ORTHOLOGY: K26747
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Entry
K26747 KO
Symbol
LYSET, TMEM251
Name
lysosomal enzyme trafficking factor
Disease
H02729
Ain-Naz type of dysostosis multiplex
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09180 Brite Hierarchies
09182 Protein families: genetic information processing
04131 Membrane trafficking
K26747 LYSET, TMEM251; lysosomal enzyme trafficking factor
Membrane trafficking [BR:
ko04131
]
Endosome - Golgi transport
Others
Others
K26747 LYSET, TMEM251; lysosomal enzyme trafficking factor
BRITE hierarchy
Other DBs
TC:
8.A.208.1
Genes
HSA:
26175
(LYSET)
PTR:
100615688
(LYSET)
PPS:
100983303
(LYSET)
GGO:
101145528
(LYSET)
PON:
100448831
(LYSET)
PPYG:
129012104
(LYSET)
NLE:
100579217
(TMEM251)
HMH:
116456311
(LYSET)
SSYN:
129487506
(LYSET)
MCC:
708131
(TMEM251)
MCF:
102133560
(LYSET)
MTHB:
126959695
MNI:
105467525
(TMEM251)
CSAB:
103229582
(TMEM251)
CATY:
105596599
(TMEM251)
PANU:
101025394
(TMEM251)
TGE:
112628467
(TMEM251)
MLEU:
105547941
(TMEM251)
RRO:
104679050
(TMEM251)
RBB:
108519123
(TMEM251)
TFN:
117071507
(TMEM251)
PTEH:
111538243
(TMEM251)
CANG:
105517024
(TMEM251)
CJC:
100398390
(LYSET)
SBQ:
101039121
(TMEM251)
CIMI:
108316851
(TMEM251)
ANAN:
105717786
(LYSET)
135272308
MMUR:
105856745
(TMEM251)
LCAT:
123645151
(TMEM251)
MMU:
320351
(Lyset)
MCAL:
110306503
(Tmem251)
MPAH:
110324735
(Tmem251)
RNO:
100360358
(Lyset)
MCOC:
116079681
(Tmem251)
ANU:
117697564
(Tmem251)
ASYL:
127687009
(Lyset)
MUN:
110562021
(Lyset)
CGE:
100768158
(Tmem251)
107978379
MAUA:
101822557
(Tmem251)
PROB:
127231090
(Lyset)
PLEU:
114705135
114706038
(Tmem251)
MORG:
121434374
(Tmem251)
MFOT:
126490010
126507233
AAMP:
119819271
(Tmem251)
NGI:
103724589
(Tmem251)
HGL:
101701177
(Tmem251)
CPOC:
100717328
(Tmem251)
CCAN:
109693570
(Tmem251)
DORD:
105984078
(Tmem251)
DSP:
122118689
(Tmem251)
PLOP:
125363123
(Tmem251)
125364858
NCAR:
124976022
MMMA:
107150057
(Tmem251)
ITI:
101967718
(Tmem251)
OCU:
100348345
OPI:
101533165
(TMEM251)
GVR:
103610827
(TMEM251)
CFA:
100685617
(TMEM251)
CLUD:
112657169
(TMEM251)
VVP:
112907339
(TMEM251)
VLG:
121493558
(TMEM251)
NPO:
129496294
(LYSET)
AML:
100484537
(TMEM251)
UMR:
103670048
(TMEM251)
UAH:
113267337
(LYSET)
UAR:
123798874
(TMEM251)
ELK:
111148574
LLV:
125105048
MPUF:
101683565
(TMEM251)
MNP:
132000213
(LYSET)
MLK:
131836932
(LYSET)
NVS:
122893752
(TMEM251)
ORO:
101386441
(TMEM251)
EJU:
114207226
(TMEM251)
ZCA:
113910058
(TMEM251)
MLX:
118002236
(TMEM251)
NSU:
110571525
(TMEM251)
LWW:
102730271
(TMEM251)
FCA:
101099217
(TMEM251)
PYU:
121032219
(TMEM251)
PCOO:
112856232
(TMEM251)
PBG:
122469469
(TMEM251)
PVIV:
125167808
(LYSET)
LRUF:
124512559
LGF:
123582069
(TMEM251)
AJU:
106980837
PTG:
102968919
