ORTHOLOGY: K15903
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Entry
K15903 KO
Symbol
GON7, PCC2
Name
EKC/KEOPS complex subunit GON7
Disease
H01722
Galloway-Mowat syndrome
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03016 Transfer RNA biogenesis
K15903 GON7, PCC2; EKC/KEOPS complex subunit GON7
Transfer RNA biogenesis [BR:
ko03016
]
Eukaryotic type
tRNA modification factors
KEOPS/EKC complex
K15903 GON7, PCC2; EKC/KEOPS complex subunit GON7
BRITE hierarchy
Genes
HSA:
84520
(GON7)
PTR:
453124
(GON7)
PPS:
100982644
(GON7)
GGO:
101138437
(GON7)
PON:
100449560
(GON7)
PPYG:
129012107
(GON7)
NLE:
100606978
(GON7)
HMH:
116456309
(GON7)
SSYN:
129487507
(GON7)
MCC:
704509
(GON7)
MCF:
102121299
(GON7)
MTHB:
126959706
MNI:
105467522
(GON7)
CSAB:
103229586
(GON7)
CATY:
105596602
PANU:
101025040
(GON7)
TGE:
112628468
(GON7)
MLEU:
105547942
RRO:
104679053
(GON7)
RBB:
108519124
(GON7)
TFN:
117071504
(GON7)
PTEH:
111538246
(GON7)
CANG:
105517025
CJC:
100398031
(GON7)
SBQ:
101038504
CIMI:
108316855
(GON7)
ANAN:
105717788
(GON7)
CSYR:
103254236
(GON7)
MMUR:
105856747
(GON7)
LCAT:
123645163
(GON7)
ERUF:
138380812
(GON7)
PCOQ:
105819057
OGA:
100954908
(GON7)
MMU:
100233175
(Gon7)
MCAL:
110306504
(Gon7)
MPAH:
110324883
(Gon7)
RNO:
100233176
(Gon7)
MCOC:
116079682
(Gon7)
ANU:
117697565
(Gon7)
ASYL:
127687010
(Gon7)
MUN:
110562022
(Gon7)
CGE:
113836166
MAUA:
101844900
(Gon7)
PROB:
127231091
(Gon7)
PLEU:
114706036
(Gon7)
PMAV:
102905520
(Gon7)
MORG:
121434375
(Gon7)
121460506
MFOT:
126507234
AAMP:
119819272
(Gon7)
CNL:
130883026
(Gon7)
NGI:
103724590
(Gon7)
HGL:
101701765
(Gon7)
CPOC:
100712972
(Gon7)
CCAN:
109693574
(Gon7)
DORD:
105985522
DSP:
122118685
(Gon7)
DMER:
138810498
(Gon7)
138833121
PLOP:
125363124
(Gon7)
NCAR:
124976023
MMMA:
107150066
(Gon7)
ITI:
101967998
(Gon7)
OCU:
100348092
(GON7)
OPI:
101527798
(GON7)
OCZ:
121152889
(GON7)
TUP:
102472100
(GON7)
GVR:
103589403
103610847
CFA:
612321
(GON7)
CLUD:
112657047
(GON7)
VVP:
112907321
(GON7)
VLG:
121492438
(GON7)
NPO:
129496136
(GON7)
AML:
100484283
(GON7)
UMR:
103670040
(GON7)
UAH:
113267335
(GON7)
UAR:
123798873
(GON7)
ELK:
111148562
LLV:
125104598
MPUF:
101682980
MNP:
132000216
(GON7)
MLK:
131836933
(GON7)
NVS:
122893792
(GON7)
ORO:
101362096
EJU:
114209897
(GON7)
ZCA:
113909688
(GON7)
MLX:
118002242
(GON7)
NSU:
110571526
(GON7)
LWW:
102729663
(GON7)
FCA:
101099726
(GON7)
PYU:
121032222
(GON7)
PCOO:
112855449
(GON7)
PBG:
122469472
(GON7)
PVIV:
125167809
(GON7)
LRUF:
124512557
LGF:
123582072
(GON7)
AJU:
106980831
(GON7)
PTG:
102968630
(GON7)
PPAD:
109274488
(GON7)
PUC:
125909230
PLEZ:
122223079
(GON7)
HHV:
120220239
(GON7)
BTA:
505131
(GON7)
BOM:
102278568
(GON7)
BIU:
109575496
(GON7)
BBUB:
102414430
(GON7)
BBIS:
104985826
CHX:
102169227
(GON7)
102188641
OAS:
101115656
(GON7)
BTAX:
128045749
128066564
128066567
(GON7)
CSUM:
138071166
138095416
(GON7)
ODA:
120874976
(GON7)
CCAD:
122455100
(GON7)
MREE:
136147287
(GON7)
OVR:
110126339
139029594
(GON7)
MBEZ:
129550601
(GON7)
SSC:
100155082
(GON7)
CFR:
102519157
(GON7)
CBAI:
105079879
CDK:
105095804
(GON7)
VPC:
102531633
(GON7)
BACU:
103011081
(GON7)
BMUS:
118890322
(GON7)
LVE:
103085337
OOR:
101271059
(GON7)
LALB:
132529383
(GON7)
GMF:
115867301
(GON7)
DDP:
132419438
(GON7)
DLE:
111176138
(GON7)
PCAD:
102991750
(GON7)
PSIU:
116749454
(GON7)
PPHC:
136119165
(GON7)
NASI:
112408252
(GON7)
ECB:
100053408
(GON7)
EPZ:
103557897
(GON7)
EAI:
106825386
(GON7)
MYB:
102256631
(GON7)
MYD:
102766089
(GON7)
MMYO:
118659781
(GON7)
MDT:
132230274
(GON7)
MYUM:
139009300
139010261
PKL:
118704233
(GON7)
EFUS:
103302911
(GON7)
MNA:
107536676
DRO:
112311480
(GON7)
SHON:
118976579
(GON7)
AJM:
119037948
(GON7)
PDIC:
114492949
(GON7)
114506781
PHAS:
123808186
(GON7)
MMF:
118635402
(GON7)
PPAM:
129065706
(GON7)
HAI:
109382758
(GON7)
RFQ:
117023318
(GON7)
PALE:
102890784
(GON7)
PGIG:
120619633
(GON7)
RAY:
107511251
(GON7)
MJV:
108409821
(GON7)
TOD:
119238356
(GON7)
SFUM:
130041386
(GON7)
SETR:
126003625
(GON7)
LAV:
100669373
(GON7)
TMU:
101342496
ETF:
101650092
(GON7)
DNM:
101419630
(GON7)
MDO:
100016852
(GON7)
GAS:
123235907
(GON7)
123240036
SHR:
100925737
(GON7)
AFZ:
127549389
PCW:
110217743
(GON7)
TVP:
118828709
(GON7)
PBRV:
138159702
(GON7)
OAA:
103170600
TACU:
119927501
(GON7)
GGA:
101752260
CJO:
107315187
NMEL:
110401438
SCAN:
115485437
(GON7)
OTC:
121343526
PRUF:
121356073
OMA:
130254205
(GON7)
PMAJ:
107205496
(GON7)
CCW:
120410062
(GON7)
ETL:
114060641
(GON7)
ZAB:
102066114
(GON7)
ZLE:
135448298
(GON7)
SVG:
106858031
MMEA:
130576183
(GON7)
HRT:
120754522
(GON7)
CCIC:
134045655
(GON7)
SHAB:
115606084
TALA:
116965764
(GON7)
ACHC:
115333947
(GON7)
AGEN:
126050628
HHAR:
128139911
(GON7)
BBUT:
142031976
(GON7)
GCL:
127016799
PPUS:
135174922
CBOR:
142082769
(GON7)
CBOY:
140652896
(GON7)
MAME:
142410622
(GON7)
CNIC:
135989696
(GON7)
RTD:
128909091
CRID:
134514739
LMIC:
141742274
(GON7)
DNE:
112990416
(GON7)
AMJ:
106738252
(GON7)
CPOO:
109321708
GGN:
109298508
(GON7)
PSS:
102452433
CIZ:
142014276
(GON7)
CMY:
119566457
CCAY:
125638058
(GON7)
LKP:
140913330
(GON7)
NDS:
141990172
(GON7)
DCC:
119857186
(GON7)
CPIC:
101948831
(GON7)
TST:
117876181
(GON7)
CABI:
116827597
(GON7)
MRV:
120404394
(GON7)
ACS:
103278938
(gon7)
ASAO:
132763084
(GON7)
PVT:
110083636
(GON7)
SUND:
121917430
PBI:
103051987
(GON7)
PMUR:
107287218
(GON7)
CTIG:
120318364
TSR:
106544119
PGUT:
117665934
(GON7)
PCAE:
139308087
(GON7)
PTEX:
113444572
(GON7)
NSS:
113419682
(GON7)
VKO:
123026589
(GON7)
PMUA:
114590748
(GON7)
