650 DHTKD1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 105499047 FBXL4; F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 105467312 HCFC1; host cell factor 1 isoform X1 K14966 HCFC1; host cell factor 1 D 105497723 HCFC2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2 D 105483865 HTT; huntingtin isoform X1 K04533 HD; huntingtin D 105469515 ESRRA; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha D 105495866 ESRRB; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 105493516 ESRRG; estrogen-related receptor gamma isoform X1 K08554 NR3B3; estrogen-related receptor gamma D 105483458 NRIP1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 105487437 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 105495129 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 105484910 LONP1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 105466131 SIRT1; NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 105478741 SERAC1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 105463991 UXT; protein UXT K26537 UXT; protein UXT D 105498292 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 isoform X1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 105491965 NDUFAF1; complex I intermediate-associated protein 30, mitochondrial isoform X1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 105499446 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 105480419 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 105498572 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 105481497 NDUFAF5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 105476118 NDUFAF6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X4 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 105464849 NDUFAF7; protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 112424529 NDUFAF8; LOW QUALITY PROTEIN: NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 105468950 TMEM126B; LOW QUALITY PROTEIN: complex I assembly factor TMEM126B, mitochondrial K18165 TMEM126B; complex I assembly factor TMEM126B D 105471911 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 105477783 ACAD9; acyl-CoA dehydrogenase family member 9, mitochondrial isoform X1 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 105477943 NUBPL; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning D 105476241 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 105478772 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 105470338 TIMMDC1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 105495488 SDHAF1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 105469410 SDHAF2; succinate dehydrogenase assembly factor 2, mitochondrial isoform X1 K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 105481221 mitochondrial chaperone BCS1 isoform X1 K08900 BCS1; mitochondrial chaperone BCS1 D 105491086 TTC19; tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 105467204 LYRM7; complex III assembly factor LYRM7 isoform X1 K18170 LYRM7; complex III assembly factor LYRM7 D 105496263 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 105474471 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 105469453 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 105485855 CUNH16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 105480551 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 105497728 CUNH12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 105471443 STMP1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 105468080 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1 D 105472734 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 112425666 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 105488958 CMC1; LOW QUALITY PROTEIN: COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 105491213 CMC2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2 D 105494199 cytochrome c oxidase assembly factor 1 homolog isoform X1 K18173 COA1; cytochrome c oxidase assembly factor 1 D 105472095 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 105468725 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 105490071 cytochrome c oxidase assembly factor 5 isoform X1 K18178 COA5; cytochrome c oxidase assembly factor 5 D 105464112 cytochrome c oxidase assembly factor 6 homolog isoform X1 K18179 COA6; cytochrome c oxidase assembly factor 6 D 105495059 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 105473529 protoheme IX farnesyltransferase, mitochondrial isoform X1 K02257 COX10; heme o synthase [EC:2.5.1.141] D 105476756 cytochrome c oxidase assembly protein COX11, mitochondrial isoform X1 K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 105492852 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14 D 105478412 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9] D 105472917 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 105470333 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 105477313 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X1 K17797 COX18; mitochondrial inner membrane protein COX18 D 105483424 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 105474693 cytochrome c oxidase assembly protein COX20, mitochondrial isoform X2 K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 105466021 MSS51; putative protein MSS51 homolog, mitochondrial isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 105484419 PET100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 105486842 PET117; protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 105499633 OXA1L; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 105471861 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 105473566 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 105483041 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 105464939 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 105489818 APOPT1; apoptogenic protein 1, mitochondrial isoform X1 K23506 APOPT1; apoptogenic protein 1 D 105471443 STMP1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 105468080 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1 D 105472734 short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 105480551 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 105469464 TMEM223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 105494976 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 105491058 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 105483575 TMEM70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 105489827 ATP5MPL; 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid D 105484355 LOW QUALITY PROTEIN: 6.8 kDa mitochondrial proteolipid K18193 MP68; 6.8 kDa mitochondrial proteolipid D 105478327 ATP5MD; up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 105489971 MFN1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 105473173 MFN2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 105470834 OPA1; dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 105478549 OPA3; optic atrophy 3 protein isoform X1 K23166 OPA3; optic atrophy 3 protein D 105494726 TRIAP1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 105480118 PARL; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 105474465 BAK1; bcl-2 homologous antagonist/killer isoform X1 K14021 BAK; Bcl-2 homologous antagonist/killer D 105478665 BAX; apoptosis regulator BAX isoform X1 K02159 BAX; apoptosis regulator BAX D 105484280 DNM1L; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 105492739 FIS1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 105468081 SUMO1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier D 112423183 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier D 105469154 