ORTHOLOGY: K04002
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Entry
K04002 KO
Symbol
C4BPA
Name
complement component 4 binding protein alpha
Pathway
map04610
Complement and coagulation cascades
map05133
Pertussis
Disease
H00106
Complement regulatory protein defects
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09150 Organismal Systems
09151 Immune system
04610 Complement and coagulation cascades
K04002 C4BPA; complement component 4 binding protein alpha
09160 Human Diseases
09171 Infectious disease: bacterial
05133 Pertussis
K04002 C4BPA; complement component 4 binding protein alpha
BRITE hierarchy
Genes
HSA:
722
(C4BPA)
PTR:
457688
(C4BPA)
743313
PPS:
100968163
100984709
GGO:
101138397
(C4BPA)
101151974
PON:
100440751
(C4BPA)
100443687
PPYG:
129016780
(C4BPA)
129030072
NLE:
100587775
(C4BPA)
100588098
HMH:
116457713
(C4BPA)
116457960
SSYN:
129458489
(C4BPA)
129458816
MCC:
114680255
693382
(C4BPA)
MCF:
101926212
102142263
(C4BPA)
MTHB:
126949217
126949232
MNI:
105484869
(C4BPA)
105484870
CSAB:
103231022
(C4BPA)
103247303
CATY:
105576860
(C4BPA)
105576877
PANU:
101017189
101017548
(C4BPA)
TGE:
112605229
(C4BPA)
112631192
MLEU:
105529685
105529698
RRO:
104664184
(C4BPA)
104664197
RBB:
108535128
108535130
(C4BPA)
TFN:
117075549
(C4BPA)
117075550
PTEH:
111522688
111522723
(C4BPA)
CANG:
105508839
105509464
CJC:
100390341
(C4BPA)
SBQ:
101047590
101047898
CIMI:
108301959
108302098
(C4BPA)
ANAN:
105721913
105722082
(C4BPA)
CSYR:
103266809
(C4BPA)
103266810
MMUR:
105869167
(C4BPA)
LCAT:
123626855
(C4BPA)
ERUF:
138375625
PCOQ:
105805874
(C4BPA)
OGA:
100949139
(C4BPA)
MMU:
12269
(C4bp)
22789
(Zp3r)
MCAL:
110291790
110293221
MPAH:
110322103
(C4bpa)
RNO:
24235
(C4bpa)
MCOC:
116070092
116070094
ANU:
117716073
(C4bpa)
117716346
ASYL:
127697381
127697783
MUN:
110550318
(C4bpa)
110550320
CGE:
100772422
100772713
(C4bpa)
MAUA:
101826821
(C4bpa)
101827079
PROB:
127236399
127236455
PLEU:
114696934
(C4bpa)
114696940
MORG:
121446201
121446273
MFOT:
126504985
126504999
AAMP:
119827047
(C4bpa)
NGI:
103738264
HGL:
101720618
(C4bpa)
101721321
(C4bpb)
101722923
CPOC:
100135632
(Zp3r)
100379238
(C4bpa)
CCAN:
109676886
109690738
DORD:
105986438
105986441
DSP:
122109130
122109484
DMER:
138841099
138841102
PLOP:
125359312
125360219
NCAR:
124961409
124961821
MMMA:
107140314
107140596
ITI:
101965450
101973539
OCU:
100343920
100352436
OPI:
101527865
(C4BPA)
OCZ:
121160001
(C4BPA)
121160002
TUP:
102485664
(C4BPA)
GVR:
103603178
(C4BPA)
103610433
CFA:
100687316
(C4BPA)
100855476
CLUD:
112648312
(C4BPA)
112678777
VVP:
112910985
(C4BPA)
VLG:
121473637
(C4BPA)
NPO:
129505800
(C4BPA)
AML:
100484223
(C4BPA)
UMR:
103657663
UAH:
113242607
UAR:
123785795
(C4BPA)
ELK:
111151046
LLV:
125086308
MPUF:
101691873
(C4BPA)
MNP:
132025566
MLK:
131814842
NVS:
122918161
ORO:
101384876
EJU:
114221876
(C4BPA)
ZCA:
113933640
(C4BPA)
MLX:
118013698
(C4BPA)
NSU:
110573893
(C4BPA)
LWW:
102734749
(C4BPA)
FCA:
101094897
PYU:
121022443
(C4BPA)
PCOO:
112857906
(C4BPA)
PBG:
122476559