PRAF:
128407682
(GON7)
ZVI:
118080971
(GON7)
HCG:
128326649
GJA:
107121764
EMC:
129324710
(GON7)
XLA:
108698725
108699817
XTR:
100486520
(gon7)
NPR:
108788682
PADS:
140342649
(GON7)
PWL:
138260083
(GON7)
GSH:
117363688
DRE:
568418
CCAR:
122148978
(si:dkeyp-55f12.3)
PTET:
122324894
(si:dkeyp-55f12.3)
LROH:
127183442
(si:dkeyp-55f12.3)
GRF:
141283343
OMC:
131527368
(si:dkeyp-55f12.3)
PPRM:
120493470
(si:dkeyp-55f12.3)
RKG:
130091848
(si:dkeyp-55f12.3)
MAMB:
125277925
(si:dkeyp-55f12.3)
CERY:
137018390
(si:dkeyp-55f12.3)
MASI:
127415923
(si:dkeyp-55f12.3)
TROS:
130565569
(si:dkeyp-55f12.3)
TDW:
130434748
(si:dkeyp-55f12.3)
IPU:
108257832
(si:dkeyp-55f12.3)
IFU:
128601630
(si:dkeyp-55f12.3)
PHYP:
113547696
SMEO:
124377405
(si:dkeyp-55f12.3)
TFD:
113643320
(si:dkeyp-55f12.3)
TVC:
132843020
(si:dkeyp-55f12.3)
CGAR:
128515259
(si:dkeyp-55f12.3)
NGRA:
132882682
(si:dkeyp-55f12.3)
AMEX:
103038833
(si:dkeyp-55f12.3)
CMAO:
118815667
(si:dkeyp-55f12.3)
TNG:
GSTEN00003464G001
LCO:
109140277
TBEN:
117474942
(si:dkeyp-55f12.3)
SLUC:
118493860
(si:dkeyp-55f12.3)
GAT:
120814269
(si:dkeyp-55f12.3)
AFB:
129107343
(si:dkeyp-55f12.3)
CLUM:
117727305
(si:dkeyp-55f12.3)
SCHU:
122862856
(si:dkeyp-55f12.3)
EARM:
139302134
CUD:
121521613
(si:dkeyp-55f12.3)
HTC:
141801911
OML:
118598153
(si:dkeyp-55f12.3)
CTUL:
119796708
(si:dkeyp-55f12.3)
KMR:
119617995
(si:dkeyp-55f12.3)
EJA:
138212360
BFRE:
138636832
PPLT:
128459802
(si:dkeyp-55f12.3)
SMAU:
118289840
(si:dkeyp-55f12.3)
LCF:
127142623
(si:dkeyp-55f12.3)
XGL:
120788827
(si:dkeyp-55f12.3)
PEE:
133417322
(si:dkeyp-55f12.3)
OTW:
121846509
(si:dkeyp-55f12.3)
OMY:
110529745
(si:dkeyp-55f12.3)
OGO:
123990875
(si:dkeyp-55f12.3)
OKE:
118398529
(si:dkeyp-55f12.3)
SNH:
120023882
(si:dkeyp-55f12.3)
CCLU:
121552919
(si:dkeyp-55f12.3)
OEP:
134025019
(si:dkeyp-55f12.3)
ARUT:
117422706
LCM:
102352525
(GON7)
CPLA:
122553436
(si:dkeyp-55f12.3)
CPUN:
140476155
HOC:
132818382
(si:dkeyp-55f12.3)
LERI:
129699964
(si:dkeyp-55f12.3)
HAKA:
140724706
PMRN:
116947328
LRJ:
133360880
BFO:
118417886
ZNE:
110829130
CSEC:
111865887
BGT:
106055385
GAE:
121371135
HRF:
124146436
MYI:
110455941
PMAX:
117322917
LAK:
106170416
EPA:
110233395
ADF:
107357848
AMIL:
114972539
PDAM:
113667261
SPIS:
111330372
SCE:
YJL184W
(GON7)
SEUB:
DI49_2846
SPAO:
SPAR_J00330
AGO:
AGOS_AEL144W
ERC:
Ecym_8124
KLA:
KLLA0_A06171g
KMX:
KLMA_10369
(GON7)
LTH:
KLTH0F04158g
VPO:
Kpol_2001p43
ZRO:
ZYRO0D17072g
CGR:
2887651
(GVI51_F03201)
NCS:
NCAS_0I02990
(NCAS0I02990)
NDI:
NDAI_0B00370
(NDAI0B00370)
TPF:
TPHA_0A02650
(TPHA0A02650)
TBL:
TBLA_0J01170
(TBLA0J01170)
TGB:
HG536_0A01910
TDL:
TDEL_0G01930
(TDEL0G01930)
KAF:
KAFR_0F01660
(KAFR0F01660)
KNG:
KNAG_0C02290
(KNAG0C02290)
ZMK:
HG535_0H03650
DHA:
DEHA2C02090g
PIC:
