ORTHOLOGY: K24624
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Entry
K24624 KO
Symbol
MICOS13
Name
MICOS complex subunit MIC13
Disease
H00891
Combined oxidative phosphorylation deficiency
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis
K24624 MICOS13; MICOS complex subunit MIC13
Mitochondrial biogenesis [BR:
ko03029
]
Mitochondrial protein import machinery
Inner mambrane
MICOS complex
K24624 MICOS13; MICOS complex subunit MIC13
BRITE hierarchy
Genes
HSA:
125988
(MICOS13)
PTR:
455620
(MICOS13)
PPS:
100978699
(MICOS13)
GGO:
101150711
(MICOS13)
PON:
100460472
(MICOS13)
PPYG:
129019828
(MICOS13)
NLE:
100584027
(MICOS13)
HMH:
116483304
(MICOS13)
SSYN:
129466415
(MICOS13)
MCF:
102138958
(MICOS13)
MTHB:
126942850
MNI:
105484920
(CUNH19orf70)
CSAB:
103233742
(C6H19orf70)
CATY:
105591836
PANU:
101021729
(MICOS13)
TGE:
112611830
(C19H19orf70)
MLEU:
105530052
RRO:
104665395
(MICOS13)
RBB:
108512099
(CUNH19orf70)
TFN:
117076248
(MICOS13)
PTEH:
111521950
(MICOS13)
CANG:
105512861
CJC:
100407773
(MICOS13)
SBQ:
101044332
CIMI:
108304256
(MICOS13)
ANAN:
105705947
(MICOS13)
CSYR:
103272815
(CUNH19orf70)
MMUR:
105869646
(C24H19orf70)
LCAT:
123636557
(MICOS13)
PCOQ:
105811922
OGA:
100946225
(CUNH19orf70)
MMU:
224904
(Micos13)
MCAL:
110283662
(Micos13)
MPAH:
110335913
(C18H19orf70)
RNO:
120102271
301124
(Micos13)
MCOC:
116074350
(Micos13)
ANU:
117704991
(Micos13)
ASYL:
127693005
(Micos13)
MUN:
110546271
(Micos13)
CGE:
100759422
(Micos13)
MAUA:
101830499
(Micos13)
PROB:
127216774
(Micos13)
PLEU:
114685074
(Micos13)
MORG:
121455332
121459669
(Micos13)
MFOT:
126490386
126511196
AAMP:
119808599
(Micos13)
NGI:
103737209
(CUNH19orf70)
HGL:
101711280
CPOC:
100718432
(CUNH19orf70)
CCAN:
109688201
(CUNH19orf70)
DORD:
105990375
DSP:
122122826
(Micos13)
PLOP:
125348580
(Micos13)
NCAR:
124968403
MMMA:
107157304
(Micos13)
ITI:
101978219
(Micos13)
OPI:
101528616
101528742
(MICOS13)
TUP:
102503397
GVR:
103590753
CFA:
476739
(MICOS13)
CLUD:
112666340
(MICOS13)
VVP:
112935556
(CUNH19orf70)
VLG:
121495785
(MICOS13)
NPO:
129521997
(MICOS13)
AML:
100466691
(MICOS13)
UMR:
103681697
(MICOS13)
UAH:
113242857
(MICOS13)
UAR:
123779008
(MICOS13)
ELK:
111161735
LLV:
125088470
MPUF:
101677176
MNP:
132010836
(MICOS13)
MLK:
131823355
(MICOS13)
NVS:
122909840
(MICOS13)
ORO:
101368303
EJU:
114226335
(MICOS13)
ZCA:
113918786
(MICOS13)
MLX:
118005227
(MICOS13)
NSU:
110593729
(MICOS13)
LWW:
102730640
102734239
(MICOS13)
115940376
FCA:
101092498
(MICOS13)
PYU:
121021340
(MICOS13)
PCOO:
112852814
(CUNH19orf70)
PVIV:
125152946
(MICOS13)
LRUF:
124524746
LGF:
123605170
(MICOS13)
AJU:
106975485
