KEGG ORTHOLOGY: K17654

ORTHOLOGY: K17654

Entry

K17654                      KO

Symbol

TRMT10C, MRPP1

Name

mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]

Disease

H00891

Combined oxidative phosphorylation deficiency

Brite

KEGG Orthology (KO) [BR:ko00001]
09180 Brite Hierarchies
  09182 Protein families: genetic information processing
   03029 Mitochondrial biogenesis
    K17654  TRMT10C, MRPP1; mitochondrial ribonuclease P protein 1
Mitochondrial biogenesis [BR:ko03029]
Mitochondrial DNA transcription, translation, and replication factors
  Mitochondrial transcription and translation factors
   Mitochondrial ribonuclease P
    K17654  TRMT10C, MRPP1; mitochondrial ribonuclease P protein 1

Genes

HSA:	54931(TRMT10C)

PTR:	740267(TRMT10C)

PPS:	100987585(TRMT10C)

GGO:	101147563(TRMT10C)

PON:	100460224(TRMT10C)

PPYG:

129033121(TRMT10C)

NLE:	100586698(TRMT10C)

HMH:	116467000(TRMT10C)

SSYN:

129471039(TRMT10C)

MCC:	702107(TRMT10C)

MCF:	102125574(TRMT10C)

MTHB:

126947862

MNI:	105477497(TRMT10C)

CSAB:

103228435(TRMT10C)

CATY:

105597146(TRMT10C)

PANU:

101006015(TRMT10C)

TGE:	112619527(TRMT10C)

MLEU:

105547265(TRMT10C)

RRO:	104654233(TRMT10C)

RBB:	108527951(TRMT10C)

TFN:	117083588(TRMT10C)

PTEH:

111542694(TRMT10C)

CANG:

105521020(TRMT10C)

CJC:	100392866(TRMT10C)

SBQ:	101042745(TRMT10C)

CIMI:

108286490(TRMT10C)

ANAN:

105734080(TRMT10C)

CSYR:

103277019(TRMT10C)

MMUR:

105879443(TRMT10C)

LCAT:

123630589(TRMT10C)

PCOQ:

105817211(TRMT10C)

OGA:	100943829(TRMT10C)

MMU:	52575(Trmt10c)

MCAL:

110311630(Trmt10c)

MPAH:

110329898(Trmt10c)

RNO:	304012(Trmt10c)

MCOC:

116085995(Trmt10c)

ANU:	117717488(Trmt10c)

ASYL:

127665505(Trmt10c)

MUN:	110563325(Trmt10c)

CGE:	100756944(Trmt10c)

MAUA:

101828552(Trmt10c)

PROB:

127227392(Trmt10c)

PLEU:

114691923(Trmt10c)

MORG:

121461794(Trmt10c)

MFOT:

126488700

AAMP:

119825119(Trmt10c)

NGI:	103736230(Trmt10c)

HGL:	101717306 101720714(Trmt10c)

CPOC:

100725569(Trmt10c)

CCAN:

109693873(Trmt10c)

DORD:

105991464(Trmt10c)

DSP:	122105593(Trmt10c)

PLOP:

125351635(Trmt10c)

NCAR:

124993014

MMMA:

107136355(Trmt10c)

ITI:	101971531(Trmt10c)

OCU:

100351020

OPI:	101517590(TRMT10C)

TUP:	102485963(TRMT10C)

GVR:	103585685(TRMT10C)

CFA:	478545(TRMT10C)

CLUD:

112640088(TRMT10C)

VVP:	112913392(TRMT10C)

VLG:	121501771(TRMT10C)

NPO:	129503815(TRMT10C)

AML:	100466320(TRMT10C)

UMR:	103673265(TRMT10C)

UAH:	113250698(TRMT10C)

UAR:	123784102(TRMT10C)

ELK:

111150048

LLV:

125096408

MPUF:

101672000(TRMT10C)

MNP:	132010225(TRMT10C)

MLK:	131825185(TRMT10C)

NVS:	122908456(TRMT10C)

ORO:	101378389(TRMT10C)

EJU:	114221063(TRMT10C)

ZCA:	113917223(TRMT10C)

MLX:	118017387(TRMT10C)