PICST_30592
PGU:
PGUG_01159
SPAA:
SPAPADRAFT_57942
LEL:
PVL30_001610
(GON7)
LBG:
92207971
(LODBEIA_P27750)
CAL:
CAALFM_C102310CA
(CaO19.3688)
CTP:
CTRG_04638
COT:
CORT_0B07540
CDU:
CD36_02160
CTEN:
18246196
(GON7)
CLU:
CLUG_01710
CLUS:
A9F13_13g01551
CAUR:
CJI96_0003146
ASAU:
88171525
(PUMCH_000456)
PPA:
PAS_chr2-2_0121
PKZ:
C5L36_0A12360
BBRX:
BRETT_001055
OPA:
HPODL_01553
SLB:
AWJ20_1385
NCR:
NCU01541
NTE:
NEUTE1DRAFT64833
(NEUTE1DRAFT_64833)
PBEL:
QC761_305225
PPSD:
QC762_305225
PPSP:
QC763_0052740
PPSA:
QC764_0052460
TTT:
THITE_2092830
MTM:
MYCTH_2121350
CTHR:
CTHT_0004960
RTHE:
98127813
(VTJ83DRAFT_6456)
MGR:
MGG_01055
PPEI:
PpBr36_08086
PGRI:
PgNI_08189
TMN:
UCRPA7_4090
SSCK:
SPSK_00353
FPU:
FPSE_10593
FPOA:
FPOAC1_006804
FVN:
FVRRES_07427
FVR:
FVEG_11324
FOX:
FOXG_13899
FFC:
NCS54_01060200
FKR:
NCS57_01053900
FMU:
J7337_011808
TRE:
TRIREDRAFT_110496
TRR:
M419DRAFT_46019
TATV:
90961148
(TrAtP1_012602)
TASP:
90967124
(TrAFT101_010136)
MAJ:
MAA_05341
MBRN:
26239115
(G6M90_00g008360)
PCHM:
VFPPC_13471
UVI:
66065862
(UV8b_05084)
CMT:
CCM_06787
AMUS:
LMH87_011910
PLJ:
28887068
(PLICBS_002367)
PTKZ:
JDV02_002639
DCON:
63718103
(DCS_05460)
VAL:
VDBG_03049
VDA:
VDAG_03958
CFJ:
CFIO01_10615
CLUP:
CLUP02_00668
CHIG:
CH63R_12633
CDET:
87942803
(CDEST_06300)
ELA:
UCREL1_4354
PFY:
PFICI_08430
BFU:
BCIN_04g00110
PSCO:
LY89DRAFT_153390
GLZ:
GLAREA_03412
AFM:
AFUA_7G05785
ACT:
ACLA_007470
NFI:
NFIA_027020
AOR:
AO090005000442
ANG:
An07g02120
AFV:
AFLA_003232
ALUC:
AKAW2_11944S
ACHE:
ACHE_60985A
APUU:
APUU_70231A
PCS:
N7525_008610
PDP:
PDIP_47560
POU:
POX_e06261
PPSF:
300794598
(PFLUO_LOCUS8331)
TMF:
EYB26_007371
TRG:
TRUGW13939_06960
CIM:
CIMG_13466
(CIMG05447)
CPW:
9693126
(D8B26_000195)
URE:
UREG_06271
ABE:
ARB_00662
TVE:
TRV_04788
PBL:
PAAG_00059
PBN:
PADG_07205
BGH:
BDBG_05724
PNO:
SNOG_15600
PTE:
PTT_05990
PTRR:
6343693
(PtrM4_110290)
BZE:
COCCADRAFT_89043
BOR:
COCMIDRAFT_82061
AALT:
CC77DRAFT_946424
ARAB:
EKO05_0006202
FFU:
CLAFUR5_01250
CBET:
CB0940_00939
BCOM:
BAUCODRAFT_149060
NPA:
UCRNP2_9140
» show all
Taxonomy
UniProt
Reference
PMID:
21183954
Authors
Srinivasan M, Mehta P, Yu Y, Prugar E, Koonin EV, Karzai AW, Sternglanz R
Title
The highly conserved KEOPS/EKC complex is essential for a universal tRNA modification, t6A.
Journal
EMBO J 30:873-81 (2011)
DOI:
10.1038/emboj.2010.343
Sequence
[sce:
YJL184W
]
Reference
PMID:
15679890
Authors
Jorgensen FG, Hobolth A, Hornshoj H, Bendixen C, Fredholm M, Schierup MH
Title
Comparative analysis of protein coding sequences from human, mouse and the domesticated pig.
Journal
BMC Biol 3:2 (2005)
DOI:
10.1186/1741-7007-3-2
Sequence
[ssc:
100155082
]
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DBGET
integrated database retrieval system