Entry |
|
Symbol |
BCKDHB
|
Name |
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X3
|
KO |
K00167 | 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4] |
|
Organism |
cjc Callithrix jacchus (white-tufted-ear marmoset)
|
Pathway |
cjc00280 | Valine, leucine and isoleucine degradation |
cjc01210 | 2-Oxocarboxylic acid metabolism |
|
Module |
cjc_M00036 | Leucine degradation, leucine => acetoacetate + acetyl-CoA |
|
Brite |
KEGG Orthology (KO) [BR:cjc00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
100402568 (BCKDHB)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
100402568 (BCKDHB)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
100402568 (BCKDHB)
Enzymes [BR:cjc01000]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
100402568 (BCKDHB)
|
SSDB |
|
Motif |
|
Other DBs |
|
LinkDB |
|
Position |
4:81696630..81975491
|
AA seq |
392 aa
MAAVGSAASWLFRLRAAGAEGHWRRLCGAGLARGFLHPAATGKDAAQRRQVAHFTFQPDP
EPREYGQTQKMNLFQSITSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRSPWGCVGHGALYHSQSPEAFFAHCPGIKVVIPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAVEQVPVEPYNIPLSQAEVIQEGRDVTLVAWGTQVHVIREVASMAKEKLGVSCE
IIDLRTIIPWDVDTVCKSVIKTGRLLISHEAPLTGGFASEISSTIQEECFLNLEAPISRV
CGYDTPFPHIFEPFYIPDKWKCYDALRKMINY |
NT seq |
1179 nt +upstreamnt +downstreamnt
atggcggctgtgggttcggctgccagctggctgttcaggctcagggcggcaggggctgag
gggcactggcgtcggctctgtggcgcgggcctggcgcggggctttctgcaccccgccgcg
actggcaaggatgcggctcagaggcggcaggtggctcatttcactttccagccggacccg
gagccccgggagtacgggcaaactcagaaaatgaatcttttccagtcaataacaagtgct
ttggataactcactggccaaagatcctactgcagtaatatttggtgaagatgttgccttt
ggtggagtctttagatgcactgttggcttgcgagacaaatatggaaaagatagagttttt
aataccccgttgtgtgaacaaggaatcgttggattcggaattggaattgcagtcactgga
gctactgccattgcagaaattcagtttgcagattatattttccctgcatttgatcagatt
gttaatgaagctgccaagtatcgctatcgctctggggatctgtttaactgtggaagcctc
actatccggtctccttggggctgtgttggccatggggctctgtaccattctcagagtcct
gaagcattttttgcccattgtccaggaatcaaggtggttatacccagaagccctttccag
gccaaaggacttcttttgtcatgcatagaggataaaaatccttgtatattttttgaacct
aaaatactttacagggcagcagttgaacaggttcctgtagaaccgtacaacatcccactg
tcccaggccgaagtcatacaggaagggagagatgttactctagttgcctggggcactcag
gttcatgtaattcgggaggtagcttccatggcaaaagaaaagcttggagtgtcttgtgaa
attattgatctgaggactataataccttgggatgtggacacagtttgtaagtctgtgatc
aaaacagggcgactgctaatcagtcatgaggctcccctgacaggtggctttgcatcggag
atcagctctacaattcaggaggaatgtttcttgaacttagaggctcctatatcaagagta
tgtggttatgacacaccatttcctcacatttttgaaccattctacatcccagacaaatgg
aagtgttatgatgcccttcgaaaaatgatcaactattga |