Callithrix jacchus (white-tufted-ear marmoset): 100407780
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Entry
100407780 CDS
T03264
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
cjc
Callithrix jacchus (white-tufted-ear marmoset)
Pathway
cjc00280
Valine, leucine and isoleucine degradation
cjc00640
Propanoate metabolism
cjc00785
Lipoic acid metabolism
cjc01100
Metabolic pathways
cjc01210
2-Oxocarboxylic acid metabolism
Module
cjc_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
cjc00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
100407780 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
100407780 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
100407780 (BCKDHA)
Enzymes [BR:
cjc01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
100407780 (BCKDHA)
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
100407780
NCBI-ProteinID:
XP_008986318
Ensembl:
ENSCJAG00000020155
UniProt:
U3DKQ5
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Position
22:35250382..35281011
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AA seq
447 aa
AA seq
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MAVAIAAARVWRQSRILGQAALLLLLRRPGARGLAISHPHRQQEQQFSSLDDKPQFPGAS
AEFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEKVLKFYKSMTLLNTMDRI
LYESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQC
YGNVSDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGE
GAASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRV
DGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQD
HPISRLRHYLLSQGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPS
QLRKQQESLARHLQTYGEHYPLEHFDK
NT seq
1344 nt
NT seq
+upstream
nt +downstream
nt
atggcggtagcaatcgctgcggcgagggtttggaggcaaagccgaatcctgggccaggct
gccctcctcctgctgctgcggcggcctggggctcggggactggctatatctcacccccac
aggcagcaggagcagcagttctcatctctggatgacaagccccagttcccaggggcctcg
gcagagtttatagacaagctcgaattcatccagcccaatgtcatctctggaatccccatc
taccgcgtcatggaccggcaaggccagatcatcaaccccagcgaggacccccatctgccg
aaggagaaggtgctgaagttctacaagagcatgacactgcttaacaccatggaccgcatc
ctctatgagtctcagcggcagggccggatctccttctacatgaccaactatggcgaggag
ggcacacacgtggggagtgccgccgccctggacaacacggacctggtgtttggccagtac
cgggaggcaggtgtgctgatgtatcgggactaccccctagaactattcatggcccagtgc
tatggcaacgtcagtgacttgggcaaggggcgccagatgcccgtccactacggctgcaag
gagcgtcacttcgtcactatctcctctccactggccacacagatccctcaggcggtaggg
gcggcctatgcagccaagcgggccaacgccaacagggtcgtcatctgttacttcggcgag
ggggcggccagtgagggggatgcccacgctggcttcaactttgctgccacactcgagtgc
cccatcatcttcttctgccggaacaatggctatgccatctccacacccacctccgagcag
taccgtggcgatggcattgcagcacgaggccccgggtatggcatcctgtcaatccgtgtg
gatggcaatgatgtgtttgctgtgtacaacgccacaaaggaggcccgacggcgggctgtg
gcagagaaccagcccttcctcatcgaggccatgacctacaggatcgggcaccacagcacc
agtgacgacagctcggcataccgctcggtggacgaggtcaattactgggacaagcaggac
caccccatctcccggctgcggcactacctgctgagccaaggctggtgggatgaggagcag
gagaaggcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggctgag
cggaaacccaagcccaaccccaacctgctcttctcagacgtttatcaggagatgcccagc
cagctccgcaagcagcaggagtccctggcccgccacctgcagacctacggggaacactac
ccactggagcacttcgataagtga
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