KEGG   ORTHOLOGY: K21032
Entry
K21032                      KO                                     
Symbol
B4GAT1
Name
beta-1,4-glucuronyltransferase 1 [EC:2.4.1.-]
Pathway
map00515  Mannose type O-glycan biosynthesis
map01100  Metabolic pathways
Module
M00872  O-glycan biosynthesis, mannose type (core M3)
Disease
H00120  Muscular dystrophy-dystroglycanopathy type A
H02307  Muscular dystrophy-dystroglycanopathy
Brite
KEGG Orthology (KO) [BR:ko00001]
 09100 Metabolism
  09107 Glycan biosynthesis and metabolism
   00515 Mannose type O-glycan biosynthesis
    K21032  B4GAT1; beta-1,4-glucuronyltransferase 1
 09180 Brite Hierarchies
  09181 Protein families: metabolism
   01003 Glycosyltransferases
    K21032  B4GAT1; beta-1,4-glucuronyltransferase 1
Enzymes [BR:ko01000]
 2. Transferases
  2.4  Glycosyltransferases
   2.4.1  Hexosyltransferases
    2.4.1.-
     K21032  B4GAT1; beta-1,4-glucuronyltransferase 1
Glycosyltransferases [BR:ko01003]
 Glycan extension
  O-Glycan
   K21032  B4GAT1; beta-1,4-glucuronyltransferase 1
Other DBs
RN: R12296
CAZy: GT49
Genes
HSA: 11041(B4GAT1)
PTR: 451344(B4GAT1)
PPS: 100969129(B4GAT1)
GGO: 101144764(B4GAT1)
PON: 100173924(B4GAT1)
NLE: 100593252(B4GAT1)
MCC: 714270(B4GAT1)
MCF: 101925726(B4GAT1)
CSAB: 103223299(B4GAT1)
CATY: 105577393(B4GAT1)
PANU: 100999526(B4GAT1)
TGE: 112605754(B4GAT1)
RRO: 104664780(B4GAT1)
RBB: 108518698(B4GAT1)
TFN: 117080480(B4GAT1)
PTEH: 111522268(B4GAT1)
CJC: 100396330(B4GAT1)
SBQ: 101053044(B3GNT1)
CSYR: 103265002(B4GAT1)
MMUR: 105867454(B4GAT1)
LCAT: 123642890(B4GAT1)
OGA: 100951486(B4GAT1)
MMU: 108902(B4gat1)
MCAL: 110285649(B4gat1)
MPAH: 110316678(B4gat1)
RNO: 293667(B4gat1)
MCOC: 116103362(B4gat1)
MUN: 110556483(B4gat1)
CGE: 100762253(B4gat1)
MAUA: 101840053(B4gat1)
PLEU: 114709134(B4gat1)
MORG: 121454179(B4gat1)
AAMP: 119800856(B4gat1)
NGI: 103725028(B4gat1)
HGL: 101724680(B4gat1)
CPOC: 100714753(B4gat1)
CCAN: 109687072(B4gat1)
DORD: 105989120(B4gat1)
DSP: 122104924(B4gat1)
NCAR: 124958822
OCU: 100355603(B4GAT1)
OPI: 101523563(B4GAT1)
TUP: 102495897(B4GAT1)
CFA: 476013(B4GAT1)
CLUD: 112659288(B4GAT1)
VVP: 112924219(B4GAT1)
VLG: 121471470(B4GAT1)
AML: 100481988(B4GAT1)
UMR: 103679492(B4GAT1)
UAH: 113244067(B4GAT1)
UAR: 123778504(B4GAT1)
ELK: 111149691
LLV: 125078604
MPUF: 101674829(B4GAT1)
ORO: 101369271(B4GAT1)
EJU: 114220166(B4GAT1)
ZCA: 113914836(B4GAT1)
MLX: 118016091(B4GAT1)
FCA: 101084574(B4GAT1)
PYU: 121023890(B4GAT1)
PBG: 122484509(B4GAT1)
PTG: 102965050(B4GAT1)
PPAD: 109246797(B4GAT1)
AJU: 106971119(B4GAT1)
HHV: 120240097(B4GAT1)
BTA: 618055(B4GAT1)
BOM: 102278081(B4GAT1)
BIU: 109554460(B4GAT1)
BBUB: 102412589(B4GAT1)
CHX: 102175929(B4GAT1)
OAS: 101105702(B4GAT1)
ODA: 120874733(B4GAT1)
CCAD: 122430868(B4GAT1)
SSC: 100518412(B4GAT1)
CFR: 102509238(B4GAT1)