(MICOS13)
PTG:
102954695
PPAD:
109255930
(CUNH19orf70)
PUC:
125928895
PLEZ:
122213812
(MICOS13)
HHV:
120242095
(MICOS13)
120242847
BTA:
540962
(MICOS13)
BOM:
102269931
(MICOS13)
BIU:
109561723
(C7H19orf70)
BBUB:
102411438
(MICOS13)
BBIS:
104979711
CHX:
102183141
(C7H19orf70)
OAS:
101109702
(MICOS13)
BTAX:
128051438
(MICOS13)
CSUM:
138085595
(MICOS13)
ODA:
120864859
(MICOS13)
CCAD:
122440274
(MICOS13)
MREE:
136155826
(MICOS13)
OVR:
110131228
(MICOS13)
MBEZ:
129558822
(MICOS13)
SSC:
100037978
(C2H19orf70)
CFR:
102506272
(MICOS13)
CBAI:
105078238
CDK:
105091758
(MICOS13)
VPC:
102529756
(MICOS13)
BACU:
103009364
BMUS:
118891961
(MICOS13)
LVE:
103075746
OOR:
101274049
(MICOS13)
LALB:
132517720
(MICOS13)
DLE:
111165963
(MICOS13)
PCAD:
102977905
(MICOS13)
PSIU:
116750484
(MICOS13)
NASI:
112400145
(CUNH19orf70)
ECB:
100064983
(C7H19orf70)
EPZ:
103545855
(MICOS13)
EAI:
106832396
(MICOS13)
MYB:
102246932
MYD:
102775140
MMYO:
118658805
(MICOS13)
MLF:
102435993
(CUNH19orf70)
MDT:
132235147
(MICOS13)
MYUM:
139010873
(MICOS13)
PKL:
118731178
(MICOS13)
EFUS:
103294205
(MICOS13)
MNA:
107525667
DRO:
112312482
(CUNH19orf70)
SHON:
118984542
(MICOS13)
AJM:
119063756
(MICOS13)
PDIC:
114503945
(MICOS13)
PHAS:
123813656
(MICOS13)
MMF:
118615613
(MICOS13)
PPAM:
129061577
(MICOS13)
HAI:
109388582
(CUNH19orf70)
RFQ:
117037630
(MICOS13)
PALE:
102898301
(CUNH19orf70)
PGIG:
120615420
(MICOS13)
PVP:
105301064
(CUNH19orf70)
RAY:
107510936
(MICOS13)
MJV:
108404624
(MICOS13)
TOD:
119240610
(MICOS13)
SARA:
101555493
SFUM:
130016557
(MICOS13)
SETR:
126029753
(MICOS13)
LAV:
100664605
(CUNH19orf70)
TMU:
101352119
ETF:
101646204
(MICOS13)
DNM:
101410971
101439322
(CUNH19orf70)
MDO:
100024969
(C3H19orf70)
GAS:
123242762
(MICOS13)
SHR:
100922702
(MICOS13)
AFZ:
127544904
PCW:
110197393
(CUNH19orf70)
TVP:
118834174
(MICOS13)
PBRV:
138160202
(MICOS13)
OAA:
114806348
(MICOS13)
TACU:
119919493
(MICOS13)
GGA:
100858091
(C19orf70)
PCOC:
116236149
(MICOS13)
MGP:
100540720
(MICOS13)
CJO:
107325412
(MICOS13)
TPAI:
128090424
(MICOS13)
LMUT:
125685053
(MICOS13)
NMEL:
110388944
(C27H19orf70)
APLA:
101804515
(MICOS13)
ACYG:
106049550
(MICOS13)
CATA:
118260025
(MICOS13)
AFUL:
116499040
(MICOS13)
TGU:
100224292
(MICOS13)
LSR:
110475768
(MICOS13)
SCAN:
103821932
(MICOS13)
PMOA:
120498087
(MICOS13)
OTC:
121342453
(MICOS13)
PRUF:
121361284
(MICOS13)
ATRC:
139602122
(MICOS13)
GFR:
102033634
FAB:
101814253
(C28H19orf70)
OMA:
130264444
(MICOS13)
PHI:
102104180
PMAJ:
107215367
(MICOS13)
CCAE:
111940333
(C28H19orf70)
CCW:
104696994
(MICOS13)
CBRC:
103622158
(CUNH19orf70)
ACOE:
138099839
(MICOS13)
ETL:
114066354
