Entry |
|
Name |
Branched-chain amino acids degradation
|
Definition |
Leu,Val,Ile -- BCAT1/2 >> (BCKDHA+BCKDHB+DBT+DLD) -> IV-CoA,IB-CoA,2-MB-CoA |
Expanded |
(C00123,C00183,C00407) -- (586,587) >> (593+594+1629+1738) -> (C02939,C00630,C15980) |
Class |
nt06024 Valine, leucine and isoleucine degradation
|
Type |
Reference
|
Pathway |
hsa00280 | Valine, leucine and isoleucine degradation |
|
Gene |
586 | BCAT1; branched chain amino acid transaminase 1 |
587 | BCAT2; branched chain amino acid transaminase 2 |
593 | BCKDHA; branched chain keto acid dehydrogenase E1 subunit alpha |
594 | BCKDHB; branched chain keto acid dehydrogenase E1 subunit beta |
1629 | DBT; dihydrolipoamide branched chain transacylase E2 |
1738 | DLD; dihydrolipoamide dehydrogenase |
|
Metabolite |
C15980 | (S)-2-Methylbutanoyl-CoA |
|
LinkDB |
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