CBAI: 105070298(B4GAT1)
CDK: 105104463(B4GAT1)
VPC: 102535854(B4GAT1)
BACU: 103006629(B4GAT1)
LVE: 103077012(B4GAT1)
OOR: 101279614(B4GAT1)
DLE: 111183711(B4GAT1)
PCAD: 102986256(B4GAT1)
PSIU: 116757851(B4GAT1)
ECB: 100058396(B4GAT1)
EPZ: 103559584(B4GAT1)
EAI: 106833533(B4GAT1)
MYB: 102238971(B4GAT1)
MYD: 102754559(B4GAT1)
MMYO: 118665260(B4GAT1)
MLF: 102435475(B4GAT1)
MNA: 107533565(B4GAT1)
PKL: 118706889(B4GAT1)
HAI: 109384117(B4GAT1)
DRO: 112317315(B4GAT1)
SHON: 118991775(B4GAT1)
AJM: 119041933(B4GAT1)
PDIC: 114499799(B4GAT1)
PHAS: 123829363(B4GAT1)
MMF: 118627999(B4GAT1)
RFQ: 117031121(B4GAT1)
PALE: 102879580(B4GAT1)
PGIG: 120584806(B4GAT1)
PVP: 105297941(B4GAT1)
RAY: 107497539(B4GAT1)
MJV: 108394839(B4GAT1)
TOD: 119250515(B4GAT1)
SARA: 101548961(B4GAT1)
LAV: 100655204(B4GAT1)
TMU: 101354202
DNM: 101443586(B4GAT1)
MDO: 100029667(B4GAT1)
GAS: 123253897(B4GAT1)
SHR: 100928923(B4GAT1)
PCW: 110195462(B4GAT1)
OAA: 100086023(B4GAT1)
PCOC: 116240148(B4GAT1)
MGP: 104915973(B4GAT1)
CJO: 107307812(B4GAT1)
NMEL: 110391858(B4GAT1)
TGU: 100231337(B4GAT1)
LSR: 110480986(B4GAT1)
OTC: 121340084(B4GAT1)
PRUF: 121360889(B4GAT1)
PHI: 102111308(B4GAT1)
NNI: 104013856(B3GNT1)
AAM: 106484565(B4GAT1)
ASN: 112551418(B4GAT1)
AMJ: 102559888(B4GAT1)
PSS: 102453435(B4GAT1)
CMY: 102939993(B4GAT1)
CPIC: 101948990(B4GAT1)
TST: 117880554(B4GAT1)
CABI: 116838737(B4GAT1)
MRV: 120369244(B4GAT1)
ACS: 100563251(b4gat1)
PVT: 110091755(B4GAT1)
SUND: 121915326(B4GAT1)
PBI: 103060672(B4GAT1)
PMUR: 107302635(B4GAT1)
TSR: 106546981(B4GAT1)
PGUT: 117669731(B4GAT1)
VKO: 123032462(B4GAT1)
PMUA: 114586272(B4GAT1)
GJA: 107111037(B4GAT1)
STOW: 125446094(B4GAT1)
XLA: 108713949(b4gat1.L)
XTR: 100170600(b4gat1)
NPR: 108784141(B4GAT1)
RTEM: 120917524(B4GAT1)
BBUF: 120980813(B4GAT1)
BGAR: 122920384(B4GAT1)
DRE: 101669768(b4gat1)
SGH: 107553543(b4gat1) 107553758
PPRM: 120469823(b4gat1)
MAMB: 125265372(b4gat1)
IPU: 108267907(b4gat1)
PHYP: 113539856(b4gat1)
SMEO: 124388051(b4gat1)
TFD: 113663032(b4gat1)
AMEX: 103038107(b4gat1)
EEE: 113585148(b4gat1)
TRU: 101062587(b4gat1)
LCO: 104932297(b4gat1)
NCC: 104954535(b4gat1)
CGOB: 115023423(b4gat1)
ELY: 117272744(b4gat1)
EFO: 125884502(b4gat1)
PLEP: 121962160(b4gat1)
SLUC: 116053375(b4gat1)
ECRA: 117934577(b4gat1)
ESP: 116707261(b4gat1)
PFLV: 114545532(b4gat1)
GAT: 120821255(b4gat1)
PPUG: 119223507(b4gat1)
MSAM: 119913059(b4gat1)
CUD: 121504260(b4gat1)
ALAT: 119027601(b4gat1)
MZE: 101481909(b4gat1)
ONL: 100711477(b4gat1)
OAU: 116314332(b4gat1)
OLA: 101175112(b4gat1)
OML: 112156425(b4gat1)
XMA: 102232247(b4gat1)
XCO: 114157967(b4gat1)
XHE: 116732286(b4gat1)
PRET: 103475932(b4gat1)
PLAI: 106946466(b4gat1)
PMEI: 106917608(b4gat1)
GAF: 122820149(b4gat1)
CVG: 107085247(b4gat1)
CTUL: 119773428(b4gat1)
GMU: 124880714(b4gat1)