(TMEM251)
PPAD:
109274485
(TMEM251)
PUC:
125909229
PLEZ:
122223077
(TMEM251)
HHV:
120220226
(TMEM251)
BTA:
768076
(LYSET)
BOM:
102279126
138984406
(LYSET)
BIU:
109575673
(TMEM251)
BBUB:
102414098
(TMEM251)
BBIS:
104985825
(TMEM251)
104994100
CHX:
102168945
(TMEM251)
OAS:
101115406
(LYSET)
BTAX:
128066563
128066566
(LYSET)
CSUM:
138095403
(LYSET)
ODA:
120874977
(TMEM251)
CCAD:
122419617
(TMEM251)
MREE:
136147255
(LYSET)
OVR:
110126343
(LYSET)
MBEZ:
129550600
(LYSET)
SSC:
414384
(TMEM251)
CFR:
102508694
(TMEM251)
CBAI:
105079878
(TMEM251)
CDK:
105095813
(TMEM251)
VPC:
102545135
(TMEM251)
BACU:
103011365
(TMEM251)
BMUS:
118888977
(TMEM251)
LVE:
103085056
(TMEM251)
OOR:
101270575
(LYSET)
LALB:
132529803
(LYSET)
DLE:
111176139
(TMEM251)
PCAD:
102992025
(LYSET)
PSIU:
116749664
(TMEM251)
NASI:
112409155
(TMEM251)
ECB:
100053356
(TMEM251)
111772187
EPZ:
103557896
(LYSET)
EAI:
106825391
(TMEM251)
MYB:
102255936
(TMEM251)
MYD:
102765522
(TMEM251)
MMYO:
118659773
(TMEM251)
MLF:
102427167
(TMEM251)
MDT:
132230266
(LYSET)
MYUM:
139001658
139001885
PKL:
118704232
(TMEM251)
EFUS:
103302899
(LYSET)
MNA:
107536652
(TMEM251)
DRO:
112311441
(TMEM251)
SHON:
118976791
(TMEM251)
AJM:
119037983
(LYSET)
PDIC:
114493242
(TMEM251)
PHAS:
123808400
(TMEM251)
MMF:
118638703
(TMEM251)
PPAM:
129065814
(LYSET)
HAI:
109382718
(TMEM251)
RFQ:
117023317
(TMEM251)
PALE:
102890041
(TMEM251)
PGIG:
120619634
(TMEM251)
PVP:
105300796
(TMEM251)
RAY:
107511248
(TMEM251)
MJV:
108409824
(TMEM251)
TOD:
119239448
(LYSET)
SARA:
101555995
(TMEM251)
SFUM:
130041385
(LYSET)
SETR:
126003618
(LYSET)
LAV:
100669093
(TMEM251)
TMU:
101342082
ETF:
101658209
(TMEM251)
DNM:
101420497
(TMEM251)
MDO:
100014416
(TMEM251)
GAS:
123235908
(TMEM251)
SHR:
100925213
(TMEM251)
AFZ:
127549386
PCW:
110217781
(TMEM251)
TVP:
118830335
(TMEM251)
118853335
PBRV:
138159700
(LYSET)
OAA:
100079855
(TMEM251)
TACU:
119925515
(TMEM251)
GGA:
423422
(TMEM251)
PCOC:
116228891
(TMEM251)
MGP:
116216692
(TMEM251)
CJO:
107315186
(TMEM251)
TPAI:
128085937
(LYSET)
LMUT:
125695595
(TMEM251)
NMEL:
110401850
(TMEM251)
APLA:
113843803
(TMEM251)
ACYG:
106036467
(LYSET)
CATA:
118244789
(LYSET)
AFUL:
116489832
(TMEM251)
TGU:
100219981
(TMEM251)
LSR:
110476413
(LYSET)
SCAN:
115485436
(TMEM251)
PMOA:
120503734
(TMEM251)
OTC:
121341916
(TMEM251)
PRUF:
121356072
(TMEM251)
ATRC:
139589821
(LYSET)
GFR:
106632231
(TMEM251)
PMAJ:
117244584
(TMEM251)
CCAE:
111943624
(TMEM251)
CCW:
104686145
(TMEM251)
CBRC:
108445392
(TMEM251)
ACOE:
138111789
(LYSET)
ETL:
114060645
(TMEM251)
ZAB:
113458768
(TMEM251)
ZLE:
135448989
(LYSET)
ACHL:
103800888
(TMEM251)
MMEA:
130576180
(LYSET)
HRT:
120754722
(LYSET)
SATI:
136362872
(LYSET)
CCIC:
134045653
(LYSET)
FCH:
114015740
(TMEM251)
CCRI:
104154427
(TMEM251)
SHAB:
115606083
(TMEM251)
ACUN:
113480820
(TMEM251)
TALA:
116965768
(TMEM251)
ACHC:
115337091
(TMEM251)
AGEN:
126050627
HHAR:
128139910
(LYSET)
GCL:
127016831
CSTI:
104552673
(TMEM251)
MNB:
103782282
(TMEM251)
PPUS:
135174864
(LYSET)
EGZ:
118451681
(TMEM251)
PCRI:
104023728
(TMEM251)
FGA:
104072451
(TMEM251)
CBOY:
140653280
(LYSET)
CUCA:
128852422
(LYSET)
BREG:
104631826
(TMEM251)
ACAR:
114818843
(TMEM251)
RTD:
128908681
(LYSET)
CRID:
134515049
(LYSET)
AROW:
112972613
(TMEM251)
NPD:
112953763
(TMEM251)
DNE:
112990410
(TMEM251)
ASN:
112550568
(TMEM251)
PSS:
102452266
(TMEM251)
CMY:
114018382
(TMEM251)
CCAY:
125638056
(TMEM251)
DCC:
119857185
(TMEM251)
CPIC:
112059200
(TMEM251)
TST:
117876180
(TMEM251)
CABI:
116827595
(TMEM251)
MRV:
120402794
(TMEM251)
ACS:
100566075
(tmem251)
ASAO:
132763079
(LYSET)
PVT:
110083641
(TMEM251)
SUND:
121919738
(TMEM251)
PBI:
112541502
(TMEM251)
PMUR:
114922549
(TMEM251)
CTIG:
120318378
(TMEM251)
TSR:
106544118
106544121
PGUT:
117665931
(LYSET)
APRI:
131187870
(LYSET)
PTEX:
113444553
(TMEM251)
NSS:
113419681
(TMEM251)
VKO:
123026588
(TMEM251)
PMUA:
114590740
(TMEM251)
PRAF:
128407693
(LYSET)
128408061
ZVI:
118080963
118081181
HCG:
128326640
(LYSET)
GJA:
107121771
(TMEM251)
STOW:
125427424
(TMEM251)
EMC:
129324709
(LYSET)
XLA:
444608
(tmem251-b)
447520
(tmem251.L)
XTR:
497000
(tmem251)
NPR:
108788683
(TMEM251)
RTEM:
120920286
(TMEM251)
BBUF:
120982262
(TMEM251)
BGAR:
122922137
(TMEM251)
PWL:
138260082
(LYSET)
MUO:
115477455
(TMEM251)
GSH:
117364185
(TMEM251)
DRE:
619265
(tmem251)
SGH:
107580136
(tmem251)
CCAR:
109105664
109108870
(tmem251)
122148977
CAUA:
113062905
113120914
CGIB:
127938903
127984444
PTET:
122324893
(tmem251)
LROH:
127183441
(tmem251)
OMC:
131527367
(tmem251)
PPRM:
120493469
(tmem251)
RKG:
130091847
(tmem251)
MAMB:
125277924
(tmem251)
CIDE:
127501764
CERY:
137018389
(tmem251)
MASI:
127410204
127415922
MANU:
129429667
(tmem251)
129429668
PDAB:
135737792
135737967
135738646
135738647
(tmem251)
IPU:
108257831
IFU:
128601550
(tmem251)
PHYP:
113547683
(tmem251)
SMEO:
124377172
TFD:
113643325
(tmem251)
TVC:
132843019
(tmem251)
CGAR:
128515173
(tmem251)
NGRA:
132882681
(tmem251)
TRN:
134320127
(tmem251)
AMEX:
111189850
(tmem251)
CMAO:
118815666
(tmem251)
EEE:
113570506
(tmem251)
CHAR:
105897038
(tmem251)
SPIL:
134097500
(tmem251)
TBEN:
117474944
(tmem251)
EMAC:
134863217
(tmem251)
ELY:
117271209
(tmem251)
EFO:
125896861
(tmem251)
PLEP:
121955660
(tmem251)
SLUC:
116061041
(tmem251)
ESP:
116685500
(tmem251)
PFLV:
114573374
(tmem251)
GAT:
120814268
(tmem251)
PPUG:
119195025
(tmem251)
AFB:
129107344
(tmem251)
CLUM:
117727304
(tmem251)
CANA:
137782464
(tmem251)
CVE:
137871389
(tmem251)
MSAM:
119908936
(tmem251)
SCHU:
122862855
