Entry |
|
Symbol |
BCKDHB
|
Name |
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1
|
KO |
K00167 | 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4] |
|
Organism |
aml Ailuropoda melanoleuca (giant panda)
|
Pathway |
aml00280 | Valine, leucine and isoleucine degradation |
aml01210 | 2-Oxocarboxylic acid metabolism |
|
Module |
aml_M00036 | Leucine degradation, leucine => acetoacetate + acetyl-CoA |
|
Brite |
KEGG Orthology (KO) [BR:aml00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
100476045 (BCKDHB)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
100476045 (BCKDHB)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
100476045 (BCKDHB)
Enzymes [BR:aml01000]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
100476045 (BCKDHB)
|
SSDB |
|
Motif |
|
Other DBs |
|
LinkDB |
|
Position |
19:30872272..31091536
|
AA seq |
392 aa
MAALAATAGGLLRLRAAGAEGQWRRLRGAGLLRGLLQPDSATGVAAQRRLVAHFTFQPDP
EPQEYGQTQKMNLFQAITSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRAPWGCVGHGALYHSQSPEAFFAHCPGIKVVVPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAVEQVPVEPYNVPLSQAEVIQEGSDITLVAWGTQVHVIREVAAMAQEKLGVSCE
VIDLRTILPWDVDTVCKSVIKTGRLLISHEAPLTGGFASEISSTVQEECFLNLEAPISRV
CGYDTPFPHIFEPFYIPDKWKCYDALRKMINY |
NT seq |
1179 nt +upstreamnt +downstreamnt
atggcggcgcttgcggcgactgcgggcgggcttttgaggttgcgtgcggccggggcagaa
ggacagtggcgtcggcttcgaggcgcggggctgctgcggggcttgctgcagcccgactcg
gcaactggggttgcagcgcagaggaggcttgtggctcacttcactttccagcccgacccg
gagccccaggagtatgggcaaactcagaaaatgaatcttttccaggcgataacaagtgcc
ttggataactcattggctaaagatcctactgcagtgatatttggtgaagatgttgccttt
ggtggagtctttagatgtactgttggcttgcgagacaaatatggaaaagatagagttttc
aacacgccattgtgcgaacaaggaattgttgggtttggaattgggattgcagtcactggg
gctactgccattgcagaaattcagtttgcagattatattttccccgctttcgatcagatt
gttaatgaagcggccaagtatcgctatcgctctggggatcttttcaattgtggaagcctc
accatccgggccccttggggctgtgttggccatggagctctttatcattctcagagtcct
gaagctttttttgctcactgcccaggaatcaaggtggttgtacccagaagccctttccag
gccaagggacttcttttgtcatgcatagaggataaaaatccttgtatattttttgaacct
aaaatactttacagggcagcagttgaacaggttcctgtagaaccatacaacgttcctctg
tcccaggccgaagtcattcaggaagggagtgacattactctggtcgcctggggcactcag
gttcatgtgatccgagaggtggctgccatggctcaagagaagcttggagtgtcttgtgaa
gtcattgatctgaggactatactaccttgggatgtggatacagtttgcaagtctgtgatc
aaaacagggcgattgcttatcagtcatgaggctccgttgacaggcggctttgcgtcggag
atcagctccacagttcaggaagaatgtttcctgaacctggaggctcctatatcaagagta
tgtggttatgacacaccgtttcctcacattttcgagccgttctacatcccagacaaatgg
aagtgctacgatgcccttcgaaaaatgatcaactactga |