KEGG   Ailuropoda melanoleuca (giant panda): 100476045
Entry
100476045         CDS       T01329                                 
Symbol
BCKDHB
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1
  KO
K00167  2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
Organism
aml  Ailuropoda melanoleuca (giant panda)
Pathway
aml00280  Valine, leucine and isoleucine degradation
aml00640  Propanoate metabolism
aml00785  Lipoic acid metabolism
aml01100  Metabolic pathways
aml01210  2-Oxocarboxylic acid metabolism
Module
aml_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:aml00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    100476045 (BCKDHB)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    100476045 (BCKDHB)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    100476045 (BCKDHB)
Enzymes [BR:aml01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     100476045 (BCKDHB)
SSDB
Motif
Pfam: Transket_pyr Transketolase_C Toxin_YhaV
Other DBs
NCBI-GeneID: 100476045
NCBI-ProteinID: XP_002916344
Ensembl: ENSAMEG00000012810
UniProt: G1M2C9
LinkDB
Position
19:30872272..31091536
AA seq 392 aa
MAALAATAGGLLRLRAAGAEGQWRRLRGAGLLRGLLQPDSATGVAAQRRLVAHFTFQPDP
EPQEYGQTQKMNLFQAITSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRAPWGCVGHGALYHSQSPEAFFAHCPGIKVVVPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAVEQVPVEPYNVPLSQAEVIQEGSDITLVAWGTQVHVIREVAAMAQEKLGVSCE
VIDLRTILPWDVDTVCKSVIKTGRLLISHEAPLTGGFASEISSTVQEECFLNLEAPISRV
CGYDTPFPHIFEPFYIPDKWKCYDALRKMINY
NT seq 1179 nt   +upstreamnt  +downstreamnt
atggcggcgcttgcggcgactgcgggcgggcttttgaggttgcgtgcggccggggcagaa
ggacagtggcgtcggcttcgaggcgcggggctgctgcggggcttgctgcagcccgactcg
gcaactggggttgcagcgcagaggaggcttgtggctcacttcactttccagcccgacccg
gagccccaggagtatgggcaaactcagaaaatgaatcttttccaggcgataacaagtgcc
ttggataactcattggctaaagatcctactgcagtgatatttggtgaagatgttgccttt
ggtggagtctttagatgtactgttggcttgcgagacaaatatggaaaagatagagttttc
aacacgccattgtgcgaacaaggaattgttgggtttggaattgggattgcagtcactggg
gctactgccattgcagaaattcagtttgcagattatattttccccgctttcgatcagatt
gttaatgaagcggccaagtatcgctatcgctctggggatcttttcaattgtggaagcctc
accatccgggccccttggggctgtgttggccatggagctctttatcattctcagagtcct
gaagctttttttgctcactgcccaggaatcaaggtggttgtacccagaagccctttccag
gccaagggacttcttttgtcatgcatagaggataaaaatccttgtatattttttgaacct
aaaatactttacagggcagcagttgaacaggttcctgtagaaccatacaacgttcctctg
tcccaggccgaagtcattcaggaagggagtgacattactctggtcgcctggggcactcag
gttcatgtgatccgagaggtggctgccatggctcaagagaagcttggagtgtcttgtgaa
gtcattgatctgaggactatactaccttgggatgtggatacagtttgcaagtctgtgatc
aaaacagggcgattgcttatcagtcatgaggctccgttgacaggcggctttgcgtcggag
atcagctccacagttcaggaagaatgtttcctgaacctggaggctcctatatcaagagta
tgtggttatgacacaccgtttcctcacattttcgagccgttctacatcccagacaaatgg
aagtgctacgatgcccttcgaaaaatgatcaactactga

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