ORTHOLOGY: K01135
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Entry
K01135 KO
Name
ARSB
Definition
arylsulfatase B [EC:
3.1.6.12
]
Pathway
ko00531
Glycosaminoglycan degradation
ko01100
Metabolic pathways
ko04142
Lysosome
Module
M00076
Dermatan sulfate degradation
M00077
Chondroitin sulfate degradation
Disease
H00131
Mucopolysaccharidosis type VI
H00421
Mucopolysaccharidosis
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09100 Metabolism
09107 Glycan biosynthesis and metabolism
00531 Glycosaminoglycan degradation
K01135 ARSB; arylsulfatase B
09140 Cellular Processes
09141 Transport and catabolism
04142 Lysosome
K01135 ARSB; arylsulfatase B
Enzymes [BR:
ko01000
]
3. Hydrolases
3.1 Acting on ester bonds
3.1.6 Sulfuric-ester hydrolases
3.1.6.12 N-acetylgalactosamine-4-sulfatase
K01135 ARSB; arylsulfatase B
BRITE hierarchy
Other DBs
RN:
R07823
GO:
0003943
Genes
HSA:
411
(ARSB)
PTR:
737316
(ARSB)
PPS:
100987929
(ARSB)
GGO:
101138081
(ARSB)
PON:
100457196
(ARSB)
NLE:
100587589
(ARSB)
MCC:
709136
(ARSB)
MCF:
102116401
(ARSB)
CSAB:
103223561
(ARSB)
RRO:
104662974
(ARSB)
RBB:
108528898
(ARSB)
CJC:
100394090
(ARSB)
SBQ:
101045515
(ARSB)
MMU:
11881
(Arsb)
MCAL:
110308214
(Arsb)
MPAH:
110328948
(Arsb)
RNO:
25227
(Arsb)
MUN:
110558794
CGE:
100759794
(Arsb)
NGI:
103750289
(Arsb)
HGL:
101719731
(Arsb)
CCAN:
109675293
(Arsb)
OCU:
103346484
(ARSB)
103346606
TUP:
102469500
(ARSB)
CFA:
610364
(ARSB)
VVP:
112919590
(ARSB)
AML:
100467836
(ARSB)
UMR:
103681492
(ARSB)
UAH:
113255173
(ARSB)
ORO:
101374250
(ARSB)
ELK:
111148285
FCA:
100216331
(ARSB)
PTG:
102963642
(ARSB)
PPAD:
109274943
AJU:
106974796
(ARSB)
BTA:
538401
(ARSB)
BOM:
102279001
(ARSB)
BIU:
109564662
(ARSB)
BBUB:
102401475
(ARSB)
CHX:
102189402
(ARSB)
OAS:
101108314
(ARSB)
SSC:
102158016
(ARSB)
CFR:
102507706
(ARSB)
CDK:
105084869
(ARSB)
BACU:
103001911
(ARSB)
LVE:
103080763
(ARSB)
OOR:
101281243
(ARSB)
DLE:
111184985
(ARSB)
PCAD:
102973706
(ARSB)
ECB:
100073268
(ARSB)
EPZ:
103548666
(ARSB)
EAI:
106841176
(ARSB)
MYB:
102252145
(ARSB)
MYD:
102758054
(ARSB)
HAI:
109381893
(ARSB)
DRO:
112307472
(ARSB)
PALE:
102887255
(ARSB)
RAY:
107497236
(ARSB)
MJV:
108398416
(ARSB)
LAV:
100665589
(ARSB)
TMU:
101359357
MDO:
100032622
(ARSB)
SHR:
100931900
(ARSB)
PCW:
110216573
(ARSB)
OAA:
100088121
(ARSB)
GGA:
771459
(ARSB)
MGP:
104914958
CJO:
107305934
(ARSB)
NMEL:
110389380
(ARSB)
APLA:
101802978
(ARSB)
ACYG:
106042122
(ARSB)
TGU:
100228383
(ARSB)
LSR:
110479755
(ARSB)
SCAN:
103819543
(ARSB)
GFR:
102044758
(ARSB)
FAB:
101813661
(ARSB)
PHI:
102102961
(ARSB)
PMAJ:
107216097
(ARSB)
CCAE:
111941403
(ARSB)
CCW:
104695689
(ARSB)
ETL:
114057492
(ARSB)
FPG:
101910790
(ARSB)
FCH:
102049359
(ARSB)
CLV:
102091560
(ARSB)
EGZ:
104124897
(ARSB)
NNI:
104017612
(ARSB)
ACUN:
113489665
(ARSB)
PADL:
103919762
(ARSB)
AAM:
106487821
ASN:
102377963
(ARSB)
AMJ:
106737251
(ARSB)
PSS:
102445150
(ARSB)
CMY:
102947173
(ARSB)
CPIC:
101938081
(ARSB)
ACS:
100564703
(arsb)
PVT:
110084605
