Cinclus cinclus (white-throated dipper): 134055991
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Entry
134055991 CDS
T10813
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
ccic Cinclus cinclus (white-throated dipper)
Pathway
ccic00280
Valine, leucine and isoleucine degradation
ccic00640
Propanoate metabolism
ccic00785
Lipoic acid metabolism
ccic01100
Metabolic pathways
ccic01210
2-Oxocarboxylic acid metabolism
Module
ccic_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
ccic00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
134055991 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
134055991 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
134055991 (BCKDHA)
Enzymes [BR:
ccic01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
134055991 (BCKDHA)
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
134055991
NCBI-ProteinID:
XP_062368450
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Position
37:complement(1038814..1045232)
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AA seq
424 aa
AA seq
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MAALRALRWRRLPGLVPRRLLSTAESPEERPQFPGASAEFAERLEFIQPNVLAGIPVYRV
MDRQGQVLRPSEDPQLPKEQVLKLYKTMTLLNTMDRILYESQRQGRISFYMTNYGEEGTH
VGSAAALDASDLVFGQYREAGVLLYRGYPLELFMAQCYGNASDPGKGRQMPVHYGCPERH
FVTISSPLATQIPQAVGAAYAIKRADANRAVVCYFGEGAASEGDAHAGFNFAATLECPIV
FFCRNNGYAISTPTAEQYRGDGIAARGPGYGLLSIRVDGNDVLAVYNATREARRRAVAEN
QPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPISRLRLYLARRGWWDEQQEQA
WRKSSRKMVLEAFEQAEREPKPPPHLLFSDVYLEMPPRLRRQREELERHLETYGEHYPLQ
HFQK
NT seq
1275 nt
NT seq
+upstream
nt +downstream
nt
atggcggcgctgcgggcgctgcggtggcggcggctcccggggctcgtcccgaggcggctc
ctgagcacggccgagtcccccgaggagcggccgcagttcccgggggcctcggccgagttc
gccgagcgcctcgagttcatccagcccaacgtgctggccgggatcccggtgtaccgggtg
atggaccggcagggccaggtgctgcgcccctccgaggacccccagctgcccaaggagcag
gtgctgaagctctacaagaccatgacgctgctcaacaccatggaccggatcctgtacgag
tcccagcgccagggccggatctcattctacatgaccaactacggcgaggaggggacgcac
gtgggcagcgccgctgcccttgacgcctccgacctcgtctttgggcagtaccgtgaggca
ggtgtgctgctgtaccgtggctaccccctggagctgttcatggcccagtgctacggcaac
gccagcgaccccggcaagggccggcagatgccggtgcactacggctgccccgagcgacac
tttgtcaccatctcgtcccccctggccacgcagatcccgcaagccgtgggcgccgcctac
gccatcaagcgtgcggacgcgaaccgagccgtggtttgttattttggggagggggcggcg
agcgagggcgacgcccacgccggcttcaacttcgcggccaccctcgagtgcccgatcgtt
ttcttctgccgcaacaacggctacgccatctccacccccacggccgagcagtaccggggc
gacggcatcgcggcgcggggtcccggctacgggctgctctcgatccgcgtggacggcaac
gacgtcttggccgtgtacaacgccacgcgcgaggctcggcgccgcgccgtggccgagaac
cagcccttcctcatcgaggccatgacctaccggatcggccaccacagcacgagcgacgac
agctcggcgtaccgctcggtggacgaggtgaattactgggacaagcaggatcatcccatc
tcccgcctgcggctctacctggccaggaggggctggtgggacgagcagcaggagcaggcc
tggaggaagagctcccgaaaaatggtgctggaggcgttcgagcaggcggagcgggagccg
aagccgccgcctcacctgctcttctccgacgtttacctggagatgcccccgcggctgcgg
cggcagcgggaggagctggagcgacacctggagacctacggggagcactacccgctccag
cacttccagaagtga
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