Entry |
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Name |
iduronate-2-sulfatase;
chondroitinsulfatase;
idurono-2-sulfatase;
iduronide-2-sulfate sulfatase;
L-iduronosulfatase;
L-idurono sulfate sulfatase;
iduronate sulfatase;
sulfo-L-iduronate sulfatase;
L-iduronate 2-sulfate sulfatase;
sulfoiduronate sulfohydrolase;
2-sulfo-L-iduronate 2-sulfatase;
iduronate-2-sulfate sulfatase;
iduronate sulfate sulfatase
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Class |
Hydrolases;
Acting on ester bonds;
Sulfuric-ester hydrolases
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Sysname |
L-iduronate-2-sulfate 2-sulfohydrolase
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Reaction(IUBMB) |
Hydrolysis of the 2-sulfate groups of the L-iduronate 2-sulfate units of dermatan sulfate, heparan sulfate and heparin [RN: R07812 R07821]
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Reaction(KEGG) |
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History |
EC 3.1.6.13 created 1984
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Pathway |
ec00531 | Glycosaminoglycan degradation |
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Orthology |
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Genes |
» show all
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Reference |
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Authors |
Archer IM, Harper PS, Wusteman FS. |
Title |
Multiple forms of iduronate 2-sulphate sulphatase in human tissues and body fluids. |
Journal |
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Reference |
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Authors |
Bach G, Eisenberg F Jr, Cantz M, Neufeld EF. |
Title |
The defect in the Hunter syndrome: deficiency of sulfoiduronate sulfatase. |
Journal |
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Reference |
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Authors |
Di Natale P, Ronsisvalle L. |
Title |
Identification and partial characterization of two enzyme forms of iduronate sulfatase from human placenta. |
Journal |
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Reference |
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Authors |
Yutaka T, Fluharty AL, Stevens RL, Kihara H. |
Title |
Purification and some properties of human liver iduronate sulfatase. |
Journal |
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Other DBs |
ExplorEnz - The Enzyme Database: | 3.1.6.13 |
ExPASy - ENZYME nomenclature database: | 3.1.6.13 |
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LinkDB |
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