(ARSB)
PBI:
103060554
(ARSB)
PMUR:
107287875
(ARSB)
TSR:
106544488
(ARSB)
PMUA:
114606559
(ARSB)
GJA:
107117399
(ARSB)
XLA:
108717994
(arsb.L)
XTR:
100493013
(arsb)
NPR:
108799973
(ARSB)
DRE:
100538007
(arsb)
SRX:
107724712
(arsb)
SANH:
107694537
(arsb)
SGH:
107574102
(arsb)
CCAR:
109046309
IPU:
108279373
(arsb)
PHYP:
113543096
(arsb)
AMEX:
103041418
(arsb)
EEE:
113590451
(arsb)
TRU:
101061832
(arsb)
LCO:
104926623
(arsb)
NCC:
104966860
(arsb)
MZE:
101485324
(arsb)
ONL:
100697368
(arsb)
OLA:
101169377
(arsb)
XMA:
102227522
(arsb)
XCO:
114149560
(arsb)
PRET:
103473308
(arsb)
CVG:
107093772
(arsb)
NFU:
107374848
(arsb)
KMR:
108251298
(arsb)
ALIM:
106515071
(arsb)
AOCE:
111570347
(arsb)
CSEM:
103390009
103390010
103390011
103390012
103390027
POV:
109626042
(arsb)
LCF:
108895444
(arsb)
SDU:
111239020
(arsb)
SLAL:
111666800
(arsb)
HCQ:
109517689
(arsb)
BPEC:
110157319
(arsb)
MALB:
109953005
(arsb)
SASA:
100380367
(arsb)
OTW:
112230814
(arsb)
SALP:
111963905
(arsb)
ELS:
105015172
(arsb)
SFM:
108925070
(arsb)
PKI:
111849813
(arsb)
LCM:
102353782
(ARSB)
CMK:
103177857
(arsb)
RTP:
109923016
(arsb)
BFO:
118403590
118403591
118404651
118405951
118407366
118407458
118410571
118410754
118411641
118412106
118422400
118428666
118428667
118428764
118429766
118430529
118430580
CIN:
100185884
100187202
100187242
SPU:
100891337
105439655
115918901
115925932
583464
583878
584709
586205
587189
591704
APLC:
110978032
110982778
110982779
110984133
110984141
110984263
110986227
SKO:
100367265
100367284
100367451
100367841
100367915
100368065
100368130
100368255
100368279
100368400
100368517
100368670
100369267
100369301
100369410
100369474
100369888
100370868
100371460
100371615
100371768
100372000
100373029
100373229
100373276
100373562
100373775
100374292
100374639
100374997
100375292
100375535
100376019
100377092
100377632
100377677
100377827
100378421
100378661
100378747
100378957
102801346
102801374
102804222
102804409
102805297
102805475
102805529
102805609
102805724
102805842
102805902
102806010
102806349
102806641
102807117
102807169
102808053
102808173
102809375
102809734
102810355
DME:
Dmel_CG7402
(CG7402)
Dmel_CG8646
(CG8646)
DER:
6546392
DSE:
6606148
DSI:
Dsimw501_GD14734
(Dsim_GD14734)
DYA:
Dyak_GE19935
DAN:
6507210
DSR:
110178876
DPO:
Dpse_GA21235
Dpse_GA23896
DPE:
6590802
6598916
DMN:
108160908
108165341
DWI:
6640948
6645691
DGR:
Dgri_GH14469
DMO:
Dmoj_GI18487
DNV:
108653866
DHE:
111593491
111593520
MDE:
101894738
LCQ:
111681211
AGA:
AgaP_AGAP011347
AgaP_AGAP011348
AgaP_AGAP012047
AAG:
110680266
23687612
23687723
5566067
5579667
AALB:
109422334
CQU:
CpipJ_CPIJ006774
CpipJ_CPIJ011047
AME:
411657
412829
551758
552073
BIM:
100743595
100745153
100745993
100748801
BTER:
100646129
100646246
100647958
100650037
CCAL:
108623175
108626707
108627331
OBB:
114880106
114880647
114881981
SOC:
105195249
105205601
105205602
113004483
MPHA:
105829515
105829516
105833694
AEC:
105146955
105153878
105153880
ACEP:
105618404
