KEGG   Bison bison bison (American bison): 104999996
Entry
104999996         CDS       T08726                                 
Symbol
MCCC1
Name
(RefSeq) methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X1
  KO
K01968  3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
Organism
bbis  Bison bison bison (American bison)
Pathway
bbis00280  Valine, leucine and isoleucine degradation
bbis01100  Metabolic pathways
Module
bbis_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:bbis00001]
 09100 Metabolism
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    104999996 (MCCC1)
Enzymes [BR:bbis01000]
 6. Ligases
  6.4  Forming carbon-carbon bonds
   6.4.1  Ligases that form carbon-carbon bonds (only sub-subclass identified to date)
    6.4.1.4  methylcrotonoyl-CoA carboxylase
     104999996 (MCCC1)
SSDB
Motif
Pfam: CPSase_L_D2 Biotin_carb_N Biotin_carb_C Biotin_lipoyl Dala_Dala_lig_C ATP-grasp Biotin_lipoyl_2 ATP-grasp_3 RimK ATPgrasp_ST GARS_A ATP-grasp_4 BT_MCC_alpha NQRA_N RnfC_N DUF2118 2OG-FeII_Oxy_2
Other DBs
NCBI-GeneID: 104999996
NCBI-ProteinID: XP_010853945
Ensembl: ENSBBBG00000015686
UniProt: A0A6P3IS10
LinkDB
Position
Unknown
AA seq 725 aa
MSAASLVSVLLVAAERHRWQRVPRLLLPPRGWAWKQRTRKYATTTGQNISKVLIANRGEI
ACRVIRTAKKMGVQSVAVYSEADRNSMHVDMADEAYLIGPAPSQQSYLSMEKIIQVAKIS
AAQAIHPGYGFLSENMEFAELCKQEGIIFVGPPSSAIRDMGIKSTSKSIMAAAGVPVVEG
YHGEDQSDQCLKEHARTIGYPVMIKAVRGGGGKGMRIVRSEKEFQEQLESARREAKKSFN
DDAMLIEKFVDTPRHVEVQVFGDHHGNAVYLFERDCSVQRRHQKIIEEAPGPGIKPEVRK
KLGEAAVRAAKAVNYVGAGTVEFIMDSKHNFYFMEMNTRLQVEHPVTEMITGTDLVEWQL
RIAAGEKIPLSQEEITLRGHAFEARIYAEDPNNNFMPGAGPLVHLSTPRADLTTRIETGV
RQGDEVSMHYDPMIAKLVVWAADRQAALTKLKYSLRQYNIVGLHTNIDFLLSLSSHPEFE
AGNVHTDFIPQHRKELLPDRKTTAKEFLCHAALALILKEKAVSDVFKIQTQDQYSPFASS
SGRRLNICYSRNMTLRDGKNNVAIAVTYNRDGSYSMQIEDKTFHVLGDLCSEGDCTYLKS
SVNGVASKIKLIILKNTIYLFSMDGSIQIGIPVPRYLSSASSGETQGGAVAPMTGTVEKV
FVKAGDRVKAGDSLMVMIAMKMEHTIKAPKDGTIKKVFYKEGSQANRHAPLVEFEEEDSD
EREAD
NT seq 2178 nt   +upstreamnt  +downstreamnt
atgtcggcggcctctttggtgtcggtgctgctcgtggcggcggagaggcatcggtggcag
cgagtcccgcgcttgctgctgccgccgaggggatgggcttggaagcaaagaacaaggaag
tatgcaacaaccacaggacaaaacatttccaaggtcctcattgcaaacagaggagaaatt
gcctgcagggtgatacggacagccaaaaaaatgggtgtacagtctgtggctgtttatagt
gaggccgacaggaattccatgcatgttgacatggcagatgaagcctatctcatcggcccc
gctccctctcagcagagctacctttctatggaaaaaatcattcaagtggccaagatctct
gccgcacaggctatccatccaggatatggctttctctcagaaaacatggaatttgccgaa
ctgtgtaagcaagaaggaattatttttgtaggtcctccttcatcagcaattagagacatg
ggtataaagagcacatccaaatccatcatggctgctgctggagtgcctgtggtggagggt
tatcacggggaggaccagtcagaccaatgcctgaaagagcacgctaggacaatcggttac
cccgtcatgattaaagccgtccgtggcggaggaggaaaaggtatgaggatcgttagatct
gaaaaagaatttcaagagcagttagaatcagcacggagagaagctaagaagtctttcaat
gatgatgccatgctgattgagaagtttgtggacacaccaaggcatgtagaagtgcaggtg
tttggtgaccaccatggcaatgccgtgtacttgtttgaaagagactgtagtgtacagaga
agacatcagaagatcattgaagaggccccagggcctggtattaaacctgaagtaagaaaa
aagcttggagaagctgcagtcagagctgctaaagctgtaaattatgttggtgcaggaacc
gtggagtttatcatggactcaaagcacaatttctactttatggagatgaatacaaggctg
caagtggaacatcctgtcaccgagatgatcacaggaactgacttggtggaatggcaactt
aggattgcagcaggagagaagattcctttgagccaggaagaaataactctgcggggccat
gcctttgaagctagaatatatgcagaagatcctaacaataacttcatgccgggggccgga
ccactagtgcatctctccacccctcgagcagaccttaccactaggattgaaactggagta
cggcaaggagatgaagtttcaatgcattatgaccccatgattgcaaagctggttgtgtgg
gctgctgatcgccaggcagccttgacgaaacttaagtacagccttcgacagtacaatatt
gttggactgcacaccaacattgacttcctccttagcctgtctagccacccggaatttgaa
gctgggaacgtgcacactgatttcatccctcaacaccgcaaagaactgttgcccgaccgg
aagaccacagccaaggagtttttatgtcacgcagctctggccctcatcctcaaggagaaa
gctgtgtctgatgtcttcaaaattcagacacaagatcaatactctccttttgcatccagc
agtggaagaagactgaatatctgttactctagaaacatgactcttagggatggtaaaaac
aatgtagccatagctgtaacatataaccgtgatggatcatatagcatgcagattgaagat
aaaactttccatgtccttggtgatctttgcagtgagggagactgcacttatctgaaatct
tctgttaatggagttgctagtaaaattaagctaattatcctgaaaaacactatttaccta
ttttccatggatggaagtattcagattggcattccggttccccgatacttgtcttcagca
agctcaggagaaacccaagggggtgctgtagctcctatgactggaactgttgaaaaggtg
tttgtgaaagctggagacagagtaaaagctggagactctctgatggttatgattgccatg
aaaatggaacataccataaaggcgccaaaggatggcacaatcaagaaggtattctacaaa
gaaggttctcaggccaacagacacgctcctttagtcgagtttgaggaggaagactctgac
gaaagggaagcagattaa

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