(MICOS13)
ZLE:
135458954
(MICOS13)
ACHL:
103806742
SVG:
106857112
MMEA:
130580222
(MICOS13)
HRT:
120763285
(MICOS13)
SATI:
136371899
(MICOS13)
CCIC:
134054403
(MICOS13)
FPG:
101918228
FCH:
102054240
(MICOS13)
CCRI:
104156017
NNT:
104404457
SHAB:
115618300
(MICOS13)
ACUN:
113489282
(C28H19orf70)
TALA:
104356290
(MICOS13)
ACHC:
115348810
(MICOS13)
HALD:
104312906
HLE:
104829058
AGEN:
126041661
HHAR:
128148007
(MICOS13)
GCL:
127025657
CSTI:
104550818
LDI:
104341849
MNB:
103778591
DPUB:
104300813
PPUS:
135192250
(MICOS13)
AVIT:
104274333
BRHI:
104496360
EGZ:
104124429
(MICOS13)
NNI:
104016323
PCRI:
104024809
PCAO:
104040003
PADL:
103923459
AFOR:
103899350
(CUNH19orf70)
FGA:
104070952
GSTE:
104259664
CBOY:
140643615
(MICOS13)
CLV:
102096333
(CUNH19orf70)
MUI:
104535285
PGUU:
104459062
PLET:
104614812
EHS:
104506052
CMAC:
104475707
CUCA:
104065104
(MICOS13)
TEO:
104377325
OHA:
104335038
ACAR:
104519600
(MICOS13)
CPEA:
104397512
CVF:
104294395
RTD:
128900726
(MICOS13)
CRID:
134526182
(MICOS13)
AAM:
106486394
AROW:
112973864
(CUNH19orf70)
NPD:
112946807
(CUNH19orf70)
TGT:
104580080
DNE:
112988080
(CUNH19orf70)
SCAM:
104151019
ASN:
102371532
(CUNH19orf70)
AMJ:
102560547
(CUNH19orf70)
CPOO:
109320462
(CUNH19orf70)
GGN:
109294894
(CUNH19orf70)
PSS:
102461583
(CUNH19orf70)
CMY:
102936248
(MICOS13)
CCAY:
125627002
(MICOS13)
CPIC:
101950051
(MICOS13)
TST:
117868880
(MICOS13)
CABI:
116823636
(MICOS13)
MRV:
120391581
(MICOS13)
ACS:
100565143
ASAO:
132781055
(MICOS13)
PVT:
110079277
(CUNH19orf70)
SUND:
121928987
121936829
(MICOS13)
PBI:
103052867
(CUNH19orf70)
PMUR:
107298643
(MICOS13)
CTIG:
120297077
(MICOS13)
PGUT:
132712210
(MICOS13)
APRI:
131188355
(MICOS13)
PTEX:
113453444
113453445
NSS:
113427750
(CUNH19orf70)
VKO:
123016879
(MICOS13)
PMUA:
114588581
(MICOS13)
PRAF:
128405618
(MICOS13)
ZVI:
118087596
(MICOS13)
HCG:
128343478
(MICOS13)
GJA:
107106733
107110505
EMC:
129331004
(MICOS13)
XLA:
108700956
108713429
XTR:
100489521
(micos13)
NPR:
108791248
(CUNH19orf70)
RTEM:
120909897
(MICOS13)
BBUF:
120989409
(MICOS13)
BGAR:
122931085
(MICOS13)
PWL:
138267898
(MICOS13)
MUO:
115480320
(MICOS13)
GSH:
117365382
DRE:
558738
(micos13)
SRX:
107719663
107726536
SANH:
107655188
107675912
SGH:
107586453
107596903
CCAR:
109046640
109094154
122134014
122141596
CAUA:
113040079
113064908
113072749
CGIB:
127942681
127987862
PTET:
122327851
(micos13)
LROH:
127153140
(micos13)
OMC:
131529640
(micos13)
PPRM:
120495288
(micos13)
RKG:
130089211
(micos13)
MAMB:
125263770
(micos13)
CIDE:
127521380
CERY:
137029146
(micos13)
MASI:
127437978
127438654
TROS:
130548870
(micos13)
TDW:
130429824
(micos13)