SUMO2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 105472510 SUMO3; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 105482787 SH3GLB1; endophilin-B1 isoform X1 K11248 SH3GLB1; endophilin-B1 D 105474535 MTCH1; mitochondrial carrier homolog 1 isoform X1 K17885 MTCH; mitochondrial carrier D 105471720 MTCH2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 105473983 MFF; mitochondrial fission factor isoform X1 K22076 MFF; mitochondrial fission factor D 105496395 GDAP1L1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 105483571 GDAP1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 105472078 VAT1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 105464414 MIEF1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 105491049 MIEF2; mitochondrial dynamics protein MID49 isoform X1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 105491073 PLD6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 105482686 MIGA1; mitoguardin 1 isoform X1 K27289 MIGA; mitoguardin D 105464003 MIGA2; mitoguardin 2 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 105497365 ACTB; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 105469296 ACTG1; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 105486883 NAA20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 105493389 NAA25; N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 105491240 prohibitin-like K17080 PHB1; prohibitin 1 D 105472345 PHB; prohibitin K17080 PHB1; prohibitin 1 D 105484217 PHB2; prohibitin-2 K17081 PHB2; prohibitin 2 D 105473588 KTN1; kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 105484280 DNM1L; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 105489400 MYO5B; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V D 105490167 MYO5C; unconventional myosin-Vc isoform X1 K10357 MYO5; myosin V D 105493105 MYO5A; LOW QUALITY PROTEIN: unconventional myosin-Va K10357 MYO5; myosin V D 105468434 XIAP; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 105494410 DIABLO; diablo homolog, mitochondrial isoform X2 K10522 DIABLO; diablo C Morphogenesis factors D 105466567 SNX25; sorting nexin-25 isoform X4 K17887 SNX25; sorting nexin-25 D 105485218 RHOT1; mitochondrial Rho GTPase 1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 105465399 IMMT; MICOS complex subunit MIC60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 105487234 MTFP1; mitochondrial fission process protein 1 isoform X1 K17981 MTFP1; mitochondrial fission process protein 1 D 105498018 DAP3; 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29 D 105493093 NEDD4; E3 ubiquitin-protein ligase NEDD4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 105475999 OXR1; oxidation resistance protein 1 isoform X1 K25437 OXR1; oxidation resistance protein 1 D 105498021 protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 105467451 ATG2B; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2 D 105469538 ATG2A; autophagy-related protein 2 homolog A isoform X5 K17906 ATG2; autophagy-related protein 2 D 105470399 ATG3; ubiquitin-like-conjugating enzyme ATG3 isoform X1 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 105473756 ATG4B; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 105475438 ATG4D; cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 105490454 ATG4A; cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 105495177 ATG4C; cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 105478775 ATG5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5 D 105474659 BECN2; beclin-2 K08334 BECN; beclin D 105472097 BECN1; beclin-1 isoform X1 K08334 BECN; beclin D 105477709 ATG7; ubiquitin-like modifier-activating enzyme ATG7 isoform X1 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 105473310 GABARAP; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 105499929 GABARAPL1; gamma-aminobutyric acid receptor-associated protein-like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 105491261 GABARAPL2; gamma-aminobutyric acid receptor-associated protein-like 2 isoform X1 K08341 GABARAP; GABA(A) receptor-associated protein D 105474904 ATG9B; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9 D 105481253 ATG9A; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9 D 105475055 ATG10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 105500001 ATG12; ubiquitin-like protein ATG12 isoform X1 K08336 ATG12; ubiquitin-like protein ATG12 D 105473586 ATG14; LOW QUALITY PROTEIN: beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 105473896 ATG16L1; autophagy-related protein 16-1 isoform X1 K17890 ATG16L1; autophagy-related protein 16-1 D 105468709 ATG16L2; autophagy-related protein 16-2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2 D 105497373 WIPI2; WD repeat domain phosphoinositide-interacting protein 2 isoform X1 K17908 WIPI1_2; autophagy-related protein 18 D 105469044 WIPI1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 105487519 PRKN; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31] D 105474149 RNF41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 105467772 CLEC16A; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A D 105483085 PINK1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 105480118 PARL; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 105483997 SQSTM1; sequestosome-1 isoform X1 K14381 SQSTM1; sequestosome 1 D 105475772 TAX1BP1; tax1-binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1 D 105472331 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 105471664 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 105471665 ATG13; autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13 D 105490544 ULK1; serine/threonine-protein kinase ULK1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 105493332 ULK2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 105463388 RB1CC1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 105466741 LOW QUALITY PROTEIN: heat shock protein HSP 90-alpha-like K04079 HSP90A; molecular chaperone HtpG D 105467389 heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG D 105489542 HSP90AB1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 105475808 CDC37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 105469005 SMURF2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 105498089 SMURF1; E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 105482031 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 105463454 FUNDC1; FUN14 domain-containing protein 1 isoform X1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 105487437 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 105495129 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 105496242 MAP1LC3A; microtubule-associated proteins 1A/1B light chain 3A isoform X1 K10435 MAP1LC; microtubule-associated protein 1 light chain D 105474793 microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 105476784 microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 105488814 MAP1LC3B; microtubule-associated proteins 1A/1B light chain 3B isoform X1 K10435 MAP1LC; microtubule-associated protein 1 light chain D 105472076 NBR1; next to BRCA1 gene 1 protein isoform X1 K17987 NBR1; next to BRCA1 gene 1 protein D 105497799 TECPR1; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 105494296 ZFYVE1; zinc finger FYVE domain-containing protein 1 isoform X1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 105472113 COASY; bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 105464455 PLA2G6; 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 105487657 CUNH19orf12; protein C19orf12 homolog K23168 MPAN; protein MPAN D 105468353 FUNDC2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024