KEGG   Bos taurus (cow): 513504
Entry
513504            CDS       T01008                                 
Symbol
MCCC1
Name
(RefSeq) methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial
  KO
K01968  3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
Organism
bta  Bos taurus (cow)
Pathway
bta00280  Valine, leucine and isoleucine degradation
bta01100  Metabolic pathways
Brite
KEGG Orthology (KO) [BR:bta00001]
 09100 Metabolism
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    513504 (MCCC1)
Enzymes [BR:bta01000]
 6. Ligases
  6.4  Forming carbon-carbon bonds
   6.4.1  Ligases that form carbon-carbon bonds (only sub-subclass identified to date)
    6.4.1.4  methylcrotonoyl-CoA carboxylase
     513504 (MCCC1)
SSDB
Motif
Pfam: CPSase_L_D2 Biotin_carb_N Biotin_carb_C Biotin_lipoyl Dala_Dala_lig_C ATP-grasp Biotin_lipoyl_2 ATP-grasp_3 RimK ATPgrasp_ST GARS_A ATP-grasp_4 RnfC_N HlyD_D23 DUF2118 2OG-FeII_Oxy_2
Other DBs
NCBI-GeneID: 513504
NCBI-ProteinID: NP_001192687
BGD-bta: BT16791
Ensembl: ENSBTAG00000006548
VGNC: 31298
UniProt: A0A3Q1LRD6
LinkDB
Position
1:83960747..84019357
AA seq 725 aa
MSAASLVSVLLVAAERHRWQRVPRLLLPPRGWAWKQRTRKYATTTGQNISKVLIANRGEI
ACRVIRTAKKMGVQSVAVYSEADRNSMHVDMADEAYLIGPAPSQQSYLSMEKIIQVAKIS
AAQAIHPGYGFLSENMEFAELCKQEGIIFVGPPSSAIRDMGIKSTSKSIMAAAGVPVVEG
YHGEDQSDQCLKEHARTIGYPVMIKAVRGGGGKGMRIVRSEKEFQEQLESARREAKKSFN
DDAMLIEKFVDTPRHVEVQVFGDHHGNAVYLFERDCSVQRRHQKIIEEAPGPGIKPEVRK
KLGEAAVRAAKAVNYVGAGTVEFIMDSKHNFYFMEMNTRLQVEHPVTEMITGTDLVEWQL
RIAAGEKIPLSQEEITLRGHAFEARIYAEDPNNNFMPGAGPLVHLSTPRADLTTRIETGV
RQGDEVSMHYDPMIAKLVVWAADRQAALTKLKYSLRQYNIVGLHTNIDFLLSLSGHPEFE
AGNVHTDFIAQHRKELLPDRKTTAKEFLCHAALALILKEKAVSDVFKIQTQDQYSPFASS
SGRRLNICYSRNMTLRDGKNNVAIAVTYNRDGSYSMQIEDKTFHVLGDLCSEGDCTYLKS
SVNGVASKIKLIILKNTIYLFSMDGSIQIGIPVPRYLSSASSGETQGGAVAPMTGTVEKV
FVKAGDRVKAGDSLMVMIAMKMEHTIKAPKDGTIKKVFYKEGSQANRHAPLVEFEEEDSD
EREAD
NT seq 2178 nt   +upstreamnt  +downstreamnt
atgtcggcggcctctttggtgtcggtgctgctcgtggcggcggagaggcaccggtggcag
cgagtcccgcgcttgctgctgccgccgaggggatgggcttggaagcaaagaacaaggaag
tatgcaacaaccacaggacaaaacatttccaaggtcctcattgcaaacagaggagaaatt
gcctgcagggtgatacggacagccaaaaaaatgggtgtacagtctgtggctgtttatagt
gaggccgacaggaattccatgcatgttgacatggcagatgaagcctatctcatcggcccc
gctccctctcagcagagctacctttctatggaaaaaatcattcaagtggccaagatctct
gccgcacaggctatccatccaggatatggctttctctcagaaaacatggaatttgccgaa
ctgtgtaagcaagaaggaattatttttgtaggtcctccttcatcagcaattagagacatg
ggtataaagagcacatccaaatccatcatggctgctgctggagtgcctgtggtggagggt
tatcacggggaggaccagtcagaccaatgcctgaaagagcacgctaggacaatcggttac
cccgtcatgattaaagccgtccgtggcggaggaggaaaaggtatgaggatcgttagatct
gaaaaagaatttcaagagcagttagaatcagcacggagagaagctaagaagtctttcaat
gatgatgccatgctgattgagaagtttgtggacacaccaaggcatgtagaagtgcaggtg
tttggtgaccaccatggcaatgccgtgtacttgtttgaaagagactgtagtgtacagaga
agacatcagaagatcattgaagaggccccagggcctggtattaaacctgaagtaagaaaa
aagcttggagaagctgcagtcagagctgctaaagctgtaaattatgttggtgcaggaacc
gtggagtttatcatggactcaaagcacaatttctactttatggagatgaatacaaggctg
caagtggaacatcctgtcaccgagatgatcacaggaactgacttggtggaatggcaactt
aggattgcagcaggagagaagattcctttgagccaggaagaaataactctgcggggccat
gcctttgaagctagaatatatgcagaagatcctaacaataacttcatgccgggggccgga
ccactagtgcatctctccacccctcgagcagaccttaccactaggattgaaactggagta
cggcaaggagatgaagtttcaatgcattatgaccccatgattgcaaagctggttgtgtgg
gctgctgatcgccaggcagccttgacgaaacttaagtacagccttcgacagtacaatatt
gttggactgcacaccaacattgacttcctccttagcctgtctggccacccggaatttgaa
gctgggaacgtgcacactgatttcatcgctcaacaccgcaaagaactgttgcccgaccgg
aagaccacagccaaggagtttttatgtcacgcagctctggccctcatcctcaaggagaaa
gctgtgtctgatgtcttcaaaattcagacacaagatcaatactctccttttgcatccagc
agtggaagaagactgaatatctgttactctagaaacatgactcttagggatggtaaaaac
aatgtagccatagctgtaacatataaccgtgatggatcatatagcatgcagattgaagat
aaaactttccatgtccttggtgatctttgcagtgagggagactgcacttatctgaaatct
tctgttaatggagttgctagtaaaattaagctaattatcctgaaaaacactatttaccta
ttttccatggatggaagtattcagattggcattccggttccccgatacttgtcttcagca
agctcaggagaaacccaagggggtgctgtagctcctatgactggaactgttgaaaaggtg
tttgtgaaagctggagacagagtaaaagctggagactctctgatggttatgattgccatg
aaaatggaacataccataaaggcgccaaaggatggcacaatcaagaaggtattctacaaa
gaaggttctcaggccaacagacacgctcctttagtcgagtttgaggaggaagactctgac
gaaagggaagcagattaa

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