MANU:
129452769
(micos13)
PDAB:
135728357
(micos13)
IPU:
108271266
(micos13)
IFU:
128613718
(micos13)
PHYP:
113531748
(cunh19orf70)
SMEO:
124391293
(micos13)
TFD:
113657948
(micos13)
TVC:
132842023
(micos13)
CGAR:
128542656
(micos13)
NGRA:
132899493
(micos13)
TRN:
134331218
(micos13)
AMEX:
103030686
(micos13)
CMAO:
118819469
(micos13)
EEE:
113576182
(cunh19orf70)
CHAR:
105895245
(micos13)
SPIL:
134101927
(micos13)
TRU:
101071979
(micos13)
TFS:
130528651
(micos13)
TNG:
GSTEN00020117G001
LCO:
104918748
(micos13)
NCC:
104964520
TBEN:
117495612
(micos13)
CGOB:
115006954
(micos13)
PGEO:
117445589
(micos13)
GACU:
117546128
(micos13)
EMAC:
134870094
(micos13)
ELY:
117254013
(micos13)
EFO:
125896414
(micos13)
PLEP:
121939147
(micos13)
SLUC:
116063254
(micos13)
ECRA:
117950238
(micos13)
ESP:
116695455
(micos13)
PFLV:
114562127
(micos13)
GAT:
120823467
(micos13)
PPUG:
119217159
(micos13)
AFB:
129095099
(micos13)
CLUM:
117729504
(micos13)
PSWI:
130194173
(micos13)
CANA:
137794449
(micos13)
CVE:
137884221
(micos13)
MSAM:
119900901
(micos13)
SCHU:
122877496
(micos13)
CUD:
121512259
(micos13)
SPUL:
138607437
(micos13)
LMIX:
132962545
(micos13)
ALAT:
119028539
(micos13)
ASTR:
137598969
(micos13)
MZE:
101487367
ONL:
100710867
(lg23h19orf70)
OAU:
116310022
(micos13)
OLA:
101170416
(c4h19orf70)
OML:
112140961
(micos13)
CSAI:
133458138
(micos13)
XMA:
102223262
(c9h19orf70)
XCO:
114150805
(micos13)
XHE:
116725473
(micos13)
PRET:
103463672
(clg4h19orf70)
PFOR:
103149840
PLAI:
106940985
PMEI:
106924196
GAF:
122839013
(micos13)
PPRL:
129374786
(micos13)
CVG:
107099383
CTUL:
119780667
(micos13)
GMU:
124873991
(micos13)
NFU:
107393311
(csgr17h19orf70)
KMR:
108230814
(micos13)
ALIM:
106536194
NWH:
119430716
(micos13)
AOCE:
111578535
(micos13)
EJA:
138198656
(micos13)
BFRE:
138618863
(micos13)
MCEP:
125009935
125009936
CSEM:
103399921
(c2h19orf70)
POV:
109625895
(cunh19orf70)
SSEN:
122781111
(micos13)
SSOE:
131466100
(micos13)
HHIP:
117760052
(micos13)
HSP:
124854690
(micos13)
PPLT:
128447563
(micos13)
SMAU:
118318336
(micos13)
LCF:
108877314
(micos13)
SDU:
111232071
(cunh19orf70)
SLAL:
111657474
(cunh19orf70)
XGL:
120790446
(micos13)
HCQ:
109532031
(cunh19orf70)
SSCV:
125965819
(micos13)
SBIA:
133502998
(micos13)
PEE:
133406277
(micos13)
PTAO:
133480310
(micos13)
BPEC:
110174089
(cunh19orf70)
ENY:
140353731
(micos13)
MALB:
109965747
(cunh19orf70)
BSPL:
114853500
(micos13)
SJO:
128361522
(micos13)
SSCO:
133984701
(micos13)
GMH:
115555693
(micos13)
SASA:
106584447
(QIL1)
106613757
(QIL1)
STRU:
115158235
115192642
OTW:
112250862
112266022
OMY:
110521421
110524277
OGO:
123996911