PVIV:
125155534
LRUF:
124510066
LGF:
123587004
(C4BPA)
AJU:
106981808
PTG:
102960497
(C4BPA)
PPAD:
109255431
(C4BPA)
PUC:
125925802
PLEZ:
122212429
(C4BPA)
HHV:
120245590
(C4BPA)
BTA:
281651
(C4BPA)
506707
BOM:
102268232
(C4BPA)
102272644
BBUB:
102405381
(C4BPA)
BKE:
129652801
(C4BPA)
BBIS:
104998837
(C4BPA)
104998882
CHX:
102179118
(C4BPA)
102185487
OAS:
101114456
101119740
(C4BPA)
BTAX:
128061719
(C4BPA)
128061742
CSUM:
138090702
138090874
(C4BPA)
ODA:
120879869
120879926
(C4BPA)
CCAD:
122451770
122452581
(C4BPA)
MREE:
136168958
136169335
OVR:
110151195
110152766
(C4BPA)
MBEZ:
129551007
129551722
(C4BPA)
SSC:
100520761
(C4BPA)
396982
(C4BPA)
CFR:
102512977
(C4BPA)
CBAI:
105075418
(C4BPA)
CDK:
105098603
(C4BPA)
VPC:
102528215
(C4BPA)
BACU:
102997936
103017329
(C4BPA)
BMUS:
118892747
(C4BPA)
LVE:
103087891
OOR:
101269843
(C4BPA)
LALB:
132509401
(C4BPA)
GMF:
115861779
(C4BPA)
DDP:
132413448
DLE:
111184733
PCAD:
102978455
(C4BPA)
PSIU:
116759861
(C4BPA)
PPHC:
136118087
NASI:
112403525
(C4BPA)
ECB:
100056222
(C4BPA)
100056262
EPZ:
103558806
103558807
(C4BPA)
EAI:
106822939
106823168
MYB:
102259104
102259392
MYD:
102758036
(C4BPA)
MMYO:
118673666
(C4BPA)
MLF:
102435037
(C4BPA)
MDT:
132220982
(C4BPA)
MYUM:
138996356
(C4BPA)
PKL:
118721394
(C4BPA)
EFUS:
103297546
(C4BPA)
MNA:
107539517
(C4BPA)
DRO:
112315982
(C4BPA)
SHON:
119001661
(C4BPA)
AJM:
119056784
PDIC:
114511946
(C4BPA)
PHAS:
123820673
(C4BPA)
MMF:
118637741
118637953
(C4BPA)
PPAM:
129062469
HAI:
109374509
(C4BPA)
RFQ:
117014779
PGIG:
120617919
(C4BPA)
RAY:
107502235
(C4BPA)
MJV:
108386643
TOD:
119234694
SARA:
101553545
SFUM:
130020165
SETR:
126004298
LAV:
100660771
(C4BPA)
TMU:
101359097
ETF:
101653530
(C4BPA)
DNM:
101423535
(C4BPA)
MDO:
100020253
(C4BPA)
103093588
GAS:
123245977
(C4BPA)
SHR:
100920044
(C4BPA)
105750613
AFZ:
127562615
PCW:
110219685
(C4BPA)
TVP:
118845821
(C4BPA)
118846815
PBRV:
138151213
(C4BPA)
OAA:
100087150
(C4BPA)
114813132
TACU:
119930661
119930665
119930968
LSR:
110473473
(CD46)
PMAJ:
107214875
(CD46)
CCAE:
111945069
DCC:
119846319
CPIC:
101936145
101950288
CABI:
116832972
PBI:
103058528
TSR:
106540486
106548899
PGUT:
117663848
PCAE:
139315080
VKO:
123031558
PMUA:
114599338
114599923
ZVI:
118088518
(CD46)
118088522
XTR:
779565
(arc2)
RTEM:
120928427
120928428
PADS:
140340139
(CD46)
IFU:
128619827
PHYP:
113530320
113530570
TVC:
132862789
NGRA:
132896550
TNG:
GSTEN00023444G001
XMA:
106700284
XCO:
114140458
KMR:
108237638
AOCE:
111586001
BPEC:
110154006
CMK:
103182516
CPLA:
122563172
122563181
CPUN:
140467327
140467333
HOC:
132828227
SCAU:
119978177
119979045
LERI:
129708952
EGL:
EGR_10532
» show all
Taxonomy
UniProt
Reference
PMID:
19155499
Authors
Happonen KE, Sjoberg AP, Morgelin M, Heinegard D, Blom AM
Title
Complement inhibitor C4b-binding protein interacts directly with small glycoproteins of the extracellular matrix.
Journal
J Immunol 182:1518-25 (2009)
DOI:
10.4049/jimmunol.182.3.1518
Sequence
[hsa:
722
]
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