KEGG   Bison bison bison (American bison): 104999119
Entry
104999119         CDS       T08726                                 
Symbol
BCKDHB
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
  KO
K00167  2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
Organism
bbis  Bison bison bison (American bison)
Pathway
bbis00280  Valine, leucine and isoleucine degradation
bbis00640  Propanoate metabolism
bbis00785  Lipoic acid metabolism
bbis01100  Metabolic pathways
bbis01210  2-Oxocarboxylic acid metabolism
Module
bbis_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:bbis00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    104999119 (BCKDHB)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    104999119 (BCKDHB)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    104999119 (BCKDHB)
Enzymes [BR:bbis01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     104999119 (BCKDHB)
SSDB
Motif
Pfam: Transket_pyr Transketolase_C
Other DBs
NCBI-GeneID: 104999119
NCBI-ProteinID: XP_010852891
Ensembl: ENSBBBG00000008641
UniProt: A0A6P3IEF4
LinkDB
Position
Unknown
AA seq 392 aa
MAAVAAFAGWLLRLRAAGADGPWRRLCGAGLSRGFLQSSSAYGAAAQRRQVAHFTFQPDP
EPVEYGQTQKMNLFQAVTSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRSPWGCVGHGALYHSQSPEAFFAHCPGIKVVVPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAVEQVPVEPYNIPLSQAEVIQEGSDVTLVAWGTQVHVIREVAAMAREKLGVSCE
VIDLRTILPWDVDTVCKSVIKTGRLLVSHEAPLTGGFASEISSTVQEECFLNLEAPISRV
CGYDTPFPHIFEPFYIPDKWKCYDALRKMINY
NT seq 1179 nt   +upstreamnt  +downstreamnt
atggcggctgtggcggcgttcgcgggctggctgctgcggctccgtgcagccggggccgac
ggaccctggcgtcggctgtgtggcgcggggctgtcgaggggcttcctgcagtcctcctcg
gcctacggggctgcggcccagaggcggcaggtggctcacttcactttccagcctgacccg
gagcccgtggagtacgggcagactcagaagatgaatctcttccaggcagtaacaagtgcc
ttagataactcattggccaaagatcctacggcagtaatatttggtgaagacgttgccttt
ggtggagtctttagatgtactgtcggcttgcgagacaagtatggtaaagatagagttttt
aataccccactgtgtgaacaaggaatcgttggatttggaattggaatcgcagtcaccggt
gctactgccatagcagaaattcagtttgcagattatattttccctgcttttgatcagatt
gttaatgaagctgccaagtatcgctaccggtctggggacctttttaattgtggaagcctc
accatccggtccccttggggctgtgtcggccacggggctctctatcattcccagagtcct
gaagctttctttgcccactgcccaggaatcaaggtggttgtacccagaagccctttccag
gccaagggacttcttttatcatgcatagaggataaaaatccttgtatattttttgaacct
aaaatactttacagggcagcagtggagcaggttcctgtagagccatacaacatccccctt
tcccaagctgaagtcatccaagaagggagtgatgtcactctagttgcctggggcactcag
gttcatgtgatccgagaggtggctgccatggctcgagagaagcttggggtgtcttgtgag
gtcattgatctgaggactatactaccttgggatgtggatacagtttgcaagtctgtgatc
aaaacagggcgactgctagtaagtcatgaggctcctttgacgggcggctttgcctctgag
atcagctcaacggttcaggaagaatgtttcctgaacctggaagctcctatatcaagggtg
tgtgggtacgacacaccgttccctcacatttttgaaccgttctacatcccagacaagtgg
aagtgctatgatgcccttcgaaaaatgatcaactattaa

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