124037038
ONE:
115108296
115145447
OKI:
109897841
109901549
OKE:
118359246
118389505
OMM:
135511718
135556537
OCLA:
139407594
139410150
SALP:
111972159
111976076
SNH:
120051790
120054457
CCLU:
121533544
121539916
ELS:
105011539
(micos13)
OEP:
134016217
(micos13)
SFM:
108919774
(micos13)
PKI:
111860535
(cunh19orf70)
AANG:
118226611
(micos13)
AROT:
135252319
(micos13)
CCOG:
133127535
(micos13)
LOC:
102685276
(clg19h19orf70)
PSPA:
121300664
121309575
ARUT:
117401437
117428877
PSEX:
120537692
(micos13)
LCM:
102350217
CMK:
103181943
(micos13)
RTP:
109918268
(micos13)
CPLA:
122565411
(micos13)
HOC:
132829100
(micos13)
LERI:
129711366
(micos13)
PMRN:
116953508
(MICOS13)
LRJ:
133355155
(MICOS13)
BFO:
118411914
BBEL:
109468648
SCLV:
120328565
SPU:
100888331
115919244
AJJ:
139966710
APLC:
110984551
ARUN:
117288575
AAMU:
139937731
AFIL:
140141884
SKO:
102810349
PFLL:
139125078
DME:
Dmel_CG7603
(QIL1)
DER:
6546327
DSE:
6606088
DSI:
Dsimw501_GD14707
(Dsim_GD14707)
DYA:
Dyak_GE19912
DAN:
6506837
DSR:
110190177
DPO:
4812916
DPE:
6601404
DMN:
108153554
DWI:
6646014
DGR:
6557247
DMO:
Dmoj_GI12127
DAZ:
108612930
DNV:
108652198
DHE:
111604775
DVI:
6623936
(QIL1)
CCAT:
101455334
BOD:
106617350
BDR:
105230107
RZE:
108377411
AOQ:
129241003
ALUD:
128859665
TDA:
119668901
MDE:
101887702
SCAC:
106092691
LCQ:
111687208
LSQ:
119600893
CVJ:
135961265
(QIL1)
GFS:
119632581
ECOE:
129945836
CLON:
129610352
HIS:
119650277
AGA:
1274785
ACOZ:
120961509
AARA:
120908686
AMER:
121592130
ASTE:
118509781
AMAP:
126563307
AFUN:
125768949
AMOU:
128304464
AMRS:
128714591
AALI:
118466294
ACOS:
131267460
AAG:
5576079
AALB:
109406008
115259321
ASUA:
134210593
CQU:
CpipJ_CPIJ015390
CpipJ_CPIJ016053
CPII:
120413184
CBRI:
134829780
BCOO:
119073419
LLL:
129792016
PPAP:
129801614
AME:
725253
ACER:
107995679
ALAB:
122719726
ADR:
102678629
AFLR:
100864313
BIM:
100740787
BBIF:
117204045
BVK:
117230893
BVAN:
117155925
BHUN:
126867700
BTER:
100642752
BAFF:
126914098
BPAS:
132910030
FVI:
122538798
CCAL:
108626625
OBB:
114874317
OLG:
117607738
MGEN:
117219892
NMEA:
116427856
CGIG:
122395201
SOC:
105198208
MPHA:
105834224
AEC:
105149830
ACEP:
105621512
PBAR:
105425327
VEM:
105568442
COBS:
139111308
TLN:
139816215
HST:
105185840
DQU:
106746264
CFO:
105250064
FEX:
115235190
PMEC:
138941624
LHU:
105668468
PGC:
109857800
OBO:
105287570
PCF:
106793871
PFUC:
122520123
VPS:
122631986
VCRB:
124426833
VVE:
124952278
NVI:
100115502
CSOL:
105363474
TPRE:
106656147
LHT:
122505452
LBD:
127277663
MDL:
103572352
CGLO:
123258944
FAS:
105268275
DAM:
107045809
AGIF:
122854351
VCAN:
122409417
CCIN:
107265041
DSM:
124410249
NPT:
124224708
NFB:
124188200
NLO:
107227643
NVG:
124301842
AROA:
105693197
TCA:
103314453
DPA:
109537764
EFOR:
136345430
SOY:
115882666
ATD:
109598280
CSET:
123318439
HAXR:
123672844
AGB:
108917216
DVV:
114326903
NVL:
108566246
PPYR:
116164350
OTU:
111428175
BMOR:
101746538
BMAN:
114242102
MSEX:
115448219
DPL:
KGM_208946
BANY:
112050824
MJU:
123867856
NIQ:
126769302
VCD:
124532278
MCIX:
123655277
PMAC:
106720717
PPOT:
106103710
PXU:
106115902
ZCE:
119840405
CCRC:
123693010
AAGE:
121727474
HAW:
110384025
HZE:
124631642
TNL:
113500763
SLIU:
111355401
OFU:
114350267
ONU:
135073769
ATRA:
106142842
GMW:
113515572
PXY:
105383068
PGW:
126369449
LGLY:
125224797
CSTB:
134743525
CCRN:
123290437
API:
100164794
DNX:
107167431
AGS:
114128415
RMD:
113552330
ACOO:
126832963
DVT:
126904281
DCI:
108253331
CLEC:
106664797
HHAL:
106688295
(QIL1)
NLU:
111046841
MQU:
128998495
PHU:
Phum_PHUM050950
FOC:
113208901
TPAL:
117649498
ZNE:
110840081
CSEC:
111862526
PAME:
138694777
BROR:
134533824
HAMR:
139690672
(QIL1)
DPX:
DAPPUDRAFT_308664
DPZ:
124342163
AFRA:
136031317
PVM:
113827213
(QIL1)
PJA:
122242517
PCHN:
125038768
PMOO:
119598174
HAME:
121853717
PCLA:
123774720
(QIL1)
CQD:
128696076
(QIL1)
PTRU:
123510511
ESN:
127000266
MNZ:
135203084
MRJ:
136834916
(QIL1)
PORN:
139752033
(QIL1)
HAZT:
108680479
EAF:
111716174
LSM:
121117595
121117597
PPOI:
119095509
DSV:
119455755
RSAN:
119393764
RMP:
119171982
VDE:
111251673
VJA:
111259588
TUT:
107362702
CSCU:
111622598
CVS:
136989007
(QIL1)
PTEP:
107447664
ABRU:
129972254
UDV:
129221413
SDM:
118192658
LPOL:
106460370
PMEO:
129602836
CEL:
CELE_W04C9.2
(W04C9.2)
CBR:
CBG_22669
CRQ:
GCK72_001347
NAI:
NECAME_11910
LOA:
LOAG_01606
TSP:
Tsp_05478
HRO:
HELRODRAFT_180872
PCAN:
112560306
BGT:
106062121
GAE:
121373379
HRF:
124116675
HRJ:
124279071
HASI:
137259997
137260326
HCRA:
139461031
CRG:
117680332
CANU:
128172926
OED:
125660691
MYI:
110463421
AIRR:
138306772
MMER:
123542463
DPOL:
127867691
MAEA:
128224464
OBI:
106874425
OSN:
115216594
LJP:
135462928
LAK:
106173248
SMM:
Smp_143000
EGL:
EGR_09933
LLON:
135498902
NVE:
116613944
ATEN:
116302887
ADF:
107347277
AMIL:
114975992
MCAZ:
138041955
MFOO:
138008290
PDAM:
113685061
SPIS:
111334341
TAD:
TRIADDRAFT_55163
» show all
Taxonomy
UniProt
Reference
PMID:
25997101
Authors
Guarani V, McNeill EM, Paulo JA, Huttlin EL, Frohlich F, Gygi SP, Van Vactor D, Harper JW
Title
QIL1 is a novel mitochondrial protein required for MICOS complex stability and cristae morphology.
Journal
Elife 4:e06265 (2015)
DOI:
10.7554/eLife.06265
Sequence
[hsa:
125988
]
LinkDB
All DBs
DBGET
integrated database retrieval system