KEGG   Callithrix jacchus (white-tufted-ear marmoset): 100407780
Entry
100407780         CDS       T03264                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
cjc  Callithrix jacchus (white-tufted-ear marmoset)
Pathway
cjc00280  Valine, leucine and isoleucine degradation
cjc00640  Propanoate metabolism
cjc00785  Lipoic acid metabolism
cjc01100  Metabolic pathways
cjc01210  2-Oxocarboxylic acid metabolism
Module
cjc_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:cjc00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    100407780 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    100407780 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    100407780 (BCKDHA)
Enzymes [BR:cjc01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     100407780 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 100407780
NCBI-ProteinID: XP_008986318
Ensembl: ENSCJAG00000020155
UniProt: U3DKQ5
LinkDB
Position
22:35250382..35281011
AA seq 447 aa
MAVAIAAARVWRQSRILGQAALLLLLRRPGARGLAISHPHRQQEQQFSSLDDKPQFPGAS
AEFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEKVLKFYKSMTLLNTMDRI
LYESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQC
YGNVSDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGE
GAASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRV
DGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQD
HPISRLRHYLLSQGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPS
QLRKQQESLARHLQTYGEHYPLEHFDK
NT seq 1344 nt   +upstreamnt  +downstreamnt
atggcggtagcaatcgctgcggcgagggtttggaggcaaagccgaatcctgggccaggct
gccctcctcctgctgctgcggcggcctggggctcggggactggctatatctcacccccac
aggcagcaggagcagcagttctcatctctggatgacaagccccagttcccaggggcctcg
gcagagtttatagacaagctcgaattcatccagcccaatgtcatctctggaatccccatc
taccgcgtcatggaccggcaaggccagatcatcaaccccagcgaggacccccatctgccg
aaggagaaggtgctgaagttctacaagagcatgacactgcttaacaccatggaccgcatc
ctctatgagtctcagcggcagggccggatctccttctacatgaccaactatggcgaggag
ggcacacacgtggggagtgccgccgccctggacaacacggacctggtgtttggccagtac
cgggaggcaggtgtgctgatgtatcgggactaccccctagaactattcatggcccagtgc
tatggcaacgtcagtgacttgggcaaggggcgccagatgcccgtccactacggctgcaag
gagcgtcacttcgtcactatctcctctccactggccacacagatccctcaggcggtaggg
gcggcctatgcagccaagcgggccaacgccaacagggtcgtcatctgttacttcggcgag
ggggcggccagtgagggggatgcccacgctggcttcaactttgctgccacactcgagtgc
cccatcatcttcttctgccggaacaatggctatgccatctccacacccacctccgagcag
taccgtggcgatggcattgcagcacgaggccccgggtatggcatcctgtcaatccgtgtg
gatggcaatgatgtgtttgctgtgtacaacgccacaaaggaggcccgacggcgggctgtg
gcagagaaccagcccttcctcatcgaggccatgacctacaggatcgggcaccacagcacc
agtgacgacagctcggcataccgctcggtggacgaggtcaattactgggacaagcaggac
caccccatctcccggctgcggcactacctgctgagccaaggctggtgggatgaggagcag
gagaaggcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggctgag
cggaaacccaagcccaaccccaacctgctcttctcagacgtttatcaggagatgcccagc
cagctccgcaagcagcaggagtccctggcccgccacctgcagacctacggggaacactac
ccactggagcacttcgataagtga

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