105618405
105627005
PBAR:
105422468
105432242
105433969
105434003
VEM:
105559557
105562117
105568724
105569613
105569617
HST:
105180566
105180571
105182628
105191573
DQU:
106742444
106742445
106742451
106742452
106745848
106749778
CFO:
105257710
105259242
105259243
105259244
LHU:
105675071
105675079
105678114
PGC:
109852204
109856743
109857397
OBO:
105280178
105283953
105283954
105284162
PCF:
106787109
106787778
NVI:
100120225
100120251
100121172
100122775
100123823
CSOL:
105364395
105364511
105366204
105368206
MDL:
103571122
103571123
103572887
TCA:
659525
659587
(ARSB)
664109
DPA:
109535454
109539982
109541530
ATD:
109595271
109595272
109597944
109601898
109605475
NVL:
108556673
108557734
108557751
108558186
108561317
108561318
BMOR:
101737544
101737902
BMAN:
114239795
114243605
114243622
114243648
DPL:
KGM_211903
PMAC:
106709565
106717721
106718139
PRAP:
110996498
110996500
110998364
HAW:
110374404
110374783
110375086
110375159
TNL:
113500687
113501874
PXY:
105382281
105385659
105385673
105385674
105390597
(Gss)
API:
100163725
100167141
100169526
DNX:
107165744
107168015
107169055
AGS:
114123259
114126617
114127012
114132461
114132505
RMD:
113552555
113556052
113556643
113557146
BTAB:
109036051
109036852
109037766
109039068
109042265
109042336
109042337
109042345
109044026
109044747
109044749
CLEC:
106661985
106666275
106666289
106670001
106670042
PHU:
Phum_PHUM168260
Phum_PHUM570670
Phum_PHUM604070
Phum_PHUM616230
Phum_PHUM616890
ZNE:
110827813
110827898
110829584
110830065
110830356
110833850
110834448
110835042
110835045
FCD:
110845904
DPX:
DAPPUDRAFT_303738
PVM:
113818036
113818038
113824334
113824571
113824803
ISC:
IscW_ISCW001140
IscW_ISCW003809
IscW_ISCW004669
IscW_ISCW005802
IscW_ISCW006047
IscW_ISCW006919
IscW_ISCW006920
IscW_ISCW006921
IscW_ISCW008712
IscW_ISCW010087
IscW_ISCW011661
IscW_ISCW012148
IscW_ISCW014096
IscW_ISCW014599
IscW_ISCW014600
IscW_ISCW016893
IscW_ISCW019335
IscW_ISCW020211
IscW_ISCW020731
IscW_ISCW022771
TUT:
107359178
CSCU:
111618473
111624330
111624331
111624367
111626041
111627899
111631434
111634628
111634634
PTEP:
107436156
107436815
107436822
107437881
107442262
107455078
107455733
107457152
107457162
107457163
LGI:
LOTGIDRAFT_105309
LOTGIDRAFT_112980
LOTGIDRAFT_124040
LOTGIDRAFT_168762
LOTGIDRAFT_182669
LOTGIDRAFT_197818
LOTGIDRAFT_206748
LOTGIDRAFT_225566
LOTGIDRAFT_235167
LOTGIDRAFT_71987
PCAN:
112555109
112557037
112557446
112558224
112558739
112558827
112558828
112558937
112559749
112559784
112560458
112560459
112566597
112568594
112573812
112574237
112574451
112575575
112575688
CRG:
105320184
105320186
105325173
105341749
105345766
105349071
105349072
105349073
MYI:
110441366
110446197
110446205
110447882
110447883
110447887
110453798
110453799
110459647
110464404
110464405
110464406
110464407
110464431
OBI:
106871320
106872930
106883114
LAK:
106152974
106160231
106160972
106169745
106174598
106175140
106176485
106181460
112041454
NVE:
116602018