NSU:	110582473(TRMT10C)

LWW:	102733321 102749118(TRMT10C)

FCA:	101094782(TRMT10C)

PYU:	121036170(TRMT10C)

PCOO:

112850198(TRMT10C)

PBG:	122491381(TRMT10C)

PVIV:

125175780(TRMT10C)

LRUF:

124526831

LGF:	123610800(TRMT10C)

AJU:

106972250

PTG:	102959071(TRMT10C)

PPAD:

109266326(TRMT10C)

PUC:

125920895

PLEZ:

122229518(TRMT10C)

HHV:	120224042(TRMT10C)

BTA:	532418(TRMT10C)

BOM:	102284857(TRMT10C)

BIU:	109567323(TRMT10C)

BBUB:

102392489(TRMT10C)

BBIS:

104990064(TRMT10C)

CHX:	102184375(TRMT10C)

OAS:	101111763(TRMT10C)

BTAX:

128050772(TRMT10C)

CSUM:

138084630(TRMT10C)

ODA:	120852516(TRMT10C)

CCAD:

122428982(TRMT10C)

MREE:

136152291(TRMT10C)

OVR:	110139172(TRMT10C)

MBEZ:

129548908(TRMT10C)

SSC:	100522163(TRMT10C)

CFR:	102517722(TRMT10C)

CBAI:

105077908(TRMT10C)

CDK:	105087719(TRMT10C)

VPC:	102540644(TRMT10C)

BACU:

103016524(TRMT10C)

BMUS:

118893875(TRMT10C)

LVE:	103074726(TRMT10C)

OOR:	101280997(TRMT10C)

DLE:	111184171(TRMT10C)

PCAD:

102989258(TRMT10C)

PSIU:

116752549(TRMT10C)

NASI:

112409239(TRMT10C)

ECB:	100072187(TRMT10C)

EPZ:	103564787(TRMT10C)

EAI:	106838880(TRMT10C)

MYB:	102257770(TRMT10C)

MYD:	102760696(TRMT10C)

MMYO:

118677154(TRMT10C)

MLF:	102419202 102420896(TRMT10C)

MDT:	132230474(TRMT10C)

MYUM:

139003791(TRMT10C)

PKL:	118724456(TRMT10C)

EFUS:

103304488(TRMT10C)

MNA:	107527104(TRMT10C)

DRO:	112302627(TRMT10C)

SHON:

118995843(TRMT10C)

AJM:	119039004(TRMT10C)

PDIC:

114490967(TRMT10C)

PHAS:

123827123(TRMT10C)

MMF:	118617389(TRMT10C)

PPAM:

129073603(TRMT10C)

HAI:	109385784(TRMT10C)

RFQ:	117032448(TRMT10C)

PALE:

102891696(TRMT10C)

PGIG:

120598097(TRMT10C)

PVP:	105311159(TRMT10C)

RAY:	107510810(TRMT10C)

MJV:	108407087(TRMT10C)

TOD:	119256843(TRMT10C)

SARA:

101555267(TRMT10C)

SFUM:

130018522(TRMT10C)

SETR:

126025935(TRMT10C)

LAV:	100675040(TRMT10C)

TMU:

101351331

ETF:	101645098(TRMT10C)

DNM:	101444741(TRMT10C)

MDO:	100016471(TRMT10C)

GAS:	123239527(TRMT10C)

SHR:	100917929(TRMT10C)

AFZ:

127554013

PCW:	110217475(TRMT10C)

TVP:	118840276(TRMT10C)

PBRV:

138144061(TRMT10C)

OAA:	100089544(TRMT10C)

TACU:

119945186(TRMT10C)

GGA:	418397(TRMT10C)

PCOC:

116242375(TRMT10C)

MGP:	100545358(TRMT10C)

CJO:	107320871(TRMT10C)

TPAI:

128072003(TRMT10C)

LMUT:

125702612(TRMT10C)

NMEL:

110400417(TRMT10C)

APLA:

101790961(TRMT10C)

ACYG:

106038703(TRMT10C)

CATA:

118245003(TRMT10C)

AFUL:

116492038(TRMT10C)

TGU:	100224864(TRMT10C)