(tmem251)
CUD:
121520991
(tmem251)
SPUL:
138583600
(tmem251)
LMIX:
132985488
(tmem251)
ALAT:
119012808
(tmem251)
ASTR:
137613354
(tmem251)
MZE:
101482900
(tmem251)
ONL:
100700046
(tmem251)
OAU:
116332905
(tmem251)
OLA:
101169507
(tmem251)
OML:
112158052
(tmem251)
CSAI:
133464744
(tmem251)
XMA:
102218976
(tmem251)
XCO:
114158980
(tmem251)
XHE:
116733953
(tmem251)
PRET:
103457073
(tmem251)
PFOR:
103130368
(tmem251)
PLAI:
106961017
(tmem251)
PMEI:
106905638
(tmem251)
GAF:
122825306
(tmem251)
PPRL:
129353685
(tmem251)
CVG:
107104324
(tmem251)
CTUL:
119796707
(tmem251)
GMU:
124882384
(tmem251)
NFU:
107377478
(tmem251)
KMR:
108249103
(tmem251)
ALIM:
106526956
(tmem251)
NWH:
119412179
(tmem251)
AOCE:
111574123
(tmem251)
EJA:
138212359
(tmem251)
BFRE:
138636831
(tmem251)
MCEP:
124999035
(tmem251)
POV:
109643846
(tmem251)
SSEN:
122784221
(tmem251)
SSOE:
131443929
(tmem251)
HHIP:
117758770
(tmem251)
HSP:
118104016
(tmem251)
PPLT:
128459801
(tmem251)
SMAU:
118289839
(tmem251)
LCF:
108890064
SDU:
111231739
(tmem251)
SLAL:
111645949
(tmem251)
XGL:
120788826
(tmem251)
MALB:
109974465
(tmem251)
BSPL:
114849414
(tmem251)
SJO:
128377379
(tmem251)
SSCO:
133976751
133977149
SASA:
106571692
(tmem251)
STRU:
115174640
(tmem251)
OTW:
112250447
(tmem251)
OMY:
110529744
(tmem251)
OGO:
123990874
(tmem251)
ONE:
115107883
(tmem251)
OKI:
109900859
(tmem251)
OKE:
118398528
(tmem251)
OMM:
135505842
(tmem251)
OCLA:
139415252
SALP:
111954232
(tmem251)
SNH:
120023881
(tmem251)
CCLU:
121552917
(tmem251)
ELS:
105017669
(tmem251)
OEP:
134025018
(tmem251)
SFM:
108942610
114912326
(tmem251)
PKI:
111838838
(tmem251)
111852738
AANG:
118212737
(tmem251)
118229491
AROT:
135249702
(tmem251)
135257134
CCOG:
133128119
133136483
LOC:
102693091
(tmem251)
PSPA:
121324583
(tmem251)
121330056
ARUT:
117422705
117424223
PSEX:
120518650
(tmem251)
CMK:
103185400
(tmem251)
RTP:
109929101
(tmem251)
CPLA:
122553437
(tmem251)
HOC:
132818379
(tmem251)
LERI:
129699965
(tmem251)
PMRN:
116939660
(TMEM251)
LRJ:
133347319
(LYSET)
BFO:
118413136
SPU:
115918070
LPIC:
129264108
AJJ:
139970424
APLC:
110979291
AAMU:
139940683
BGT:
106075006
MYI:
110440597
PMAX:
117323183
AIRR:
138318599
OBI:
106877471
LAK:
106160605
106170418
» show all
Taxonomy
UniProt
Reference
PMID:
36074822
Authors
Pechincha C, Groessl S, Kalis R, de Almeida M, Zanotti A, Wittmann M, Schneider M, de Campos RP, Rieser S, Brandstetter M, Schleiffer A, Muller-Decker K, Helm D, Jabs S, Haselbach D, Lemberg MK, Zuber J, Palm W
Title
Lysosomal enzyme trafficking factor LYSET enables nutritional usage of extracellular proteins.
Journal
Science 378:eabn5637 (2022)
DOI:
10.1126/science.abn5637
Sequence
[hsa:
26175
]
LinkDB
All DBs
DBGET
integrated database retrieval system