5498671
5501660
5503369
5503856
5505596
5507089
5510518
5519814
EPA:
110240881
110244428
110244429
110244430
110251142
110251521
110253174
ADF:
107327108
107336127
107336130
107336131
107341039
107351713
107353264
107353266
AMIL:
114952768
114952775
114952793
114958897
114958932
114962210
114963012
114966486
114970384
PDAM:
113673636
113673638
113675104
113676218
113676334
113676488
113677649
113677788
113678231
113678237
113684900
SPIS:
111320759
111321416
111322000
111322101
111331497
111333830
111333997
111338690
111342241
111342786
DGT:
114515982
114528126
HMG:
100212594
AQU:
100632436
100632563
100632818
100632939
100632944
100633070
100634880
100635593
100636537
100638166
100639099
100640253
100641487
105312142
109581016
109583239
MBR:
MONBRDRAFT_13917
MONBRDRAFT_16015
MONBRDRAFT_16099
(ASB)
MONBRDRAFT_2548
MONBRDRAFT_28433
MONBRDRAFT_32685
MONBRDRAFT_891
SRE:
PTSG_00448
PTSG_04073
PTSG_05666
PTSG_08011
PTSG_08687
PTSG_09899
SMIN:
v1.2.004770.t3
(symbB.v1.2.004770.t3)
v1.2.006990.t1
(symbB.v1.2.006990.t1)
v1.2.006992.t1
(symbB.v1.2.006992.t1)
v1.2.025906.t1
(symbB.v1.2.025906.t1)
v1.2.033030.t1
(symbB.v1.2.033030.t1)
v1.2.034521.t1
(symbB.v1.2.034521.t1)
PTI:
PHATRDRAFT_42934
FCY:
FRACYDRAFT_182357
(ARSB1)
NGD:
NGA_0431201
(ARSB)
NGA_0431202
(ARSB)
AAF:
AURANDRAFT_13369
AURANDRAFT_22180
(ARS)
AURANDRAFT_23174
(ARS13)
AURANDRAFT_2359
AURANDRAFT_2707
AURANDRAFT_30634
(ARS20)
AURANDRAFT_32660
(ARS12)
AURANDRAFT_33025
AURANDRAFT_66030
(ARS6)
AURANDRAFT_67258
AURANDRAFT_72312
(ARS3)
EHX:
EMIHUDRAFT_213721
EMIHUDRAFT_222125
EMIHUDRAFT_226193
EMIHUDRAFT_248910
EMIHUDRAFT_433677
EMIHUDRAFT_62301
EMIHUDRAFT_73553
SJA:
SJ2017_1926
PAT:
Patl_0889
OSG:
BST96_10725
MTHD:
A3224_10135
MAGA:
Mag101_05810
HJA:
BST95_16145
RBS:
RHODOSMS8_00747
(atsA)
BSYM:
CIT39_22215
BOS:
BSY19_414
(arsb)
RHZ:
RHPLAN_52420
DPM:
FNV33_04605
CHRE:
IE160_10675
BRX:
BH708_11250
BRV:
CFK39_06980
BGG:
CFK41_15095
BRZ:
CFK38_04065
BSAU:
DWV08_16070
CYN:
Cyan7425_1449
ROO:
G5S37_23450
LUO:
HHL09_15300
RBA:
RB1475
(arsB)
PSL:
Psta_1162
PIR:
VN12_02835
(atsA_6)
AHEL:
Q31a_15220
(atsA_22)
BVO:
Pan97_28610
(atsA_35)
AMUC:
Pan181_07500
(atsA_6)
FMR:
Fuma_03883
(atsA_24)
GIM:
F1728_19930
FTJ:
FTUN_6165
ULI:
ETAA1_13480
(atsA_4)
SACI:
Sinac_5718
PBU:
L21SP3_02067
(atsA_28)
PBP:
STSP1_01762
(atsA_37)
HBS:
IPV69_11400
OCK:
EXM22_16245
ASH:
AL1_00180
AGI:
FSB73_00300
OLI:
FKG96_22690
ECHI:
FKX85_19170
RUF:
TH63_11970
GFL:
GRFL_1426
FGL:
EM308_15790
DOK:
MED134_14677
LVN:
BWR22_11120
AHZ:
APS56_01130
MARF:
CJ739_1062
» show all
Taxonomy
UniProt
Reference
PMID:
2303452
Authors
Peters C, Schmidt B, Rommerskirch W, Rupp K, Zuhlsdorf M, Vingron M, Meyer HE, Pohlmann R, von Figura K
Title
Phylogenetic conservation of arylsulfatases. cDNA cloning and expression of human arylsulfatase B.
Journal
J Biol Chem 265:3374-81 (1990)
Sequence
[hsa:
411
]
LinkDB
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DBGET
integrated database retrieval system