LSR:	110476450(TRMT10C)

SCAN:

103820713(TRMT10C)

PMOA:

120513385(TRMT10C)

OTC:	121345474(TRMT10C)

PRUF:

121351629(TRMT10C)

ATRC:

139593005(TRMT10C)

GFR:	102042744(TRMT10C)

FAB:	101807617(TRMT10C)

OMA:	130260108(TRMT10C)

PHI:	102102501(TRMT10C)

PMAJ:

107204980(TRMT10C)

CCAE:

111940087(TRMT10C)

CCW:	104687018(TRMT10C)

CBRC:

103613866(TRMT10C)

ACOE:

138113490(TRMT10C)

ETL:	114062868(TRMT10C)

ZAB:	102070429(TRMT10C)

ZLE:	135453845(TRMT10C)

ACHL:

103800087(TRMT10C)

SVG:	106858842(TRMT10C)

MMEA:

130572443(TRMT10C)

HRT:	120749295(TRMT10C)

SATI:

136375279(TRMT10C)

CCIC:

134055763(TRMT10C)

FPG:	101917862(TRMT10C)

FCH:	102058041(TRMT10C)

CCRI:

104156964(TRMT10C)

NNT:	104401160(TRMT10C)

SHAB:

115603739(TRMT10C)

ACUN:

113482650(TRMT10C)

TALA:

104356673(TRMT10C)

ACHC:

115344149(TRMT10C)

HALD:

104312957(TRMT10C)

HLE:	104831641(TRMT10C)

AGEN:

126048972

HHAR:

128144972(TRMT10C)

GCL:

127015709

CSTI:

104557901(TRMT10C)

LDI:	104341856(TRMT10C)

MNB:	103773576(TRMT10C)

DPUB:

104297091(TRMT10C)

PPUS:

135175273(TRMT10C)

AVIT:

104269559(TRMT10C)

BRHI:

104488658(TRMT10C)

EGZ:	104129281(TRMT10C)

NNI:	104014110(TRMT10C)

PCRI:

104026618(TRMT10C)

PCAO:

104040711(TRMT10C)

PADL:

103915683(TRMT10C)

AFOR:

103907511(TRMT10C)

FGA:	104080870(TRMT10C)

GSTE:

104264005(TRMT10C)

CBOY:

140661626(TRMT10C)

CLV:	102085279(TRMT10C)

MUI:	104535503(TRMT10C)

PGUU:

104460440(TRMT10C)

PLET:

104616105(TRMT10C)

EHS:	104505181(TRMT10C)

CMAC:

104475248(TRMT10C)

CUCA:

104054267(TRMT10C)

TEO:	104371328(TRMT10C)

BREG:

104631426(TRMT10C)

OHA:	104333871(TRMT10C)

ACAR:

104520033(TRMT10C)

CPEA:

104384957(TRMT10C)

CVF:	104292282(TRMT10C)

RTD:	128901954(TRMT10C)

CRID:

134522428(TRMT10C)

AAM:	106490597(TRMT10C)

AROW:

112973098(TRMT10C)

NPD:	112944452(TRMT10C)

TGT:	104570531(TRMT10C)

DNE:	112990570(TRMT10C)

SCAM:

104144232(TRMT10C)

ASN:	102373421(TRMT10C)

AMJ:	102563994(TRMT10C)

CPOO:

109305637(TRMT10C)

GGN:	109302167(TRMT10C)

PSS:	102452002(TRMT10C)

CMY:	102939578(TRMT10C)

CCAY:

125620619(TRMT10C)

DCC:	119844400(TRMT10C)

CPIC:

101938780(TRMT10C)

TST:	117887555(TRMT10C)

CABI:

116838937(TRMT10C)

MRV:	120398721(TRMT10C)

ACS:	100559390(trmt10c)

ASAO:

132772022(TRMT10C)

PVT:	110074589(TRMT10C)

SUND:

121927101(TRMT10C)

PBI:	103052754(TRMT10C)

PMUR:

107285101(TRMT10C)

CTIG:

120298557(TRMT10C)

TSR:	106548436(TRMT10C)

PGUT:

117662885(TRMT10C)

PTEX:

113436395(TRMT10C)

