KEGG   Aythya fuligula (tufted duck): 116501533
Entry
116501533         CDS       T07966                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
aful  Aythya fuligula (tufted duck)
Pathway
aful00280  Valine, leucine and isoleucine degradation
aful00640  Propanoate metabolism
aful00785  Lipoic acid metabolism
aful01100  Metabolic pathways
aful01210  2-Oxocarboxylic acid metabolism
Module
aful_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:aful00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    116501533 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    116501533 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    116501533 (BCKDHA)
Enzymes [BR:aful01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     116501533 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N CDV3
Other DBs
NCBI-GeneID: 116501533
NCBI-ProteinID: XP_032063023
UniProt: A0A6J3ENP4
LinkDB
Position
Unknown
AA seq 438 aa
MAAALRALRARLLRAAPGAGPGRGLGTARGPRAQQEFPTPEEKPQFPGASAEFAERLEFI
QPNVISGIPVYRVMDRQGHILNPHEDPQLPKELVLKLYKTMTLLNTMDRILYESQRQGRI
SFYMTNYGEEGTHVGSAAALDDTDLVFGQYREAGVLMYRGYPLDLFMAQCYGNTSDPGKG
RQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAIKRADANRAVICYFGEGAASEGDAHA
GFNFAATLECPIVFFCRNNGYAISTPTSEQYRGDGIAARGPGYGLLSIRVDGNDVFAVYN
ATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPISRLRHHM
LNRGWWDDEQEKAWRKSSRRKVMEAFEQAERKPKPSPQQHLFSDVYREMPPHLRKQRAAL
ERHLQHYGEHYPLEHFEK
NT seq 1317 nt   +upstreamnt  +downstreamnt
atggcggcggcgctgcgggcgctgcgggcgcggctcctgcgggcggctccaggcgcgggc
cccgggcgcggcctcggcaccgcccggggtccgcgggcgcagcaggagttcccgacccca
gaggagaagccgcagttccccggggcctcggccgaattcgccgagcgcctggagttcatc
cagcccaacgtcatctcgggcatccccgtctaccgcgtgatggatcgccagggccacatc
ctaaacccccacgaggacccccagctgcccaaggagctggtgctgaagctctacaagacc
atgacgctgctcaacaccatggaccgcatcctctacgagtcccagcggcagggccgcatc
tccttctacatgaccaactacggcgaggaggggacgcacgtgggcagcgcggcggcgctg
gacgacaccgacctggttttcgggcagtaccgggaggccggcgtgctgatgtaccggggc
taccccttggacctcttcatggcgcagtgctacggcaacaccagcgaccccgggaagggc
cgccagatgcccgtgcactacggctgccgcgagcgccacttcgtcaccatctcctccccc
ctggccacccaaattccacaagccgtgggggccgcctacgccatcaagcgcgccgacgcc
aaccgggcggtcatctgctattttggggagggggcggccagcgagggggacgcccacgcc
ggcttcaatttcgccgccaccctcgagtgccccatcgtcttcttctgccgcaacaacggc
tacgccatctccaccccgacctccgagcagtaccgcggcgacggcatcgccgctcggggt
cccggttacgggctgctgtcgatccgggtggatggcaacgacgttttcgccgtctacaac
gccaccaaggaggcgcggcggcgcgccgtggcggagaaccagcccttcctcatcgaggcc
atgacctaccgcatcgggcaccacagcaccagcgacgacagctctgcctaccgctcggtg
gacgaggtgaattactgggacaagcaggaccaccccatctcccgcctgcgccaccacatg
ctgaaccgcggctggtgggacgacgagcaggaaaaagcctggagaaaaagctcccggaga
aaggtgatggaggcgtttgagcaggcggaacggaagcccaagcccagcccgcagcagcac
ctcttctccgacgtgtaccgcgagatgcccccccacctgcgtaagcagagggcggccctg
gagcggcacctgcagcactacggggagcactaccccctggagcactttgagaagtga

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