NFU: 107377042(b4gat1)
KMR: 108249080(b4gat1)
ALIM: 106530434(b4gat1)
NWH: 119415860(b4gat1)
AOCE: 111576837(b4gat1)
MCEP: 125010783(b4gat1)
CSEM: 103386489(b4gat1)
POV: 109623831(b4gat1)
SSEN: 122766475(b4gat1)
HHIP: 117779114(b4gat1)
HSP: 118102784(b4gat1)
LCF: 108883766(b4gat1)
SDU: 111235688(b4gat1)
SLAL: 111647128(b4gat1)
XGL: 120797657(b4gat1)
HCQ: 109508371(b4gat1)
BPEC: 110170816(b4gat1)
MALB: 109971452(b4gat1)
BSPL: 114845318(b4gat1)
SASA: 106577863(b4gat1)
OTW: 112214956 112259864(b4gat1)
OMY: 110531594(b4gat1)
OGO: 124008174(b4gat1)
ONE: 115137946
SALP: 111960404(b4gat1)
SNH: 120030407 120049467(b4gat1)
CCLU: 121572715 123483323(b4gat1)
ELS: 105026761(b4gat1)
SFM: 108926568(b4gat1)
PKI: 111858497(b4gat1)
AANG: 118224170(b4gat1)
LOC: 102694260(b4gat1)
PSPA: 121310042(b4gat1)
LCM: 102352330(B4GAT1)
RTP: 109926147(b4gat1)
BFO: 118410851
BBEL: 109471157
SPU: 577047
APLC: 110975153
DME: Dmel_CG3253(CG3253)
DER: 6547964
DSE: 6613024
DSI: Dsimw501_GD15463(Dsim_GD15463)
DAN: 6494237
DSR: 110191694
DGR: 6559354
CCAT: 101448708
BOD: 106617495
MDE: 101899356
SCAC: 106083445
LSQ: 119600647
HIS: 119658741
ACOZ: 120955518
AARA: 120903330
ASTE: 118506165
AAG: 5568204
CNS: 116350531
BCOO: 119070640
TPRE: 106656833
FAS: 105271304
DAM: 107041205
AGIF: 122855633
LHT: 122503481
CCIN: 107272772
SOY: 115886809
CSET: 123316142
AGB: 108917876
LDC: 111504816
APLN: 108737592
PPYR: 116165924
MSEX: 115441994
BANY: 112050225
PPOT: 106111295
PRAP: 111001450
HZE: 124632801
SLIU: 111358692
OFU: 114354769
PXY: 105388197
API: 100159373
RMD: 113552909
DCI: 103517302
DMK: 116921760
LSM: 121113686
DFR: 124492778
CEL: CELE_C18G1.3(bgnt-1.4) CELE_K08H2.9(bgnt-1.5)
CBR: CBG_05262
PCAN: 112569737
BGT: 106062232
GAE: 121372249
HRF: 124124478
HRJ: 124272907
CRG: 105329187
MYI: 110466043
PMAX: 117324508
MMER: 123544167
OBI: 106872017
OSN: 115215863
LAK: 106155404
EPA: 110234538
ATEN: 116306402
ADF: 107340247
AMIL: 114958382
PDAM: 113672752
SPIS: 111323414
DGT: 114523001
XEN: 124452955
HMG: 100203530
 » show all
Reference
  Authors
Praissman JL, Live DH, Wang S, Ramiah A, Chinoy ZS, Boons GJ, Moremen KW, Wells L
  Title
B4GAT1 is the priming enzyme for the LARGE-dependent functional glycosylation of alpha-dystroglycan.
  Journal
Elife 3:e03943 (2014)
DOI:10.7554/eLife.03943
  Sequence
[hsa:11041]
LinkDB

KEGG   REACTION: R12296
Entry
R12296                      Reaction                               
Definition
G13095 + UDP-D-glucuronate <=> G13096 + UDP
Equation
Enzyme
2.4.1.-
Pathway
rn00515  Mannose type O-glycan biosynthesis
rn01100  Metabolic pathways
Module
M00872  O-glycan biosynthesis, mannose type (core M3)
Orthology
K21032  beta-1,4-glucuronyltransferase 1 [EC:2.4.1.-]
Other DBs
RHEA: 46863
LinkDB

DBGET integrated database retrieval system