NSS:	113409763(TRMT10C)

VKO:	123029074(TRMT10C)

PMUA:

114595880(TRMT10C)

PRAF:

128412820(TRMT10C)

ZVI:	118084953(TRMT10C)

HCG:	128349633(TRMT10C)

GJA:	107120446(TRMT10C)

STOW:

125431606(TRMT10C)

EMC:	129325450(TRMT10C)

XLA:	100381127(trmt10c.L) 108709677(trmt10c.S)

XTR:	100124885(trmt10c)

NPR:	108794260(TRMT10C)

RTEM:

120926545(TRMT10C)

BBUF:

120995630(TRMT10C)

BGAR:

122931283(TRMT10C)

PWL:	138250236(TRMT10C) 138262454

MUO:	115460505 115471404(TRMT10C)

GSH:

117359012

DRE:	492460(trmt10c)

SRX:	107748342 107751070

SANH:

SGH:

CAUA:

CGIB:

PTET:

122342655(trmt10c)

LROH:

127165298(trmt10c)

OMC:	131546459(trmt10c)

PPRM:

120459059(trmt10c)

RKG:	130077230(trmt10c)

MAMB:

125272993(trmt10c)

CIDE:

127519001

CERY:

137031868(trmt10c)

MASI:

127443446 127445345

TROS:

130552991(trmt10c)

TDW:	130440019(trmt10c)

MANU:

129445143(trmt10c)

PDAB:

135735616(trmt10c)

IPU:

108258702

IFU:	128601920(trmt10c)

PHYP:

113537345(trmt10c)

SMEO:

124378652(trmt10c)

TFD:	113648669(trmt10c)

TVC:	132839631(trmt10c)

CGAR:

128506266(trmt10c)

NGRA:

132866692(trmt10c)

TRN:	134329259(trmt10c)

AMEX:

103044792(trmt10c)

CMAO:

118797852(trmt10c)

EEE:	113576750(trmt10c)

CHAR:

105893245(trmt10c)

SPIL:

134071496(trmt10c)

TRU:	101078321(trmt10c)

TFS:	130516592(trmt10c)

TNG:	GSTEN00017922G001

LCO:	104922559(trmt10c)

NCC:	104958915(trmt10c)

TBEN:

117471546(trmt10c)

CGOB:

115023601

PGEO:

117466317(trmt10c)

GACU:

117548198(trmt10c)

EMAC:

134862919(trmt10c)

ELY:	117253968(trmt10c)

EFO:	125901569(trmt10c)

PLEP:

121947579(trmt10c)

SLUC:

116067693(trmt10c)

ECRA:

117948771(trmt10c)

ESP:	116700148(trmt10c)

PFLV:

114554543(trmt10c)

GAT:	120831334(trmt10c)

PPUG:

119228026(trmt10c)

AFB:	129103953(trmt10c)

CLUM:

117750845(trmt10c)

PSWI:

130192334(trmt10c)

CANA:

137787305(trmt10c)

CVE:	137887296(trmt10c)

MSAM:

119890376(trmt10c)

SCHU:

122878059(trmt10c)

CUD:	121511459(trmt10c)

SPUL:

138593544(trmt10c)

LMIX:

132972903(trmt10c)

ALAT:

119018578(trmt10c)

ASTR:

137589497(trmt10c)

MZE:	101479672(trmt10c)

ONL:	100712104(trmt10c)

OAU:	116312232(trmt10c)

OLA:	101173046(trmt10c)

OML:	112160935(trmt10c)

CSAI:

133420297(trmt10c)

XMA:	102218806(trmt10c)

XCO:	114142771(trmt10c)

XHE:	116718391(trmt10c)

PRET:

103461957(trmt10c)

PFOR:

103139375(trmt10c)

PLAI:

106955601(trmt10c)

PMEI:

106930431(trmt10c)

GAF:	122822757(trmt10c)

PPRL:

129369517(trmt10c)

CVG:	107103564(trmt10c)

CTUL:

119782736(trmt10c)

GMU:	124866767(trmt10c)

NFU:	107381141(trmt10c)

KMR:	108228301(trmt10c)

ALIM:

106534422(trmt10c)

NWH:	119429496 119429499

AOCE:

111573074(trmt10c)

EJA:	138213436(trmt10c)

BFRE:

138620499(trmt10c)

MCEP:

125005306(trmt10c)

CSEM:

103378890(trmt10c)

POV:	109624994(trmt10c)

SSEN:

122772181(trmt10c)

SSOE:

131459643(trmt10c)

HHIP:

117759599(trmt10c)

HSP:	118110018(trmt10c)

PPLT:

128439677(trmt10c)

SMAU:

118302822(trmt10c)

LCF:

108888022

SDU:	111238412(trmt10c)

SLAL:

111668311(trmt10c)

XGL:	120794498(trmt10c)

HCQ:	109519662(trmt10c)

SSCV:

125967178(trmt10c)

SBIA:

133498334(trmt10c)

PEE:	133399070(trmt10c)

PTAO:

133472464(trmt10c)

BPEC:

110173035(trmt10c)

ENY:	140381771(trmt10c)

MALB:

109963398(trmt10c)

BSPL:

114851757(trmt10c)

SJO:	128361543(trmt10c)

SSCO:

133984455(trmt10c)

GMH:	115558733(trmt10c)

SASA:

106575027 106575889

STRU:

115181168 115181198

OTW:	112240636(trmt10c) 112240637

OMY:	118947135(trmt10c)

OGO:	124018306 124018309 124023160

ONE:

115127615

OKI:	109885857 109885862

OKE:	118381870 127922131(trmt10c)

OMM:	135530364(trmt10c)

OCLA:

139372974 139412757

SALP:

112077570

SNH:	120038748 120040456 120043652

CCLU:

121537582

ELS:	105020105(trmt10c)

OEP:	134007148(trmt10c)

SFM:	108937897(trmt10c)

PKI:	111855560(trmt10c)

AANG:

118214436(trmt10c)

AROT:

135241371(trmt10c)

CCOG:

133116776(trmt10c)

LOC:	102687456(trmt10c)

PSPA:

121320844 121328097

ARUT:

117405510 117406922

PSEX:

120523485(trmt10c)

LCM:	102353829(TRMT10C)

CMK:	103180116(trmt10c)

RTP:

CPLA:

HOC:

LERI:

PMRN:

116952892(TRMT10C)

LRJ:

BFO:

BBEL:

CIN:

SCLV:

SPU:

LPIC:

AJJ:

APLC:

ARUN:

AAMU:

AFIL:

SKO:

PFLL:

DME:	Dmel_CG5190(rswl)

DER:

6546929

DSE:

6609801

DSI:	Dsimw501_GD11387(Dsim_GD11387)

DYA:	Dyak_GE11974

DAN:

DSR:

DPO:

DPE:

DMN:

DWI:

DGR:

DMO:	Dmoj_GI20132

DAZ:

108615691

DNV:

108654834

DHE:

111602367

DVI:	6624886(rswl)

CCAT:

BOD:

BDR:

RZE:

AOQ:

ALUD:

TDA:	119680415 119684175

MDE:

SCAC:

LCQ:

LSQ:

CVJ:	135961993(rswl)

GFS:

ECOE:

CLON:

HIS:

AGA:

ACOZ:

AARA:

AMER:

ASTE:

AMAP:

AFUN:

AMOU:

AMRS:

AALI:

ACOS:

AAG:

AALB:

ASUA:

CQU:	CpipJ_CPIJ011262

CBRI:

134830768 134832296

CNS:	116338379 116339672 116341031 116342048 116347335 116348525 116349079 116352085

BCOO:

119066452 119082619 119085051 119085839

LLL:

PPAP:

AME:

ACER:

ALAB:

ADR:

AFLR:

BIM:

BBIF:

BVK:

BVAN:

BHUN:

BTER:

BAFF:

BPYO:

BPAS:

FVI:

CCAL:

OBB:	114883064 114883073

OLG:

MGEN:

NMEA:

CGIG:

SOC:

MPHA:

AEC:

ACEP:

PBAR:

VEM:

COBS:

139111490(Rswl)

TLN:	139816042(Rswl)

HST:

105188576

DQU:

106751063

CFO:	105253938 105257690

FEX:	115235485 115238103

PMEC:

138939905 138944418

LHU:	105678623(rswl)

PGC:

OBO:

PCF:

PFUC:

VPS:

VCRB:

VVE:

NVI:

CSOL:

TPRE:

MDL:

CGLO:

FAS:

DAM:

AGIF:

VCAN:

CCIN:

NPT:	124223937(rswl)

NFB:

NLO:

NVG:

AROA:

TCA:

TMOL:

138125908(rswl)

DPA:

109543473

ESIM:

136408765(rswl)

EFOR:

136343559(rswl)

SOY:

AGRG:

ATD:

CSET:

AGB:

LDC:

DVV:

NVL:

APLN:

PPYR:

OTU:

BMOR:

BMAN:

MSEX:

DPL:	KGM_215608

BANY:

112043022

MJU:

123876141

NIQ:

126780972

VCD:	124532166 124532176

MCIX:

PMAC:

PPOT:

PXU:

BPHI:

137926918(rswl)

PRAP:

PBX:

PNAP:

ZCE:

CCRC:

LSIN:

AAGE:

HAW:

HZE:

TNL:

SLIU:

OFU:

ONU:

ATRA:

GMW:

PXY:

PGW:

LGLY:

CSTB:

CFEL:

CCRN:

API:	100164107 100575519

DNX:

AGS:

RMD:

ACOO:

DVT:

BTAB:

DCI:

CLEC:

HHAL:

106677839(rswl)

NLU:

111059165

HVI:

124366106

MQU:	129002957 129003002

PHU:	Phum_PHUM467390

FOC:	113208743 113211687

TPAL:

117646591 117646866 117651530 117651659

ZNE:

110836774

CSEC:

111864523

PAME:

138701193(rswl)

SGRE:

126353758

BROR:

134539370

IEL:

124159381

HAMR:

139692001(rswl)

FCD:

110853832

DPX:	DAPPUDRAFT_308823

DMK:

116927972

DPZ:

124315334

AFRA:

136035256

PVM:	113822128(rswl)

PJA:

PCHN:

PMOO:

HAME:

PCLA:

123775113(rswl)

CQD:	128684919(rswl)

ESN:

127007921

MNZ:

135196383

MRJ:	136840764(rswl)

PORN:

139762920(rswl)

HAZT:

108664793

LSM:	121127993(rswl)

PPOI:

119099033

DSV:	119431208 119465316

RSAN:

119377868 119406887

RMP:	119163380 119174165

VDE:	111245528 111252040 111252044 111252060

VJA:	111259073 111259074 111259075 111273988

TUT:	107363524 107364088 107367393 107367401 107368717

DPTE:

113790811 113791682 113793792 113796296

DFR:	124490537 124492886 124496686 124498879

CSCU:

111642034

CVS:	136976722(rswl)

PTEP:

ABRU:

UDV:

SDM:

LPOL:

PMEO:

CEL:	CELE_F46F11.10(trmt-10C.1)

CBR:

CBG_14899

CRQ:	GCK72_001300

NAI:	NECAME_05545

BMY:	BM_BM10056(Bm10056) BM_BM4159(Bm4159)

LOA:	LOAG_02839 LOAG_03512

TSP:

Tsp_05738

HRO:	HELRODRAFT_68039

PVUL:

PCAN:

LSAX:

BGT:

GAE:

HRF:

HRJ:

HASI:

HCRA:

CRG:	105320543 105320547

CANU:

128160662 128161482

MYI:	110442511 110449201

PMAX:

AIRR:

MMER:

RPHI:

MAEA:

OBI:

OSN:

LJP:

LAK:

SMM:	Smp_210580

SHX:	MS3_00003540(SUN1_1)

EGL:

EGR_04609

LLON:

135491672

» show all

Reference

PMID:18984158

Authors

Holzmann J, Frank P, Loffler E, Bennett KL, Gerner C, Rossmanith W

Title

RNase P without RNA: identification and functional reconstitution of the human mitochondrial tRNA processing enzyme.

Journal

Cell 135:462-74 (2008)
DOI:10.1016/j.cell.2008.09.013

Sequence

[hsa:54931]

LinkDB

DBGET integrated database retrieval system