The human and mouse SLC25A29 mitochondrial transporters rescue the deficient ornithine metabolism in fibroblasts of patients with the hyperornithinemia-hyperammonemia-homocitrullinuria (HHH) syndrome.
Palmieri L, Todd CD, Arrigoni R, Hoyos ME, Santoro A, Polacco JC, Palmieri F
Title
Arabidopsis mitochondria have two basic amino acid transporters with partially overlapping specificities and differential expression in seedling development.