DISEASE: Complete transposition of the great arteries
Entry
H00550 Disease
Name
Complete transposition of the great arteries
Description
Complete transposition of the great arteries is a congenital heart defect with atrioventricular concordance and ventriculoarterial discordance in which the aorta arises from the morphologic right ventricle and the pulmonary artery arises from the morphologic left ventricle, resulting in severe cyanosis. Transposition of the great arteries (TGA) is frequently associated with other cardiac malformations such as ventricular septal defect. TGA is divided into three groups. Group I is TGA with intact ventricular septum. Group II is TGA with ventricular septal defect (TGA/VSD). Group III is TGA/VSD with pulmonary stenosis.
Category
Congenital malformation
Brite
Human diseases in ICD-11 classification [BR:br08403]
20 Developmental anomalies
Structural developmental anomalies primarily affecting one body system
Structural developmental anomalies of the circulatory system
Structural developmental anomaly of heart or great vessels
LA85 Congenital anomaly of an atrioventricular or ventriculo-arterial connection
H00550 Complete transposition of the great arteries
